| Compound | Description |
|---|---|
| valine | A branched-chain essential amino acid that has stimulant activity. It promotes muscle growth and tissue repair. It is a precursor in the penicillin biosynthetic pathway. |
| isovaleryl-coenzyme a | |
| isobutyryl-coenzyme a | |
| 3-hydroxy-3-methylglutaryl-coenzyme a | RN given refers to cpd without isomeric designation |
| 2-oxo-3-methylvalerate | |
| methylmalonic acid | A malonic acid derivative which is a vital intermediate in the metabolism of fat and protein. Abnormalities in methylmalonic acid metabolism lead to methylmalonic aciduria. This metabolic disease is attributed to a block in the enzymatic conversion of methylmalonyl CoA to succinyl CoA. |
| alpha-ketoisovalerate | RN given refers to parent cpd |
| leucine | An essential branched-chain amino acid important for hemoglobin formation. |
| isoleucine | An essential branched-chain aliphatic amino acid found in many proteins. It is an isomer of LEUCINE. It is important in hemoglobin synthesis and regulation of blood sugar and energy levels. |
| tiglyl-coenzyme a | |
| 2-keto-4-methylvalerate | |
| succinyl-coenzyme a | |
| acetoacetic acid | |
| methacrylyl-coenzyme A | |
| acetyl coenzyme a | Acetyl CoA participates in the biosynthesis of fatty acids and sterols, in the oxidation of fatty acids and in the metabolism of many amino acids. It also acts as a biological acetylating agent. |
| acetoacetyl coa | |
| propionyl-coenzyme a | RN given refers to parent cpd |