Threonine and 2-Oxobutanoate Degradation

Proteins (8)

Protein	Synonyms	Taxonomy
Propionyl-CoA carboxylase alpha chain, mitochondrial	PCCase subunit alpha; EC 6.4.1.3; Propanoyl-CoA:carbon dioxide ligase subunit alpha	Homo sapiens (human)
Propionyl-CoA carboxylase beta chain, mitochondrial	PCCase subunit beta; EC 6.4.1.3; Propanoyl-CoA:carbon dioxide ligase subunit beta	Homo sapiens (human)
Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial	EC 2.3.1.168; 52 kDa mitochondrial autoantigen of primary biliary cirrhosis; Branched chain 2-oxo-acid dehydrogenase complex component E2; BCOADC-E2; Branched-chain alpha-keto acid dehydrogenase complex component E2; BCKAD-E2; BCKADE2; Dihydrolipoamide ac	Homo sapiens (human)
L-serine dehydratase/L-threonine deaminase	SDH; EC 4.3.1.17; L-serine deaminase; L-threonine dehydratase; TDH; 4.3.1.19	Homo sapiens (human)
Dihydrolipoyl dehydrogenase, mitochondrial	EC 1.8.1.4; Dihydrolipoamide dehydrogenase; Glycine cleavage system L protein	Homo sapiens (human)
Methylmalonyl-CoA mutase, mitochondrial	MCM; EC 5.4.99.2; Methylmalonyl-CoA isomerase	Homo sapiens (human)
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial	EC 1.2.4.4; Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain; BCKDE1A; BCKDH E1-alpha	Homo sapiens (human)
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial	EC 1.2.4.4; Branched-chain alpha-keto acid dehydrogenase E1 component beta chain; BCKDE1B; BCKDH E1-beta	Homo sapiens (human)

Compound	Description
ammonium hydroxide	The hydroxy salt of ammonium ion. It is formed when AMMONIA reacts with water molecules in solution.
NADH
Adenosine Triphosphate	An adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter.
adenosine diphosphate	Adenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position.
threonine	An essential amino acid occurring naturally in the L-form, which is the active form. It is found in eggs, milk, gelatin, and other proteins.
hydrogen carbonate
Coenzyme A
alpha-ketobutyric acid	RN given refers to parent cpd; structure
NAD	A coenzyme composed of ribosylnicotinamide 5'-diphosphate coupled to adenosine 5'-phosphate by pyrophosphate linkage. It is found widely in nature and is involved in numerous enzymatic reactions in which it serves as an electron carrier by being alternately oxidized (NAD+) and reduced (NADH). (Dorland, 27th ed)