Pathways > mitochondrial L-carnitine shuttle
Page last updated: 2024-10-06
mitochondrial L-carnitine shuttle
Proteins (8)
Protein | Synonyms | Taxonomy |
Mitochondrial carnitine/acylcarnitine carrier protein | Carnitine/acylcarnitine translocase; CAC; Solute carrier family 25 member 20 | Homo sapiens (human) |
Carnitine O-palmitoyltransferase 2, mitochondrial | EC 2.3.1.21; Carnitine palmitoyltransferase II; CPT II | Rattus norvegicus (Norway rat) |
Carnitine O-palmitoyltransferase 2, mitochondrial | EC 2.3.1.21; Carnitine palmitoyltransferase II; CPT II | Homo sapiens (human) |
Carnitine O-palmitoyltransferase 1, liver isoform | CPT1-L; EC 2.3.1.21; Carnitine O-palmitoyltransferase I, liver isoform; CPT I; CPTI-L; Carnitine palmitoyltransferase 1A | Rattus norvegicus (Norway rat) |
Carnitine O-palmitoyltransferase 1, liver isoform | CPT1-L; EC 2.3.1.21; Carnitine O-palmitoyltransferase I, liver isoform; CPT I; CPTI-L; Carnitine palmitoyltransferase 1A | Homo sapiens (human) |
Carnitine O-palmitoyltransferase 1, muscle isoform | CPT1-M; EC 2.3.1.21; Carnitine O-palmitoyltransferase I, muscle isoform; CPT I; CPTI-M; Carnitine palmitoyltransferase 1B; Carnitine palmitoyltransferase I-like protein | Homo sapiens (human) |
Mitochondrial carnitine/acylcarnitine carrier protein | Carnitine/acylcarnitine translocase; CAC; Solute carrier family 25 member 20 | Rattus norvegicus (Norway rat) |
Carnitine O-palmitoyltransferase 1, brain isoform | CPT1-B; EC 2.3.1.21; CPT IC; Carnitine O-palmitoyltransferase I, brain isoform; CPTI-B; Carnitine palmitoyltransferase 1C | Homo sapiens (human) |
Compounds (7)
Compound | Description |
levocarnitine | |
palmitoylcarnitine | A long-chain fatty acid ester of carnitine which facilitates the transfer of long-chain fatty acids from cytoplasm into mitochondria during the oxidation of fatty acids. |
ethylmaleimide | A sulfhydryl reagent that is widely used in experimental biochemical studies. |
zwittergent 3-12 | zwitterionic detergent |
Coenzyme A | |
Palmitoyl Coenzyme A | A fatty acid coenzyme derivative which plays a key role in fatty acid oxidation and biosynthesis. |
Malonyl Coenzyme A | A coenzyme A derivative which plays a key role in the fatty acid synthesis in the cytoplasmic and microsomal systems. |