Page last updated: 2024-10-06

super pathway of glycosphingolipids biosynthesis

Proteins (26)

ProteinSynonymsTaxonomy
Beta-galactoside alpha-2,6-sialyltransferase 1Alpha 2,6-ST 1; EC 2.4.99.1; B-cell antigen CD75; CMP-N-acetylneuraminate-beta-galactosamide-alpha-2,6-sialyltransferase 1; ST6Gal I; ST6GalI; Sialyltransferase 1Homo sapiens (human)
Beta-1,3-galactosyltransferase 1Beta-1,3-GalTase 1; Beta3Gal-T1; Beta3GalT1; EC 2.4.1.86; UDP-galactose:beta-N-acetyl-glucosamine-beta-1,3-galactosyltransferase 1Homo sapiens (human)
Beta-1,3-galactosyltransferase 5Beta-1,3-GalTase 5; Beta3Gal-T5; Beta3GalT5; b3Gal-T5; EC 2.4.1.-; Beta-3-Gx-T5; UDP-Gal:beta-GlcNAc beta-1,3-galactosyltransferase 5; UDP-galactose:beta-N-acetylglucosamine beta-1,3-galactosyltransferase 5Homo sapiens (human)
Beta-1,4-galactosyltransferase 1Beta-1,4-GalTase 1; Beta4Gal-T1; b4Gal-T1; EC 2.4.1.-; Beta-N-acetylglucosaminyl-glycolipid beta-1,4-galactosyltransferase; Beta-N-acetylglucosaminylglycopeptide beta-1,4-galactosyltransferase; 2.4.1.38; Lactose synthase A protein; 2.4.1.22; N-acetyllactoHomo sapiens (human)
Ceramide glucosyltransferaseEC 2.4.1.80; GLCT-1; Glucosylceramide synthase; GCS; UDP-glucose ceramide glucosyltransferase; UDP-glucose:N-acylsphingosine D-glucosyltransferaseHomo sapiens (human)
CMP-N-acetylneuraminate-beta-1,4-galactoside alpha-2,3-sialyltransferaseEC 2.4.99.6; Beta-galactoside alpha-2,3-sialyltransferase 3; Alpha 2,3-ST 3; Gal beta-1,3(4) GlcNAc alpha-2,3 sialyltransferase; N-acetyllactosaminide alpha-2,3-sialyltransferase; ST3Gal III; ST3GalIII; ST3N; Sialyltransferase 6Homo sapiens (human)
Beta-1,4-galactosyltransferase 3Beta-1,4-GalTase 3; Beta4Gal-T3; b4Gal-T3; EC 2.4.1.-; Beta-N-acetylglucosaminyl-glycolipid beta-1,4-galactosyltransferase; Beta-N-acetylglucosaminylglycopeptide beta-1,4-galactosyltransferase; 2.4.1.38; N-acetyllactosamine synthase; 2.4.1.90; Nal synthasHomo sapiens (human)
Beta-1,4-galactosyltransferase 4Beta-1,4-GalTase 4; Beta4Gal-T4; b4Gal-T4; EC 2.4.1.-; Beta-N-acetylglucosaminyl-glycolipid beta-1,4-galactosyltransferase; Lactotriaosylceramide beta-1,4-galactosyltransferase; 2.4.1.275; N-acetyllactosamine synthase; 2.4.1.90; Nal synthase; UDP-Gal:betaHomo sapiens (human)
Beta-1,4-galactosyltransferase 2Beta-1,4-GalTase 2; Beta4Gal-T2; b4Gal-T2; EC 2.4.1.-; Beta-N-acetylglucosaminyl-glycolipid beta-1,4-galactosyltransferase; Beta-N-acetylglucosaminylglycopeptide beta-1,4-galactosyltransferase; 2.4.1.38; Lactose synthase A protein; 2.4.1.22; N-acetyllactoHomo sapiens (human)
Lactosylceramide 4-alpha-galactosyltransferaseEC 2.4.1.228; Alpha-1,4-N-acetylglucosaminyltransferase; Alpha-1,4-galactosyltransferase; Alpha4Gal-T1; CD77 synthase; Globotriaosylceramide synthase; Gb3 synthase; P1/Pk synthase; UDP-galactose:beta-D-galactosyl-beta1-R 4-alpha-D-galactosyltransferaseHomo sapiens (human)
Galactoside alpha-(1,2)-fucosyltransferase 2Alpha(1,2)FT 2; Fucosyltransferase 2; GDP-L-fucose:beta-D-galactoside 2-alpha-L-fucosyltransferase 2; SE2; Secretor blood group alpha-2-fucosyltransferase; Secretor factor; Se; Type 1 galactoside alpha-(1,2)-fucosyltransferase FUT2; 2.4.1.69; Type 2 galacHomo sapiens (human)
Alpha-2,8-sialyltransferase 8BEC 2.4.99.-; Sialyltransferase 8B; SIAT8-B; Sialyltransferase St8Sia II; ST8SiaII; Sialyltransferase X; STXHomo sapiens (human)
CMP-N-acetylneuraminate-beta-galactosamide-alpha-2,3-sialyltransferase 4Alpha 2,3-ST 4; Beta-galactoside alpha-2,3-sialyltransferase 4; EC 2.4.99.2; EC 2.4.99.4; Alpha 2,3-sialyltransferase IV; Gal-NAc6S; Gal-beta-1,3-GalNAc-alpha-2,3-sialyltransferase; Gal-beta-1,4-GlcNAc-alpha-2,3-sialyltransferase; N-acetyllactosaminide alHomo sapiens (human)
CMP-N-acetylneuraminate-beta-galactosamide-alpha-2,3-sialyltransferase 2Alpha 2,3-ST 2; Beta-galactoside alpha-2,3-sialyltransferase 2; EC 2.4.99.4; Gal-NAc6S; Gal-beta-1,3-GalNAc-alpha-2,3-sialyltransferase; Monosialoganglioside sialyltransferase; 2.4.99.2; ST3Gal II; ST3GalII; ST3GalA.2; Sialyltransferase 4B; SIAT4-BHomo sapiens (human)
Beta-1,4 N-acetylgalactosaminyltransferase 1EC 2.4.1.92; (N-acetylneuraminyl)-galactosylglucosylceramide; GM2/GD2 synthase; GalNAc-THomo sapiens (human)
Beta-1,3-galactosyltransferase 4Beta-1,3-GalTase 4; Beta3Gal-T4; Beta3GalT4; GalT4; b3Gal-T4; EC 2.4.1.62; Gal-T2; Ganglioside galactosyltransferase; UDP-galactose:beta-N-acetyl-galactosamine-beta-1,3-galactosyltransferaseHomo sapiens (human)
Lactosylceramide 1,3-N-acetyl-beta-D-glucosaminyltransferaseEC 2.4.1.206; Lactotriaosylceramide synthase; Lc(3)Cer synthase; Lc3 synthase; UDP-GlcNAc:beta-Gal beta-1,3-N-acetylglucosaminyltransferase 5; BGnT-5; Beta-1,3-Gn-T5; Beta-1,3-N-acetylglucosaminyltransferase 5; Beta3Gn-T5Homo sapiens (human)
UDP-GalNAc:beta-1,3-N-acetylgalactosaminyltransferase 1Beta-1,3-GalNAc-T1; EC 2.4.1.79; Beta-1,3-galactosyltransferase 3; Beta-1,3-GalTase 3; Beta3Gal-T3; Beta3GalT3; b3Gal-T3; Beta-3-Gx-T3; Galactosylgalactosylglucosylceramide beta-D-acetyl-galactosaminyltransferase; Globoside synthase; UDP-N-acetylgalactosaHomo sapiens (human)
Sia-alpha-2,3-Gal-beta-1,4-GlcNAc-R:alpha 2,8-sialyltransferaseEC 2.4.99.-; Alpha-2,8-sialyltransferase 8C; Alpha-2,8-sialyltransferase III; ST8 alpha-N-acetyl-neuraminide alpha-2,8-sialyltransferase 3; Sialyltransferase 8C; SIAT8-C; Sialyltransferase St8Sia III; ST8SiaIIIHomo sapiens (human)
Galactoside alpha-(1,2)-fucosyltransferase 1Alpha(1,2)FT 1; Blood group H alpha 2-fucosyltransferase; Fucosyltransferase 1; GDP-L-fucose:beta-D-galactoside 2-alpha-L-fucosyltransferase 1; Type 1 galactoside alpha-(1,2)-fucosyltransferase FUT1; 2.4.1.69; Type 2 galactoside alpha-(1,2)-fucosyltransfeHomo sapiens (human)
Globoside alpha-1,3-N-acetylgalactosaminyltransferase 1EC 2.4.1.-; Forssman glycolipid synthase-like proteinHomo sapiens (human)
Alpha-N-acetylneuraminide alpha-2,8-sialyltransferaseEC 2.4.99.8; Alpha-2,8-sialyltransferase 8A; Ganglioside GD3 synthase; Ganglioside GT3 synthase; Sialyltransferase 8A; SIAT8-A; Sialyltransferase St8Sia I; ST8SiaIHomo sapiens (human)
N-acetyllactosaminide beta-1,3-N-acetylglucosaminyltransferase 2EC 2.4.1.149; Beta-1,3-N-acetylglucosaminyltransferase 1; BGnT-1; Beta-1,3-Gn-T1; Beta3Gn-T1; Beta-1,3-galactosyltransferase 7; Beta-1,3-GalTase 7; Beta3Gal-T7; Beta3GalT7; b3Gal-T7; Beta-3-Gx-T7; UDP-Gal:beta-GlcNAc beta-1,3-galactosyltransferase 7; UDP-Homo sapiens (human)
Beta-1,4-galactosyltransferase 6Beta-1,4-GalTase 6; Beta4Gal-T6; b4Gal-T6; EC 2.4.1.-; Glucosylceramide beta-1,4-galactosyltransferase; 2.4.1.274; Lactosylceramide synthase; LacCer synthase; UDP-Gal:beta-GlcNAc beta-1,4-galactosyltransferase 6; UDP-Gal:glucosylceramide beta-1,4-galactosHomo sapiens (human)
Lactosylceramide alpha-2,3-sialyltransferaseEC 2.4.99.9; CMP-NeuAc:lactosylceramide alpha-2,3-sialyltransferase; GM3 synthase; Ganglioside GM3 synthase; ST3Gal V; ST3GalV; Sialyltransferase 9Homo sapiens (human)
Type 2 lactosamine alpha-2,3-sialyltransferaseEC 2.4.99.-; CMP-NeuAc:beta-galactoside alpha-2,3-sialyltransferase VI; ST3Gal VI; ST3GalVI; Sialyltransferase 10Homo sapiens (human)

Compounds (4)

CompoundDescription
hydronium ion
uridine diphosphateA uracil nucleotide containing a pyrophosphate group esterified to C5 of the sugar moiety.
ManganeseA trace element with atomic symbol Mn, atomic number 25, and atomic weight 54.94. It is concentrated in cell mitochondria, mostly in the pituitary gland, liver, pancreas, kidney, and bone, influences the synthesis of mucopolysaccharides, stimulates hepatic synthesis of cholesterol and fatty acids, and is a cofactor in many enzymes, including arginase and alkaline phosphatase in the liver. (From AMA Drug Evaluations Annual 1992, p2035)
Cytidine MonophosphateCytidine (dihydrogen phosphate). A cytosine nucleotide containing one phosphate group esterified to the sugar moiety in the 2', 3' or 5' position.