Page last updated: 2024-10-06
Fructosuria
Proteins (18)
| Protein | Synonyms | Taxonomy |
|---|---|---|
| Fructose-bisphosphate aldolase A | EC 4.1.2.13; Lung cancer antigen NY-LU-1; Muscle-type aldolase | Homo sapiens (human) |
| Mannose-6-phosphate isomerase | EC 5.3.1.8; Phosphohexomutase; Phosphomannose isomerase; PMI | Homo sapiens (human) |
| Aldo-keto reductase family 1 member B1 | EC 1.1.1.300; EC 1.1.1.372; EC 1.1.1.54; Aldehyde reductase; Aldose reductase; AR; 1.1.1.21 | Homo sapiens (human) |
| 14 kDa phosphohistidine phosphatase | EC 3.9.1.3; Phosphohistidine phosphatase 1; PHPT1; Protein histidine phosphatase; PHP; Protein janus-A homolog | Homo sapiens (human) |
| ATP-dependent 6-phosphofructokinase, liver type | ATP-PFK; PFK-L; EC 2.7.1.11; 6-phosphofructokinase type B; Phosphofructo-1-kinase isozyme B; PFK-B; Phosphohexokinase | Homo sapiens (human) |
| Fructose-1,6-bisphosphatase 1 | FBPase 1; EC 3.1.3.11; D-fructose-1,6-bisphosphate 1-phosphohydrolase 1; Liver FBPase | Homo sapiens (human) |
| Triosephosphate isomerase | TIM; EC 5.3.1.1; Methylglyoxal synthase; 4.2.3.3; Triose-phosphate isomerase | Homo sapiens (human) |
| Sorbitol dehydrogenase | SDH; EC 1.1.1.-; (R,R)-butanediol dehydrogenase; 1.1.1.4; L-iditol 2-dehydrogenase; 1.1.1.14; Polyol dehydrogenase; Ribitol dehydrogenase; RDH; 1.1.1.56; Xylitol dehydrogenase; XDH; 1.1.1.9 | Homo sapiens (human) |
| Ketohexokinase | EC 2.7.1.3; Hepatic fructokinase | Homo sapiens (human) |
| Hexokinase-1 | EC 2.7.1.1; Brain form hexokinase; Hexokinase type I; HK I; Hexokinase-A | Homo sapiens (human) |
| Fructose-bisphosphate aldolase B | EC 4.1.2.13; Liver-type aldolase | Homo sapiens (human) |
| GDP-mannose 4,6 dehydratase | EC 4.2.1.47; GDP-D-mannose dehydratase; GMD | Homo sapiens (human) |
| 6-phosphofructo-2-kinase/fructose-2,6-bisphosphatase 1 | 6PF-2-K/Fru-2,6-P2ase 1; PFK/FBPase 1; 6PF-2-K/Fru-2,6-P2ase liver isozyme | Homo sapiens (human) |
| Fucose-1-phosphate guanylyltransferase | EC 2.7.7.30; GDP-L-fucose diphosphorylase; GDP-L-fucose pyrophosphorylase | Homo sapiens (human) |
| L-fucose kinase | Fucokinase; EC 2.7.1.52 | Homo sapiens (human) |
| GDP-L-fucose synthase | EC 1.1.1.271; GDP-4-keto-6-deoxy-D-mannose-3,5-epimerase-4-reductase; Protein FX; Red cell NADP(H)-binding protein; Short-chain dehydrogenase/reductase family 4E member 1 | Homo sapiens (human) |
| Phosphomannomutase 1 | PMM 1; EC 5.4.2.8; PMMH-22 | Homo sapiens (human) |
| Mannose-1-phosphate guanyltransferase beta | EC 2.7.7.13; GDP-mannose pyrophosphorylase B; GTP-mannose-1-phosphate guanylyltransferase beta | Homo sapiens (human) |
Compounds (22)
| Compound | Description |
|---|---|
| phosphoric acid | concise etchant is 37% H3PO4 |
| Orthophosphate | |
| NADH | |
| sorbitol | A polyhydric alcohol with about half the sweetness of sucrose. Sorbitol occurs naturally and is also produced synthetically from glucose. It was formerly used as a diuretic and may still be used as a laxative and in irrigating solutions for some surgical procedures. It is also used in many manufacturing processes, as a pharmaceutical aid, and in several research applications. |
| Adenosine Triphosphate | An adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter. |
| adenosine diphosphate | Adenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position. |
| Water | A clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed) |
| fucose | A six-member ring deoxysugar with the chemical formula C6H12O5. It lacks a hydroxyl group on the carbon at position 6 of the molecule. |
| mannose | A hexose or fermentable monosaccharide and isomer of glucose from manna, the ash Fraxinus ornus and related plants. (From Grant & Hackh's Chemical Dictionary, 5th ed & Random House Unabridged Dictionary, 2d ed) |
| mannose-6-phosphate | RN given refers to (D)-isomer |
| fuculose 1-phosphate | |
| NAD | A coenzyme composed of ribosylnicotinamide 5'-diphosphate coupled to adenosine 5'-phosphate by pyrophosphate linkage. It is found widely in nature and is involved in numerous enzymatic reactions in which it serves as an electron carrier by being alternately oxidized (NAD+) and reduced (NADH). (Dorland, 27th ed) |
| mannose 1-phosphate | |
| dihydroxyacetone phosphate | An important intermediate in lipid biosynthesis and in glycolysis. |
| fructose-6-phosphate | RN given refers to parent cpd with unspecified isomeric designation |
| Glyceraldehyde 3-Phosphate | An aldotriose which is an important intermediate in glycolysis and in tryptophan biosynthesis. |
| glyceraldehyde | An aldotriose containing the propionaldehyde structure with hydroxy groups at the 2- and 3-positions. It is involved in the formation of ADVANCED GLYCOSYLATION END PRODUCTS. |
| fructose 2,6-diphosphate | phosphofructokinase activator synthesized via Mg-ATP & fructose-6-P |
| fructose-2-phosphate | intermediate of the dephosphorylation of fructose 2,6-bisphosphate with a yeast enzyme |
| creolin | from refined coal tar oils |
| pyrophosphate | |
| glucose | A primary source of energy for living organisms. It is naturally occurring and is found in fruits and other parts of plants in its free state. It is used therapeutically in fluid and nutrient replacement. |