Page last updated: 2024-10-06

Mitochondrial fatty acid oxidation disorders

Proteins (7)

ProteinSynonymsTaxonomy
Trifunctional enzyme subunit alpha, mitochondrial78 kDa gastrin-binding protein; Monolysocardiolipin acyltransferase; 2.3.1.-; TP-alphaHomo sapiens (human)
Trifunctional enzyme subunit beta, mitochondrialTP-betaHomo sapiens (human)
Medium-chain specific acyl-CoA dehydrogenase, mitochondrialMCAD; EC 1.3.8.7; Medium chain acyl-CoA dehydrogenase; MCADHHomo sapiens (human)
Very long-chain specific acyl-CoA dehydrogenase, mitochondrialVLCAD; EC 1.3.8.9Homo sapiens (human)
Mitochondrial carnitine/acylcarnitine carrier proteinCarnitine/acylcarnitine translocase; CAC; Solute carrier family 25 member 20Homo sapiens (human)
Short-chain specific acyl-CoA dehydrogenase, mitochondrialSCAD; EC 1.3.8.1; Butyryl-CoA dehydrogenaseHomo sapiens (human)
Long-chain specific acyl-CoA dehydrogenase, mitochondrialLCAD; EC 1.3.8.8Homo sapiens (human)

Compounds (1)

CompoundDescription
coenzyme a