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Valine, leucine and isoleucine degradation

Proteins (0)

Compounds (17)

CompoundDescription
valineA branched-chain essential amino acid that has stimulant activity. It promotes muscle growth and tissue repair. It is a precursor in the penicillin biosynthetic pathway.
isovaleryl-coenzyme a
isobutyryl-coenzyme a
3-hydroxy-3-methylglutaryl-coenzyme aRN given refers to cpd without isomeric designation
2-oxo-3-methylvalerate
methylmalonic acidA malonic acid derivative which is a vital intermediate in the metabolism of fat and protein. Abnormalities in methylmalonic acid metabolism lead to methylmalonic aciduria. This metabolic disease is attributed to a block in the enzymatic conversion of methylmalonyl CoA to succinyl CoA.
alpha-ketoisovalerateRN given refers to parent cpd
leucineAn essential branched-chain amino acid important for hemoglobin formation.
isoleucineAn essential branched-chain aliphatic amino acid found in many proteins. It is an isomer of LEUCINE. It is important in hemoglobin synthesis and regulation of blood sugar and energy levels.
tiglyl-coenzyme a
2-keto-4-methylvalerate
succinyl-coenzyme a
acetoacetic acid
methacrylyl-coenzyme A
acetyl coenzyme aAcetyl CoA participates in the biosynthesis of fatty acids and sterols, in the oxidation of fatty acids and in the metabolism of many amino acids. It also acts as a biological acetylating agent.
acetoacetyl coa
propionyl-coenzyme aRN given refers to parent cpd