u03B1-dystroglycan glycosylation

Proteins (7)

Protein	Synonyms	Taxonomy
Beta-1,4-glucuronyltransferase 1	EC 2.4.1.-; I-beta-1,3-N-acetylglucosaminyltransferase; iGnT; N-acetyllactosaminide beta-1,3-N-acetylglucosaminyltransferase; Poly-N-acetyllactosamine extension enzyme; UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 1	Homo sapiens (human)
D-ribitol-5-phosphate cytidylyltransferase	EC 2.7.7.40; 2-C-methyl-D-erythritol 4-phosphate cytidylyltransferase-like protein; Isoprenoid synthase domain-containing protein; hISPD	Homo sapiens (human)
Fukutin	EC 2.4.2.-; Fukuyama-type congenital muscular dystrophy protein; Ribitol-5-phosphate transferase	Homo sapiens (human)
LARGE xylosyl- and glucuronyltransferase 1	EC 2.4.-.-; Acetylglucosaminyltransferase-like 1A; Glycosyltransferase-like protein	Homo sapiens (human)
LARGE xylosyl- and glucuronyltransferase 2	EC 2.4.-.-; Glycosyltransferase-like 1B	Homo sapiens (human)
Fukutin-related protein	EC 2.4.2.-; Ribitol-5-phosphate transferase	Homo sapiens (human)
Ribitol-5-phosphate xylosyltransferase 1	EC 2.4.2.-; Transmembrane protein 5; UDP-D-xylose:ribitol-5-phosphate beta1,4-xylosyltransferase	Homo sapiens (human)

Compound	Description
diphosphoric acid
hydronium ion
uridine diphosphate	A uracil nucleotide containing a pyrophosphate group esterified to C5 of the sugar moiety.
Manganese	A trace element with atomic symbol Mn, atomic number 25, and atomic weight 54.94. It is concentrated in cell mitochondria, mostly in the pituitary gland, liver, pancreas, kidney, and bone, influences the synthesis of mucopolysaccharides, stimulates hepatic synthesis of cholesterol and fatty acids, and is a cofactor in many enzymes, including arginase and alkaline phosphatase in the liver. (From AMA Drug Evaluations Annual 1992, p2035)
Cytidine Monophosphate	Cytidine (dihydrogen phosphate). A cytosine nucleotide containing one phosphate group esterified to the sugar moiety in the 2', 3' or 5' position.
Cytidine Triphosphate	Cytidine 5'-(tetrahydrogen triphosphate). A cytosine nucleotide containing three phosphate groups esterified to the sugar moiety.
cytidine diphosphate ribitol	serves as the donor of ribitol residues for teichoic acid biosynthesis; minor descriptor (75-83); on-line & Index Medicus search NUCLEOSIDE DIPHOSPHATE SUGARS (75-83)