Pathways > valine degradation
Page last updated: 2024-10-06

valine degradation

Proteins (13)

ProteinSynonymsTaxonomy
Branched-chain-amino-acid aminotransferase, mitochondrialBCAT(m); EC 2.6.1.42; Placental protein 18; PP18Homo sapiens (human)
Trifunctional enzyme subunit alpha, mitochondrial78 kDa gastrin-binding protein; Monolysocardiolipin acyltransferase; 2.3.1.-; TP-alphaHomo sapiens (human)
Enoyl-CoA hydratase, mitochondrialEC 4.2.1.17; Enoyl-CoA hydratase 1; Short-chain enoyl-CoA hydratase; SCEHHomo sapiens (human)
4-aminobutyrate aminotransferase, mitochondrialEC 2.6.1.19; (S)-3-amino-2-methylpropionate transaminase; 2.6.1.22; GABA aminotransferase; GABA-AT; Gamma-amino-N-butyrate transaminase; GABA transaminase; GABA-T; L-AIBATHomo sapiens (human)
Branched-chain-amino-acid aminotransferase, cytosolicBCAT(c); EC 2.6.1.42; Protein ECA39Homo sapiens (human)
3-hydroxyisobutyrate dehydrogenase, mitochondrialHIBADH; EC 1.1.1.31Homo sapiens (human)
3-hydroxyisobutyryl-CoA hydrolase, mitochondrialEC 3.1.2.4; 3-hydroxyisobutyryl-coenzyme A hydrolase; HIB-CoA hydrolase; HIBYL-CoA-HHomo sapiens (human)
Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrialEC 2.3.1.168; 52 kDa mitochondrial autoantigen of primary biliary cirrhosis; Branched chain 2-oxo-acid dehydrogenase complex component E2; BCOADC-E2; Branched-chain alpha-keto acid dehydrogenase complex component E2; BCKAD-E2; BCKADE2; Dihydrolipoamide acHomo sapiens (human)
Dihydrolipoyl dehydrogenase, mitochondrialEC 1.8.1.4; Dihydrolipoamide dehydrogenase; Glycine cleavage system L proteinHomo sapiens (human)
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrialEC 1.2.4.4; Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain; BCKDE1A; BCKDH E1-alphaHomo sapiens (human)
2-oxoisovalerate dehydrogenase subunit beta, mitochondrialEC 1.2.4.4; Branched-chain alpha-keto acid dehydrogenase E1 component beta chain; BCKDE1B; BCKDH E1-betaHomo sapiens (human)
Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrialMMSDH; Malonate-semialdehyde dehydrogenase [acylating]; EC 1.2.1.18; EC 1.2.1.27; Aldehyde dehydrogenase family 6 member A1Homo sapiens (human)
Isobutyryl-CoA dehydrogenase, mitochondrialIBDH; EC 1.3.8.-; Activator-recruited cofactor 42 kDa component; ARC42; Acyl-CoA dehydrogenase family member 8; ACAD-8Homo sapiens (human)

Compounds (15)

CompoundDescription
hydronium ion
NADH
Carbon DioxideA colorless, odorless gas that can be formed by the body and is necessary for the respiration cycle of plants and animals.
hydrogen carbonate
WaterA clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed)
1,5-dihydro-FADchromophore component of E coli DNA photolyase
methacrylyl-coenzyme A
nadA coenzyme composed of ribosylnicotinamide 5'-diphosphate coupled to adenosine 5'-phosphate by pyrophosphate linkage. It is found widely in nature and is involved in numerous enzymatic reactions in which it serves as an electron carrier by being alternately oxidized (NAD+) and reduced (NADH). (Dorland, 27th ed)
alpha-Ketoglutarate
alpha-keto-isovaleric acid
glutamate
Coenzyme A
isobutyryl-coenzyme A
propionyl-coenzyme ARN given refers to parent cpd
Flavin-Adenine DinucleotideA condensation product of riboflavin and adenosine diphosphate. The coenzyme of various aerobic dehydrogenases, e.g., D-amino acid oxidase and L-amino acid oxidase. (Lehninger, Principles of Biochemistry, 1982, p972)
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