Page last updated: 2024-08-17

lactose and Lipidoses

lactose has been researched along with Lipidoses in 10 studies

Research

Studies (10)

TimeframeStudies, this research(%)All Research%
pre-199010 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
PARKE, DV2
Callahan, JW; Gerrie, J1
Clark, C; Dawson, G; Sattler, M; Suzuki, K; Tanaka, H; Wenger, DA1
Basu, S; Kaufman, B; Roseman, S; Steigerwald, JC1
Cocquyt, G; Dacremont, G; Kint, JA1
Hiatt, W; Sattler, M; Wenger, DA1
Ledeen, RW; Yu, RK1
Dawson, G; Matalon, R; Stein, AO1
Krivit, W; Sweeley, CC; Vance, DE1

Other Studies

10 other study(ies) available for lactose and Lipidoses

ArticleYear
The occurrence of lactose in the spleen cerebrosides of a case of Gaucher's disease.
    The Biochemical journal, 1953, Nov-14, Volume: 56, Issue:323rd Meet

    Topics: Cerebrosides; Gaucher Disease; Humans; Lactose; Lipidoses; Spleen

1953
The occurrence of lactose in the spleen cerebrosides of Gaucher's disease.
    Clinical science, 1962, Volume: 22

    Topics: Cerebrosides; Gaucher Disease; Humans; Lactose; Lipidoses; Spleen

1962
Purification of G-M-1-ganglioside and ceramide lactoside beta-galactosidase from rabbit brain.
    Biochimica et biophysica acta, 1975, May-23, Volume: 391, Issue:1

    Topics: Animals; Brain; Ceramides; Chromatography, DEAE-Cellulose; Chromatography, Gel; Chromatography, Ion Exchange; Electrophoresis, Polyacrylamide Gel; Galactosidases; Gangliosides; Glycolipids; Hydrogen-Ion Concentration; Isoelectric Focusing; Kinetics; Lactose; Lipidoses; Rabbits

1975
Lactosyl ceramidosis: normal activity for two lactosyl ceramide beta-galactosidases.
    Science (New York, N.Y.), 1975, Jun-27, Volume: 188, Issue:4195

    Topics: Cells, Cultured; Ceramides; Child; Fibroblasts; Galactosidases; Humans; Lactose; Lipidoses; Sphingomyelin Phosphodiesterase

1975
Sialic acids. Enzymatic synthesis of Tay-Sachs ganglioside.
    The Journal of biological chemistry, 1975, Sep-10, Volume: 250, Issue:17

    Topics: Animals; Brain; Cations, Divalent; Cations, Monovalent; Chick Embryo; Enzyme Activation; Erythrocytes; Gangliosides; Glycosphingolipids; Hexosyltransferases; Kinetics; Lactose; Lipidoses; Manganese; Sialic Acids; Species Specificity; Uridine Diphosphate N-Acetylgalactosamine

1975
Brain sphingolipids in I cell disease (mucolipidosis II).
    Journal of neurochemistry, 1974, Volume: 22, Issue:4

    Topics: Abnormalities, Multiple; Ceramides; Cerebrosides; Child, Preschool; Chromatography, Gas; Chromatography, Thin Layer; Cytoplasmic Granules; Fibroblasts; Galactose; Gangliosides; Glucose; Humans; Lactose; Lipidoses; Mucopolysaccharidosis I; Mucopolysaccharidosis II; Neuraminic Acids; Retinitis Pigmentosa; Sphingolipids; Sphingomyelins; Sulfoglycosphingolipids; Syndrome

1974
Globoid cell leukodystrophy: deficiency of lactosyl ceramide beta-galactosidase.
    Proceedings of the National Academy of Sciences of the United States of America, 1974, Volume: 71, Issue:3

    Topics: Adult; Brain; Ceramides; Female; Galactose; Galactosidases; Gangliosides; Humans; Infant; Lactose; Leukodystrophy, Globoid Cell; Leukodystrophy, Metachromatic; Lipidoses; Liver; Male; Niemann-Pick Diseases; Skin; Spleen; Syndrome

1974
Gas--liquid chromatographic assay of lipid-bound sialic acids: measurement of gangliosides in brain of several species.
    Journal of lipid research, 1970, Volume: 11, Issue:6

    Topics: Adrenal Medulla; Adult; Animals; Anura; Brain Chemistry; Cattle; Cerebrosides; Chromatography, Gas; Chromatography, Thin Layer; Colorimetry; Cyprinidae; Esters; Female; Gangliosides; Humans; Lactose; Lipidoses; Male; Mathematics; Methods; Methylation; Microchemistry; Middle Aged; Neuraminic Acids; Rats; Species Specificity; Time Factors

1970
Lactosylceramidosis: lactosylceramide galactosyl hydrolase deficiency and accumulation of lactosylceramide in cultured skin fibroblasts.
    The Journal of pediatrics, 1971, Volume: 79, Issue:3

    Topics: Brain Diseases; Cerebrosides; Chromatography, Gas; Chromatography, Thin Layer; Culture Techniques; Fibroblasts; Galactose; Glycoside Hydrolases; Heterozygote; Lactose; Lipid Metabolism, Inborn Errors; Lipidoses; Liver; Sphingolipids

1971
Concentrations of glycosyl ceramides in plasma and red cells in Fabry's disease, a glycolipid lipidosis.
    Journal of lipid research, 1969, Volume: 10, Issue:2

    Topics: Adolescent; Adult; Cerebrosides; Child; Erythrocytes; Female; Galactose; Gaucher Disease; Glucose; Heterozygote; Humans; Lactose; Lipidoses; Male; Middle Aged

1969