Pathways > Mitochondrial Fatty Acid Beta-Oxidation
Page last updated: 2024-10-06

Mitochondrial Fatty Acid Beta-Oxidation

Proteins (22)

ProteinSynonymsTaxonomy
Trifunctional enzyme subunit alpha, mitochondrial78 kDa gastrin-binding protein; Monolysocardiolipin acyltransferase; 2.3.1.-; TP-alphaHomo sapiens (human)
Enoyl-CoA hydratase, mitochondrialEC 4.2.1.17; Enoyl-CoA hydratase 1; Short-chain enoyl-CoA hydratase; SCEHHomo sapiens (human)
Trifunctional enzyme subunit beta, mitochondrialTP-betaHomo sapiens (human)
Medium-chain specific acyl-CoA dehydrogenase, mitochondrialMCAD; EC 1.3.8.7; Medium chain acyl-CoA dehydrogenase; MCADHHomo sapiens (human)
Very long-chain specific acyl-CoA dehydrogenase, mitochondrialVLCAD; EC 1.3.8.9Homo sapiens (human)
Acyl-CoA dehydrogenase family member 10ACAD-10; EC 1.3.99.-Homo sapiens (human)
Propionyl-CoA carboxylase alpha chain, mitochondrialPCCase subunit alpha; EC 6.4.1.3; Propanoyl-CoA:carbon dioxide ligase subunit alphaHomo sapiens (human)
Propionyl-CoA carboxylase beta chain, mitochondrialPCCase subunit beta; EC 6.4.1.3; Propanoyl-CoA:carbon dioxide ligase subunit betaHomo sapiens (human)
Enoyl-CoA delta isomerase 1, mitochondrialEC 5.3.3.8; 3,2-trans-enoyl-CoA isomerase; Delta(3),Delta(2)-enoyl-CoA isomerase; D3,D2-enoyl-CoA isomerase; Dodecenoyl-CoA isomeraseHomo sapiens (human)
Acyl carrier protein, mitochondrialACP; CI-SDAP; NADH-ubiquinone oxidoreductase 9.6 kDa subunitHomo sapiens (human)
Phosphatidylcholine transfer proteinPC-TP; START domain-containing protein 2; StARD2; StAR-related lipid transfer protein 2Homo sapiens (human)
Enoyl-[acyl-carrier-protein] reductase, mitochondrialEC 1.3.1.104; 2-enoyl thioester reductase; Nuclear receptor-binding factor 1; HsNrbf-1; NRBF-1Homo sapiens (human)
Methylmalonyl-CoA epimerase, mitochondrialEC 5.1.99.1; DL-methylmalonyl-CoA racemaseHomo sapiens (human)
Acyl-CoA dehydrogenase family member 11ACAD-11; EC 1.3.8.-Homo sapiens (human)
Malonyl-CoA-acyl carrier protein transacylase, mitochondrialMCT; EC 2.3.1.39; Mitochondrial malonyl CoA:ACP acyltransferase; Mitochondrial malonyltransferase; [Acyl-carrier-protein] malonyltransferaseHomo sapiens (human)
Short-chain specific acyl-CoA dehydrogenase, mitochondrialSCAD; EC 1.3.8.1; Butyryl-CoA dehydrogenaseHomo sapiens (human)
Long-chain specific acyl-CoA dehydrogenase, mitochondrialLCAD; EC 1.3.8.8Homo sapiens (human)
Medium-chain acyl-CoA ligase ACSF2, mitochondrialEC 6.2.1.2Homo sapiens (human)
3-ketoacyl-CoA thiolase, mitochondrialEC 2.3.1.16; Acetyl-CoA acetyltransferase; 2.3.1.9; Acetyl-CoA acyltransferase; Acyl-CoA hydrolase, mitochondrial; 3.1.2.-; 3.1.2.1; 3.1.2.2; Beta-ketothiolase; Mitochondrial 3-oxoacyl-CoA thiolase; T1Homo sapiens (human)
2,4-dienoyl-CoA reductase [(3E)-enoyl-CoA-producing], mitochondrialEC 1.3.1.124; 2,4-dienoyl-CoA reductase [NADPH]; 4-enoyl-CoA reductase [NADPH]; Short chain dehydrogenase/reductase family 18C member 1Homo sapiens (human)
Hydroxyacyl-coenzyme A dehydrogenase, mitochondrialHCDH; EC 1.1.1.35; Medium and short-chain L-3-hydroxyacyl-coenzyme A dehydrogenase; Short-chain 3-hydroxyacyl-CoA dehydrogenaseHomo sapiens (human)
Acyl-CoA-binding domain-containing protein 6Homo sapiens (human)

Compounds (34)

CompoundDescription
hydronium ion
n-Butyrate
NADH
Carbon DioxideA colorless, odorless gas that can be formed by the body and is necessary for the respiration cycle of plants and animals.
Orthophosphate
adenosine diphosphateAdenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position.
WaterA clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed)
succinyl-coenzyme A
1,5-dihydro-FADchromophore component of E coli DNA photolyase
hexanoyl-coenzyme A
cobamamide
s-tetradecanoyl-coenzyme a
adenosine monophosphateAdenine nucleotide containing one phosphate group esterified to the sugar moiety in the 2'-, 3'-, or 5'-position.
nadA coenzyme composed of ribosylnicotinamide 5'-diphosphate coupled to adenosine 5'-phosphate by pyrophosphate linkage. It is found widely in nature and is involved in numerous enzymatic reactions in which it serves as an electron carrier by being alternately oxidized (NAD+) and reduced (NADH). (Dorland, 27th ed)
decanoyl-coenzyme A
3-ketohexanoyl-coenzyme A
octanoyl-coenzyme A
adenosine triphosphateAn adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter.
linoleoyl-coenzyme ARN from 9th CI Form Index & given refers to cpd without isomeric designation
2,4-decadienoyl-coenzyme A
3-hydroxybutyryl-coenzyme A, (S)-isomer
behenyl-coenzyme A
beta-ketohexadecanoyl-coenzyme A
4-decenoyl-coenzyme A
Coenzyme A
lauroyl-coenzyme A
acetoacetyl CoA
Acetyl Coenzyme AAcetyl CoA participates in the biosynthesis of fatty acids and sterols, in the oxidation of fatty acids and in the metabolism of many amino acids. It also acts as a biological acetylating agent.
butyryl-coenzyme A
Palmitoyl Coenzyme AA fatty acid coenzyme derivative which plays a key role in fatty acid oxidation and biosynthesis.
Malonyl Coenzyme AA coenzyme A derivative which plays a key role in the fatty acid synthesis in the cytoplasmic and microsomal systems.
Flavin-Adenine DinucleotideA condensation product of riboflavin and adenosine diphosphate. The coenzyme of various aerobic dehydrogenases, e.g., D-amino acid oxidase and L-amino acid oxidase. (Lehninger, Principles of Biochemistry, 1982, p972)
creolinfrom refined coal tar oils
propionyl-coenzyme aRN given refers to parent cpd
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