Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex, mitochondrial | EC 2.3.1.12; 70 kDa mitochondrial autoantigen of primary biliary cirrhosis; PBC; Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex; M2 antigen complex 70 kDa subunit; Pyruvate dehydrogenase complex component E2; PDC-E2; PDCE2 | Homo sapiens (human) |
Succinate dehydrogenase [ubiquinone] iron-sulfur subunit, mitochondrial | EC 1.3.5.1; Iron-sulfur subunit of complex II; Ip | Homo sapiens (human) |
Pyruvate dehydrogenase E1 component subunit beta, mitochondrial | PDHE1-B; EC 1.2.4.1 | Homo sapiens (human) |
Citrate synthase, mitochondrial | EC 2.3.3.1; Citrate (Si)-synthase | Homo sapiens (human) |
Isocitrate dehydrogenase [NAD] subunit alpha, mitochondrial | EC 1.1.1.41; Isocitric dehydrogenase subunit alpha; NAD(+)-specific ICDH subunit alpha | Homo sapiens (human) |
Succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial | EC 1.3.5.1; Flavoprotein subunit of complex II; Fp | Homo sapiens (human) |
Aconitate hydratase, mitochondrial | Aconitase; EC 4.2.1.3; Citrate hydro-lyase | Homo sapiens (human) |
Succinate dehydrogenase cytochrome b560 subunit, mitochondrial | Integral membrane protein CII-3; QPs-1; QPs1; Succinate dehydrogenase complex subunit C; Succinate-ubiquinone oxidoreductase cytochrome B large subunit; CYBL | Homo sapiens (human) |
Malate dehydrogenase, cytoplasmic | EC 1.1.1.37; Cytosolic malate dehydrogenase; Diiodophenylpyruvate reductase; 1.1.1.96 | Homo sapiens (human) |
Dihydrolipoyl dehydrogenase, mitochondrial | EC 1.8.1.4; Dihydrolipoamide dehydrogenase; Glycine cleavage system L protein | Homo sapiens (human) |
Pyruvate carboxylase, mitochondrial | EC 6.4.1.1; Pyruvic carboxylase; PCB | Homo sapiens (human) |
Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial | EC 1.2.4.1; PDHE1-A type I | Homo sapiens (human) |
Probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial | EC 1.2.4.2; Dehydrogenase E1 and transketolase domain-containing protein 1 | Homo sapiens (human) |
Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial | EC 6.2.1.4; EC 6.2.1.5; Succinyl-CoA synthetase subunit alpha; SCS-alpha | Homo sapiens (human) |
Dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial | EC 2.3.1.61; 2-oxoglutarate dehydrogenase complex component E2; OGDC-E2; Dihydrolipoamide succinyltransferase component of 2-oxoglutarate dehydrogenase complex; E2K | Homo sapiens (human) |
Succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial | EC 6.2.1.4; GTP-specific succinyl-CoA synthetase subunit beta; G-SCS; GTPSCS; Succinyl-CoA synthetase beta-G chain; SCS-betaG | Homo sapiens (human) |
Succinate dehydrogenase [ubiquinone] cytochrome b small subunit, mitochondrial | CybS; CII-4; QPs3; Succinate dehydrogenase complex subunit D; Succinate-ubiquinone oxidoreductase cytochrome b small subunit; Succinate-ubiquinone reductase membrane anchor subunit | Homo sapiens (human) |
Isocitrate dehydrogenase [NAD] subunit beta, mitochondrial | Isocitric dehydrogenase subunit beta; NAD(+)-specific ICDH subunit beta | Homo sapiens (human) |
Fumarate hydratase, mitochondrial | Fumarase; HsFH; EC 4.2.1.2 | Homo sapiens (human) |
Isocitrate dehydrogenase [NAD] subunit gamma, mitochondrial | Isocitric dehydrogenase subunit gamma; NAD(+)-specific ICDH subunit gamma | Homo sapiens (human) |
Mitochondrial pyruvate carrier 1 | Brain protein 44-like protein | Homo sapiens (human) |