Page last updated: 2024-10-06

Sialuria or French Type Sialuria

Proteins (17)

ProteinSynonymsTaxonomy
N-acylneuraminate-9-phosphataseEC 3.1.3.29; Haloacid dehalogenase-like hydrolase domain-containing protein 4; Neu5Ac-9-PaseHomo sapiens (human)
Chitotriosidase-1EC 3.2.1.14; Chitinase-1Homo sapiens (human)
Bifunctional UDP-N-acetylglucosamine 2-epimerase/N-acetylmannosamine kinaseUDP-GlcNAc-2-epimerase/ManAc kinaseHomo sapiens (human)
Beta-hexosaminidase subunit alphaEC 3.2.1.52; Beta-N-acetylhexosaminidase subunit alpha; Hexosaminidase subunit A; N-acetyl-beta-glucosaminidase subunit alphaHomo sapiens (human)
SialinH(+)/nitrate cotransporter; H(+)/sialic acid cotransporter; AST; Membrane glycoprotein HP59; Solute carrier family 17 member 5; Vesicular H(+)/Aspartate-glutamate cotransporterHomo sapiens (human)
Hexokinase-1EC 2.7.1.1; Brain form hexokinase; Hexokinase type I; HK I; Hexokinase-AHomo sapiens (human)
Glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1EC 2.6.1.16; D-fructose-6-phosphate amidotransferase 1; Glutamine:fructose-6-phosphate amidotransferase 1; GFAT 1; GFAT1; Hexosephosphate aminotransferase 1Homo sapiens (human)
N-acylneuraminate cytidylyltransferaseEC 2.7.7.43; CMP-N-acetylneuraminic acid synthase; CMP-NeuNAc synthaseHomo sapiens (human)
N-acetylglucosamine-6-phosphate deacetylaseGlcNAc 6-P deacetylase; EC 3.5.1.25; Amidohydrolase domain-containing protein 2Homo sapiens (human)
N-acetyl-D-glucosamine kinaseN-acetylglucosamine kinase; EC 2.7.1.59; GlcNAc kinaseHomo sapiens (human)
Glucosamine 6-phosphate N-acetyltransferaseEC 2.3.1.4; Phosphoglucosamine acetylase; Phosphoglucosamine transacetylaseHomo sapiens (human)
N-acetylneuraminate lyaseNALase; EC 4.1.3.3; N-acetylneuraminate pyruvate-lyase; N-acetylneuraminic acid aldolase; Sialate lyase; Sialate-pyruvate lyase; Sialic acid aldolase; Sialic acid lyaseHomo sapiens (human)
Glucosamine-6-phosphate isomerase 1EC 3.5.99.6; Glucosamine-6-phosphate deaminase 1; GNPDA 1; GlcN6P deaminase 1; OscillinHomo sapiens (human)
N-acylglucosamine 2-epimeraseAGE; EC 5.1.3.8; GlcNAc 2-epimerase; N-acetyl-D-glucosamine 2-epimerase; Renin-binding protein; RnBPHomo sapiens (human)
Phosphoacetylglucosamine mutasePAGM; EC 5.4.2.3; Acetylglucosamine phosphomutase; N-acetylglucosamine-phosphate mutase; Phosphoglucomutase-3; PGM 3Homo sapiens (human)
UDP-N-acetylhexosamine pyrophosphorylaseAntigen X; AGX; Sperm-associated antigen 2Homo sapiens (human)
Sialic acid synthaseN-acetylneuraminate synthase; 2.5.1.56; N-acetylneuraminate-9-phosphate synthase; 2.5.1.57; N-acetylneuraminic acid phosphate synthase; N-acetylneuraminic acid synthaseHomo sapiens (human)

Compounds (25)

CompoundDescription
pyruvic acidAn intermediate compound in the metabolism of carbohydrates, proteins, and fats. In thiamine deficiency, its oxidation is retarded and it accumulates in the tissues, especially in nervous structures. (From Stedman, 26th ed)
Orthophosphate
acetic acidProduct of the oxidation of ethanol and of the destructive distillation of wood. It is used locally, occasionally internally, as a counterirritant and also as a reagent. (Stedman, 26th ed)
ammonium hydroxideThe hydroxy salt of ammonium ion. It is formed when AMMONIA reacts with water molecules in solution.
glutamic acidA non-essential amino acid naturally occurring in the L-form. Glutamic acid is the most common excitatory neurotransmitter in the CENTRAL NERVOUS SYSTEM.
glucosamine
Adenosine TriphosphateAn adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter.
glutamineA non-essential amino acid present abundantly throughout the body and is involved in many metabolic processes. It is synthesized from GLUTAMIC ACID and AMMONIA. It is the principal carrier of NITROGEN in the body and is an important energy source for many cells.
adenosine diphosphateAdenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position.
uridine diphosphateA uracil nucleotide containing a pyrophosphate group esterified to C5 of the sugar moiety.
uridine triphosphateUridine 5'-(tetrahydrogen triphosphate). A uracil nucleotide containing three phosphate groups esterified to the sugar moiety.
WaterA clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed)
Coenzyme A
phosphoenolpyruvateA monocarboxylic acid anion derived from selective deprotonation of the carboxy group of phosphoenolpyruvic acid. It is a metabolic intermediate in GLYCOLYSIS; GLUCONEOGENESIS; and other pathways.
acetylglucosamineThe N-acetyl derivative of glucosamine.
glucosamine 6-phosphateRN given refers to parent cpd
n-acetylglucosamine-1-phosphatefound in proteinase I from Dictyostelium discoideum
n-acetylneuraminic acidAn N-acyl derivative of neuraminic acid. N-acetylneuraminic acid occurs in many polysaccharides, glycoproteins, and glycolipids in animals and bacteria. (From Dorland, 28th ed, p1518)
Uridine Diphosphate N-AcetylglucosamineServes as the biological precursor of insect chitin, of muramic acid in bacterial cell walls, and of sialic acids in mammalian glycoproteins.
cytidine triphosphateCytidine 5'-(tetrahydrogen triphosphate). A cytosine nucleotide containing three phosphate groups esterified to the sugar moiety.
fructose-6-phosphateRN given refers to parent cpd with unspecified isomeric designation
N-acetylglucosamine 6-phosphate
acetyl coenzyme aAcetyl CoA participates in the biosynthesis of fatty acids and sterols, in the oxidation of fatty acids and in the metabolism of many amino acids. It also acts as a biological acetylating agent.
cytidine monophosphate n-acetylneuraminic acidA nucleoside monophosphate sugar which donates N-acetylneuraminic acid to the terminal sugar of a ganglioside or glycoprotein.
pyrophosphate