| Protein | Synonyms | Taxonomy |
|---|
| Alpha-L-iduronidase | EC 3.2.1.76 | Homo sapiens (human) |
| Heparanase | EC 3.2.1.166; Endo-glucoronidase; Heparanase-1; Hpa1 | Homo sapiens (human) |
| Inactive heparanase-2 | Hpa2 | Homo sapiens (human) |
| Exostosin-2 | EC 2.4.1.224; EC 2.4.1.225; Glucuronosyl-N-acetylglucosaminyl-proteoglycan/N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase; Multiple exostoses protein 2; Putative tumor suppressor protein EXT2 | Homo sapiens (human) |
| Beta-glucuronidase | EC 3.2.1.31; Beta-G1 | Homo sapiens (human) |
| Iduronate 2-sulfatase | EC 3.1.6.13; Alpha-L-iduronate sulfate sulfatase; Idursulfase | Homo sapiens (human) |
| Beta-1,4-galactosyltransferase 7 | Beta-1,4-GalTase 7; Beta4Gal-T7; b4Gal-T7; EC 2.4.1.-; Proteoglycan UDP-galactose:beta-xylose beta1,4-galactosyltransferase I; UDP-Gal:beta-GlcNAc beta-1,4-galactosyltransferase 7; UDP-galactose:beta-N-acetylglucosamine beta-1,4-galactosyltransferase 7; U | Homo sapiens (human) |
| Galactosylgalactosylxylosylprotein 3-beta-glucuronosyltransferase 3 | EC 2.4.1.135; Beta-1,3-glucuronyltransferase 3; Glucuronosyltransferase I; GlcAT-I; UDP-GlcUA:Gal beta-1,3-Gal-R glucuronyltransferase; GlcUAT-I | Homo sapiens (human) |
| Galactosylgalactosylxylosylprotein 3-beta-glucuronosyltransferase 2 | EC 2.4.1.135; Beta-1,3-glucuronyltransferase 2; GlcAT-D; UDP-glucuronosyltransferase S; GlcAT-S; Glucuronosyltransferase S | Homo sapiens (human) |
| Exostosin-1 | EC 2.4.1.224; EC 2.4.1.225; Glucuronosyl-N-acetylglucosaminyl-proteoglycan/N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase; Multiple exostoses protein 1; Putative tumor suppressor protein EXT1 | Homo sapiens (human) |
| Galactosylgalactosylxylosylprotein 3-beta-glucuronosyltransferase 1 | EC 2.4.1.135; Beta-1,3-glucuronyltransferase 1; Glucuronosyltransferase P; GlcAT-P; UDP-GlcUA:glycoprotein beta-1,3-glucuronyltransferase; GlcUAT-P | Homo sapiens (human) |
| Heparan sulfate glucosamine 3-O-sulfotransferase 1 | EC 2.8.2.23; Heparan sulfate D-glucosaminyl 3-O-sulfotransferase 1; 3-OST-1; Heparan sulfate 3-O-sulfotransferase 1; h3-OST-1 | Homo sapiens (human) |
| Beta-1,3-galactosyltransferase 6 | Beta-1,3-GalTase 6; Beta3Gal-T6; Beta3GalT6; EC 2.4.1.134; GAG GalTII; Galactosyltransferase II; Galactosylxylosylprotein 3-beta-galactosyltransferase; UDP-Gal:betaGal beta 1,3-galactosyltransferase polypeptide 6 | Homo sapiens (human) |
| D-glucuronyl C5-epimerase | EC 5.1.3.17; Heparan sulfate C5-epimerase; Hsepi; Heparin/heparan sulfate:glucuronic acid C5-epimerase; Heparosan-N-sulfate-glucuronate 5-epimerase | Homo sapiens (human) |
| N-sulphoglucosamine sulphohydrolase | EC 3.10.1.1; Sulfoglucosamine sulfamidase; Sulphamidase | Homo sapiens (human) |
| Alpha-N-acetylglucosaminidase | EC 3.2.1.50; N-acetyl-alpha-glucosaminidase; NAG | Homo sapiens (human) |
| UDP-N-acetylglucosamine/UDP-glucose/GDP-mannose transporter | Homolog of Fringe connection protein 1; HFRC1; SQV7-like protein; SQV7L; Solute carrier family 35 member D2; UDP-galactose transporter-related protein 8; UGTrel8 | Homo sapiens (human) |
| Heparan sulfate 2-O-sulfotransferase 1 | 2-O-sulfotransferase; 2OST; EC 2.8.2.- | Homo sapiens (human) |
| Compound | Description |
|---|
| Acetylglucosamine | The N-acetyl derivative of glucosamine. |
| acetic acid | Product of the oxidation of ethanol and of the destructive distillation of wood. It is used locally, occasionally internally, as a counterirritant and also as a reagent. (Stedman, 26th ed) |
| uridine diphosphate | A uracil nucleotide containing a pyrophosphate group esterified to C5 of the sugar moiety. |
| Calcium | A basic element found in nearly all tissues. It is a member of the alkaline earth family of metals with the atomic symbol Ca, atomic number 20, and atomic weight 40. Calcium is the most abundant mineral in the body and combines with phosphorus to form calcium phosphate in the bones and teeth. It is essential for the normal functioning of nerves and muscles and plays a role in blood coagulation (as factor IV) and in many enzymatic processes. |
| Manganese | A trace element with atomic symbol Mn, atomic number 25, and atomic weight 54.94. It is concentrated in cell mitochondria, mostly in the pituitary gland, liver, pancreas, kidney, and bone, influences the synthesis of mucopolysaccharides, stimulates hepatic synthesis of cholesterol and fatty acids, and is a cofactor in many enzymes, including arginase and alkaline phosphatase in the liver. (From AMA Drug Evaluations Annual 1992, p2035) |
| galactose | An aldohexose that occurs naturally in the D-form in lactose, cerebrosides, gangliosides, and mucoproteins. Deficiency of galactosyl-1-phosphate uridyltransferase (GALACTOSE-1-PHOSPHATE URIDYL-TRANSFERASE DEFICIENCY DISEASE) causes an error in galactose metabolism called GALACTOSEMIA, resulting in elevations of galactose in the blood. |
| Aspartate | |
| Xylose | |
| Water | A clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed) |
| Uridine Monophosphate | 5'-Uridylic acid. A uracil nucleotide containing one phosphate group esterified to the sugar moiety in the 2', 3' or 5' position. |
| adenosine 3'-phosphate-5'-phosphate | |
| Coenzyme A | |
| Acetyl Coenzyme A | Acetyl CoA participates in the biosynthesis of fatty acids and sterols, in the oxidation of fatty acids and in the metabolism of many amino acids. It also acts as a biological acetylating agent. |