Page last updated: 2024-10-06

Taurine and Hypotaurine Metabolism

Proteins (5)

ProteinSynonymsTaxonomy
Glutamate decarboxylase 1EC 4.1.1.15; 67 kDa glutamic acid decarboxylase; GAD-67; Glutamate decarboxylase 67 kDa isoformHomo sapiens (human)
Cysteine dioxygenase type 1EC 1.13.11.20; Cysteine dioxygenase type I; CDO; CDO-IHomo sapiens (human)
Cysteine sulfinic acid decarboxylaseEC 4.1.1.29; Aspartate 1-decarboxylase; 4.1.1.11; Cysteine-sulfinate decarboxylase; Sulfinoalanine decarboxylaseHomo sapiens (human)
2-aminoethanethiol dioxygenaseEC 1.13.11.19; Cysteamine dioxygenaseHomo sapiens (human)
Glutathione hydrolase 6EC 3.4.19.13; Gamma-glutamyltransferase 6; GGT 6; 2.3.2.2; Gamma-glutamyltranspeptidase 6Homo sapiens (human)

Compounds (8)

CompoundDescription
taurineA conditionally essential nutrient, important during mammalian development. It is present in milk but is isolated mostly from ox bile and strongly conjugates bile acids.
Carbon DioxideA colorless, odorless gas that can be formed by the body and is necessary for the respiration cycle of plants and animals.
cysteineA thiol-containing non-essential amino acid that is oxidized to form CYSTINE.
cysteamineA mercaptoethylamine compound that is endogenously derived from the COENZYME A degradative pathway. The fact that cysteamine is readily transported into LYSOSOMES where it reacts with CYSTINE to form cysteine-cysteamine disulfide and CYSTEINE has led to its use in CYSTINE DEPLETING AGENTS for the treatment of CYSTINOSIS.
OxygenAn element with atomic symbol O, atomic number 8, and atomic weight [15.99903; 15.99977]. It is the most abundant element on earth and essential for respiration.
hypotaurineintermediate in production of taurine in the liver; structure
cysteic acidBeta-Sulfoalanine. An amino acid with a C-terminal sulfonic acid group which has been isolated from human hair oxidized with permanganate. It occurs normally in the outer part of the sheep's fleece, where the wool is exposed to light and weather.
glutaurinerecently deteccted hormone of parathyroid gland; structure; RN given refers to (L)-isomer