Pathways > Tyrosine metabolism and related disorders
Page last updated: 2024-10-06
Tyrosine metabolism and related disorders
Proteins (6)
| Protein | Synonyms | Taxonomy |
|---|
| Tyrosine aminotransferase | TAT; EC 2.6.1.5; L-tyrosine:2-oxoglutarate aminotransferase | Homo sapiens (human) |
| 4-hydroxyphenylpyruvate dioxygenase | EC 1.13.11.27; 4-hydroxyphenylpyruvic acid oxidase; 4HPPD; HPD; HPPDase | Homo sapiens (human) |
| 4-hydroxyphenylpyruvate dioxygenase | | Homo sapiens (human) |
| Homogentisate 1,2-dioxygenase | EC 1.13.11.5; Homogentisate oxygenase; Homogentisic acid oxidase; Homogentisicase | Homo sapiens (human) |
| Fumarylacetoacetase | FAA; EC 3.7.1.2; Beta-diketonase; Fumarylacetoacetate hydrolase | Homo sapiens (human) |
| Phenylalanine ammonia lyase | | Rhodotorula glutinis |
Compounds (20)
| Compound | Description |
|---|
| nitisinone | used in treatment of hereditary tyrosinaemia type I |
| sapropterin | RN given refers to parent cpd; co-factor required for catalytic activity of nitric oxide synthases |
| aminolevulinic acid | A compound produced from succinyl-CoA and GLYCINE as an intermediate in heme synthesis. It is used as a PHOTOCHEMOTHERAPY for actinic KERATOSIS. |
| ammonium hydroxide | The hydroxy salt of ammonium ion. It is formed when AMMONIA reacts with water molecules in solution. |
| Carbon Dioxide | A colorless, odorless gas that can be formed by the body and is necessary for the respiration cycle of plants and animals. |
| hydrogen sulfide | A flammable, poisonous gas with a characteristic odor of rotten eggs. It is used in the manufacture of chemicals, in metallurgy, and as an analytical reagent. (From Merck Index, 11th ed) |
| fumarates | Compounds based on fumaric acid. |
| phenylalanine | An essential aromatic amino acid that is a precursor of MELANIN; DOPAMINE; noradrenalin (NOREPINEPHRINE), and THYROXINE. |
| 4-hydroxyphenylacetate | |
| 4a-hydroxytetrahydrobiopterin | structure given in first source |
| porphobilinogen | |
| succinylacetoacetate | |
| 4-hydroxyphenylacetic acid | |
| fumarylacetoacetate | metabolite of tyrosine; RN given for (E)-isomer; structure in first source |
| succinylacetone | inhibitor of heme biosynthesis |
| acetoacetate | |
| 4-hydroxyphenylpyruvate | |
| Cefsulodin | A pyridinium-substituted semisynthetic, broad-spectrum antibacterial used especially for Pseudomonas infections in debilitated patients. |
| hawkinsin | structure |
| e-z cinnamic acid | |