| Protein | Synonyms | Taxonomy |
|---|
| Glutaminase liver isoform, mitochondrial | GLS; EC 3.5.1.2; L-glutaminase; L-glutamine amidohydrolase | Homo sapiens (human) |
| Alanine aminotransferase 1 | ALT1; EC 2.6.1.2; Glutamate pyruvate transaminase 1; GPT 1; Glutamic--alanine transaminase 1; Glutamic--pyruvic transaminase 1 | Homo sapiens (human) |
| Coagulation factor X | EC 3.4.21.6; Stuart factor; Stuart-Prower factor | Homo sapiens (human) |
| Coagulation factor VII | EC 3.4.21.21; Proconvertin; Serum prothrombin conversion accelerator; SPCA | Homo sapiens (human) |
| Aspartate aminotransferase, cytoplasmic | cAspAT; EC 2.6.1.1; EC 2.6.1.3; Cysteine aminotransferase, cytoplasmic; Cysteine transaminase, cytoplasmic; cCAT; Glutamate oxaloacetate transaminase 1; Transaminase A | Homo sapiens (human) |
| Guanidinoacetate N-methyltransferase | EC 2.1.1.2 | Homo sapiens (human) |
| Arginase-1 | EC 3.5.3.1; Liver-type arginase; Type I arginase | Homo sapiens (human) |
| Ornithine transcarbamylase, mitochondrial | OTCase; EC 2.1.3.3; Ornithine carbamoyltransferase, mitochondrial | Homo sapiens (human) |
| Argininosuccinate synthase | EC 6.3.4.5; Citrulline--aspartate ligase | Homo sapiens (human) |
| N-acetylglutamate synthase, mitochondrial | EC 2.3.1.1; Amino-acid acetyltransferase | Homo sapiens (human) |
| Argininosuccinate lyase | ASAL; EC 4.3.2.1; Arginosuccinase | Homo sapiens (human) |
| Glycine amidinotransferase, mitochondrial | EC 2.1.4.1; L-arginine:glycine amidinotransferase; Transamidinase | Homo sapiens (human) |
| Compound | Description |
|---|
| urea | A compound formed in the liver from ammonia produced by the deamination of amino acids. It is the principal end product of protein catabolism and constitutes about one half of the total urinary solids. |
| Arginine | An essential amino acid that is physiologically active in the L-form. |
| Ammonium | |
| galactose | An aldohexose that occurs naturally in the D-form in lactose, cerebrosides, gangliosides, and mucoproteins. Deficiency of galactosyl-1-phosphate uridyltransferase (GALACTOSE-1-PHOSPHATE URIDYL-TRANSFERASE DEFICIENCY DISEASE) causes an error in galactose metabolism called GALACTOSEMIA, resulting in elevations of galactose in the blood. |
| Aspartate | |
| fumarates | Compounds based on fumaric acid. |
| tyrosine | A non-essential amino acid. In animals it is synthesized from PHENYLALANINE. It is also the precursor of EPINEPHRINE; THYROID HORMONES; and melanin. |
| methionine | A sulfur-containing essential L-amino acid that is important in many body functions. |
| threonine | An essential amino acid occurring naturally in the L-form, which is the active form. It is found in eggs, milk, gelatin, and other proteins. |
| Carbamyl Phosphate | The monoanhydride of carbamic acid with PHOSPHORIC ACID. It is an important intermediate metabolite and is synthesized enzymatically by CARBAMYL-PHOSPHATE SYNTHASE (AMMONIA) and CARBAMOYL-PHOSPHATE SYNTHASE (GLUTAMINE-HYDROLYZING). |
| glutamate | |
| polyglutamine | RN given for (D)-isomer |
| orotic acid | An intermediate product in PYRIMIDINE synthesis which plays a role in chemical conversions between DIHYDROFOLATE and TETRAHYDROFOLATE. |