Page last updated: 2024-10-06

Mitochondrial tRNA aminoacylation

Proteins (21)

ProteinSynonymsTaxonomy
Phenylalanine--tRNA ligase, mitochondrialEC 6.1.1.20; Phenylalanyl-tRNA synthetase; PheRSHomo sapiens (human)
Methionine--tRNA ligase, mitochondrialEC 6.1.1.10; Methionyl-tRNA synthetase 2; Mitochondrial methionyl-tRNA synthetase; MtMetRSHomo sapiens (human)
Lysine--tRNA ligaseEC 2.7.7.-; EC 6.1.1.6; Lysyl-tRNA synthetase; LysRSHomo sapiens (human)
Threonine--tRNA ligase, mitochondrialEC 6.1.1.3; Threonyl-tRNA synthetase; ThrRS; Threonyl-tRNA synthetase-like 1Homo sapiens (human)
Glutamine--tRNA ligaseEC 6.1.1.18; Glutaminyl-tRNA synthetase; GlnRSHomo sapiens (human)
Isoleucine--tRNA ligase, mitochondrialEC 6.1.1.5; Isoleucyl-tRNA synthetase; IleRSHomo sapiens (human)
Alanine--tRNA ligase, mitochondrialEC 6.1.1.7; Alanyl-tRNA synthetase; AlaRSHomo sapiens (human)
Probable leucine--tRNA ligase, mitochondrialEC 6.1.1.4; Leucyl-tRNA synthetase; LeuRSHomo sapiens (human)
Glycine--tRNA ligaseEC 6.1.1.14; Diadenosine tetraphosphate synthetase; Ap4A synthetase; 2.7.7.-; Glycyl-tRNA synthetase; GlyRS; Glycyl-tRNA synthetase 1Homo sapiens (human)
Inorganic pyrophosphatase 2, mitochondrialEC 3.6.1.1; Pyrophosphatase SID6-306; Pyrophosphate phospho-hydrolase 2; PPase 2Homo sapiens (human)
Aspartate--tRNA ligase, mitochondrialEC 6.1.1.12; Aspartyl-tRNA synthetase; AspRSHomo sapiens (human)
Probable glutamate--tRNA ligase, mitochondrialEC 6.1.1.17; Glutamyl-tRNA synthetase; GluRSHomo sapiens (human)
Histidine--tRNA ligase, mitochondrialEC 6.1.1.21; Histidine--tRNA ligase-like; Histidyl-tRNA synthetase; HisRSHomo sapiens (human)
Valine--tRNA ligase, mitochondrialEC 6.1.1.9; Valyl-tRNA synthetase; ValRS; Valyl-tRNA synthetase-likeHomo sapiens (human)
Probable arginine--tRNA ligase, mitochondrialEC 6.1.1.19; Arginyl-tRNA synthetase; ArgRSHomo sapiens (human)
Probable proline--tRNA ligase, mitochondrialEC 6.1.1.15; Prolyl-tRNA synthetase; ProRSHomo sapiens (human)
Probable asparagine--tRNA ligase, mitochondrialEC 6.1.1.22; Asparaginyl-tRNA synthetase; AsnRSHomo sapiens (human)
Probable cysteine--tRNA ligase, mitochondrialEC 6.1.1.16; Cysteinyl-tRNA synthetase; CysRSHomo sapiens (human)
Serine--tRNA ligase, mitochondrialEC 6.1.1.11; SerRSmt; Seryl-tRNA synthetase; SerRS; Seryl-tRNA(Ser/Sec) synthetaseHomo sapiens (human)
Tryptophan--tRNA ligase, mitochondrialEC 6.1.1.2; (Mt)TrpRS; Tryptophanyl-tRNA synthetase; TrpRSHomo sapiens (human)
Tyrosine--tRNA ligase, mitochondrialEC 6.1.1.1; Tyrosyl-tRNA synthetase; TyrRSHomo sapiens (human)

Compounds (10)

CompoundDescription
ArginineAn essential amino acid that is physiologically active in the L-form.
Orthophosphate
Aspartate
MagnesiumA metallic element that has the atomic symbol Mg, atomic number 12, and atomic weight 24.31. It is important for the activity of many enzymes, especially those involved in OXIDATIVE PHOSPHORYLATION.
WaterA clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed)
adenosine monophosphateAdenine nucleotide containing one phosphate group esterified to the sugar moiety in the 2'-, 3'-, or 5'-position.
glutamate
adenosine triphosphateAn adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter.
CysteineA thiol-containing non-essential amino acid that is oxidized to form CYSTINE.
polyglutamineRN given for (D)-isomer