Page last updated: 2024-10-06

Fructosuria

Proteins (18)

ProteinSynonymsTaxonomy
Fructose-bisphosphate aldolase AEC 4.1.2.13; Lung cancer antigen NY-LU-1; Muscle-type aldolaseHomo sapiens (human)
Mannose-6-phosphate isomeraseEC 5.3.1.8; Phosphohexomutase; Phosphomannose isomerase; PMIHomo sapiens (human)
Aldo-keto reductase family 1 member B1EC 1.1.1.300; EC 1.1.1.372; EC 1.1.1.54; Aldehyde reductase; Aldose reductase; AR; 1.1.1.21Homo sapiens (human)
14 kDa phosphohistidine phosphataseEC 3.9.1.3; Phosphohistidine phosphatase 1; PHPT1; Protein histidine phosphatase; PHP; Protein janus-A homologHomo sapiens (human)
ATP-dependent 6-phosphofructokinase, liver typeATP-PFK; PFK-L; EC 2.7.1.11; 6-phosphofructokinase type B; Phosphofructo-1-kinase isozyme B; PFK-B; PhosphohexokinaseHomo sapiens (human)
Fructose-1,6-bisphosphatase 1FBPase 1; EC 3.1.3.11; D-fructose-1,6-bisphosphate 1-phosphohydrolase 1; Liver FBPaseHomo sapiens (human)
Triosephosphate isomeraseTIM; EC 5.3.1.1; Methylglyoxal synthase; 4.2.3.3; Triose-phosphate isomeraseHomo sapiens (human)
Sorbitol dehydrogenaseSDH; EC 1.1.1.-; (R,R)-butanediol dehydrogenase; 1.1.1.4; L-iditol 2-dehydrogenase; 1.1.1.14; Polyol dehydrogenase; Ribitol dehydrogenase; RDH; 1.1.1.56; Xylitol dehydrogenase; XDH; 1.1.1.9Homo sapiens (human)
KetohexokinaseEC 2.7.1.3; Hepatic fructokinaseHomo sapiens (human)
Hexokinase-1EC 2.7.1.1; Brain form hexokinase; Hexokinase type I; HK I; Hexokinase-AHomo sapiens (human)
Fructose-bisphosphate aldolase BEC 4.1.2.13; Liver-type aldolaseHomo sapiens (human)
GDP-mannose 4,6 dehydrataseEC 4.2.1.47; GDP-D-mannose dehydratase; GMDHomo sapiens (human)
6-phosphofructo-2-kinase/fructose-2,6-bisphosphatase 16PF-2-K/Fru-2,6-P2ase 1; PFK/FBPase 1; 6PF-2-K/Fru-2,6-P2ase liver isozymeHomo sapiens (human)
Fucose-1-phosphate guanylyltransferaseEC 2.7.7.30; GDP-L-fucose diphosphorylase; GDP-L-fucose pyrophosphorylaseHomo sapiens (human)
L-fucose kinaseFucokinase; EC 2.7.1.52Homo sapiens (human)
GDP-L-fucose synthaseEC 1.1.1.271; GDP-4-keto-6-deoxy-D-mannose-3,5-epimerase-4-reductase; Protein FX; Red cell NADP(H)-binding protein; Short-chain dehydrogenase/reductase family 4E member 1Homo sapiens (human)
Phosphomannomutase 1PMM 1; EC 5.4.2.8; PMMH-22Homo sapiens (human)
Mannose-1-phosphate guanyltransferase betaEC 2.7.7.13; GDP-mannose pyrophosphorylase B; GTP-mannose-1-phosphate guanylyltransferase betaHomo sapiens (human)

Compounds (22)

CompoundDescription
phosphoric acidconcise etchant is 37% H3PO4
Orthophosphate
NADH
sorbitolA polyhydric alcohol with about half the sweetness of sucrose. Sorbitol occurs naturally and is also produced synthetically from glucose. It was formerly used as a diuretic and may still be used as a laxative and in irrigating solutions for some surgical procedures. It is also used in many manufacturing processes, as a pharmaceutical aid, and in several research applications.
Adenosine TriphosphateAn adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter.
adenosine diphosphateAdenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position.
WaterA clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed)
fucoseA six-member ring deoxysugar with the chemical formula C6H12O5. It lacks a hydroxyl group on the carbon at position 6 of the molecule.
mannoseA hexose or fermentable monosaccharide and isomer of glucose from manna, the ash Fraxinus ornus and related plants. (From Grant & Hackh's Chemical Dictionary, 5th ed & Random House Unabridged Dictionary, 2d ed)
mannose-6-phosphateRN given refers to (D)-isomer
fuculose 1-phosphate
NADA coenzyme composed of ribosylnicotinamide 5'-diphosphate coupled to adenosine 5'-phosphate by pyrophosphate linkage. It is found widely in nature and is involved in numerous enzymatic reactions in which it serves as an electron carrier by being alternately oxidized (NAD+) and reduced (NADH). (Dorland, 27th ed)
mannose 1-phosphate
dihydroxyacetone phosphateAn important intermediate in lipid biosynthesis and in glycolysis.
fructose-6-phosphateRN given refers to parent cpd with unspecified isomeric designation
Glyceraldehyde 3-PhosphateAn aldotriose which is an important intermediate in glycolysis and in tryptophan biosynthesis.
glyceraldehydeAn aldotriose containing the propionaldehyde structure with hydroxy groups at the 2- and 3-positions. It is involved in the formation of ADVANCED GLYCOSYLATION END PRODUCTS.
fructose 2,6-diphosphatephosphofructokinase activator synthesized via Mg-ATP & fructose-6-P
fructose-2-phosphateintermediate of the dephosphorylation of fructose 2,6-bisphosphate with a yeast enzyme
creolinfrom refined coal tar oils
pyrophosphate
glucoseA primary source of energy for living organisms. It is naturally occurring and is found in fruits and other parts of plants in its free state. It is used therapeutically in fluid and nutrient replacement.