Page last updated: 2024-10-06

Complex I biogenesis

Proteins (57)

ProteinSynonymsTaxonomy
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2B17.2-like; B17.2L; Mimitin; Myc-induced mitochondrial protein; MMTN; NDUFA12-like proteinHomo sapiens (human)
Protein arginine methyltransferase NDUFAF7, mitochondrialEC 2.1.1.320; NADH dehydrogenase [ubiquinone] complex I, assembly factor 7; Protein midA homologHomo sapiens (human)
NADH dehydrogenase [ubiquinone] iron-sulfur protein 8, mitochondrialEC 7.1.1.2; Complex I-23kD; CI-23kD; NADH-ubiquinone oxidoreductase 23 kDa subunit; TYKY subunitHomo sapiens (human)
Acyl carrier protein, mitochondrialACP; CI-SDAP; NADH-ubiquinone oxidoreductase 9.6 kDa subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 subunit C1, mitochondrialComplex I-KFYI; CI-KFYI; NADH-ubiquinone oxidoreductase KFYI subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrialEC 7.1.1.2; Complex I-49kD; CI-49kD; NADH-ubiquinone oxidoreductase 49 kDa subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrialComplex I-13kD-A; CI-13kD-A; NADH-ubiquinone oxidoreductase 13 kDa-A subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 4 Complex I-B15; CI-B15; NADH-ubiquinone oxidoreductase B15 subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 7Complex I-B14.5a; CI-B14.5a; NADH-ubiquinone oxidoreductase subunit B14.5aHomo sapiens (human)
NADH-ubiquinone oxidoreductase chain 4EC 7.1.1.2; NADH dehydrogenase subunit 4Homo sapiens (human)
NADH-ubiquinone oxidoreductase chain 5EC 7.1.1.2; NADH dehydrogenase subunit 5Homo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 7Cell adhesion protein SQM1; Complex I-B18; CI-B18; NADH-ubiquinone oxidoreductase B18 subunitHomo sapiens (human)
NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrialEC 7.1.1.2; Complex I-75kD; CI-75kDHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 6Complex I-B14; CI-B14; LYR motif-containing protein 6; NADH-ubiquinone oxidoreductase B14 subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 11, mitochondrialComplex I-ESSS; CI-ESSS; NADH-ubiquinone oxidoreductase ESSS subunit; Neuronal protein 17.3; Np17.3; p17.3Homo sapiens (human)
Complex I intermediate-associated protein 30, mitochondrialNADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1Homo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1Complex I-MWFE; CI-MWFE; NADH-ubiquinone oxidoreductase MWFE subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] iron-sulfur protein 4, mitochondrialComplex I-18 kDa; CI-18 kDa; Complex I-AQDQ; CI-AQDQ; NADH-ubiquinone oxidoreductase 18 kDa subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 5, mitochondrialComplex I-SGDH; CI-SGDH; NADH-ubiquinone oxidoreductase SGDH subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 3Complex I-B12; CI-B12; NADH-ubiquinone oxidoreductase B12 subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 2 Complex I-B8; CI-B8; NADH-ubiquinone oxidoreductase B8 subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] iron-sulfur protein 5Complex I-15 kDa; CI-15 kDa; NADH-ubiquinone oxidoreductase 15 kDa subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] iron-sulfur protein 7, mitochondrialEC 7.1.1.2; Complex I-20kD; CI-20kD; NADH-ubiquinone oxidoreductase 20 kDa subunit; PSST subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 1Complex I-MNLL; CI-MNLL; NADH-ubiquinone oxidoreductase MNLL subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] iron-sulfur protein 3, mitochondrialEC 7.1.1.2; Complex I-30kD; CI-30kD; NADH-ubiquinone oxidoreductase 30 kDa subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 6Complex I-B17; CI-B17; NADH-ubiquinone oxidoreductase B17 subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 3Complex I-B9; CI-B9; NADH-ubiquinone oxidoreductase B9 subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 8, mitochondrialComplex I-ASHI; CI-ASHI; NADH-ubiquinone oxidoreductase ASHI subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 2, mitochondrialComplex I-AGGG; CI-AGGG; NADH-ubiquinone oxidoreductase AGGG subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 subunit C2Complex I-B14.5b; CI-B14.5b; Human lung cancer oncogene 1 protein; HLC-1; NADH-ubiquinone oxidoreductase subunit B14.5bHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 10, mitochondrialComplex I-42kD; CI-42kD; NADH-ubiquinone oxidoreductase 42 kDa subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 10Complex I-PDSW; CI-PDSW; NADH-ubiquinone oxidoreductase PDSW subunitHomo sapiens (human)
NADH-ubiquinone oxidoreductase chain 1EC 7.1.1.2; NADH dehydrogenase subunit 1Homo sapiens (human)
NADH-ubiquinone oxidoreductase chain 2EC 7.1.1.2; NADH dehydrogenase subunit 2Homo sapiens (human)
NADH-ubiquinone oxidoreductase chain 3EC 7.1.1.2; NADH dehydrogenase subunit 3Homo sapiens (human)
NADH-ubiquinone oxidoreductase chain 6EC 7.1.1.2; NADH dehydrogenase subunit 6Homo sapiens (human)
NADH dehydrogenase [ubiquinone] flavoprotein 2, mitochondrialEC 7.1.1.2; NADH-ubiquinone oxidoreductase 24 kDa subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrialEC 7.1.1.2; Complex I-51kD; CI-51kD; NADH dehydrogenase flavoprotein 1; NADH-ubiquinone oxidoreductase 51 kDa subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 8Complex I-19kD; CI-19kD; Complex I-PGIV; CI-PGIV; NADH-ubiquinone oxidoreductase 19 kDa subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] flavoprotein 3, mitochondrialComplex I-9kD; CI-9kD; NADH-ubiquinone oxidoreductase 9 kDa subunit; Renal carcinoma antigen NY-REN-4Homo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 5Complex I subunit B13; Complex I-13kD-B; CI-13kD-B; NADH-ubiquinone oxidoreductase 13 kDa-B subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 9, mitochondrialComplex I-39kD; CI-39kD; NADH-ubiquinone oxidoreductase 39 kDa subunitHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 11Complex I-B14.7; CI-B14.7; NADH-ubiquinone oxidoreductase subunit B14.7Homo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3Homo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4Hormone-regulated proliferation-associated protein of 20 kDaHomo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 13Cell death regulatory protein GRIM-19; Complex I-B16.6; CI-B16.6; Gene associated with retinoic and interferon-induced mortality 19 protein; GRIM-19; Gene associated with retinoic and IFN-induced mortality 19 protein; NADH-ubiquinone oxidoreductase B16.6 Homo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1213 kDa differentiation-associated protein; Complex I-B17.2; CI-B17.2; CIB17.2; NADH-ubiquinone oxidoreductase subunit B17.2Homo sapiens (human)
NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 9Complex I-B22; CI-B22; LYR motif-containing protein 3; NADH-ubiquinone oxidoreductase B22 subunitHomo sapiens (human)
NADH dehydrogenase (ubiquinone) complex I, assembly factor 6Putative phytoene synthaseHomo sapiens (human)
Arginine-hydroxylase NDUFAF5, mitochondrialEC 1.-.-.-; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5; Putative methyltransferase NDUFAF5; 2.1.1.-Homo sapiens (human)
Complex I assembly factor TMEM126B, mitochondrialTransmembrane protein 126BHomo sapiens (human)
Iron-sulfur protein NUBPLIND1 homolog; Nucleotide-binding protein-like; huInd1Homo sapiens (human)
Transmembrane protein 186Homo sapiens (human)
Evolutionarily conserved signaling intermediate in Toll pathway, mitochondrialProtein SITPECHomo sapiens (human)
Cytochrome c oxidase assembly factor 1 homologMitochondrial translation regulation assembly intermediate of cytochrome c oxidase protein of 15 kDaHomo sapiens (human)
Complex I assembly factor ACAD9, mitochondrialAcyl-CoA dehydrogenase family member 9; ACAD-9; 1.3.8.-Homo sapiens (human)
Complex I assembly factor TIMMDC1, mitochondrialProtein M5-14; Translocase of inner mitochondrial membrane domain-containing protein 1; TIMM domain containing-protein 1Homo sapiens (human)

Compounds (2)

CompoundDescription
Flavin MononucleotideA coenzyme for a number of oxidative enzymes including NADH DEHYDROGENASE. It is the principal form in which RIBOFLAVIN is found in cells and tissues.
Flavin-Adenine DinucleotideA condensation product of riboflavin and adenosine diphosphate. The coenzyme of various aerobic dehydrogenases, e.g., D-amino acid oxidase and L-amino acid oxidase. (Lehninger, Principles of Biochemistry, 1982, p972)