Protein | Synonyms | Taxonomy |
Arginine--tRNA ligase, cytoplasmic | EC 6.1.1.19; Arginyl-tRNA synthetase; ArgRS | Homo sapiens (human) |
Hydroxyacid oxidase 1 | HAOX1; EC 1.1.3.15; Glycolate oxidase; GOX | Homo sapiens (human) |
Glycoprotein hormones alpha chain | Anterior pituitary glycoprotein hormones common subunit alpha; Choriogonadotropin alpha chain; Chorionic gonadotrophin subunit alpha; CG-alpha; Follicle-stimulating hormone alpha chain; FSH-alpha; Follitropin alpha chain; Luteinizing hormone alpha chain; | Homo sapiens (human) |
[3-methyl-2-oxobutanoate dehydrogenase [lipoamide]] kinase, mitochondrial | EC 2.7.11.4; Branched-chain alpha-ketoacid dehydrogenase kinase; BCKD-kinase; BCKDHKIN | Homo sapiens (human) |
Branched-chain-amino-acid aminotransferase, mitochondrial | BCAT(m); EC 2.6.1.42; Placental protein 18; PP18 | Homo sapiens (human) |
Aspartate aminotransferase, mitochondrial | mAspAT; EC 2.6.1.1; EC 2.6.1.7; Fatty acid-binding protein; FABP-1; Glutamate oxaloacetate transaminase 2; Kynurenine aminotransferase 4; Kynurenine aminotransferase IV; Kynurenine--oxoglutarate transaminase 4; Kynurenine--oxoglutarate transaminase IV; Pl | Homo sapiens (human) |
Thyroid peroxidase | TPO; EC 1.11.1.8 | Homo sapiens (human) |
Serine--pyruvate aminotransferase | SPT; EC 2.6.1.51; Alanine--glyoxylate aminotransferase; AGT; 2.6.1.44 | Homo sapiens (human) |
Cystathionine gamma-lyase | EC 4.4.1.1; Cysteine-protein sulfhydrase; Gamma-cystathionase | Homo sapiens (human) |
4-trimethylaminobutyraldehyde dehydrogenase | TMABA-DH; TMABALDH; EC 1.2.1.47; Aldehyde dehydrogenase E3 isozyme; Aldehyde dehydrogenase family 9 member A1; 1.2.1.3; Gamma-aminobutyraldehyde dehydrogenase; 1.2.1.19; R-aminobutyraldehyde dehydrogenase | Homo sapiens (human) |
Iodotyrosine deiodinase 1 | IYD-1; EC 1.21.1.1; Iodotyrosine dehalogenase 1 | Homo sapiens (human) |
2-amino-3-carboxymuconate-6-semialdehyde decarboxylase | EC 4.1.1.45; Picolinate carboxylase | Homo sapiens (human) |
Glutaryl-CoA dehydrogenase, mitochondrial | GCD; EC 1.3.8.6 | Homo sapiens (human) |
3-hydroxyacyl-CoA dehydrogenase type-2 | EC 1.1.1.35; 17-beta-estradiol 17-dehydrogenase; 1.1.1.62; 2-methyl-3-hydroxybutyryl-CoA dehydrogenase; MHBD; 3-alpha-(17-beta)-hydroxysteroid dehydrogenase (NAD(+)); 1.1.1.239; 3-hydroxy-2-methylbutyryl-CoA dehydrogenase; 1.1.1.178; 3-hydroxyacyl-CoA deh | Homo sapiens (human) |
NmrA-like family domain-containing protein 1 | | Homo sapiens (human) |
Hydroxyproline dehydrogenase | HYPDH; EC 1.5.5.3; Kidney and liver proline oxidase 1; HsPOX1; Probable proline dehydrogenase 2; 1.5.5.2; Probable proline oxidase 2 | Homo sapiens (human) |
Glutaminase liver isoform, mitochondrial | GLS; EC 3.5.1.2; L-glutaminase; L-glutamine amidohydrolase | Homo sapiens (human) |
Sulfide:quinone oxidoreductase, mitochondrial | SQOR; EC 1.8.5.8; Sulfide dehydrogenase-like; Sulfide quinone oxidoreductase | Homo sapiens (human) |
Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial | P5C dehydrogenase; EC 1.2.1.88; Aldehyde dehydrogenase family 4 member A1; L-glutamate gamma-semialdehyde dehydrogenase | Homo sapiens (human) |
D-amino-acid oxidase | DAAO; DAMOX; DAO; EC 1.4.3.3 | Homo sapiens (human) |
Proteasome subunit beta type-9 | EC 3.4.25.1; Low molecular mass protein 2; Macropain chain 7; Multicatalytic endopeptidase complex chain 7; Proteasome chain 7; Proteasome subunit beta-1i; Really interesting new gene 12 protein | Homo sapiens (human) |
Glutamine synthetase | GS; EC 6.3.1.2; Glutamate--ammonia ligase; Palmitoyltransferase GLUL; 2.3.1.225 | Homo sapiens (human) |
Isoleucine--tRNA ligase, cytoplasmic | EC 6.1.1.5; Isoleucyl-tRNA synthetase; IRS; IleRS | Homo sapiens (human) |
Methionine--tRNA ligase, cytoplasmic | EC 6.1.1.10; Methionyl-tRNA synthetase; MetRS | Homo sapiens (human) |
5,6-dihydroxyindole-2-carboxylic acid oxidase | DHICA oxidase; EC 1.14.18.-; Catalase B; Glycoprotein 75; Melanoma antigen gp75; Tyrosinase-related protein 1; TRP; TRP-1; TRP1 | Homo sapiens (human) |
Enoyl-CoA hydratase, mitochondrial | EC 4.2.1.17; Enoyl-CoA hydratase 1; Short-chain enoyl-CoA hydratase; SCEH | Homo sapiens (human) |
Maleylacetoacetate isomerase | MAAI; EC 5.2.1.2; GSTZ1-1; Glutathione S-transferase zeta 1; 2.5.1.18 | Homo sapiens (human) |
Alanine aminotransferase 1 | ALT1; EC 2.6.1.2; Glutamate pyruvate transaminase 1; GPT 1; Glutamic--alanine transaminase 1; Glutamic--pyruvic transaminase 1 | Homo sapiens (human) |
Serine hydroxymethyltransferase, cytosolic | SHMT; EC 2.1.2.1; Glycine hydroxymethyltransferase; Serine methylase | Homo sapiens (human) |
Tyrosinase | EC 1.14.18.1; LB24-AB; Monophenol monooxygenase; SK29-AB; Tumor rejection antigen AB | Homo sapiens (human) |
Indoleamine 2,3-dioxygenase 1 | IDO-1; EC 1.13.11.52; Indoleamine-pyrrole 2,3-dioxygenase | Homo sapiens (human) |
NAD | EC 1.6.5.2; Azoreductase; DT-diaphorase; DTD; Menadione reductase; NAD(P)H:quinone oxidoreductase 1; Phylloquinone reductase; Quinone reductase 1; QR1 | Homo sapiens (human) |
S-adenosylmethionine decarboxylase proenzyme | AdoMetDC; SAMDC; EC 4.1.1.50 | Homo sapiens (human) |
Proteasome subunit beta type-1 | Macropain subunit C5; Multicatalytic endopeptidase complex subunit C5; Proteasome component C5; Proteasome gamma chain | Homo sapiens (human) |
Adenosylhomocysteinase | AdoHcyase; EC 3.3.1.1; S-adenosyl-L-homocysteine hydrolase | Homo sapiens (human) |
D-aspartate oxidase | DASOX; DDO; EC 1.4.3.1 | Homo sapiens (human) |
Serine racemase | EC 5.1.1.18; D-serine ammonia-lyase; D-serine dehydratase; 4.3.1.18; L-serine ammonia-lyase; L-serine dehydratase; 4.3.1.17 | Homo sapiens (human) |
Aminoacyl tRNA synthase complex-interacting multifunctional protein 2 | Multisynthase complex auxiliary component p38; Protein JTV-1 | Homo sapiens (human) |
Indoleamine 2,3-dioxygenase 2 | IDO-2; EC 1.13.11.-; Indoleamine 2,3-dioxygenase-like protein 1; Indoleamine-pyrrole 2,3-dioxygenase-like protein 1 | Homo sapiens (human) |
Dimethylaniline monooxygenase [N-oxide-forming] 1 | EC 1.14.13.8; Dimethylaniline oxidase 1; Fetal hepatic flavin-containing monooxygenase 1; FMO 1 | Homo sapiens (human) |
Aminoacyl tRNA synthase complex-interacting multifunctional protein 1 | Multisynthase complex auxiliary component p43 | Homo sapiens (human) |
Pyrroline-5-carboxylate reductase 1, mitochondrial | P5C reductase 1; P5CR 1; EC 1.5.1.2 | Homo sapiens (human) |
Proteasome activator complex subunit 3 | 11S regulator complex subunit gamma; REG-gamma; Activator of multicatalytic protease subunit 3; Ki nuclear autoantigen; Proteasome activator 28 subunit gamma; PA28g; PA28gamma | Homo sapiens (human) |
Pyrroline-5-carboxylate reductase 2 | P5C reductase 2; P5CR 2; EC 1.5.1.2 | Homo sapiens (human) |
Glyoxylate reductase/hydroxypyruvate reductase | EC 1.1.1.79; EC 1.1.1.81 | Homo sapiens (human) |
Leucine--tRNA ligase, cytoplasmic | EC 6.1.1.4; Leucyl-tRNA synthetase; LeuRS | Homo sapiens (human) |
Ornithine aminotransferase, mitochondrial | EC 2.6.1.13; Ornithine delta-aminotransferase; Ornithine--oxo-acid aminotransferase | Homo sapiens (human) |
Creatine kinase M-type | EC 2.7.3.2; Creatine kinase M chain; Creatine phosphokinase M-type; CPK-M; M-CK | Homo sapiens (human) |
Tyrosine 3-monooxygenase | EC 1.14.16.2; Tyrosine 3-hydroxylase; TH | Homo sapiens (human) |
Ornithine decarboxylase | ODC; EC 4.1.1.17 | Homo sapiens (human) |
Creatine kinase B-type | EC 2.7.3.2; Brain creatine kinase; B-CK; Creatine kinase B chain; Creatine phosphokinase B-type; CPK-B | Homo sapiens (human) |
Tyrosine aminotransferase | TAT; EC 2.6.1.5; L-tyrosine:2-oxoglutarate aminotransferase | Homo sapiens (human) |
Spermidine synthase | SPDSY; EC 2.5.1.16; Putrescine aminopropyltransferase | Homo sapiens (human) |
Proteasome subunit beta type-3 | Proteasome chain 13; Proteasome component C10-II; Proteasome theta chain | Homo sapiens (human) |
Large neutral amino acids transporter small subunit 1 | 4F2 light chain; 4F2 LC; 4F2LC; CD98 light chain; Integral membrane protein E16; E16; L-type amino acid transporter 1; hLAT1; Solute carrier family 7 member 5; y+ system cationic amino acid transporter | Homo sapiens (human) |
Kynureninase | EC 3.7.1.3; L-kynurenine hydrolase | Homo sapiens (human) |
4-hydroxy-2-oxoglutarate aldolase, mitochondrial | EC 4.1.3.16; Dihydrodipicolinate synthase-like; DHDPS-like protein; Probable 2-keto-4-hydroxyglutarate aldolase; Probable KHG-aldolase; Protein 569272 | Homo sapiens (human) |
D-3-phosphoglycerate dehydrogenase | 3-PGDH; EC 1.1.1.95; 2-oxoglutarate reductase; 1.1.1.399; Malate dehydrogenase; 1.1.1.37 | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 10 | 26S proteasome regulatory subunit p28; Gankyrin; p28(GANK) | Homo sapiens (human) |
Kynurenine--oxoglutarate transaminase 3 | EC 2.6.1.7; Cysteine-S-conjugate beta-lyase 2; 4.4.1.13; Kynurenine aminotransferase 3; Kynurenine aminotransferase III; KATIII; Kynurenine--glyoxylate transaminase; 2.6.1.63; Kynurenine--oxoglutarate transaminase III | Homo sapiens (human) |
S-methylmethionine--homocysteine S-methyltransferase BHMT2 | SMM-hcy methyltransferase; EC 2.1.1.10; Betaine--homocysteine S-methyltransferase 2 | Homo sapiens (human) |
Formimidoyltransferase-cyclodeaminase | Formiminotransferase-cyclodeaminase; FTCD; LCHC1 | Homo sapiens (human) |
Acyl carrier protein, mitochondrial | ACP; CI-SDAP; NADH-ubiquinone oxidoreductase 9.6 kDa subunit | Homo sapiens (human) |
Aspartate aminotransferase, cytoplasmic | cAspAT; EC 2.6.1.1; EC 2.6.1.3; Cysteine aminotransferase, cytoplasmic; Cysteine transaminase, cytoplasmic; cCAT; Glutamate oxaloacetate transaminase 1; Transaminase A | Homo sapiens (human) |
Diamine acetyltransferase 1 | EC 2.3.1.57; Polyamine N-acetyltransferase 1; Putrescine acetyltransferase; Spermidine/spermine N(1)-acetyltransferase 1; SSAT; SSAT-1 | Homo sapiens (human) |
Histamine N-methyltransferase | HMT; EC 2.1.1.8 | Homo sapiens (human) |
Branched-chain-amino-acid aminotransferase, cytosolic | BCAT(c); EC 2.6.1.42; Protein ECA39 | Homo sapiens (human) |
Peroxisomal N(1)-acetyl-spermine/spermidine oxidase | EC 1.5.3.13; Polyamine oxidase | Homo sapiens (human) |
Histidine decarboxylase | HDC; EC 4.1.1.22 | Homo sapiens (human) |
Carbamoyl-phosphate synthase [ammonia], mitochondrial | EC 6.3.4.16; Carbamoyl-phosphate synthetase I; CPSase I | Homo sapiens (human) |
3-hydroxyisobutyrate dehydrogenase, mitochondrial | HIBADH; EC 1.1.1.31 | Homo sapiens (human) |
Serine--tRNA ligase, cytoplasmic | EC 6.1.1.11; Seryl-tRNA synthetase; SerRS; Seryl-tRNA(Ser/Sec) synthetase | Homo sapiens (human) |
Guanidinoacetate N-methyltransferase | EC 2.1.1.2 | Homo sapiens (human) |
Glycine N-methyltransferase | EC 2.1.1.20 | Homo sapiens (human) |
Serotonin N-acetyltransferase | Serotonin acetylase; EC 2.3.1.87; Aralkylamine N-acetyltransferase; AA-NAT | Homo sapiens (human) |
Mitochondrial 2-oxodicarboxylate carrier | Solute carrier family 25 member 21 | Homo sapiens (human) |
Glutaminase kidney isoform, mitochondrial | GLS; EC 3.5.1.2; K-glutaminase; L-glutamine amidohydrolase | Homo sapiens (human) |
Arginase-1 | EC 3.5.3.1; Liver-type arginase; Type I arginase | Homo sapiens (human) |
Asparagine synthetase [glutamine-hydrolyzing] | EC 6.3.5.4; Cell cycle control protein TS11; Glutamine-dependent asparagine synthetase | Homo sapiens (human) |
Phenylethanolamine N-methyltransferase | PNMTase; EC 2.1.1.28; Noradrenaline N-methyltransferase | Homo sapiens (human) |
Proteasome subunit beta type-8 | EC 3.4.25.1; Low molecular mass protein 7; Macropain subunit C13; Multicatalytic endopeptidase complex subunit C13; Proteasome component C13; Proteasome subunit beta-5i; Really interesting new gene 10 protein | Homo sapiens (human) |
Proteasome subunit beta type-5 | EC 3.4.25.1; Macropain epsilon chain; Multicatalytic endopeptidase complex epsilon chain; Proteasome chain 6; Proteasome epsilon chain; Proteasome subunit MB1; Proteasome subunit X | Homo sapiens (human) |
Tryptophan 2,3-dioxygenase | TDO; EC 1.13.11.11; Tryptamin 2,3-dioxygenase; Tryptophan oxygenase; TO; TRPO; Tryptophan pyrrolase; Tryptophanase | Homo sapiens (human) |
Proteasome subunit beta type-2 | Macropain subunit C7-I; Multicatalytic endopeptidase complex subunit C7-I; Proteasome component C7-I | Homo sapiens (human) |
Arginase-2, mitochondrial | EC 3.5.3.1; Arginase II; Kidney-type arginase; Non-hepatic arginase; Type II arginase | Homo sapiens (human) |
S-methyl-5'-thioadenosine phosphorylase | EC 2.4.2.28; 5'-methylthioadenosine phosphorylase; MTA phosphorylase; MTAP; MTAPase | Homo sapiens (human) |
Lysine--tRNA ligase | EC 2.7.7.-; EC 6.1.1.6; Lysyl-tRNA synthetase; LysRS | Homo sapiens (human) |
Kynurenine--oxoglutarate transaminase 1 | EC 2.6.1.7; Cysteine-S-conjugate beta-lyase; 4.4.1.13; Glutamine transaminase K; GTK; Glutamine--phenylpyruvate transaminase; 2.6.1.64; Kynurenine aminotransferase 1; Kynurenine aminotransferase I; KATI; Kynurenine--oxoglutarate transaminase I | Homo sapiens (human) |
Thioredoxin reductase 1, cytoplasmic | TR; EC 1.8.1.9; Gene associated with retinoic and interferon-induced mortality 12 protein; GRIM-12; Gene associated with retinoic and IFN-induced mortality 12 protein; KM-102-derived reductase-like factor; Thioredoxin reductase TR1 | Homo sapiens (human) |
Kynurenine/alpha-aminoadipate aminotransferase, mitochondrial | KAT/AadAT; 2-aminoadipate aminotransferase; 2-aminoadipate transaminase; 2.6.1.39; Alpha-aminoadipate aminotransferase; AadAT; Kynurenine aminotransferase II; Kynurenine--oxoglutarate aminotransferase II; Kynurenine--oxoglutarate transaminase 2; 2.6.1.7; | Homo sapiens (human) |
Betaine--homocysteine S-methyltransferase 1 | EC 2.1.1.5 | Homo sapiens (human) |
Thioredoxin, mitochondrial | MTRX; Mt-Trx; Thioredoxin-2 | Homo sapiens (human) |
Cystathionine beta-synthase | EC 4.2.1.22; Beta-thionase; Serine sulfhydrase | Homo sapiens (human) |
Methionine synthase | MS; EC 2.1.1.13; 5-methyltetrahydrofolate--homocysteine methyltransferase; Cobalamin-dependent methionine synthase; Vitamin-B12 dependent methionine synthase | Homo sapiens (human) |
Phenylalanine-4-hydroxylase | PAH; EC 1.14.16.1; Phe-4-monooxygenase | Homo sapiens (human) |
Ornithine transcarbamylase, mitochondrial | OTCase; EC 2.1.3.3; Ornithine carbamoyltransferase, mitochondrial | Homo sapiens (human) |
Bifunctional glutamate/proline--tRNA ligase | Bifunctional aminoacyl-tRNA synthetase; Cell proliferation-inducing gene 32 protein; Glutamatyl-prolyl-tRNA synthetase | Homo sapiens (human) |
Dopamine beta-hydroxylase | EC 1.14.17.1; Dopamine beta-monooxygenase | Homo sapiens (human) |
Dihydropteridine reductase | EC 1.5.1.34; HDHPR; Quinoid dihydropteridine reductase; Short chain dehydrogenase/reductase family 33C member 1 | Homo sapiens (human) |
Histidine ammonia-lyase | Histidase; EC 4.3.1.3 | Homo sapiens (human) |
Glutamine--tRNA ligase | EC 6.1.1.18; Glutaminyl-tRNA synthetase; GlnRS | Homo sapiens (human) |
Spermine synthase | SPMSY; EC 2.5.1.22; Spermidine aminopropyltransferase | Homo sapiens (human) |
Thyroxine 5-deiodinase | EC 1.21.99.3; 5DIII; DIOIII; Type 3 DI; Type III iodothyronine deiodinase | Homo sapiens (human) |
Peroxisomal sarcosine oxidase | PSO; EC 1.5.3.1; EC 1.5.3.7; L-pipecolate oxidase; L-pipecolic acid oxidase | Homo sapiens (human) |
L-dopachrome tautomerase | DCT; DT; EC 5.3.3.12; L-dopachrome Delta-isomerase; Tyrosinase-related protein 2; TRP-2; TRP2 | Homo sapiens (human) |
Choline dehydrogenase, mitochondrial | CDH; CHD; EC 1.1.99.1 | Homo sapiens (human) |
Thiosulfate:glutathione sulfurtransferase | TST; EC 2.8.1.- | Homo sapiens (human) |
O-phosphoseryl-tRNA(Sec) selenium transferase | EC 2.9.1.2; Liver-pancreas antigen; LP; SLA-p35; SLA/LP autoantigen; Selenocysteine synthase; Sec synthase; Selenocysteinyl-tRNA(Sec) synthase; Sep-tRNA:Sec-tRNA synthase; SepSecS; Soluble liver antigen; SLA; UGA suppressor tRNA-associated protein; tRNA(S | Homo sapiens (human) |
Phosphoserine phosphatase | PSP; PSPase; EC 3.1.3.3; L-3-phosphoserine phosphatase; O-phosphoserine phosphohydrolase | Homo sapiens (human) |
Cysteine dioxygenase type 1 | EC 1.13.11.20; Cysteine dioxygenase type I; CDO; CDO-I | Homo sapiens (human) |
Kynurenine formamidase | KFA; KFase; EC 3.5.1.9; Arylformamidase; N-formylkynurenine formamidase; FKF | Homo sapiens (human) |
Cysteine sulfinic acid decarboxylase | EC 4.1.1.29; Aspartate 1-decarboxylase; 4.1.1.11; Cysteine-sulfinate decarboxylase; Sulfinoalanine decarboxylase | Homo sapiens (human) |
Carnosine synthase 1 | EC 6.3.2.11; ATP-grasp domain-containing protein 1 | Homo sapiens (human) |
Proteasome subunit beta type-11 | EC 3.4.25.1; Proteasome subunit beta-5t | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 11 | 26S proteasome regulatory subunit RPN6; 26S proteasome regulatory subunit S9; 26S proteasome regulatory subunit p44.5 | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 12 | 26S proteasome regulatory subunit RPN5; 26S proteasome regulatory subunit p55 | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 14 | EC 3.4.19.-; 26S proteasome regulatory subunit RPN11; 26S proteasome-associated PAD1 homolog 1 | Homo sapiens (human) |
Proteasome subunit alpha type-7 | Proteasome subunit RC6-1; Proteasome subunit XAPC7 | Homo sapiens (human) |
Kynurenine 3-monooxygenase | EC 1.14.13.9; Kynurenine 3-hydroxylase | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 3 | 26S proteasome regulatory subunit RPN3; 26S proteasome regulatory subunit S3; Proteasome subunit p58 | Homo sapiens (human) |
Gamma-butyrobetaine dioxygenase | EC 1.14.11.1; Gamma-butyrobetaine hydroxylase; Gamma-BBH; Gamma-butyrobetaine,2-oxoglutarate dioxygenase | Homo sapiens (human) |
Indolethylamine N-methyltransferase | Indolamine N-methyltransferase; EC 2.1.1.49; EC 2.1.1.96; Aromatic alkylamine N-methyltransferase; Amine N-methyltransferase; Arylamine N-methyltransferase; Thioether S-methyltransferase; TEMT | Homo sapiens (human) |
26S proteasome regulatory subunit 6A | 26S proteasome AAA-ATPase subunit RPT5; Proteasome 26S subunit ATPase 3; Proteasome subunit P50; Tat-binding protein 1; TBP-1 | Homo sapiens (human) |
Aromatic-L-amino-acid decarboxylase | AADC; EC 4.1.1.28; DOPA decarboxylase; DDC | Homo sapiens (human) |
Acetyl-CoA acetyltransferase, mitochondrial | EC 2.3.1.9; Acetoacetyl-CoA thiolase; T2 | Homo sapiens (human) |
Proteasome subunit alpha type-1 | 30 kDa prosomal protein; PROS-30; Macropain subunit C2; Multicatalytic endopeptidase complex subunit C2; Proteasome component C2; Proteasome nu chain | Homo sapiens (human) |
Proteasome subunit alpha type-2 | Macropain subunit C3; Multicatalytic endopeptidase complex subunit C3; Proteasome component C3 | Homo sapiens (human) |
Proteasome subunit alpha type-3 | Macropain subunit C8; Multicatalytic endopeptidase complex subunit C8; Proteasome component C8 | Homo sapiens (human) |
Proteasome subunit alpha type-4 | Macropain subunit C9; Multicatalytic endopeptidase complex subunit C9; Proteasome component C9; Proteasome subunit L | Homo sapiens (human) |
Proteasome subunit alpha type-5 | Macropain zeta chain; Multicatalytic endopeptidase complex zeta chain; Proteasome zeta chain | Homo sapiens (human) |
Proteasome subunit beta type-4 | 26 kDa prosomal protein; HsBPROS26; PROS-26; Macropain beta chain; Multicatalytic endopeptidase complex beta chain; Proteasome beta chain; Proteasome chain 3; HsN3 | Homo sapiens (human) |
Proteasome subunit beta type-6 | EC 3.4.25.1; Macropain delta chain; Multicatalytic endopeptidase complex delta chain; Proteasome delta chain; Proteasome subunit Y | Homo sapiens (human) |
4-hydroxyphenylpyruvate dioxygenase | EC 1.13.11.27; 4-hydroxyphenylpyruvic acid oxidase; 4HPPD; HPD; HPPDase | Homo sapiens (human) |
26S proteasome regulatory subunit 7 | 26S proteasome AAA-ATPase subunit RPT1; Proteasome 26S subunit ATPase 2; Protein MSS1 | Homo sapiens (human) |
Proteasome subunit beta type-10 | EC 3.4.25.1; Low molecular mass protein 10; Macropain subunit MECl-1; Multicatalytic endopeptidase complex subunit MECl-1; Proteasome MECl-1; Proteasome subunit beta-2i | Homo sapiens (human) |
26S proteasome regulatory subunit 6B | 26S proteasome AAA-ATPase subunit RPT3; MB67-interacting protein; MIP224; Proteasome 26S subunit ATPase 4; Tat-binding protein 7; TBP-7 | Homo sapiens (human) |
3-hydroxyanthranilate 3,4-dioxygenase | EC 1.13.11.6; 3-hydroxyanthranilate oxygenase; 3-HAO; h3HAO; 3-hydroxyanthranilic acid dioxygenase; HAD | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 8 | 26S proteasome regulatory subunit RPN12; 26S proteasome regulatory subunit S14; p31 | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 7 | 26S proteasome regulatory subunit RPN8; 26S proteasome regulatory subunit S12; Mov34 protein homolog; Proteasome subunit p40 | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 4 | 26S proteasome regulatory subunit RPN10; 26S proteasome regulatory subunit S5A; Antisecretory factor 1; AF; ASF; Multiubiquitin chain-binding protein | Homo sapiens (human) |
26S proteasome complex subunit SEM1 | 26S proteasome complex subunit DSS1; Deleted in split hand/split foot protein 1; Split hand/foot deleted protein 1; Split hand/foot malformation type 1 protein | Homo sapiens (human) |
Proteasome subunit alpha type-6 | 27 kDa prosomal protein; PROS-27; p27K; Macropain iota chain; Multicatalytic endopeptidase complex iota chain; Proteasome iota chain | Homo sapiens (human) |
26S proteasome regulatory subunit 4 | P26s4; 26S proteasome AAA-ATPase subunit RPT2; Proteasome 26S subunit ATPase 1 | Homo sapiens (human) |
26S proteasome regulatory subunit 8 | 26S proteasome AAA-ATPase subunit RPT6; Proteasome 26S subunit ATPase 5; Proteasome subunit p45; Thyroid hormone receptor-interacting protein 1; TRIP1; p45/SUG | Homo sapiens (human) |
26S proteasome regulatory subunit 10B | 26S proteasome AAA-ATPase subunit RPT4; Proteasome 26S subunit ATPase 6; Proteasome subunit p42 | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 2 | 26S proteasome regulatory subunit RPN1; 26S proteasome regulatory subunit S2; 26S proteasome subunit p97; Protein 55.11; Tumor necrosis factor type 1 receptor-associated protein 2 | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 6 | 26S proteasome regulatory subunit RPN7; 26S proteasome regulatory subunit S10; Breast cancer-associated protein SGA-113M; Phosphonoformate immuno-associated protein 4; Proteasome regulatory particle subunit p44S10; p42A | Homo sapiens (human) |
Proteasome subunit alpha-type 8 | Proteasome alpha 4 subunit; Alpha4s; Proteasome subunit alpha-type 7-like | Homo sapiens (human) |
Proteasome subunit beta type-7 | EC 3.4.25.1; Macropain chain Z; Multicatalytic endopeptidase complex chain Z; Proteasome subunit Z | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 1 | 26S proteasome regulatory subunit RPN2; 26S proteasome regulatory subunit S1; 26S proteasome subunit p112 | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 13 | 26S proteasome regulatory subunit RPN9; 26S proteasome regulatory subunit S11; 26S proteasome regulatory subunit p40.5 | Homo sapiens (human) |
Proteasome activator complex subunit 1 | 11S regulator complex subunit alpha; REG-alpha; Activator of multicatalytic protease subunit 1; Interferon gamma up-regulated I-5111 protein; IGUP I-5111; Proteasome activator 28 subunit alpha; PA28a; PA28alpha | Homo sapiens (human) |
Thiosulfate sulfurtransferase | EC 2.8.1.1; Rhodanese | Homo sapiens (human) |
3-hydroxyisobutyryl-CoA hydrolase, mitochondrial | EC 3.1.2.4; 3-hydroxyisobutyryl-coenzyme A hydrolase; HIB-CoA hydrolase; HIBYL-CoA-H | Homo sapiens (human) |
Proteasome activator complex subunit 2 | 11S regulator complex subunit beta; REG-beta; Activator of multicatalytic protease subunit 2; Proteasome activator 28 subunit beta; PA28b; PA28beta | Homo sapiens (human) |
L-amino-acid oxidase | LAAO; LAO; EC 1.4.3.2; EC 1.4.3.25; Interleukin-4-induced protein 1; IL4-induced protein 1; hIL4I1; Protein Fig-1; hFIG1 | Homo sapiens (human) |
Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial | EC 2.3.1.168; 52 kDa mitochondrial autoantigen of primary biliary cirrhosis; Branched chain 2-oxo-acid dehydrogenase complex component E2; BCOADC-E2; Branched-chain alpha-keto acid dehydrogenase complex component E2; BCKAD-E2; BCKADE2; Dihydrolipoamide ac | Homo sapiens (human) |
Antizyme inhibitor 1 | AZI; AZI1; Ornithine decarboxylase antizyme inhibitor | Homo sapiens (human) |
Persulfide dioxygenase ETHE1, mitochondrial | EC 1.13.11.18; Ethylmalonic encephalopathy protein 1; Hepatoma subtracted clone one protein; Sulfur dioxygenase ETHE1 | Homo sapiens (human) |
60 kDa lysophospholipase | LysoLP; EC 3.1.1.5; Lysophospholipase-transacylase | Homo sapiens (human) |
1,2-dihydroxy-3-keto-5-methylthiopentene dioxygenase | EC 1.13.11.54; Acireductone dioxygenase (Fe(2+)-requiring); ARD; Fe-ARD; Membrane-type 1 matrix metalloproteinase cytoplasmic tail-binding protein 1; MTCBP-1; Submergence-induced protein-like factor; Sip-L | Homo sapiens (human) |
Homogentisate 1,2-dioxygenase | EC 1.13.11.5; Homogentisate oxygenase; Homogentisic acid oxidase; Homogentisicase | Homo sapiens (human) |
L-serine dehydratase/L-threonine deaminase | SDH; EC 4.3.1.17; L-serine deaminase; L-threonine dehydratase; TDH; 4.3.1.19 | Homo sapiens (human) |
Serine dehydratase-like | L-serine deaminase; L-serine dehydratase/L-threonine deaminase; L-threonine dehydratase; TDH; 4.3.1.19; Serine dehydratase 2; SDH 2; 4.3.1.17 | Homo sapiens (human) |
Argininosuccinate synthase | EC 6.3.4.5; Citrulline--aspartate ligase | Homo sapiens (human) |
Dihydrolipoyl dehydrogenase, mitochondrial | EC 1.8.1.4; Dihydrolipoamide dehydrogenase; Glycine cleavage system L protein | Homo sapiens (human) |
Isovaleryl-CoA dehydrogenase, mitochondrial | IVD; EC 1.3.8.4; Butyryl-CoA dehydrogenase; 1.3.8.1 | Homo sapiens (human) |
Sulfite oxidase, mitochondrial | EC 1.8.3.1 | Homo sapiens (human) |
Pyrroline-5-carboxylate reductase 3 | P5C reductase 3; P5CR 3; EC 1.5.1.2; Pyrroline-5-carboxylate reductase-like protein | Homo sapiens (human) |
Sodium/iodide cotransporter | Na(+)/I(-) cotransporter; Sodium-iodide symporter; Na(+)/I(-) symporter; Solute carrier family 5 member 5 | Homo sapiens (human) |
Antizyme inhibitor 2 | AzI2; Arginine decarboxylase; ADC; ARGDC; Ornithine decarboxylase-like protein; ODC-like protein; ornithine decarboxylase paralog; ODC-p | Homo sapiens (human) |
Phosphoserine aminotransferase | EC 2.6.1.52; Phosphohydroxythreonine aminotransferase; PSAT | Homo sapiens (human) |
Trimethyllysine dioxygenase, mitochondrial | EC 1.14.11.8; Epsilon-trimethyllysine 2-oxoglutarate dioxygenase; Epsilon-trimethyllysine hydroxylase; TML hydroxylase; TML-alpha-ketoglutarate dioxygenase; TML dioxygenase; TMLD | Homo sapiens (human) |
Creatine kinase U-type, mitochondrial | EC 2.7.3.2; Acidic-type mitochondrial creatine kinase; Mia-CK; Ubiquitous mitochondrial creatine kinase; U-MtCK | Homo sapiens (human) |
Fumarylacetoacetase | FAA; EC 3.7.1.2; Beta-diketonase; Fumarylacetoacetate hydrolase | Homo sapiens (human) |
Creatine kinase S-type, mitochondrial | EC 2.7.3.2; Basic-type mitochondrial creatine kinase; Mib-CK; Sarcomeric mitochondrial creatine kinase; S-MtCK | Homo sapiens (human) |
Acetylserotonin O-methyltransferase | EC 2.1.1.4; Hydroxyindole O-methyltransferase; HIOMT | Homo sapiens (human) |
Agmatinase, mitochondrial | EC 3.5.3.11; Agmatine ureohydrolase; AUH | Homo sapiens (human) |
Methionine synthase reductase | MSR; EC 1.16.1.8; Aquacobalamin reductase; AqCbl reductase; 1.16.1.- | Homo sapiens (human) |
2-aminoethanethiol dioxygenase | EC 1.13.11.19; Cysteamine dioxygenase | Homo sapiens (human) |
Aspartoacylase | EC 3.5.1.15; Aminoacylase-2; ACY-2 | Homo sapiens (human) |
Lipoyl synthase, mitochondrial | EC 2.8.1.8; Lipoate synthase; LS; Lip-syn; Lipoic acid synthase | Homo sapiens (human) |
Sarcosine dehydrogenase, mitochondrial | SarDH; EC 1.5.8.3; BPR-2 | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 9 | 26S proteasome regulatory subunit p27 | Homo sapiens (human) |
Aspartate--tRNA ligase, cytoplasmic | EC 6.1.1.12; Aspartyl-tRNA synthetase; AspRS; Cell proliferation-inducing gene 40 protein | Homo sapiens (human) |
Acidic amino acid decarboxylase GADL1 | Aspartate 1-decarboxylase; ADC; HuADC; 4.1.1.11; Cysteine sulfinic acid decarboxylase; CSADC; HuCSADC; 4.1.1.29; Glutamate decarboxylase-like protein 1 | Homo sapiens (human) |
N-acetylglutamate synthase, mitochondrial | EC 2.3.1.1; Amino-acid acetyltransferase | Homo sapiens (human) |
Type I iodothyronine deiodinase | EC 1.21.99.4; 5DI; DIOI; Type 1 DI; Type-I 5'-deiodinase | Homo sapiens (human) |
Type II iodothyronine deiodinase | EC 1.21.99.4; 5DII; DIOII; Type 2 DI; Type-II 5'-deiodinase | Homo sapiens (human) |
Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial | MCCase subunit alpha; EC 6.4.1.4; 3-methylcrotonyl-CoA carboxylase 1; 3-methylcrotonyl-CoA carboxylase biotin-containing subunit; 3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha | Homo sapiens (human) |
Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial | MCCase subunit beta; EC 6.4.1.4; 3-methylcrotonyl-CoA carboxylase 2; 3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit; 3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta | Homo sapiens (human) |
Dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial | EC 2.3.1.61; 2-oxoglutarate dehydrogenase complex component E2; OGDC-E2; Dihydrolipoamide succinyltransferase component of 2-oxoglutarate dehydrogenase complex; E2K | Homo sapiens (human) |
Dimethylglycine dehydrogenase, mitochondrial | EC 1.5.8.4; ME2GLYDH | Homo sapiens (human) |
Selenocysteine lyase | hSCL; EC 4.4.1.16 | Homo sapiens (human) |
2-amino-3-ketobutyrate coenzyme A ligase, mitochondrial | AKB ligase; EC 2.3.1.29; Aminoacetone synthase; Glycine acetyltransferase | Homo sapiens (human) |
Lipoyltransferase 1, mitochondrial | EC 2.3.1.-; Lipoate biosynthesis protein; Lipoate-protein ligase; Lipoyl ligase | Homo sapiens (human) |
Isoaspartyl peptidase/L-asparaginase | EC 3.4.19.5; EC 3.5.1.1; Asparaginase-like protein 1; Beta-aspartyl-peptidase; Isoaspartyl dipeptidase; L-asparagine amidohydrolase | Homo sapiens (human) |
Urocanate hydratase | Urocanase; EC 4.2.1.49; Imidazolonepropionate hydrolase | Homo sapiens (human) |
3-mercaptopyruvate sulfurtransferase | MST; EC 2.8.1.2 | Homo sapiens (human) |
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial | EC 1.2.4.4; Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain; BCKDE1A; BCKDH E1-alpha | Homo sapiens (human) |
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial | EC 1.2.4.4; Branched-chain alpha-keto acid dehydrogenase E1 component beta chain; BCKDE1B; BCKDH E1-beta | Homo sapiens (human) |
Enolase-phosphatase E1 | EC 3.1.3.77; 2,3-diketo-5-methylthio-1-phosphopentane phosphatase; MASA homolog | Homo sapiens (human) |
Selenide, water dikinase 2 | EC 2.7.9.3; Selenium donor protein 2; Selenophosphate synthase 2 | Homo sapiens (human) |
Probable imidazolonepropionase | EC 3.5.2.7; Amidohydrolase domain-containing protein 1 | Homo sapiens (human) |
Methylthioribose-1-phosphate isomerase | M1Pi; MTR-1-P isomerase; EC 5.3.1.23; Mediator of RhoA-dependent invasion; S-methyl-5-thioribose-1-phosphate isomerase; Translation initiation factor eIF-2B subunit alpha/beta/delta-like protein | Homo sapiens (human) |
Pterin-4-alpha-carbinolamine dehydratase | PHS; EC 4.2.1.96; 4-alpha-hydroxy-tetrahydropterin dehydratase; Dimerization cofactor of hepatocyte nuclear factor 1-alpha; DCoH; Dimerization cofactor of HNF1; Phenylalanine hydroxylase-stimulating protein; Pterin carbinolamine dehydratase; PCD | Homo sapiens (human) |
Putative lipoyltransferase 2, mitochondrial | EC 2.3.1.181; Lipoate-protein ligase B; Lipoyl/octanoyl transferase; Octanoyl-[acyl-carrier-protein]-protein N-octanoyltransferase | Homo sapiens (human) |
Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial | MMSDH; Malonate-semialdehyde dehydrogenase [acylating]; EC 1.2.1.18; EC 1.2.1.27; Aldehyde dehydrogenase family 6 member A1 | Homo sapiens (human) |
Hydroxylysine kinase | 5-hydroxy-L-lysine kinase; EC 2.7.1.81; Aminoglycoside phosphotransferase domain-containing protein 1 | Homo sapiens (human) |
Proline dehydrogenase 1, mitochondrial | EC 1.5.5.2; Proline oxidase; Proline oxidase 2; p53-induced gene 6 protein | Homo sapiens (human) |
Eukaryotic translation elongation factor 1 epsilon-1 | Aminoacyl tRNA synthetase complex-interacting multifunctional protein 3; Elongation factor p18; Multisynthase complex auxiliary component p18 | Homo sapiens (human) |
Thyrotropin subunit beta | Thyroid-stimulating hormone subunit beta; TSH-B; TSH-beta; Thyrotropin beta chain | Homo sapiens (human) |
Argininosuccinate lyase | ASAL; EC 4.3.2.1; Arginosuccinase | Homo sapiens (human) |
4F2 cell-surface antigen heavy chain | 4F2hc; 4F2 heavy chain antigen; Lymphocyte activation antigen 4F2 large subunit; Solute carrier family 3 member 2 | Homo sapiens (human) |
Glycine dehydrogenase (decarboxylating), mitochondrial | EC 1.4.4.2; Glycine cleavage system P protein; Glycine decarboxylase; Glycine dehydrogenase (aminomethyl-transferring) | Homo sapiens (human) |
Glycine cleavage system H protein, mitochondrial | Lipoic acid-containing protein | Homo sapiens (human) |
Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial | SBCAD; EC 1.3.8.5; 2-methyl branched chain acyl-CoA dehydrogenase; 2-MEBCAD; 2-methylbutyryl-coenzyme A dehydrogenase; 2-methylbutyryl-CoA dehydrogenase | Homo sapiens (human) |
Aminomethyltransferase, mitochondrial | EC 2.1.2.10; Glycine cleavage system T protein; GCVT | Homo sapiens (human) |
Alpha-aminoadipic semialdehyde dehydrogenase | Alpha-AASA dehydrogenase; EC 1.2.1.31; Aldehyde dehydrogenase family 7 member A1; 1.2.1.3; Antiquitin-1; Betaine aldehyde dehydrogenase; 1.2.1.8; Delta1-piperideine-6-carboxylate dehydrogenase; P6c dehydrogenase | Homo sapiens (human) |
Glycine amidinotransferase, mitochondrial | EC 2.1.4.1; L-arginine:glycine amidinotransferase; Transamidinase | Homo sapiens (human) |
2-iminobutanoate/2-iminopropanoate deaminase | EC 3.5.99.10; 14.5 kDa translational inhibitor protein; hp14.5; p14.5; Heat-responsive protein 12; Reactive intermediate imine deaminase A homolog; Translation inhibitor L-PSP ribonuclease; UK114 antigen homolog | Homo sapiens (human) |
Selenocysteine-specific elongation factor | Elongation factor sec; Eukaryotic elongation factor, selenocysteine-tRNA-specific | Homo sapiens (human) |
P protein | Melanocyte-specific transporter protein; Pink-eyed dilution protein homolog | Homo sapiens (human) |
Methylglutaconyl-CoA hydratase, mitochondrial | EC 4.2.1.18; AU-specific RNA-binding enoyl-CoA hydratase; AU-binding protein/enoyl-CoA hydratase; Itaconyl-CoA hydratase; 4.2.1.56 | Homo sapiens (human) |
Ketimine reductase mu-crystallin | EC 1.5.1.25; NADP-regulated thyroid-hormone-binding protein | Homo sapiens (human) |
Proteasome activator complex subunit 4 | Proteasome activator PA200 | Homo sapiens (human) |
26S proteasome non-ATPase regulatory subunit 5 | 26S protease subunit S5 basic; 26S proteasome subunit S5B | Homo sapiens (human) |
Proton-coupled amino acid transporter 4 | Proton/amino acid transporter 4; Solute carrier family 36 member 4 | Homo sapiens (human) |
5-phosphohydroxy-L-lysine phospho-lyase | EC 4.2.3.134; Alanine--glyoxylate aminotransferase 2-like 2 | Homo sapiens (human) |
L-seryl-tRNA(Sec) kinase | EC 2.7.1.164; O-phosphoseryl-tRNA(Sec) kinase | Homo sapiens (human) |
Inactive L-threonine 3-dehydrogenase, mitochondrial | Short chain dehydrogenase/reductase family 14E member 1 pseudogene | Homo sapiens (human) |
Protein phosphatase 1K, mitochondrial | EC 3.1.3.16; PP2C domain-containing protein phosphatase 1K; PP2C-like mitochondrial protein; PP2C-type mitochondrial phosphoprotein phosphatase; PTMP; Protein phosphatase 2C isoform kappa; PP2C-kappa | Homo sapiens (human) |
Carnosine N-methyltransferase | EC 2.1.1.22 | Homo sapiens (human) |
N-acetylaspartate synthetase | NAA synthetase; EC 2.3.1.17; Camello-like protein 3; N-acetyltransferase 8-like protein | Homo sapiens (human) |
Choline transporter-like protein 1 | CDw92; Solute carrier family 44 member 1 | Homo sapiens (human) |
Proteasome inhibitor PI31 subunit | hPI31 | Homo sapiens (human) |
Methylthioribulose-1-phosphate dehydratase | MTRu-1-P dehydratase; EC 4.2.1.109; APAF1-interacting protein; hAPIP | Homo sapiens (human) |
Solute carrier family 25 member 44 | | Homo sapiens (human) |
Selenocysteine insertion sequence-binding protein 2 | SECIS-binding protein 2 | Homo sapiens (human) |
Alanine--glyoxylate aminotransferase 2, mitochondrial | AGT 2; EC 2.6.1.44; (R)-3-amino-2-methylpropionate--pyruvate transaminase; 2.6.1.40; Beta-ALAAT II; Beta-alanine-pyruvate aminotransferase; D-AIBAT | Homo sapiens (human) |
Peroxisomal membrane protein 2 | 22 kDa peroxisomal membrane protein | Homo sapiens (human) |
Mitochondrial dicarboxylate carrier | Solute carrier family 25 member 10 | Homo sapiens (human) |
Alpha-aminoadipic semialdehyde synthase, mitochondrial | LKR/SDH | Homo sapiens (human) |
Isobutyryl-CoA dehydrogenase, mitochondrial | IBDH; EC 1.3.8.-; Activator-recruited cofactor 42 kDa component; ARC42; Acyl-CoA dehydrogenase family member 8; ACAD-8 | Homo sapiens (human) |
Membrane-associated transporter protein | Melanoma antigen AIM1; Protein AIM-1; Solute carrier family 45 member 2 | Homo sapiens (human) |
Compound | Description |
hydronium ion | |
hydrogen sulfite | |
selenomethionine | Diagnostic aid in pancreas function determination. |
selenic acid | A strong dibasic acid with the molecular formula H2SeO4. Included under this heading is the acid form, and inorganic salts of dihydrogen selenium tetraoxide. |
urea | A compound formed in the liver from ammonia produced by the deamination of amino acids. It is the principal end product of protein catabolism and constitutes about one half of the total urinary solids. |
Glutathione | A tripeptide with many roles in cells. It conjugates to drugs to make them more soluble for excretion, is a cofactor for some enzymes, is involved in protein disulfide bond rearrangement and reduces peroxides. |
Arginine | An essential amino acid that is physiologically active in the L-form. |
Thiamine Pyrophosphate | The coenzyme form of Vitamin B1 present in many animal tissues. It is a required intermediate in the PYRUVATE DEHYDROGENASE COMPLEX and the KETOGLUTARATE DEHYDROGENASE COMPLEX. |
Succinate | |
acetic acid | Product of the oxidation of ethanol and of the destructive distillation of wood. It is used locally, occasionally internally, as a counterirritant and also as a reagent. (Stedman, 26th ed) |
adenine | A purine base and a fundamental unit of ADENINE NUCLEOTIDES. |
NADH | |
ammonium hydroxide | The hydroxy salt of ammonium ion. It is formed when AMMONIA reacts with water molecules in solution. |
Ammonium | |
Copper | A heavy metal trace element with the atomic symbol Cu, atomic number 29, and atomic weight 63.55. |
betaine | A naturally occurring compound that has been of interest for its role in osmoregulation. As a drug, betaine hydrochloride has been used as a source of hydrochloric acid in the treatment of hypochlorhydria. Betaine has also been used in the treatment of liver disorders, for hyperkalemia, for homocystinuria, and for gastrointestinal disturbances. (From Martindale, The Extra Pharmacopoeia, 30th ed, p1341) |
hydroiodic acid | |
Copper | A heavy metal trace element with the atomic symbol Cu, atomic number 29, and atomic weight 63.55. |
iron | A metallic element with atomic symbol Fe, atomic number 26, and atomic weight 55.85. It is an essential constituent of HEMOGLOBINS; CYTOCHROMES; and IRON-BINDING PROTEINS. It plays a role in cellular redox reactions and in the transport of OXYGEN. |
Manganese | A trace element with atomic symbol Mn, atomic number 25, and atomic weight 54.94. It is concentrated in cell mitochondria, mostly in the pituitary gland, liver, pancreas, kidney, and bone, influences the synthesis of mucopolysaccharides, stimulates hepatic synthesis of cholesterol and fatty acids, and is a cofactor in many enzymes, including arginase and alkaline phosphatase in the liver. (From AMA Drug Evaluations Annual 1992, p2035) |
Carbon Dioxide | A colorless, odorless gas that can be formed by the body and is necessary for the respiration cycle of plants and animals. |
iodine | A nonmetallic element of the halogen group that is represented by the atomic symbol I, atomic number 53, and atomic weight of 126.90. It is a nutritionally essential element, especially important in thyroid hormone synthesis. In solution, it has anti-infective properties and is used topically. |
choline | A basic constituent of lecithin that is found in many plants and animal organs. It is important as a precursor of acetylcholine, as a methyl donor in various metabolic processes, and in lipid metabolism. |
Zinc | A metallic element of atomic number 30 and atomic weight 65.38. It is a necessary trace element in the diet, forming an essential part of many enzymes, and playing an important role in protein synthesis and in cell division. Zinc deficiency is associated with ANEMIA, short stature, HYPOGONADISM, impaired WOUND HEALING, and geophagia. It is known by the symbol Zn. |
Orthophosphate | |
Dopamine Hydrochloride | |
hydrogen sulfide | A flammable, poisonous gas with a characteristic odor of rotten eggs. It is used in the manufacture of chemicals, in metallurgy, and as an analytical reagent. (From Merck Index, 11th ed) |
Glutathione Disulfide | A GLUTATHIONE dimer formed by a disulfide bond between the cysteine sulfhydryl side chains during the course of being oxidized. |
Flavin Mononucleotide | A coenzyme for a number of oxidative enzymes including NADH DEHYDROGENASE. It is the principal form in which RIBOFLAVIN is found in cells and tissues. |
ubiquinol 1 | |
coenzyme q10 | Ubiquinone ring with a chain of 10 isoprene units; redox equilibrium with ubiqunol serving in mitochondrial inner membrane to transfer electrons; presence during reconstitution of acetylcholine receptor into phospholipid vesicles yields vesicles active in catalyzing carbamylcholine-sensitive Na+ flux; coenzyme Q10 depletion has been noted with use of statins |
Cobalamins | |
Aspartate | |
fumarates | Compounds based on fumaric acid. |
thyroxine | The major hormone derived from the thyroid gland. Thyroxine is synthesized via the iodination of tyrosines (MONOIODOTYROSINE) and the coupling of iodotyrosines (DIIODOTYROSINE) in the THYROGLOBULIN. Thyroxine is released from thyroglobulin by proteolysis and secreted into the blood. Thyroxine is peripherally deiodinated to form TRIIODOTHYRONINE which exerts a broad spectrum of stimulatory effects on cell metabolism. |
adenosine | A nucleoside that is composed of ADENINE and D-RIBOSE. Adenosine or adenosine derivatives play many important biological roles in addition to being components of DNA and RNA. Adenosine itself is a neurotransmitter. |
selenocysteine | A naturally occurring amino acid in both eukaryotic and prokaryotic organisms. It is found in tRNAs and in the catalytic site of some enzymes. The genes for glutathione peroxidase and formate dehydrogenase contain the TGA codon, which codes for this amino acid. |
adenosine diphosphate | Adenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position. |
formaldehyde | A highly reactive aldehyde gas formed by oxidation or incomplete combustion of hydrocarbons. In solution, it has a wide range of uses: in the manufacture of resins and textiles, as a disinfectant, and as a laboratory fixative or preservative. Formaldehyde solution (formalin) is considered a hazardous compound, and its vapor toxic. (From Reynolds, Martindale The Extra Pharmacopoeia, 30th ed, p717) |
hydrogen carbonate | |
Hydrogen Peroxide | A strong oxidizing agent used in aqueous solution as a ripening agent, bleach, and topical anti-infective. It is relatively unstable and solutions deteriorate over time unless stabilized by the addition of acetanilide or similar organic materials. |
iodine | A nonmetallic element of the halogen group that is represented by the atomic symbol I, atomic number 53, and atomic weight of 126.90. It is a nutritionally essential element, especially important in thyroid hormone synthesis. In solution, it has anti-infective properties and is used topically. |
methanol | A colorless, flammable liquid used in the manufacture of FORMALDEHYDE and ACETIC ACID, in chemical synthesis, antifreeze, and as a solvent. Ingestion of methanol is toxic and may cause blindness. |
Magnesium | A metallic element that has the atomic symbol Mg, atomic number 12, and atomic weight 24.31. It is important for the activity of many enzymes, especially those involved in OXIDATIVE PHOSPHORYLATION. |
melatonin | A biogenic amine that is found in animals and plants. In mammals, melatonin is produced by the PINEAL GLAND. Its secretion increases in darkness and decreases during exposure to light. Melatonin is implicated in the regulation of SLEEP, mood, and REPRODUCTION. Melatonin is also an effective antioxidant. |
Sodium | A member of the alkali group of metals. It has the atomic symbol Na, atomic number 11, and atomic weight 23. |
Water | A clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed) |
Oxygen | An element with atomic symbol O, atomic number 8, and atomic weight [15.99903; 15.99977]. It is the most abundant element on earth and essential for respiration. |
Guanosine Monophosphate | A guanine nucleotide containing one phosphate group esterified to the sugar moiety and found widely in nature. |
5,6,7,8-tetrahydrofolic acid | RN given refers to (DL)-isomer |
5,10-methylenetetrahydrofolate | |
5'-methylthioribose 1-phosphate | |
1,5-dihydro-FAD | chromophore component of E coli DNA photolyase |
selenodiglutathione | |
Guanosine Diphosphate | A guanine nucleotide containing two phosphate groups esterified to the sugar moiety. |
sapropterin | RN given refers to parent cpd; co-factor required for catalytic activity of nitric oxide synthases |
4a-hydroxytetrahydrobiopterin | structure given in first source |
pqq cofactor | A pyrrolo-quinoline having two adjacent keto-groups at the 4 and 5 positions and three acidic carboxyl groups. It is a coenzyme of some DEHYDROGENASES. |
2-amino-4-(2-aminoethoxy)butanoic acid, (DL)-isomer | |
phosphohydroxypyruvic acid | |
Pyruvic Acid | An intermediate compound in the metabolism of carbohydrates, proteins, and fats. In thiamine deficiency, its oxidation is retarded and it accumulates in the tissues, especially in nervous structures. (From Stedman, 26th ed) |
Selenite | |
sulfites | Inorganic salts of sulfurous acid. |
dimethylselenide | RN given refers to unlabeled cpd |
3-hydroxykynurenine, (L)-isomer | |
dopachrome | cyclization product of L-DOPA |
delta-1-pyrroline-5-carboxylate | (L)-isomer is the biologically active form; RN given refers to cpd without isomeric designation; structure |
imidazol-4-one-5-propionic acid | structure |
gamma-trimethylaminobutyraldehyde | intermediate in biosynthesis of carnitine from lysine; structure in first source |
Methylmethionine Sulfonium Chloride | |
adenosine monophosphate | Adenine nucleotide containing one phosphate group esterified to the sugar moiety in the 2'-, 3'-, or 5'-position. |
nad | A coenzyme composed of ribosylnicotinamide 5'-diphosphate coupled to adenosine 5'-phosphate by pyrophosphate linkage. It is found widely in nature and is involved in numerous enzymatic reactions in which it serves as an electron carrier by being alternately oxidized (NAD+) and reduced (NADH). (Dorland, 27th ed) |
NADP | Nicotinamide adenine dinucleotide phosphate. A coenzyme composed of ribosylnicotinamide 5'-phosphate (NMN) coupled by pyrophosphate linkage to the 5'-phosphate adenosine 2',5'-bisphosphate. It serves as an electron carrier in a number of reactions, being alternately oxidized (NADP+) and reduced (NADPH). (Dorland, 27th ed) |
NADP | Nicotinamide adenine dinucleotide phosphate. A coenzyme composed of ribosylnicotinamide 5'-phosphate (NMN) coupled by pyrophosphate linkage to the 5'-phosphate adenosine 2',5'-bisphosphate. It serves as an electron carrier in a number of reactions, being alternately oxidized (NADP+) and reduced (NADPH). (Dorland, 27th ed) |
saccharopine | lysine precursor in the aminoadipic acid-lysine pathway in yeast; minor descriptor (75-85); on-line & Index Medicus search LYSINE/analogs & derivatives (75-85); RN given refers to (L)-isomer |
kynurenine | A metabolite of the essential amino acid tryptophan metabolized via the tryptophan-kynurenine pathway. |
leukodopachrome | proposed metabolite in pathway from tyrosine to dopachrome; RN given refers to (S)-isomer; structure given in first source |
methylselenic acid | |
alpha-Ketoglutarate | |
Oxaloacetate | An anionic form of oxaloacetic acid. |
N-acetylaspartate | |
betaine aldehyde | |
formate | |
carnitine | A constituent of STRIATED MUSCLE and LIVER. It is an amino acid derivative and an essential cofactor for fatty acid metabolism. |
isobutyryl-coenzyme a | |
Carbamyl Phosphate | The monoanhydride of carbamic acid with PHOSPHORIC ACID. It is an important intermediate metabolite and is synthesized enzymatically by CARBAMYL-PHOSPHATE SYNTHASE (AMMONIA) and CARBAMOYL-PHOSPHATE SYNTHASE (GLUTAMINE-HYDROLYZING). |
tele-methylhistamine | histamine methyltransferase antagonist |
kynurenic acid | A broad-spectrum excitatory amino acid antagonist used as a research tool. |
Serotonin | A biochemical messenger and regulator, synthesized from the essential amino acid L-TRYPTOPHAN. In humans it is found primarily in the central nervous system, gastrointestinal tract, and blood platelets. Serotonin mediates several important physiological functions including neurotransmission, gastrointestinal motility, hemostasis, and cardiovascular integrity. Multiple receptor families (RECEPTORS, SEROTONIN) explain the broad physiological actions and distribution of this biochemical mediator. |
5'-methylthioadenosine | structure |
5'-deoxyadenosine | main heading DEOXYADENOSINE refers to the 3' cpd |
Cystathionine | Sulfur-containing amino acid formed as an intermediate in the conversion of METHIONINE to CYSTEINE. |
dopaquinone | proposed metabolite in pathway from tyrosine to dopachrome; RN given refers to cpd without isomeric designation; structure given in first source |
monoiodotyrosine | A product from the iodination of tyrosine. In the biosynthesis of thyroid hormones (THYROXINE and TRIIODOTHYRONINE), tyrosine is first iodized to monoiodotyrosine. |
2-keto-4-thiomethylbutyrate | |
3-phenylpyruvate | |
alpha-ketoglutaramate | deaminated metabolite of glutamine in csf of patients with hepatic coma; intermediate in the detoxification of ammonia in brain; structure |
n(1)-acetylspermidine | |
hydrogen selenide | RN given refers to parent cpd |
2-keto-4-hydroxyglutarate | RN given refers to parent cpd |
glutamate | |
glycolate | |
adenosine triphosphate | An adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter. |
alpha-ketobutyric acid | RN given refers to parent cpd; structure |
Creatinine | |
methaneselenol | RN given refers to (75)Se-labeled cpd |
Cysteine | A thiol-containing non-essential amino acid that is oxidized to form CYSTINE. |
tiglyl-coenzyme a | |
acetoacetate | |
trimethyllysine | stimulates growth of tumor cells; RN given refers to (S)-isomer |
polyglutamine | RN given for (D)-isomer |
Spermidine | A polyamine formed from putrescine. It is found in almost all tissues in association with nucleic acids. It is found as a cation at all pH values, and is thought to help stabilize some membranes and nucleic acid structures. It is a precursor of spermine. |
alpha-ketoadipic acid | |
gamma-butyrobetaine | RN given refers to hydroxide inner salt |
cocobetaine | N-alkyl-betaine; cause of shampoo dermatitis |
urocanic acid | 4-Imidazoleacrylic acid. |
3-aminopropionaldehyde | structure given in first source |
glyoxylic acid | RN given refers to parent cpd |
glycocyamine | RN given refers to parent cpd; structure |
hydrogen cyanide | Hydrogen cyanide (HCN); A toxic liquid or colorless gas. It is found in the smoke of various tobacco products and released by combustion of nitrogen-containing organic materials. |
indol-3-yl pyruvic acid | |
3-hydroxyanthranilic acid | An oxidation product of tryptophan metabolism. It may be a free radical scavenger and a carcinogen. |
lipoamide | RN given refers to cpd without isomeric designation |
N'-formylkynurenine | a photochemical breakdown product of tryptophan in proteins; RN given refers to parent cpd without isomeric designation |
3-mercaptopyruvic acid | RN given refers to parent cpd; structure |
5,6-dihydroxyindole | |
aspartame | Flavoring agent sweeter than sugar, metabolized as PHENYLALANINE and ASPARTIC ACID. |
selenomethylselenocysteine | RN given refers to parent cpd |
cysteine sulfinate | |
hydroxyl radical | The univalent radical OH. Hydroxyl radical is a potent oxidizing agent. |
methacrylyl-coenzyme A | |
2-methylacetoacetyl-coenzyme A | |
2-acetamidoglucal | found in urine of patient with sialuria |
adenosine 3'-phosphate-5'-phosphate | |
1-phospho-5-s-methylthioribulose | |
s-adenosylmethionine | Physiologic methyl radical donor involved in enzymatic transmethylation reactions and present in all living organisms. It possesses anti-inflammatory activity and has been used in treatment of chronic liver disease. (From Merck, 11th ed) |
2,5-dihydroxy-1,4-dithiane-2,5-dicarboxylic acid | prodrug of 3-mercaptopyruvate; antidote to cyanide poisoning; structure in first source |
Coenzyme A | |
Peremin | |
acetylgalactosamine | The N-acetyl derivative of galactosamine. |
Dehydroascorbic Acid | The reversibly oxidized form of ascorbic acid. It is the lactone of 2,3-DIKETOGULONIC ACID and has antiscorbutic activity in man on oral ingestion. |
selenocystathionine | structure in first source |
Spermine | A biogenic polyamine formed from spermidine. It is found in a wide variety of organisms and tissues and is an essential growth factor in some bacteria. It is found as a polycation at all pH values. Spermine is associated with nucleic acids, particularly in viruses, and is thought to stabilize the helical structure. |
Acetyl Coenzyme A | Acetyl CoA participates in the biosynthesis of fatty acids and sterols, in the oxidation of fatty acids and in the metabolism of many amino acids. It also acts as a biological acetylating agent. |
isovaleryl-coenzyme A | |
glutaryl-coenzyme A | |
Flavin-Adenine Dinucleotide | A condensation product of riboflavin and adenosine diphosphate. The coenzyme of various aerobic dehydrogenases, e.g., D-amino acid oxidase and L-amino acid oxidase. (Lehninger, Principles of Biochemistry, 1982, p972) |
heme | The color-furnishing portion of hemoglobin. It is found free in tissues and as the prosthetic group in many hemeproteins. |
creolin | from refined coal tar oils |
n-acetylaspartic acid | |
plasmenylserine | RN given refers to (L)-isomer |
n-acetylglutamic acid | RN given refers to (L)-isomer |
d-aspartic acid | The D-isomer of ASPARTIC ACID. |
n-acetylserotonin | |
trimethylselenonium | product of selenite metabolism in rats; RN given refers to parent cpd |
propionyl-coenzyme a | RN given refers to parent cpd |
thiocyanate | RN given refers to parent cpd |
oxalic acid | A strong dicarboxylic acid occurring in many plants and vegetables. It is produced in the body by metabolism of glyoxylic acid or ascorbic acid. It is not metabolized but excreted in the urine. It is used as an analytical reagent and general reducing agent. |
4-hydroxyphenylpyruvic acid | RN given refers to parent cpd |
lanthionine | a thioether analogue of cystine; RN given refers to (DL)-isomer; structure; a component of lantibiotics (BACTERIOCINS) |