Page last updated: 2024-10-06

Degradation pathway of sphingolipids, including diseases

Proteins (9)

ProteinSynonymsTaxonomy
Lysosomal acid glucosylceramidaseLysosomal acid GCase; EC 3.2.1.45; Acid beta-glucosidase; Alglucerase; Beta-glucocerebrosidase; Beta-GC; Cholesterol glucosyltransferase; SGTase; 2.4.1.-; Cholesteryl-beta-glucosidase; 3.2.1.-; D-glucosyl-N-acylsphingosine glucohydrolase; ImigluceraseHomo sapiens (human)
Beta-hexosaminidase subunit alphaEC 3.2.1.52; Beta-N-acetylhexosaminidase subunit alpha; Hexosaminidase subunit A; N-acetyl-beta-glucosaminidase subunit alphaHomo sapiens (human)
Beta-hexosaminidase subunit betaEC 3.2.1.52; Beta-N-acetylhexosaminidase subunit beta; Hexosaminidase subunit B; Cervical cancer proto-oncogene 7 protein; HCC-7; N-acetyl-beta-glucosaminidase subunit betaHomo sapiens (human)
Sialidase-4EC 3.2.1.18; N-acetyl-alpha-neuraminidase 4Homo sapiens (human)
Sialidase-3EC 3.2.1.18; Ganglioside sialidasedis; Membrane sialidase; N-acetyl-alpha-neuraminidase 3Homo sapiens (human)
Sialidase-2EC 3.2.1.18; Cytosolic sialidase; N-acetyl-alpha-neuraminidase 2Homo sapiens (human)
Sialidase-1EC 3.2.1.18; Acetylneuraminyl hydrolase; G9 sialidase; Lysosomal sialidase; N-acetyl-alpha-neuraminidase 1Homo sapiens (human)
ProsaposinProactivator polypeptideHomo sapiens (human)
GalactocerebrosidaseGALCERase; EC 3.2.1.46; Galactocerebroside beta-galactosidase; Galactosylceramidase; Galactosylceramide beta-galactosidaseHomo sapiens (human)

Compounds (1)

CompoundDescription
globotriaosylceramidereceptor for Shigella