| Protein | Synonyms | Taxonomy |
|---|
| Cytochrome b | Complex III subunit 3; Complex III subunit III; Cytochrome b-c1 complex subunit 3; Ubiquinol-cytochrome-c reductase complex cytochrome b subunit | Homo sapiens (human) |
| Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex, mitochondrial | EC 2.3.1.12; 70 kDa mitochondrial autoantigen of primary biliary cirrhosis; PBC; Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex; M2 antigen complex 70 kDa subunit; Pyruvate dehydrogenase complex component E2; PDC-E2; PDCE2 | Homo sapiens (human) |
| Succinate dehydrogenase [ubiquinone] iron-sulfur subunit, mitochondrial | EC 1.3.5.1; Iron-sulfur subunit of complex II; Ip | Homo sapiens (human) |
| Basigin | 5F7; Collagenase stimulatory factor; Extracellular matrix metalloproteinase inducer; EMMPRIN; Hepatoma-associated antigen; HAb18G; Leukocyte activation antigen M6; OK blood group antigen; Tumor cell-derived collagenase stimulatory factor; TCSF | Homo sapiens (human) |
| Isocitrate dehydrogenase [NADP], mitochondrial | IDH; EC 1.1.1.42; ICD-M; IDP; NADP(+)-specific ICDH; Oxalosuccinate decarboxylase | Homo sapiens (human) |
| Acylpyruvase FAHD1, mitochondrial | EC 3.7.1.5; Fumarylacetoacetate hydrolase domain-containing protein 1; FAH domain-containing protein 1; Oxaloacetate decarboxylase; OAA decarboxylase; 4.1.1.112; YisK-like protein | Homo sapiens (human) |
| Maleylacetoacetate isomerase | MAAI; EC 5.2.1.2; GSTZ1-1; Glutathione S-transferase zeta 1; 2.5.1.18 | Homo sapiens (human) |
| Cytochrome c oxidase subunit 1 | EC 7.1.1.9; Cytochrome c oxidase polypeptide I | Homo sapiens (human) |
| L-lactate dehydrogenase A chain | LDH-A; EC 1.1.1.27; Cell proliferation-inducing gene 19 protein; LDH muscle subunit; LDH-M; Renal carcinoma antigen NY-REN-59 | Homo sapiens (human) |
| Cytochrome c oxidase subunit 2 | EC 7.1.1.9; Cytochrome c oxidase polypeptide II | Homo sapiens (human) |
| Retinoic acid receptor RXR-alpha | Nuclear receptor subfamily 2 group B member 1; Retinoid X receptor alpha | Homo sapiens (human) |
| Peroxisome proliferator-activated receptor delta | PPAR-delta; NUCI; Nuclear hormone receptor 1; NUC1; Nuclear receptor subfamily 1 group C member 2; Peroxisome proliferator-activated receptor beta; PPAR-beta | Homo sapiens (human) |
| Heat shock protein 75 kDa, mitochondrial | HSP 75; TNFR-associated protein 1; Tumor necrosis factor type 1 receptor-associated protein; TRAP-1 | Homo sapiens (human) |
| Pyruvate dehydrogenase E1 component subunit beta, mitochondrial | PDHE1-B; EC 1.2.4.1 | Homo sapiens (human) |
| Succinate--CoA ligase [ADP-forming] subunit beta, mitochondrial | EC 6.2.1.5; ATP-specific succinyl-CoA synthetase subunit beta; A-SCS; Succinyl-CoA synthetase beta-A chain; SCS-betaA | Homo sapiens (human) |
| Citrate synthase, mitochondrial | EC 2.3.3.1; Citrate (Si)-synthase | Homo sapiens (human) |
| Isocitrate dehydrogenase [NAD] subunit alpha, mitochondrial | EC 1.1.1.41; Isocitric dehydrogenase subunit alpha; NAD(+)-specific ICDH subunit alpha | Homo sapiens (human) |
| Hydroxyacid-oxoacid transhydrogenase, mitochondrial | HOT; EC 1.1.99.24; Alcohol dehydrogenase iron-containing protein 1; ADHFe1; Fe-containing alcohol dehydrogenase | Homo sapiens (human) |
| Cytochrome b-c1 complex subunit 9 | Complex III subunit 9; Complex III subunit X; Cytochrome c1 non-heme 7 kDa protein; Ubiquinol-cytochrome c reductase complex 7.2 kDa protein | Homo sapiens (human) |
| L-lactate dehydrogenase B chain | LDH-B; EC 1.1.1.27; LDH heart subunit; LDH-H; Renal carcinoma antigen NY-REN-46 | Homo sapiens (human) |
| Cytochrome b-c1 complex subunit 7 | Complex III subunit 7; Complex III subunit VII; QP-C; Ubiquinol-cytochrome c reductase complex 14 kDa protein | Homo sapiens (human) |
| Succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial | EC 1.3.5.1; Flavoprotein subunit of complex II; Fp | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 | B17.2-like; B17.2L; Mimitin; Myc-induced mitochondrial protein; MMTN; NDUFA12-like protein | Homo sapiens (human) |
| Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial | ETF-QO; ETF-ubiquinone oxidoreductase; EC 1.5.5.1; Electron-transferring-flavoprotein dehydrogenase; ETF dehydrogenase | Homo sapiens (human) |
| Protein arginine methyltransferase NDUFAF7, mitochondrial | EC 2.1.1.320; NADH dehydrogenase [ubiquinone] complex I, assembly factor 7; Protein midA homolog | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] iron-sulfur protein 8, mitochondrial | EC 7.1.1.2; Complex I-23kD; CI-23kD; NADH-ubiquinone oxidoreductase 23 kDa subunit; TYKY subunit | Homo sapiens (human) |
| Cytochrome c oxidase subunit NDUFA4 | Complex I-MLRQ; CI-MLRQ; NADH-ubiquinone oxidoreductase MLRQ subunit | Homo sapiens (human) |
| Acyl carrier protein, mitochondrial | ACP; CI-SDAP; NADH-ubiquinone oxidoreductase 9.6 kDa subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 subunit C1, mitochondrial | Complex I-KFYI; CI-KFYI; NADH-ubiquinone oxidoreductase KFYI subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrial | EC 7.1.1.2; Complex I-49kD; CI-49kD; NADH-ubiquinone oxidoreductase 49 kDa subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrial | Complex I-13kD-A; CI-13kD-A; NADH-ubiquinone oxidoreductase 13 kDa-A subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 4 | Complex I-B15; CI-B15; NADH-ubiquinone oxidoreductase B15 subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 7 | Complex I-B14.5a; CI-B14.5a; NADH-ubiquinone oxidoreductase subunit B14.5a | Homo sapiens (human) |
| NADH-ubiquinone oxidoreductase chain 4 | EC 7.1.1.2; NADH dehydrogenase subunit 4 | Homo sapiens (human) |
| NADH-ubiquinone oxidoreductase chain 5 | EC 7.1.1.2; NADH dehydrogenase subunit 5 | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 7 | Cell adhesion protein SQM1; Complex I-B18; CI-B18; NADH-ubiquinone oxidoreductase B18 subunit | Homo sapiens (human) |
| NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial | EC 7.1.1.2; Complex I-75kD; CI-75kD | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 6 | Complex I-B14; CI-B14; LYR motif-containing protein 6; NADH-ubiquinone oxidoreductase B14 subunit | Homo sapiens (human) |
| Cytochrome c | | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 11, mitochondrial | Complex I-ESSS; CI-ESSS; NADH-ubiquinone oxidoreductase ESSS subunit; Neuronal protein 17.3; Np17.3; p17.3 | Homo sapiens (human) |
| Complex I intermediate-associated protein 30, mitochondrial | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1 | Complex I-MWFE; CI-MWFE; NADH-ubiquinone oxidoreductase MWFE subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] iron-sulfur protein 4, mitochondrial | Complex I-18 kDa; CI-18 kDa; Complex I-AQDQ; CI-AQDQ; NADH-ubiquinone oxidoreductase 18 kDa subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 5, mitochondrial | Complex I-SGDH; CI-SGDH; NADH-ubiquinone oxidoreductase SGDH subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 3 | Complex I-B12; CI-B12; NADH-ubiquinone oxidoreductase B12 subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 2 | Complex I-B8; CI-B8; NADH-ubiquinone oxidoreductase B8 subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] iron-sulfur protein 5 | Complex I-15 kDa; CI-15 kDa; NADH-ubiquinone oxidoreductase 15 kDa subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] iron-sulfur protein 7, mitochondrial | EC 7.1.1.2; Complex I-20kD; CI-20kD; NADH-ubiquinone oxidoreductase 20 kDa subunit; PSST subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 1 | Complex I-MNLL; CI-MNLL; NADH-ubiquinone oxidoreductase MNLL subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] iron-sulfur protein 3, mitochondrial | EC 7.1.1.2; Complex I-30kD; CI-30kD; NADH-ubiquinone oxidoreductase 30 kDa subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 6 | Complex I-B17; CI-B17; NADH-ubiquinone oxidoreductase B17 subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 3 | Complex I-B9; CI-B9; NADH-ubiquinone oxidoreductase B9 subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 8, mitochondrial | Complex I-ASHI; CI-ASHI; NADH-ubiquinone oxidoreductase ASHI subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 2, mitochondrial | Complex I-AGGG; CI-AGGG; NADH-ubiquinone oxidoreductase AGGG subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 subunit C2 | Complex I-B14.5b; CI-B14.5b; Human lung cancer oncogene 1 protein; HLC-1; NADH-ubiquinone oxidoreductase subunit B14.5b | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 10, mitochondrial | Complex I-42kD; CI-42kD; NADH-ubiquinone oxidoreductase 42 kDa subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 10 | Complex I-PDSW; CI-PDSW; NADH-ubiquinone oxidoreductase PDSW subunit | Homo sapiens (human) |
| NADH-ubiquinone oxidoreductase chain 1 | EC 7.1.1.2; NADH dehydrogenase subunit 1 | Homo sapiens (human) |
| NADH-ubiquinone oxidoreductase chain 2 | EC 7.1.1.2; NADH dehydrogenase subunit 2 | Homo sapiens (human) |
| NADH-ubiquinone oxidoreductase chain 3 | EC 7.1.1.2; NADH dehydrogenase subunit 3 | Homo sapiens (human) |
| NADH-ubiquinone oxidoreductase chain 6 | EC 7.1.1.2; NADH dehydrogenase subunit 6 | Homo sapiens (human) |
| ATP synthase subunit beta, mitochondrial | EC 7.1.2.2; ATP synthase F1 subunit beta | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] flavoprotein 2, mitochondrial | EC 7.1.1.2; NADH-ubiquinone oxidoreductase 24 kDa subunit | Homo sapiens (human) |
| ATP synthase subunit alpha, mitochondrial | ATP synthase F1 subunit alpha | Homo sapiens (human) |
| Malate dehydrogenase, mitochondrial | EC 1.1.1.37 | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial | EC 7.1.1.2; Complex I-51kD; CI-51kD; NADH dehydrogenase flavoprotein 1; NADH-ubiquinone oxidoreductase 51 kDa subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 8 | Complex I-19kD; CI-19kD; Complex I-PGIV; CI-PGIV; NADH-ubiquinone oxidoreductase 19 kDa subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] flavoprotein 3, mitochondrial | Complex I-9kD; CI-9kD; NADH-ubiquinone oxidoreductase 9 kDa subunit; Renal carcinoma antigen NY-REN-4 | Homo sapiens (human) |
| Lactoylglutathione lyase | EC 4.4.1.5; Aldoketomutase; Glyoxalase I; Glx I; Ketone-aldehyde mutase; Methylglyoxalase; S-D-lactoylglutathione methylglyoxal lyase | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 5 | Complex I subunit B13; Complex I-13kD-B; CI-13kD-B; NADH-ubiquinone oxidoreductase 13 kDa-B subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 9, mitochondrial | Complex I-39kD; CI-39kD; NADH-ubiquinone oxidoreductase 39 kDa subunit | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 11 | Complex I-B14.7; CI-B14.7; NADH-ubiquinone oxidoreductase subunit B14.7 | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 | | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 | Hormone-regulated proliferation-associated protein of 20 kDa | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 13 | Cell death regulatory protein GRIM-19; Complex I-B16.6; CI-B16.6; Gene associated with retinoic and interferon-induced mortality 19 protein; GRIM-19; Gene associated with retinoic and IFN-induced mortality 19 protein; NADH-ubiquinone oxidoreductase B16.6 | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 12 | 13 kDa differentiation-associated protein; Complex I-B17.2; CI-B17.2; CIB17.2; NADH-ubiquinone oxidoreductase subunit B17.2 | Homo sapiens (human) |
| NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 9 | Complex I-B22; CI-B22; LYR motif-containing protein 3; NADH-ubiquinone oxidoreductase B22 subunit | Homo sapiens (human) |
| Mitochondrial pyruvate carrier 2 | Brain protein 44 | Homo sapiens (human) |
| Aconitate hydratase, mitochondrial | Aconitase; EC 4.2.1.3; Citrate hydro-lyase | Homo sapiens (human) |
| Succinate dehydrogenase cytochrome b560 subunit, mitochondrial | Integral membrane protein CII-3; QPs-1; QPs1; Succinate dehydrogenase complex subunit C; Succinate-ubiquinone oxidoreductase cytochrome B large subunit; CYBL | Homo sapiens (human) |
| [Pyruvate dehydrogenase (acetyl-transferring)] kinase isozyme 2, mitochondrial | EC 2.7.11.2; Pyruvate dehydrogenase kinase isoform 2; PDH kinase 2; PDKII | Homo sapiens (human) |
| ATP synthase subunit gamma, mitochondrial | ATP synthase F1 subunit gamma; F-ATPase gamma subunit | Homo sapiens (human) |
| L-lactate dehydrogenase C chain | LDH-C; EC 1.1.1.27; Cancer/testis antigen 32; CT32; LDH testis subunit; LDH-X | Homo sapiens (human) |
| Cytochrome c1, heme protein, mitochondrial | EC 7.1.1.8; Complex III subunit 4; Complex III subunit IV; Cytochrome b-c1 complex subunit 4; Ubiquinol-cytochrome-c reductase complex cytochrome c1 subunit; Cytochrome c-1 | Homo sapiens (human) |
| Voltage-dependent anion-selective channel protein 1 | VDAC-1; hVDAC1; Outer mitochondrial membrane protein porin 1; Plasmalemmal porin; Porin 31HL; Porin 31HM | Homo sapiens (human) |
| Electron transfer flavoprotein subunit beta | Beta-ETF | Homo sapiens (human) |
| Pyruvate dehydrogenase protein X component, mitochondrial | Dihydrolipoamide dehydrogenase-binding protein of pyruvate dehydrogenase complex; E3-binding protein; E3BP; Lipoyl-containing pyruvate dehydrogenase complex component X; proX | Homo sapiens (human) |
| Cytochrome b-c1 complex subunit Rieske, mitochondrial | EC 7.1.1.8; Complex III subunit 5; Cytochrome b-c1 complex subunit 5; Rieske iron-sulfur protein; RISP; Rieske protein UQCRFS1; Ubiquinol-cytochrome c reductase iron-sulfur subunit | Homo sapiens (human) |
| Cytochrome c oxidase subunit 7A-related protein, mitochondrial | COX7a-related protein; Cytochrome c oxidase subunit VIIa-related protein; EB1 | Homo sapiens (human) |
| Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial | EC 6.2.1.4; EC 6.2.1.5; Succinyl-CoA synthetase subunit alpha; SCS-alpha | Homo sapiens (human) |
| L-2-hydroxyglutarate dehydrogenase, mitochondrial | EC 1.1.99.2; Duranin | Homo sapiens (human) |
| Dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial | EC 2.3.1.61; 2-oxoglutarate dehydrogenase complex component E2; OGDC-E2; Dihydrolipoamide succinyltransferase component of 2-oxoglutarate dehydrogenase complex; E2K | Homo sapiens (human) |
| N-fatty-acyl-amino acid synthase/hydrolase PM20D1 | EC 3.5.1.114; EC 3.5.1.14; Peptidase M20 domain-containing protein 1 | Homo sapiens (human) |
| Cytochrome c oxidase subunit 6A1, mitochondrial | Cytochrome c oxidase polypeptide VIa-liver; Cytochrome c oxidase subunit VIA-liver; COX VIa-L | Homo sapiens (human) |
| Cytochrome c oxidase subunit 5A, mitochondrial | Cytochrome c oxidase polypeptide Va | Homo sapiens (human) |
| Succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial | EC 6.2.1.4; GTP-specific succinyl-CoA synthetase subunit beta; G-SCS; GTPSCS; Succinyl-CoA synthetase beta-G chain; SCS-betaG | Homo sapiens (human) |
| Cytochrome c oxidase subunit 4 isoform 1, mitochondrial | Cytochrome c oxidase polypeptide IV; Cytochrome c oxidase subunit IV isoform 1; COX IV-1 | Homo sapiens (human) |
| Succinate dehydrogenase [ubiquinone] cytochrome b small subunit, mitochondrial | CybS; CII-4; QPs3; Succinate dehydrogenase complex subunit D; Succinate-ubiquinone oxidoreductase cytochrome b small subunit; Succinate-ubiquinone reductase membrane anchor subunit | Homo sapiens (human) |
| Cytochrome b-c1 complex subunit 8 | Complex III subunit 8; Complex III subunit VIII; Ubiquinol-cytochrome c reductase complex 9.5 kDa protein; Ubiquinol-cytochrome c reductase complex ubiquinone-binding protein QP-C | Homo sapiens (human) |
| Cytochrome b-c1 complex subunit 10 | Complex III subunit 10; Complex III subunit XI; Ubiquinol-cytochrome c reductase complex 6.4 kDa protein | Homo sapiens (human) |
| Isocitrate dehydrogenase [NAD] subunit beta, mitochondrial | Isocitric dehydrogenase subunit beta; NAD(+)-specific ICDH subunit beta | Homo sapiens (human) |
| ATP synthase subunit d, mitochondrial | ATPase subunit d; ATP synthase peripheral stalk subunit d | Homo sapiens (human) |
| ATP synthase subunit g, mitochondrial | ATPase subunit g; ATP synthase membrane subunit g | Homo sapiens (human) |
| Cytochrome c oxidase subunit 3 | EC 7.1.1.9; Cytochrome c oxidase polypeptide III | Homo sapiens (human) |
| ATP synthase subunit a | F-ATPase protein 6 | Homo sapiens (human) |
| ATP synthase protein 8 | A6L; F-ATPase subunit 8 | Homo sapiens (human) |
| ATP synthase F(0) complex subunit C1, mitochondrial | ATP synthase lipid-binding protein; ATP synthase membrane subunit c locus 1; ATP synthase proteolipid P1; ATP synthase proton-transporting mitochondrial F(0) complex subunit C1; ATPase protein 9; ATPase subunit c | Homo sapiens (human) |
| Cytochrome b-c1 complex subunit 6, mitochondrial | Complex III subunit 6; Complex III subunit VIII; Cytochrome c1 non-heme 11 kDa protein; Mitochondrial hinge protein; Ubiquinol-cytochrome c reductase complex 11 kDa protein | Homo sapiens (human) |
| Fumarate hydratase, mitochondrial | Fumarase; HsFH; EC 4.2.1.2 | Homo sapiens (human) |
| Cytochrome c oxidase subunit 6C | Cytochrome c oxidase polypeptide VIc | Homo sapiens (human) |
| Cytochrome c oxidase subunit 8A, mitochondrial | Cytochrome c oxidase polypeptide VIII-liver/heart; Cytochrome c oxidase subunit 8-2 | Homo sapiens (human) |
| Cytochrome c oxidase subunit 5B, mitochondrial | Cytochrome c oxidase polypeptide Vb | Homo sapiens (human) |
| Electron transfer flavoprotein subunit alpha, mitochondrial | Alpha-ETF | Homo sapiens (human) |
| Cytochrome c oxidase subunit 6B1 | Cytochrome c oxidase subunit VIb isoform 1; COX VIb-1 | Homo sapiens (human) |
| Cytochrome c oxidase subunit 7C, mitochondrial | Cytochrome c oxidase polypeptide VIIc | Homo sapiens (human) |
| ATP synthase-coupling factor 6, mitochondrial | ATPase subunit F6; ATP synthase peripheral stalk subunit F6 | Homo sapiens (human) |
| Cytochrome b-c1 complex subunit 2, mitochondrial | Complex III subunit 2; Core protein II; Ubiquinol-cytochrome-c reductase complex core protein 2 | Homo sapiens (human) |
| Cytochrome c oxidase subunit 7B, mitochondrial | Cytochrome c oxidase polypeptide VIIb | Homo sapiens (human) |
| ATP synthase F(0) complex subunit B1, mitochondrial | ATP synthase peripheral stalk-membrane subunit b; ATP synthase proton-transporting mitochondrial F(0) complex subunit B1; ATP synthase subunit b; ATPase subunit b | Homo sapiens (human) |
| ATP synthase subunit delta, mitochondrial | ATP synthase F1 subunit delta; F-ATPase delta subunit | Homo sapiens (human) |
| Cytochrome b-c1 complex subunit 1, mitochondrial | Complex III subunit 1; Core protein I; Ubiquinol-cytochrome-c reductase complex core protein 1 | Homo sapiens (human) |
| ATP synthase subunit O, mitochondrial | ATP synthase peripheral stalk subunit OSCP; Oligomycin sensitivity conferral protein; OSCP | Homo sapiens (human) |
| ATP synthase F(0) complex subunit C3, mitochondrial | ATP synthase lipid-binding protein; ATP synthase membrane subunit c locus 3; ATP synthase proteolipid P3; ATP synthase proton-transporting mitochondrial F(0) complex subunit C3; ATPase protein 9; ATPase subunit c | Homo sapiens (human) |
| Isocitrate dehydrogenase [NAD] subunit gamma, mitochondrial | Isocitric dehydrogenase subunit gamma; NAD(+)-specific ICDH subunit gamma | Homo sapiens (human) |
| ATP synthase subunit f, mitochondrial | ATP synthase membrane subunit f | Homo sapiens (human) |
| ATP synthase subunit epsilon, mitochondrial | ATPase subunit epsilon; ATP synthase F1 subunit epsilon | Homo sapiens (human) |
| ATP synthase subunit e, mitochondrial | ATPase subunit e; ATP synthase membrane subunit e | Homo sapiens (human) |
| ATP synthase F(0) complex subunit C2, mitochondrial | ATP synthase lipid-binding protein; ATP synthase membrane subunit c locus 2; ATP synthase proteolipid P2; ATP synthase proton-transporting mitochondrial F(0) complex subunit C2; ATPase protein 9; ATPase subunit c | Homo sapiens (human) |
| NAD(P) transhydrogenase, mitochondrial | EC 7.1.1.1; Nicotinamide nucleotide transhydrogenase; Pyridine nucleotide transhydrogenase | Homo sapiens (human) |
| NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 | Putative phytoene synthase | Homo sapiens (human) |
| Cytochrome c oxidase assembly protein COX19 | hCOX19 | Homo sapiens (human) |
| Arginine-hydroxylase NDUFAF5, mitochondrial | EC 1.-.-.-; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5; Putative methyltransferase NDUFAF5; 2.1.1.- | Homo sapiens (human) |
| L-lactate dehydrogenase A-like 6A | LDHA-like protein 6A; EC 1.1.1.27 | Homo sapiens (human) |
| Complex I assembly factor TMEM126B, mitochondrial | Transmembrane protein 126B | Homo sapiens (human) |
| D-2-hydroxyglutarate dehydrogenase, mitochondrial | EC 1.1.99.- | Homo sapiens (human) |
| Iron-sulfur protein NUBPL | IND1 homolog; Nucleotide-binding protein-like; huInd1 | Homo sapiens (human) |
| Transmembrane protein 186 | | Homo sapiens (human) |
| ATP synthase subunit s, mitochondrial | ATP synthase-coupling factor B; FB; Distal membrane arm assembly complex 2-like protein; Mitochondrial ATP synthase regulatory component factor B | Homo sapiens (human) |
| Evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial | Protein SITPEC | Homo sapiens (human) |
| L-lactate dehydrogenase A-like 6B | EC 1.1.1.27 | Homo sapiens (human) |
| Cytochrome c oxidase assembly factor 1 homolog | Mitochondrial translation regulation assembly intermediate of cytochrome c oxidase protein of 15 kDa | Homo sapiens (human) |
| Complex I assembly factor ACAD9, mitochondrial | Acyl-CoA dehydrogenase family member 9; ACAD-9; 1.3.8.- | Homo sapiens (human) |
| Complex I assembly factor TIMMDC1, mitochondrial | Protein M5-14; Translocase of inner mitochondrial membrane domain-containing protein 1; TIMM domain containing-protein 1 | Homo sapiens (human) |
| [Pyruvate dehydrogenase [acetyl-transferring]]-phosphatase 1, mitochondrial | PDP 1; EC 3.1.3.43; Protein phosphatase 2C; Pyruvate dehydrogenase phosphatase catalytic subunit 1; PDPC 1 | Homo sapiens (human) |
| [Pyruvate dehydrogenase [acetyl-transferring]]-phosphatase 2, mitochondrial | PDP 2; EC 3.1.3.43; Pyruvate dehydrogenase phosphatase catalytic subunit 2; PDPC 2 | Homo sapiens (human) |
| Mitochondrial pyruvate carrier 1 | Brain protein 44-like protein | Homo sapiens (human) |
| Compound | Description |
|---|
| hydronium ion | |
| cobalt | A trace element that is a component of vitamin B12. It has the atomic symbol Co, atomic number 27, and atomic weight 58.93. It is used in nuclear weapons, alloys, and pigments. Deficiency in animals leads to anemia; its excess in humans can lead to erythrocytosis. |
| l-lactic acid | |
| Glutathione | A tripeptide with many roles in cells. It conjugates to drugs to make them more soluble for excretion, is a cofactor for some enzymes, is involved in protein disulfide bond rearrangement and reduces peroxides. |
| Thiamine Pyrophosphate | The coenzyme form of Vitamin B1 present in many animal tissues. It is a required intermediate in the PYRUVATE DEHYDROGENASE COMPLEX and the KETOGLUTARATE DEHYDROGENASE COMPLEX. |
| Succinate | |
| NADH | |
| Copper | A heavy metal trace element with the atomic symbol Cu, atomic number 29, and atomic weight 63.55. |
| Manganese | A trace element with atomic symbol Mn, atomic number 25, and atomic weight 54.94. It is concentrated in cell mitochondria, mostly in the pituitary gland, liver, pancreas, kidney, and bone, influences the synthesis of mucopolysaccharides, stimulates hepatic synthesis of cholesterol and fatty acids, and is a cofactor in many enzymes, including arginase and alkaline phosphatase in the liver. (From AMA Drug Evaluations Annual 1992, p2035) |
| Carbon Dioxide | A colorless, odorless gas that can be formed by the body and is necessary for the respiration cycle of plants and animals. |
| carbon monoxide | Carbon monoxide (CO). A poisonous colorless, odorless, tasteless gas. It combines with hemoglobin to form carboxyhemoglobin, which has no oxygen carrying capacity. The resultant oxygen deprivation causes headache, dizziness, decreased pulse and respiratory rates, unconsciousness, and death. (From Merck Index, 11th ed) |
| 4-hydroxybutyric acid | was an entry term to Sodium Oxybate (74-98) |
| citric acid, anhydrous | |
| hydrochloric acid | A strong corrosive acid that is commonly used as a laboratory reagent. It is formed by dissolving hydrogen chloride in water. GASTRIC ACID is the hydrochloric acid component of GASTRIC JUICE. |
| Zinc | A metallic element of atomic number 30 and atomic weight 65.38. It is a necessary trace element in the diet, forming an essential part of many enzymes, and playing an important role in protein synthesis and in cell division. Zinc deficiency is associated with ANEMIA, short stature, HYPOGONADISM, impaired WOUND HEALING, and geophagia. It is known by the symbol Zn. |
| Orthophosphate | |
| Flavin Mononucleotide | A coenzyme for a number of oxidative enzymes including NADH DEHYDROGENASE. It is the principal form in which RIBOFLAVIN is found in cells and tissues. |
| tretinoin | An important regulator of GENE EXPRESSION during growth and development, and in NEOPLASMS. Tretinoin, also known as retinoic acid and derived from maternal VITAMIN A, is essential for normal GROWTH; and EMBRYONIC DEVELOPMENT. An excess of tretinoin can be teratogenic. It is used in the treatment of PSORIASIS; ACNE VULGARIS; and several other SKIN DISEASES. It has also been approved for use in promyelocytic leukemia (LEUKEMIA, PROMYELOCYTIC, ACUTE). |
| fumaric acid | see also record for ferrous fumarate; use FUMARATES for general fumaric acid esters |
| ubiquinol 1 | |
| coenzyme q10 | Ubiquinone ring with a chain of 10 isoprene units; redox equilibrium with ubiqunol serving in mitochondrial inner membrane to transfer electrons; presence during reconstitution of acetylcholine receptor into phospholipid vesicles yields vesicles active in catalyzing carbamylcholine-sensitive Na+ flux; coenzyme Q10 depletion has been noted with use of statins |
| adenosine diphosphate | Adenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position. |
| Magnesium | A metallic element that has the atomic symbol Mg, atomic number 12, and atomic weight 24.31. It is important for the activity of many enzymes, especially those involved in OXIDATIVE PHOSPHORYLATION. |
| Water | A clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed) |
| Oxygen | An element with atomic symbol O, atomic number 8, and atomic weight [15.99903; 15.99977]. It is the most abundant element on earth and essential for respiration. |
| Guanosine Monophosphate | A guanine nucleotide containing one phosphate group esterified to the sugar moiety and found widely in nature. |
| succinyl-coenzyme A | |
| 1,5-dihydro-FAD | chromophore component of E coli DNA photolyase |
| Guanosine Diphosphate | A guanine nucleotide containing two phosphate groups esterified to the sugar moiety. |
| Pyruvic Acid | An intermediate compound in the metabolism of carbohydrates, proteins, and fats. In thiamine deficiency, its oxidation is retarded and it accumulates in the tissues, especially in nervous structures. (From Stedman, 26th ed) |
| adenosine monophosphate | Adenine nucleotide containing one phosphate group esterified to the sugar moiety in the 2'-, 3'-, or 5'-position. |
| nad | A coenzyme composed of ribosylnicotinamide 5'-diphosphate coupled to adenosine 5'-phosphate by pyrophosphate linkage. It is found widely in nature and is involved in numerous enzymatic reactions in which it serves as an electron carrier by being alternately oxidized (NAD+) and reduced (NADH). (Dorland, 27th ed) |
| NADP | Nicotinamide adenine dinucleotide phosphate. A coenzyme composed of ribosylnicotinamide 5'-phosphate (NMN) coupled by pyrophosphate linkage to the 5'-phosphate adenosine 2',5'-bisphosphate. It serves as an electron carrier in a number of reactions, being alternately oxidized (NADP+) and reduced (NADPH). (Dorland, 27th ed) |
| NADP | Nicotinamide adenine dinucleotide phosphate. A coenzyme composed of ribosylnicotinamide 5'-phosphate (NMN) coupled by pyrophosphate linkage to the 5'-phosphate adenosine 2',5'-bisphosphate. It serves as an electron carrier in a number of reactions, being alternately oxidized (NADP+) and reduced (NADPH). (Dorland, 27th ed) |
| alpha-Ketoglutarate | |
| Oxaloacetate | An anionic form of oxaloacetic acid. |
| alpha-hydroxyglutarate, (l)-isomer | |
| Oleic Acid | An unsaturated fatty acid that is the most widely distributed and abundant fatty acid in nature. It is used commercially in the preparation of oleates and lotions, and as a pharmaceutical solvent. (Stedman, 26th ed) |
| adenosine triphosphate | An adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter. |
| glyoxylic acid | RN given refers to parent cpd |
| lipoamide | RN given refers to cpd without isomeric designation |
| pyruvaldehyde | An organic compound used often as a reagent in organic synthesis, as a flavoring agent, and in tanning. It has been demonstrated as an intermediate in the metabolism of acetone and its derivatives in isolated cell preparations, in various culture media, and in vivo in certain animals. |
| Coenzyme A | |
| Dichloroacetic Acid | A derivative of ACETIC ACID that contains two CHLORINE atoms attached to its methyl group. |
| d-2-hydroxyglutarate | |
| Acetyl Coenzyme A | Acetyl CoA participates in the biosynthesis of fatty acids and sterols, in the oxidation of fatty acids and in the metabolism of many amino acids. It also acts as a biological acetylating agent. |
| Flavin-Adenine Dinucleotide | A condensation product of riboflavin and adenosine diphosphate. The coenzyme of various aerobic dehydrogenases, e.g., D-amino acid oxidase and L-amino acid oxidase. (Lehninger, Principles of Biochemistry, 1982, p972) |
| creolin | from refined coal tar oils |