| Protein | Synonyms | Taxonomy |
|---|
| Lysosomal protective protein | EC 3.4.16.5; Carboxypeptidase C; Carboxypeptidase L; Cathepsin A; Protective protein cathepsin A; PPCA; Protective protein for beta-galactosidase | Homo sapiens (human) |
| Beta-galactosidase | EC 3.2.1.23; Acid beta-galactosidase; Lactase; Elastin receptor 1 | Homo sapiens (human) |
| Beta-hexosaminidase subunit alpha | EC 3.2.1.52; Beta-N-acetylhexosaminidase subunit alpha; Hexosaminidase subunit A; N-acetyl-beta-glucosaminidase subunit alpha | Homo sapiens (human) |
| Dystroglycan | Dystrophin-associated glycoprotein 1 | Homo sapiens (human) |
| UDP-glucose 4-epimerase | EC 5.1.3.2; Galactowaldenase; UDP-N-acetylgalactosamine 4-epimerase; UDP-GalNAc 4-epimerase; UDP-N-acetylglucosamine 4-epimerase; UDP-GlcNAc 4-epimerase; 5.1.3.7; UDP-galactose 4-epimerase | Homo sapiens (human) |
| Glycoprotein-N-acetylgalactosamine 3-beta-galactosyltransferase 1 | EC 2.4.1.122; B3Gal-T8; Core 1 O-glycan T-synthase; Core 1 UDP-galactose:N-acetylgalactosamine-alpha-R beta 1,3-galactosyltransferase 1; Beta-1,3-galactosyltransferase; Core 1 beta1,3-galactosyltransferase 1; C1GalT1; Core 1 beta3-Gal-T1 | Homo sapiens (human) |
| Beta-1,4-glucuronyltransferase 1 | EC 2.4.1.-; I-beta-1,3-N-acetylglucosaminyltransferase; iGnT; N-acetyllactosaminide beta-1,3-N-acetylglucosaminyltransferase; Poly-N-acetyllactosamine extension enzyme; UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 1 | Homo sapiens (human) |
| Dehydrodolichyl diphosphate synthase complex subunit NUS1 | EC 2.5.1.87; Cis-prenyltransferase subunit NgBR; Nogo-B receptor; NgBR; Nuclear undecaprenyl pyrophosphate synthase 1 homolog | Homo sapiens (human) |
| Beta-1,4-galactosyltransferase 1 | Beta-1,4-GalTase 1; Beta4Gal-T1; b4Gal-T1; EC 2.4.1.-; Beta-N-acetylglucosaminyl-glycolipid beta-1,4-galactosyltransferase; Beta-N-acetylglucosaminylglycopeptide beta-1,4-galactosyltransferase; 2.4.1.38; Lactose synthase A protein; 2.4.1.22; N-acetyllacto | Homo sapiens (human) |
| Dehydrodolichyl diphosphate synthase complex subunit DHDDS | EC 2.5.1.87; Cis-isoprenyltransferase; CIT; Cis-IPTase; Cis-prenyltransferase subunit hCIT; Epididymis tissue protein Li 189m | Homo sapiens (human) |
| Exostosin-2 | EC 2.4.1.224; EC 2.4.1.225; Glucuronosyl-N-acetylglucosaminyl-proteoglycan/N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase; Multiple exostoses protein 2; Putative tumor suppressor protein EXT2 | Homo sapiens (human) |
| Galactosylgalactosylxylosylprotein 3-beta-glucuronosyltransferase 3 | EC 2.4.1.135; Beta-1,3-glucuronyltransferase 3; Glucuronosyltransferase I; GlcAT-I; UDP-GlcUA:Gal beta-1,3-Gal-R glucuronyltransferase; GlcUAT-I | Homo sapiens (human) |
| Exostosin-1 | EC 2.4.1.224; EC 2.4.1.225; Glucuronosyl-N-acetylglucosaminyl-proteoglycan/N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase; Multiple exostoses protein 1; Putative tumor suppressor protein EXT1 | Homo sapiens (human) |
| Putative bifunctional UDP-N-acetylglucosamine transferase and deubiquitinase ALG13 | EC 2.4.1.141; EC 3.4.19.12; Asparagine-linked glycosylation 13 homolog; Glycosyltransferase 28 domain-containing protein 1; UDP-N-acetylglucosamine transferase subunit ALG13 homolog | Homo sapiens (human) |
| Protein O-mannosyl-transferase 2 | EC 2.4.1.109; Dolichyl-phosphate-mannose--protein mannosyltransferase 2 | Homo sapiens (human) |
| Protein O-mannosyl-transferase 1 | EC 2.4.1.109; Dolichyl-phosphate-mannose--protein mannosyltransferase 1 | Homo sapiens (human) |
| Beta-1,3-N-acetylglucosaminyltransferase lunatic fringe | EC 2.4.1.222; O-fucosylpeptide 3-beta-N-acetylglucosaminyltransferase | Homo sapiens (human) |
| Dolichol-phosphate mannosyltransferase subunit 1 | EC 2.4.1.83; Dolichol-phosphate mannose synthase subunit 1; DPM synthase subunit 1; Dolichyl-phosphate beta-D-mannosyltransferase subunit 1; Mannose-P-dolichol synthase subunit 1; MPD synthase subunit 1 | Homo sapiens (human) |
| Dolichol phosphate-mannose biosynthesis regulatory protein | Dolichol-phosphate mannose synthase subunit 2; DPM synthase subunit 2 | Homo sapiens (human) |
| Beta-1,3-glucosyltransferase | Beta3Glc-T; EC 2.4.1.-; Beta 3-glucosyltransferase; Beta-3-glycosyltransferase-like | Homo sapiens (human) |
| Protein RFT1 homolog | | Homo sapiens (human) |
| Dolichol-phosphate mannosyltransferase subunit 3 | Dolichol-phosphate mannose synthase subunit 3; DPM synthase subunit 3; Dolichyl-phosphate beta-D-mannosyltransferase subunit 3; Mannose-P-dolichol synthase subunit 3; MPD synthase subunit 3; Prostin-1 | Homo sapiens (human) |
| Compound | Description |
|---|
| hydronium ion | |
| Manganese | A trace element with atomic symbol Mn, atomic number 25, and atomic weight 54.94. It is concentrated in cell mitochondria, mostly in the pituitary gland, liver, pancreas, kidney, and bone, influences the synthesis of mucopolysaccharides, stimulates hepatic synthesis of cholesterol and fatty acids, and is a cofactor in many enzymes, including arginase and alkaline phosphatase in the liver. (From AMA Drug Evaluations Annual 1992, p2035) |
| Galactose | An aldohexose that occurs naturally in the D-form in lactose, cerebrosides, gangliosides, and mucoproteins. Deficiency of galactosyl-1-phosphate uridyltransferase (GALACTOSE-1-PHOSPHATE URIDYL-TRANSFERASE DEFICIENCY DISEASE) causes an error in galactose metabolism called GALACTOSEMIA, resulting in elevations of galactose in the blood. |
| Magnesium | A metallic element that has the atomic symbol Mg, atomic number 12, and atomic weight 24.31. It is important for the activity of many enzymes, especially those involved in OXIDATIVE PHOSPHORYLATION. |
| Water | A clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed) |
| isopentenyl pyrophosphate | substrate for isopentenyl pyrophosphate isomerase; RN given refers to unlabeled cpd; a nonpeptide mycobacterial antigen that stimulates gamma delta T cells |
| galactose-1-phosphate | |
| nad | A coenzyme composed of ribosylnicotinamide 5'-diphosphate coupled to adenosine 5'-phosphate by pyrophosphate linkage. It is found widely in nature and is involved in numerous enzymatic reactions in which it serves as an electron carrier by being alternately oxidized (NAD+) and reduced (NADH). (Dorland, 27th ed) |
| NADP | Nicotinamide adenine dinucleotide phosphate. A coenzyme composed of ribosylnicotinamide 5'-phosphate (NMN) coupled by pyrophosphate linkage to the 5'-phosphate adenosine 2',5'-bisphosphate. It serves as an electron carrier in a number of reactions, being alternately oxidized (NADP+) and reduced (NADPH). (Dorland, 27th ed) |
| farnesyl pyrophosphate | a sesquiterpene that dimerizes to SQUALENE; RN given refers to cpd without isomeric designation |
| adenosine triphosphate | An adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter. |
| polyglutamine | RN given for (D)-isomer |
| Cytidine Triphosphate | Cytidine 5'-(tetrahydrogen triphosphate). A cytosine nucleotide containing three phosphate groups esterified to the sugar moiety. |
| dolichol pyrophosphate | |
| dolichol monophosphate | |
| uridine diphosphate n-acetylgalactosamine | A nucleoside diphosphate sugar which serves as a source of N-acetylgalactosamine for glycoproteins, sulfatides and cerebrosides. |
| Adenosine Phosphosulfate | 5'-Adenylic acid, monoanhydride with sulfuric acid. The initial compound formed by the action of ATP sulfurylase on sulfate ions after sulfate uptake. Synonyms: adenosine sulfatophosphate; APS. |
| N-acetylmannosamine | RN given refers to cpd without isomeric designation |