| Protein | Synonyms | Taxonomy |
|---|
| Cystathionine gamma-lyase | EC 4.4.1.1; Cysteine-protein sulfhydrase; Gamma-cystathionase | Homo sapiens (human) |
| Biotinidase | Biotinase; EC 3.5.1.12 | Homo sapiens (human) |
| Glutaryl-CoA dehydrogenase, mitochondrial | GCD; EC 1.3.8.6 | Homo sapiens (human) |
| Sulfide:quinone oxidoreductase, mitochondrial | SQOR; EC 1.8.5.8; Sulfide dehydrogenase-like; Sulfide quinone oxidoreductase | Homo sapiens (human) |
| Enoyl-CoA hydratase, mitochondrial | EC 4.2.1.17; Enoyl-CoA hydratase 1; Short-chain enoyl-CoA hydratase; SCEH | Homo sapiens (human) |
| Alanine aminotransferase 1 | ALT1; EC 2.6.1.2; Glutamate pyruvate transaminase 1; GPT 1; Glutamic--alanine transaminase 1; Glutamic--pyruvic transaminase 1 | Homo sapiens (human) |
| Xanthine dehydrogenase/oxidase | | Homo sapiens (human) |
| ADP/ATP translocase 2 | ADP,ATP carrier protein 2; ADP,ATP carrier protein, fibroblast isoform; Adenine nucleotide translocator 2; ANT 2; Solute carrier family 25 member 5 | Homo sapiens (human) |
| D-3-phosphoglycerate dehydrogenase | 3-PGDH; EC 1.1.1.95; 2-oxoglutarate reductase; 1.1.1.399; Malate dehydrogenase; 1.1.1.37 | Homo sapiens (human) |
| Kynurenine/alpha-aminoadipate aminotransferase, mitochondrial | KAT/AadAT; 2-aminoadipate aminotransferase; 2-aminoadipate transaminase; 2.6.1.39; Alpha-aminoadipate aminotransferase; AadAT; Kynurenine aminotransferase II; Kynurenine--oxoglutarate aminotransferase II; Kynurenine--oxoglutarate transaminase 2; 2.6.1.7; | Homo sapiens (human) |
| Cystathionine beta-synthase | EC 4.2.1.22; Beta-thionase; Serine sulfhydrase | Homo sapiens (human) |
| Cytoplasmic aconitate hydratase | Aconitase; EC 4.2.1.3; Citrate hydro-lyase; Ferritin repressor protein; Iron regulatory protein 1; IRP1; Iron-responsive element-binding protein 1; IRE-BP 1 | Homo sapiens (human) |
| Phosphoserine phosphatase | PSP; PSPase; EC 3.1.3.3; L-3-phosphoserine phosphatase; O-phosphoserine phosphohydrolase | Homo sapiens (human) |
| Cysteine dioxygenase type 1 | EC 1.13.11.20; Cysteine dioxygenase type I; CDO; CDO-I | Homo sapiens (human) |
| Acetyl-CoA acetyltransferase, mitochondrial | EC 2.3.1.9; Acetoacetyl-CoA thiolase; T2 | Homo sapiens (human) |
| Persulfide dioxygenase ETHE1, mitochondrial | EC 1.13.11.18; Ethylmalonic encephalopathy protein 1; Hepatoma subtracted clone one protein; Sulfur dioxygenase ETHE1 | Homo sapiens (human) |
| Sulfite oxidase, mitochondrial | EC 1.8.3.1 | Homo sapiens (human) |
| Phosphoserine aminotransferase | EC 2.6.1.52; Phosphohydroxythreonine aminotransferase; PSAT | Homo sapiens (human) |
| Tricarboxylate transport protein, mitochondrial | Citrate transport protein; CTP; Solute carrier family 25 member 1; Tricarboxylate carrier protein | Homo sapiens (human) |
| Glycine amidinotransferase, mitochondrial | EC 2.1.4.1; L-arginine:glycine amidinotransferase; Transamidinase | Homo sapiens (human) |
| Cationic amino acid transporter 2 | CAT-2; CAT2; Low affinity cationic amino acid transporter 2; Solute carrier family 7 member 2 | Homo sapiens (human) |
| Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial | HCDH; EC 1.1.1.35; Medium and short-chain L-3-hydroxyacyl-coenzyme A dehydrogenase; Short-chain 3-hydroxyacyl-CoA dehydrogenase | Homo sapiens (human) |
| Compound | Description |
|---|
| phosphoric acid | concise etchant is 37% H3PO4 |
| diphosphoric acid | |
| hydronium ion | |
| pyridoxal phosphate | This is the active form of VITAMIN B 6 serving as a coenzyme for synthesis of amino acids, neurotransmitters (serotonin, norepinephrine), sphingolipids, aminolevulinic acid. During transamination of amino acids, pyridoxal phosphate is transiently converted into pyridoxamine phosphate (PYRIDOXAMINE). |
| pyruvic acid | An intermediate compound in the metabolism of carbohydrates, proteins, and fats. In thiamine deficiency, its oxidation is retarded and it accumulates in the tissues, especially in nervous structures. (From Stedman, 26th ed) |
| l-lactic acid | |
| sulfuric acid | |
| urea | A compound formed in the liver from ammonia produced by the deamination of amino acids. It is the principal end product of protein catabolism and constitutes about one half of the total urinary solids. |
| biotin | A water-soluble, enzyme co-factor present in minute amounts in every living cell. It occurs mainly bound to proteins or polypeptides and is abundant in liver, kidney, pancreas, yeast, and milk. |
| ammonium hydroxide | The hydroxy salt of ammonium ion. It is formed when AMMONIA reacts with water molecules in solution. |
| Zinc | A metallic element of atomic number 30 and atomic weight 65.38. It is a necessary trace element in the diet, forming an essential part of many enzymes, and playing an important role in protein synthesis and in cell division. Zinc deficiency is associated with ANEMIA, short stature, HYPOGONADISM, impaired WOUND HEALING, and geophagia. It is known by the symbol Zn. |
| Carbon Dioxide | A colorless, odorless gas that can be formed by the body and is necessary for the respiration cycle of plants and animals. |
| serum p-component | close relation to C reactive protein; may be ovosomucoid |
| glutamic acid | A non-essential amino acid naturally occurring in the L-form. Glutamic acid is the most common excitatory neurotransmitter in the CENTRAL NERVOUS SYSTEM. |
| hydrogen sulfide | A flammable, poisonous gas with a characteristic odor of rotten eggs. It is used in the manufacture of chemicals, in metallurgy, and as an analytical reagent. (From Merck Index, 11th ed) |
| NADH | |
| fumaric acid | see also record for ferrous fumarate; use FUMARATES for general fumaric acid esters |
| creatine | An amino acid that occurs in vertebrate tissues and in urine. In muscle tissue, creatine generally occurs as phosphocreatine. Creatine is excreted as CREATININE in the urine. |
| cysteine | A thiol-containing non-essential amino acid that is oxidized to form CYSTINE. |
| Adenosine Triphosphate | An adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter. |
| aspartic acid | One of the non-essential amino acids commonly occurring in the L-form. It is found in animals and plants, especially in sugar cane and sugar beets. It may be a neurotransmitter. |
| glutamine | A non-essential amino acid present abundantly throughout the body and is involved in many metabolic processes. It is synthesized from GLUTAMIC ACID and AMMONIA. It is the principal carrier of NITROGEN in the body and is an important energy source for many cells. |
| lysine | An essential amino acid. It is often added to animal feed. |
| adenosine diphosphate | Adenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position. |
| adenosine monophosphate | Adenine nucleotide containing one phosphate group esterified to the sugar moiety in the 2'-, 3'-, or 5'-position. |
| berlition | antioxidant preparation containing alpha-lipoic acid, used in the neuroprotective therapy of chronic brain ischemia for correction of free-radical processes |
| ornithine | An amino acid produced in the urea cycle by the splitting off of urea from arginine. |
| flavin-adenine dinucleotide | A condensation product of riboflavin and adenosine diphosphate. The coenzyme of various aerobic dehydrogenases, e.g., D-amino acid oxidase and L-amino acid oxidase. (Lehninger, Principles of Biochemistry, 1982, p972) |
| glucose, (beta-d)-isomer | |
| glycine | A non-essential amino acid. It is found primarily in gelatin and silk fibroin and used therapeutically as a nutrient. It is also a fast inhibitory neurotransmitter. |
| Hydrogen Peroxide | A strong oxidizing agent used in aqueous solution as a ripening agent, bleach, and topical anti-infective. It is relatively unstable and solutions deteriorate over time unless stabilized by the addition of acetanilide or similar organic materials. |
| Water | A clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed) |
| Guanosine Monophosphate | A guanine nucleotide containing one phosphate group esterified to the sugar moiety and found widely in nature. |
| hypoxanthine | A purine and a reaction intermediate in the metabolism of adenosine and in the formation of nucleic acids by the salvage pathway. |
| cysteine sulfinic acid | metabolite of sulfur-containing amino acids |
| phosphoenolpyruvate | A monocarboxylic acid anion derived from selective deprotonation of the carboxy group of phosphoenolpyruvic acid. It is a metabolic intermediate in GLYCOLYSIS; GLUCONEOGENESIS; and other pathways. |
| fructose-1,6-diphosphate | RN refers to (D)-isomer |
| phosphohydroxypyruvic acid | |
| sulfites | Inorganic salts of sulfurous acid. |
| uric acid | An oxidation product, via XANTHINE OXIDASE, of oxypurines such as XANTHINE and HYPOXANTHINE. It is the final oxidation product of purine catabolism in humans and primates, whereas in most other mammals URATE OXIDASE further oxidizes it to ALLANTOIN. |
| saccharopine | lysine precursor in the aminoadipic acid-lysine pathway in yeast; minor descriptor (75-85); on-line & Index Medicus search LYSINE/analogs & derivatives (75-85); RN given refers to (L)-isomer |
| allysine | structure |
| alpha-Ketoglutarate | |
| Argininosuccinic Acid | This amino acid is formed during the urea cycle from citrulline, aspartate and ATP. This reaction is catalyzed by argininosuccinic acid synthetase. |
| carbamyl phosphate | The monoanhydride of carbamic acid with PHOSPHORIC ACID. It is an important intermediate metabolite and is synthesized enzymatically by CARBAMYL-PHOSPHATE SYNTHASE (AMMONIA) and CARBAMOYL-PHOSPHATE SYNTHASE (GLUTAMINE-HYDROLYZING). |
| glutaryl-coenzyme a | |
| dihydrolipoic acid | RN given refers to parent cpd without isomeric designation |
| glyceraldehyde 3-phosphate | An aldotriose which is an important intermediate in glycolysis and in tryptophan biosynthesis. |
| glycerate 1,3-biphosphate | |
| pipecolic acid | RN given refers to cpd without isomeric designation |
| Cystathionine | Sulfur-containing amino acid formed as an intermediate in the conversion of METHIONINE to CYSTEINE. |
| alpha-ketoglutaric acid | |
| adenosine triphosphate | An adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter. |
| crotonyl-coenzyme a | |
| alpha-ketobutyric acid | RN given refers to parent cpd; structure |
| nadp | Nicotinamide adenine dinucleotide phosphate. A coenzyme composed of ribosylnicotinamide 5'-phosphate (NMN) coupled by pyrophosphate linkage to the 5'-phosphate adenosine 2',5'-bisphosphate. It serves as an electron carrier in a number of reactions, being alternately oxidized (NADP+) and reduced (NADPH). (Dorland, 27th ed) |
| nad | A coenzyme composed of ribosylnicotinamide 5'-diphosphate coupled to adenosine 5'-phosphate by pyrophosphate linkage. It is found widely in nature and is involved in numerous enzymatic reactions in which it serves as an electron carrier by being alternately oxidized (NAD+) and reduced (NADH). (Dorland, 27th ed) |
| 2-phosphoglycerate | RN given refers to cpd without isomeric designation |
| alanine | A non-essential amino acid that occurs in high levels in its free state in plasma. It is produced from pyruvate by transamination. It is involved in sugar and acid metabolism, increases IMMUNITY, and provides energy for muscle tissue, BRAIN, and the CENTRAL NERVOUS SYSTEM. |
| dihydroxyacetone phosphate | An important intermediate in lipid biosynthesis and in glycolysis. |
| alpha-ketoadipic acid | |
| 3-phosphoglycerate | |
| glycocyamine | RN given refers to parent cpd; structure |
| oxaloacetic acid | A dicarboxylic acid ketone that is an important metabolic intermediate of the CITRIC ACID CYCLE. It can be converted to ASPARTIC ACID by ASPARTATE TRANSAMINASE. |
| orotidylic acid | structure |
| s-adenosylhomocysteine | 5'-S-(3-Amino-3-carboxypropyl)-5'-thioadenosine. Formed from S-adenosylmethionine after transmethylation reactions. |
| acetyl coenzyme a | Acetyl CoA participates in the biosynthesis of fatty acids and sterols, in the oxidation of fatty acids and in the metabolism of many amino acids. It also acts as a biological acetylating agent. |
| plasmenylserine | RN given refers to (L)-isomer |
| biocytin | |
| coenzyme a | |
| homocysteine | A thiol-containing amino acid formed by a demethylation of METHIONINE. |
| acetoacetyl coa | |
| citrulline | |