| Protein | Synonyms | Taxonomy |
|---|
| Arylsulfatase A | ASA; EC 3.1.6.8; Cerebroside-sulfatase | Homo sapiens (human) |
| Lysosomal acid glucosylceramidase | Lysosomal acid GCase; EC 3.2.1.45; Acid beta-glucosidase; Alglucerase; Beta-glucocerebrosidase; Beta-GC; Cholesterol glucosyltransferase; SGTase; 2.4.1.-; Cholesteryl-beta-glucosidase; 3.2.1.-; D-glucosyl-N-acylsphingosine glucohydrolase; Imiglucerase | Homo sapiens (human) |
| Beta-galactosidase | EC 3.2.1.23; Acid beta-galactosidase; Lactase; Elastin receptor 1 | Homo sapiens (human) |
| 2-hydroxyacylsphingosine 1-beta-galactosyltransferase | EC 2.4.1.47; Ceramide UDP-galactosyltransferase; Cerebroside synthase; UDP-galactose-ceramide galactosyltransferase | Homo sapiens (human) |
| Serine palmitoyltransferase 1 | EC 2.3.1.50; Long chain base biosynthesis protein 1; LCB 1; Serine-palmitoyl-CoA transferase 1; SPT 1; SPT1 | Homo sapiens (human) |
| Serine palmitoyltransferase 2 | EC 2.3.1.50; Long chain base biosynthesis protein 2; LCB 2; Long chain base biosynthesis protein 2a; LCB2a; Serine-palmitoyl-CoA transferase 2; SPT 2 | Homo sapiens (human) |
| Ceramide kinase | hCERK; EC 2.7.1.138; Acylsphingosine kinase; Lipid kinase 4; LK4 | Homo sapiens (human) |
| Alpha-galactosidase A | EC 3.2.1.22; Alpha-D-galactosidase A; Alpha-D-galactoside galactohydrolase; Galactosylgalactosylglucosylceramidase GLA; 3.2.1.47; Melibiase | Homo sapiens (human) |
| Sialidase-3 | EC 3.2.1.18; Ganglioside sialidasedis; Membrane sialidase; N-acetyl-alpha-neuraminidase 3 | Homo sapiens (human) |
| Ceramide glucosyltransferase | EC 2.4.1.80; GLCT-1; Glucosylceramide synthase; GCS; UDP-glucose ceramide glucosyltransferase; UDP-glucose:N-acylsphingosine D-glucosyltransferase | Homo sapiens (human) |
| Sphingosine kinase 2 | SK 2; SPK 2; EC 2.7.1.91 | Homo sapiens (human) |
| Sphingosine-1-phosphate lyase 1 | S1PL; SP-lyase 1; SPL 1; hSPL; EC 4.1.2.27; Sphingosine-1-phosphate aldolase | Homo sapiens (human) |
| Sphingosine-1-phosphate phosphatase 2 | SPPase2; Spp2; hSPP2; EC 3.1.3.-; Sphingosine-1-phosphatase 2 | Homo sapiens (human) |
| 3-ketodihydrosphingosine reductase | KDS reductase; EC 1.1.1.102; 3-dehydrosphinganine reductase; Follicular variant translocation protein 1; FVT-1; Short chain dehydrogenase/reductase family 35C member 1 | Homo sapiens (human) |
| Alkaline ceramidase 1 | AlkCDase 1; Alkaline CDase 1; EC 3.5.1.-; EC 3.5.1.23; Acylsphingosine deacylase 3; N-acylsphingosine amidohydrolase 3 | Homo sapiens (human) |
| Phosphatidylcholine:ceramide cholinephosphotransferase 1 | EC 2.7.8.27; Medulla oblongata-derived protein; Protein Mob; Sphingomyelin synthase 1; Transmembrane protein 23 | Homo sapiens (human) |
| Ectonucleotide pyrophosphatase/phosphodiesterase family member 7 | E-NPP 7; NPP-7; EC 3.1.4.12; Alkaline sphingomyelin phosphodiesterase; Intestinal alkaline sphingomyelinase; Alk-SMase | Homo sapiens (human) |
| Galactocerebrosidase | GALCERase; EC 3.2.1.46; Galactocerebroside beta-galactosidase; Galactosylceramidase; Galactosylceramide beta-galactosidase | Homo sapiens (human) |
| Galactosylceramide sulfotransferase | GalCer sulfotransferase; EC 2.8.2.11; 3'-phosphoadenosine-5'-phosphosulfate:GalCer sulfotransferase; 3'-phosphoadenylylsulfate:galactosylceramide 3'-sulfotransferase; Cerebroside sulfotransferase | Homo sapiens (human) |
| Phospholipid phosphatase 1 | EC 3.1.3.-; EC 3.1.3.106; EC 3.1.3.4; EC 3.1.3.81; Lipid phosphate phosphohydrolase 1; PAP2-alpha; Phosphatidate phosphohydrolase type 2a; Phosphatidic acid phosphatase 2a; PAP-2a; PAP2a | Homo sapiens (human) |
| Sphingolipid delta(4)-desaturase/C4-monooxygenase DES2 | EC 1.14.18.5; EC 1.14.19.17; Degenerative spermatocyte homolog 2; Sphingolipid 4-desaturase; Sphingolipid C4-monooxygenase | Homo sapiens (human) |
| Alkaline ceramidase 3 | AlkCDase 3; Alkaline CDase 3; EC 3.5.1.-; EC 3.5.1.23; Alkaline dihydroceramidase SB89; Alkaline phytoceramidase; aPHC | Homo sapiens (human) |
| Beta-1,4-galactosyltransferase 6 | Beta-1,4-GalTase 6; Beta4Gal-T6; b4Gal-T6; EC 2.4.1.-; Glucosylceramide beta-1,4-galactosyltransferase; 2.4.1.274; Lactosylceramide synthase; LacCer synthase; UDP-Gal:beta-GlcNAc beta-1,4-galactosyltransferase 6; UDP-Gal:glucosylceramide beta-1,4-galactos | Homo sapiens (human) |
| Compound | Description |
|---|
| phosphorylcholine | Calcium and magnesium salts used therapeutically in hepatobiliary dysfunction. |
| Orthophosphate | |
| Carbon Dioxide | A colorless, odorless gas that can be formed by the body and is necessary for the respiration cycle of plants and animals. |
| galactose | An aldohexose that occurs naturally in the D-form in lactose, cerebrosides, gangliosides, and mucoproteins. Deficiency of galactosyl-1-phosphate uridyltransferase (GALACTOSE-1-PHOSPHATE URIDYL-TRANSFERASE DEFICIENCY DISEASE) causes an error in galactose metabolism called GALACTOSEMIA, resulting in elevations of galactose in the blood. |
| Glucose | A primary source of energy for living organisms. It is naturally occurring and is found in fruits and other parts of plants in its free state. It is used therapeutically in fluid and nutrient replacement. |
| Adenosine Triphosphate | An adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter. |
| adenosine diphosphate | Adenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position. |
| uridine diphosphate | A uracil nucleotide containing a pyrophosphate group esterified to C5 of the sugar moiety. |
| Water | A clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed) |
| Palmitoyl Coenzyme A | A fatty acid coenzyme derivative which plays a key role in fatty acid oxidation and biosynthesis. |
| phosphorylethanolamine | RN given refers to parent cpd; structure |
| adenosine 3'-phosphate-5'-phosphate | |
| ketodihydrosphingosine | RN given refers to cpd without isomeric designation |
| sphingosine 1-phosphate | RN given refers to (R-(R*,S*-(E)))-isomer; RN for cpd without isomeric designation not available 8/89 |
| ceramide 1-phosphate | |
| erythro-(2R,3S)-sphingosine | structure in first source |
| serine | A non-essential amino acid occurring in natural form as the L-isomer. It is synthesized from GLYCINE or THREONINE. It is involved in the biosynthesis of PURINES; PYRIMIDINES; and other amino acids. |
| hexadecanal | |
| phosphoadenosine phosphosulfate | 3'-Phosphoadenosine-5'-phosphosulfate. Key intermediate in the formation by living cells of sulfate esters of phenols, alcohols, steroids, sulfated polysaccharides, and simple esters, such as choline sulfate. It is formed from sulfate ion and ATP in a two-step process. This compound also is an important step in the process of sulfur fixation in plants and microorganisms. |
| Phosphatidylcholines | Derivatives of PHOSPHATIDIC ACIDS in which the phosphoric acid is bound in ester linkage to a CHOLINE moiety. |
| creolin | from refined coal tar oils |
| dihydrosphingosine 1-phosphate | RN given refers to (R-(R*,S*))-isomer |
| mephentermine | A sympathomimetic agent with specificity for alpha-1 adrenergic receptors. It is used to maintain BLOOD PRESSURE in hypotensive states such as following SPINAL ANESTHESIA. |
| dihydroceramide | lacks the 4-5 trans double bond of the sphingosine moiety of ceramides; structure in first source |