Amino acid and derivative metabolism

Proteins (245)

Protein	Synonyms	Taxonomy
Arginine--tRNA ligase, cytoplasmic	EC 6.1.1.19; Arginyl-tRNA synthetase; ArgRS	Homo sapiens (human)
Hydroxyacid oxidase 1	HAOX1; EC 1.1.3.15; Glycolate oxidase; GOX	Homo sapiens (human)
Glycoprotein hormones alpha chain	Anterior pituitary glycoprotein hormones common subunit alpha; Choriogonadotropin alpha chain; Chorionic gonadotrophin subunit alpha; CG-alpha; Follicle-stimulating hormone alpha chain; FSH-alpha; Follitropin alpha chain; Luteinizing hormone alpha chain;	Homo sapiens (human)
[3-methyl-2-oxobutanoate dehydrogenase [lipoamide]] kinase, mitochondrial	EC 2.7.11.4; Branched-chain alpha-ketoacid dehydrogenase kinase; BCKD-kinase; BCKDHKIN	Homo sapiens (human)
Branched-chain-amino-acid aminotransferase, mitochondrial	BCAT(m); EC 2.6.1.42; Placental protein 18; PP18	Homo sapiens (human)
Aspartate aminotransferase, mitochondrial	mAspAT; EC 2.6.1.1; EC 2.6.1.7; Fatty acid-binding protein; FABP-1; Glutamate oxaloacetate transaminase 2; Kynurenine aminotransferase 4; Kynurenine aminotransferase IV; Kynurenine--oxoglutarate transaminase 4; Kynurenine--oxoglutarate transaminase IV; Pl	Homo sapiens (human)
Thyroid peroxidase	TPO; EC 1.11.1.8	Homo sapiens (human)
Serine--pyruvate aminotransferase	SPT; EC 2.6.1.51; Alanine--glyoxylate aminotransferase; AGT; 2.6.1.44	Homo sapiens (human)
Cystathionine gamma-lyase	EC 4.4.1.1; Cysteine-protein sulfhydrase; Gamma-cystathionase	Homo sapiens (human)
4-trimethylaminobutyraldehyde dehydrogenase	TMABA-DH; TMABALDH; EC 1.2.1.47; Aldehyde dehydrogenase E3 isozyme; Aldehyde dehydrogenase family 9 member A1; 1.2.1.3; Gamma-aminobutyraldehyde dehydrogenase; 1.2.1.19; R-aminobutyraldehyde dehydrogenase	Homo sapiens (human)
Iodotyrosine deiodinase 1	IYD-1; EC 1.21.1.1; Iodotyrosine dehalogenase 1	Homo sapiens (human)
2-amino-3-carboxymuconate-6-semialdehyde decarboxylase	EC 4.1.1.45; Picolinate carboxylase	Homo sapiens (human)
Glutaryl-CoA dehydrogenase, mitochondrial	GCD; EC 1.3.8.6	Homo sapiens (human)
3-hydroxyacyl-CoA dehydrogenase type-2	EC 1.1.1.35; 17-beta-estradiol 17-dehydrogenase; 1.1.1.62; 2-methyl-3-hydroxybutyryl-CoA dehydrogenase; MHBD; 3-alpha-(17-beta)-hydroxysteroid dehydrogenase (NAD(+)); 1.1.1.239; 3-hydroxy-2-methylbutyryl-CoA dehydrogenase; 1.1.1.178; 3-hydroxyacyl-CoA deh	Homo sapiens (human)
NmrA-like family domain-containing protein 1		Homo sapiens (human)
Hydroxyproline dehydrogenase	HYPDH; EC 1.5.5.3; Kidney and liver proline oxidase 1; HsPOX1; Probable proline dehydrogenase 2; 1.5.5.2; Probable proline oxidase 2	Homo sapiens (human)
Glutaminase liver isoform, mitochondrial	GLS; EC 3.5.1.2; L-glutaminase; L-glutamine amidohydrolase	Homo sapiens (human)
Sulfide:quinone oxidoreductase, mitochondrial	SQOR; EC 1.8.5.8; Sulfide dehydrogenase-like; Sulfide quinone oxidoreductase	Homo sapiens (human)
Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial	P5C dehydrogenase; EC 1.2.1.88; Aldehyde dehydrogenase family 4 member A1; L-glutamate gamma-semialdehyde dehydrogenase	Homo sapiens (human)
D-amino-acid oxidase	DAAO; DAMOX; DAO; EC 1.4.3.3	Homo sapiens (human)
Proteasome subunit beta type-9	EC 3.4.25.1; Low molecular mass protein 2; Macropain chain 7; Multicatalytic endopeptidase complex chain 7; Proteasome chain 7; Proteasome subunit beta-1i; Really interesting new gene 12 protein	Homo sapiens (human)
Glutamine synthetase	GS; EC 6.3.1.2; Glutamate--ammonia ligase; Palmitoyltransferase GLUL; 2.3.1.225	Homo sapiens (human)
Isoleucine--tRNA ligase, cytoplasmic	EC 6.1.1.5; Isoleucyl-tRNA synthetase; IRS; IleRS	Homo sapiens (human)
Methionine--tRNA ligase, cytoplasmic	EC 6.1.1.10; Methionyl-tRNA synthetase; MetRS	Homo sapiens (human)
5,6-dihydroxyindole-2-carboxylic acid oxidase	DHICA oxidase; EC 1.14.18.-; Catalase B; Glycoprotein 75; Melanoma antigen gp75; Tyrosinase-related protein 1; TRP; TRP-1; TRP1	Homo sapiens (human)
Enoyl-CoA hydratase, mitochondrial	EC 4.2.1.17; Enoyl-CoA hydratase 1; Short-chain enoyl-CoA hydratase; SCEH	Homo sapiens (human)
Maleylacetoacetate isomerase	MAAI; EC 5.2.1.2; GSTZ1-1; Glutathione S-transferase zeta 1; 2.5.1.18	Homo sapiens (human)
Alanine aminotransferase 1	ALT1; EC 2.6.1.2; Glutamate pyruvate transaminase 1; GPT 1; Glutamic--alanine transaminase 1; Glutamic--pyruvic transaminase 1	Homo sapiens (human)
Serine hydroxymethyltransferase, cytosolic	SHMT; EC 2.1.2.1; Glycine hydroxymethyltransferase; Serine methylase	Homo sapiens (human)
Tyrosinase	EC 1.14.18.1; LB24-AB; Monophenol monooxygenase; SK29-AB; Tumor rejection antigen AB	Homo sapiens (human)
Indoleamine 2,3-dioxygenase 1	IDO-1; EC 1.13.11.52; Indoleamine-pyrrole 2,3-dioxygenase	Homo sapiens (human)
NAD	EC 1.6.5.2; Azoreductase; DT-diaphorase; DTD; Menadione reductase; NAD(P)H:quinone oxidoreductase 1; Phylloquinone reductase; Quinone reductase 1; QR1	Homo sapiens (human)
S-adenosylmethionine decarboxylase proenzyme	AdoMetDC; SAMDC; EC 4.1.1.50	Homo sapiens (human)
Proteasome subunit beta type-1	Macropain subunit C5; Multicatalytic endopeptidase complex subunit C5; Proteasome component C5; Proteasome gamma chain	Homo sapiens (human)
Adenosylhomocysteinase	AdoHcyase; EC 3.3.1.1; S-adenosyl-L-homocysteine hydrolase	Homo sapiens (human)
D-aspartate oxidase	DASOX; DDO; EC 1.4.3.1	Homo sapiens (human)
Serine racemase	EC 5.1.1.18; D-serine ammonia-lyase; D-serine dehydratase; 4.3.1.18; L-serine ammonia-lyase; L-serine dehydratase; 4.3.1.17	Homo sapiens (human)
Aminoacyl tRNA synthase complex-interacting multifunctional protein 2	Multisynthase complex auxiliary component p38; Protein JTV-1	Homo sapiens (human)
Indoleamine 2,3-dioxygenase 2	IDO-2; EC 1.13.11.-; Indoleamine 2,3-dioxygenase-like protein 1; Indoleamine-pyrrole 2,3-dioxygenase-like protein 1	Homo sapiens (human)
Dimethylaniline monooxygenase [N-oxide-forming] 1	EC 1.14.13.8; Dimethylaniline oxidase 1; Fetal hepatic flavin-containing monooxygenase 1; FMO 1	Homo sapiens (human)
Aminoacyl tRNA synthase complex-interacting multifunctional protein 1	Multisynthase complex auxiliary component p43	Homo sapiens (human)
Pyrroline-5-carboxylate reductase 1, mitochondrial	P5C reductase 1; P5CR 1; EC 1.5.1.2	Homo sapiens (human)
Proteasome activator complex subunit 3	11S regulator complex subunit gamma; REG-gamma; Activator of multicatalytic protease subunit 3; Ki nuclear autoantigen; Proteasome activator 28 subunit gamma; PA28g; PA28gamma	Homo sapiens (human)
Pyrroline-5-carboxylate reductase 2	P5C reductase 2; P5CR 2; EC 1.5.1.2	Homo sapiens (human)
Glyoxylate reductase/hydroxypyruvate reductase	EC 1.1.1.79; EC 1.1.1.81	Homo sapiens (human)
Leucine--tRNA ligase, cytoplasmic	EC 6.1.1.4; Leucyl-tRNA synthetase; LeuRS	Homo sapiens (human)
Ornithine aminotransferase, mitochondrial	EC 2.6.1.13; Ornithine delta-aminotransferase; Ornithine--oxo-acid aminotransferase	Homo sapiens (human)
Creatine kinase M-type	EC 2.7.3.2; Creatine kinase M chain; Creatine phosphokinase M-type; CPK-M; M-CK	Homo sapiens (human)
Tyrosine 3-monooxygenase	EC 1.14.16.2; Tyrosine 3-hydroxylase; TH	Homo sapiens (human)
Ornithine decarboxylase	ODC; EC 4.1.1.17	Homo sapiens (human)
Creatine kinase B-type	EC 2.7.3.2; Brain creatine kinase; B-CK; Creatine kinase B chain; Creatine phosphokinase B-type; CPK-B	Homo sapiens (human)
Tyrosine aminotransferase	TAT; EC 2.6.1.5; L-tyrosine:2-oxoglutarate aminotransferase	Homo sapiens (human)
Spermidine synthase	SPDSY; EC 2.5.1.16; Putrescine aminopropyltransferase	Homo sapiens (human)
Proteasome subunit beta type-3	Proteasome chain 13; Proteasome component C10-II; Proteasome theta chain	Homo sapiens (human)
Large neutral amino acids transporter small subunit 1	4F2 light chain; 4F2 LC; 4F2LC; CD98 light chain; Integral membrane protein E16; E16; L-type amino acid transporter 1; hLAT1; Solute carrier family 7 member 5; y+ system cationic amino acid transporter	Homo sapiens (human)
Kynureninase	EC 3.7.1.3; L-kynurenine hydrolase	Homo sapiens (human)
4-hydroxy-2-oxoglutarate aldolase, mitochondrial	EC 4.1.3.16; Dihydrodipicolinate synthase-like; DHDPS-like protein; Probable 2-keto-4-hydroxyglutarate aldolase; Probable KHG-aldolase; Protein 569272	Homo sapiens (human)
D-3-phosphoglycerate dehydrogenase	3-PGDH; EC 1.1.1.95; 2-oxoglutarate reductase; 1.1.1.399; Malate dehydrogenase; 1.1.1.37	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 10	26S proteasome regulatory subunit p28; Gankyrin; p28(GANK)	Homo sapiens (human)
Kynurenine--oxoglutarate transaminase 3	EC 2.6.1.7; Cysteine-S-conjugate beta-lyase 2; 4.4.1.13; Kynurenine aminotransferase 3; Kynurenine aminotransferase III; KATIII; Kynurenine--glyoxylate transaminase; 2.6.1.63; Kynurenine--oxoglutarate transaminase III	Homo sapiens (human)
S-methylmethionine--homocysteine S-methyltransferase BHMT2	SMM-hcy methyltransferase; EC 2.1.1.10; Betaine--homocysteine S-methyltransferase 2	Homo sapiens (human)
Formimidoyltransferase-cyclodeaminase	Formiminotransferase-cyclodeaminase; FTCD; LCHC1	Homo sapiens (human)
Acyl carrier protein, mitochondrial	ACP; CI-SDAP; NADH-ubiquinone oxidoreductase 9.6 kDa subunit	Homo sapiens (human)
Aspartate aminotransferase, cytoplasmic	cAspAT; EC 2.6.1.1; EC 2.6.1.3; Cysteine aminotransferase, cytoplasmic; Cysteine transaminase, cytoplasmic; cCAT; Glutamate oxaloacetate transaminase 1; Transaminase A	Homo sapiens (human)
Diamine acetyltransferase 1	EC 2.3.1.57; Polyamine N-acetyltransferase 1; Putrescine acetyltransferase; Spermidine/spermine N(1)-acetyltransferase 1; SSAT; SSAT-1	Homo sapiens (human)
Histamine N-methyltransferase	HMT; EC 2.1.1.8	Homo sapiens (human)
Branched-chain-amino-acid aminotransferase, cytosolic	BCAT(c); EC 2.6.1.42; Protein ECA39	Homo sapiens (human)
Peroxisomal N(1)-acetyl-spermine/spermidine oxidase	EC 1.5.3.13; Polyamine oxidase	Homo sapiens (human)
Histidine decarboxylase	HDC; EC 4.1.1.22	Homo sapiens (human)
Carbamoyl-phosphate synthase [ammonia], mitochondrial	EC 6.3.4.16; Carbamoyl-phosphate synthetase I; CPSase I	Homo sapiens (human)
3-hydroxyisobutyrate dehydrogenase, mitochondrial	HIBADH; EC 1.1.1.31	Homo sapiens (human)
Serine--tRNA ligase, cytoplasmic	EC 6.1.1.11; Seryl-tRNA synthetase; SerRS; Seryl-tRNA(Ser/Sec) synthetase	Homo sapiens (human)
Guanidinoacetate N-methyltransferase	EC 2.1.1.2	Homo sapiens (human)
Glycine N-methyltransferase	EC 2.1.1.20	Homo sapiens (human)
Serotonin N-acetyltransferase	Serotonin acetylase; EC 2.3.1.87; Aralkylamine N-acetyltransferase; AA-NAT	Homo sapiens (human)
Mitochondrial 2-oxodicarboxylate carrier	Solute carrier family 25 member 21	Homo sapiens (human)
Glutaminase kidney isoform, mitochondrial	GLS; EC 3.5.1.2; K-glutaminase; L-glutamine amidohydrolase	Homo sapiens (human)
Arginase-1	EC 3.5.3.1; Liver-type arginase; Type I arginase	Homo sapiens (human)
Asparagine synthetase [glutamine-hydrolyzing]	EC 6.3.5.4; Cell cycle control protein TS11; Glutamine-dependent asparagine synthetase	Homo sapiens (human)
Phenylethanolamine N-methyltransferase	PNMTase; EC 2.1.1.28; Noradrenaline N-methyltransferase	Homo sapiens (human)
Proteasome subunit beta type-8	EC 3.4.25.1; Low molecular mass protein 7; Macropain subunit C13; Multicatalytic endopeptidase complex subunit C13; Proteasome component C13; Proteasome subunit beta-5i; Really interesting new gene 10 protein	Homo sapiens (human)
Proteasome subunit beta type-5	EC 3.4.25.1; Macropain epsilon chain; Multicatalytic endopeptidase complex epsilon chain; Proteasome chain 6; Proteasome epsilon chain; Proteasome subunit MB1; Proteasome subunit X	Homo sapiens (human)
Tryptophan 2,3-dioxygenase	TDO; EC 1.13.11.11; Tryptamin 2,3-dioxygenase; Tryptophan oxygenase; TO; TRPO; Tryptophan pyrrolase; Tryptophanase	Homo sapiens (human)
Proteasome subunit beta type-2	Macropain subunit C7-I; Multicatalytic endopeptidase complex subunit C7-I; Proteasome component C7-I	Homo sapiens (human)
Arginase-2, mitochondrial	EC 3.5.3.1; Arginase II; Kidney-type arginase; Non-hepatic arginase; Type II arginase	Homo sapiens (human)
S-methyl-5'-thioadenosine phosphorylase	EC 2.4.2.28; 5'-methylthioadenosine phosphorylase; MTA phosphorylase; MTAP; MTAPase	Homo sapiens (human)
Lysine--tRNA ligase	EC 2.7.7.-; EC 6.1.1.6; Lysyl-tRNA synthetase; LysRS	Homo sapiens (human)
Kynurenine--oxoglutarate transaminase 1	EC 2.6.1.7; Cysteine-S-conjugate beta-lyase; 4.4.1.13; Glutamine transaminase K; GTK; Glutamine--phenylpyruvate transaminase; 2.6.1.64; Kynurenine aminotransferase 1; Kynurenine aminotransferase I; KATI; Kynurenine--oxoglutarate transaminase I	Homo sapiens (human)
Thioredoxin reductase 1, cytoplasmic	TR; EC 1.8.1.9; Gene associated with retinoic and interferon-induced mortality 12 protein; GRIM-12; Gene associated with retinoic and IFN-induced mortality 12 protein; KM-102-derived reductase-like factor; Thioredoxin reductase TR1	Homo sapiens (human)
Kynurenine/alpha-aminoadipate aminotransferase, mitochondrial	KAT/AadAT; 2-aminoadipate aminotransferase; 2-aminoadipate transaminase; 2.6.1.39; Alpha-aminoadipate aminotransferase; AadAT; Kynurenine aminotransferase II; Kynurenine--oxoglutarate aminotransferase II; Kynurenine--oxoglutarate transaminase 2; 2.6.1.7;	Homo sapiens (human)
Betaine--homocysteine S-methyltransferase 1	EC 2.1.1.5	Homo sapiens (human)
Thioredoxin, mitochondrial	MTRX; Mt-Trx; Thioredoxin-2	Homo sapiens (human)
Cystathionine beta-synthase	EC 4.2.1.22; Beta-thionase; Serine sulfhydrase	Homo sapiens (human)
Methionine synthase	MS; EC 2.1.1.13; 5-methyltetrahydrofolate--homocysteine methyltransferase; Cobalamin-dependent methionine synthase; Vitamin-B12 dependent methionine synthase	Homo sapiens (human)
Phenylalanine-4-hydroxylase	PAH; EC 1.14.16.1; Phe-4-monooxygenase	Homo sapiens (human)
Ornithine transcarbamylase, mitochondrial	OTCase; EC 2.1.3.3; Ornithine carbamoyltransferase, mitochondrial	Homo sapiens (human)
Bifunctional glutamate/proline--tRNA ligase	Bifunctional aminoacyl-tRNA synthetase; Cell proliferation-inducing gene 32 protein; Glutamatyl-prolyl-tRNA synthetase	Homo sapiens (human)
Dopamine beta-hydroxylase	EC 1.14.17.1; Dopamine beta-monooxygenase	Homo sapiens (human)
Dihydropteridine reductase	EC 1.5.1.34; HDHPR; Quinoid dihydropteridine reductase; Short chain dehydrogenase/reductase family 33C member 1	Homo sapiens (human)
Histidine ammonia-lyase	Histidase; EC 4.3.1.3	Homo sapiens (human)
Glutamine--tRNA ligase	EC 6.1.1.18; Glutaminyl-tRNA synthetase; GlnRS	Homo sapiens (human)
Spermine synthase	SPMSY; EC 2.5.1.22; Spermidine aminopropyltransferase	Homo sapiens (human)
Thyroxine 5-deiodinase	EC 1.21.99.3; 5DIII; DIOIII; Type 3 DI; Type III iodothyronine deiodinase	Homo sapiens (human)
Peroxisomal sarcosine oxidase	PSO; EC 1.5.3.1; EC 1.5.3.7; L-pipecolate oxidase; L-pipecolic acid oxidase	Homo sapiens (human)
L-dopachrome tautomerase	DCT; DT; EC 5.3.3.12; L-dopachrome Delta-isomerase; Tyrosinase-related protein 2; TRP-2; TRP2	Homo sapiens (human)
Choline dehydrogenase, mitochondrial	CDH; CHD; EC 1.1.99.1	Homo sapiens (human)
Thiosulfate:glutathione sulfurtransferase	TST; EC 2.8.1.-	Homo sapiens (human)
O-phosphoseryl-tRNA(Sec) selenium transferase	EC 2.9.1.2; Liver-pancreas antigen; LP; SLA-p35; SLA/LP autoantigen; Selenocysteine synthase; Sec synthase; Selenocysteinyl-tRNA(Sec) synthase; Sep-tRNA:Sec-tRNA synthase; SepSecS; Soluble liver antigen; SLA; UGA suppressor tRNA-associated protein; tRNA(S	Homo sapiens (human)
Phosphoserine phosphatase	PSP; PSPase; EC 3.1.3.3; L-3-phosphoserine phosphatase; O-phosphoserine phosphohydrolase	Homo sapiens (human)
Cysteine dioxygenase type 1	EC 1.13.11.20; Cysteine dioxygenase type I; CDO; CDO-I	Homo sapiens (human)
Kynurenine formamidase	KFA; KFase; EC 3.5.1.9; Arylformamidase; N-formylkynurenine formamidase; FKF	Homo sapiens (human)
Cysteine sulfinic acid decarboxylase	EC 4.1.1.29; Aspartate 1-decarboxylase; 4.1.1.11; Cysteine-sulfinate decarboxylase; Sulfinoalanine decarboxylase	Homo sapiens (human)
Carnosine synthase 1	EC 6.3.2.11; ATP-grasp domain-containing protein 1	Homo sapiens (human)
Proteasome subunit beta type-11	EC 3.4.25.1; Proteasome subunit beta-5t	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 11	26S proteasome regulatory subunit RPN6; 26S proteasome regulatory subunit S9; 26S proteasome regulatory subunit p44.5	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 12	26S proteasome regulatory subunit RPN5; 26S proteasome regulatory subunit p55	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 14	EC 3.4.19.-; 26S proteasome regulatory subunit RPN11; 26S proteasome-associated PAD1 homolog 1	Homo sapiens (human)
Proteasome subunit alpha type-7	Proteasome subunit RC6-1; Proteasome subunit XAPC7	Homo sapiens (human)
Kynurenine 3-monooxygenase	EC 1.14.13.9; Kynurenine 3-hydroxylase	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 3	26S proteasome regulatory subunit RPN3; 26S proteasome regulatory subunit S3; Proteasome subunit p58	Homo sapiens (human)
Gamma-butyrobetaine dioxygenase	EC 1.14.11.1; Gamma-butyrobetaine hydroxylase; Gamma-BBH; Gamma-butyrobetaine,2-oxoglutarate dioxygenase	Homo sapiens (human)
Indolethylamine N-methyltransferase	Indolamine N-methyltransferase; EC 2.1.1.49; EC 2.1.1.96; Aromatic alkylamine N-methyltransferase; Amine N-methyltransferase; Arylamine N-methyltransferase; Thioether S-methyltransferase; TEMT	Homo sapiens (human)
26S proteasome regulatory subunit 6A	26S proteasome AAA-ATPase subunit RPT5; Proteasome 26S subunit ATPase 3; Proteasome subunit P50; Tat-binding protein 1; TBP-1	Homo sapiens (human)
Aromatic-L-amino-acid decarboxylase	AADC; EC 4.1.1.28; DOPA decarboxylase; DDC	Homo sapiens (human)
Acetyl-CoA acetyltransferase, mitochondrial	EC 2.3.1.9; Acetoacetyl-CoA thiolase; T2	Homo sapiens (human)
Proteasome subunit alpha type-1	30 kDa prosomal protein; PROS-30; Macropain subunit C2; Multicatalytic endopeptidase complex subunit C2; Proteasome component C2; Proteasome nu chain	Homo sapiens (human)
Proteasome subunit alpha type-2	Macropain subunit C3; Multicatalytic endopeptidase complex subunit C3; Proteasome component C3	Homo sapiens (human)
Proteasome subunit alpha type-3	Macropain subunit C8; Multicatalytic endopeptidase complex subunit C8; Proteasome component C8	Homo sapiens (human)
Proteasome subunit alpha type-4	Macropain subunit C9; Multicatalytic endopeptidase complex subunit C9; Proteasome component C9; Proteasome subunit L	Homo sapiens (human)
Proteasome subunit alpha type-5	Macropain zeta chain; Multicatalytic endopeptidase complex zeta chain; Proteasome zeta chain	Homo sapiens (human)
Proteasome subunit beta type-4	26 kDa prosomal protein; HsBPROS26; PROS-26; Macropain beta chain; Multicatalytic endopeptidase complex beta chain; Proteasome beta chain; Proteasome chain 3; HsN3	Homo sapiens (human)
Proteasome subunit beta type-6	EC 3.4.25.1; Macropain delta chain; Multicatalytic endopeptidase complex delta chain; Proteasome delta chain; Proteasome subunit Y	Homo sapiens (human)
4-hydroxyphenylpyruvate dioxygenase	EC 1.13.11.27; 4-hydroxyphenylpyruvic acid oxidase; 4HPPD; HPD; HPPDase	Homo sapiens (human)
26S proteasome regulatory subunit 7	26S proteasome AAA-ATPase subunit RPT1; Proteasome 26S subunit ATPase 2; Protein MSS1	Homo sapiens (human)
Proteasome subunit beta type-10	EC 3.4.25.1; Low molecular mass protein 10; Macropain subunit MECl-1; Multicatalytic endopeptidase complex subunit MECl-1; Proteasome MECl-1; Proteasome subunit beta-2i	Homo sapiens (human)
26S proteasome regulatory subunit 6B	26S proteasome AAA-ATPase subunit RPT3; MB67-interacting protein; MIP224; Proteasome 26S subunit ATPase 4; Tat-binding protein 7; TBP-7	Homo sapiens (human)
3-hydroxyanthranilate 3,4-dioxygenase	EC 1.13.11.6; 3-hydroxyanthranilate oxygenase; 3-HAO; h3HAO; 3-hydroxyanthranilic acid dioxygenase; HAD	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 8	26S proteasome regulatory subunit RPN12; 26S proteasome regulatory subunit S14; p31	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 7	26S proteasome regulatory subunit RPN8; 26S proteasome regulatory subunit S12; Mov34 protein homolog; Proteasome subunit p40	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 4	26S proteasome regulatory subunit RPN10; 26S proteasome regulatory subunit S5A; Antisecretory factor 1; AF; ASF; Multiubiquitin chain-binding protein	Homo sapiens (human)
26S proteasome complex subunit SEM1	26S proteasome complex subunit DSS1; Deleted in split hand/split foot protein 1; Split hand/foot deleted protein 1; Split hand/foot malformation type 1 protein	Homo sapiens (human)
Proteasome subunit alpha type-6	27 kDa prosomal protein; PROS-27; p27K; Macropain iota chain; Multicatalytic endopeptidase complex iota chain; Proteasome iota chain	Homo sapiens (human)
26S proteasome regulatory subunit 4	P26s4; 26S proteasome AAA-ATPase subunit RPT2; Proteasome 26S subunit ATPase 1	Homo sapiens (human)
26S proteasome regulatory subunit 8	26S proteasome AAA-ATPase subunit RPT6; Proteasome 26S subunit ATPase 5; Proteasome subunit p45; Thyroid hormone receptor-interacting protein 1; TRIP1; p45/SUG	Homo sapiens (human)
26S proteasome regulatory subunit 10B	26S proteasome AAA-ATPase subunit RPT4; Proteasome 26S subunit ATPase 6; Proteasome subunit p42	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 2	26S proteasome regulatory subunit RPN1; 26S proteasome regulatory subunit S2; 26S proteasome subunit p97; Protein 55.11; Tumor necrosis factor type 1 receptor-associated protein 2	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 6	26S proteasome regulatory subunit RPN7; 26S proteasome regulatory subunit S10; Breast cancer-associated protein SGA-113M; Phosphonoformate immuno-associated protein 4; Proteasome regulatory particle subunit p44S10; p42A	Homo sapiens (human)
Proteasome subunit alpha-type 8	Proteasome alpha 4 subunit; Alpha4s; Proteasome subunit alpha-type 7-like	Homo sapiens (human)
Proteasome subunit beta type-7	EC 3.4.25.1; Macropain chain Z; Multicatalytic endopeptidase complex chain Z; Proteasome subunit Z	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 1	26S proteasome regulatory subunit RPN2; 26S proteasome regulatory subunit S1; 26S proteasome subunit p112	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 13	26S proteasome regulatory subunit RPN9; 26S proteasome regulatory subunit S11; 26S proteasome regulatory subunit p40.5	Homo sapiens (human)
Proteasome activator complex subunit 1	11S regulator complex subunit alpha; REG-alpha; Activator of multicatalytic protease subunit 1; Interferon gamma up-regulated I-5111 protein; IGUP I-5111; Proteasome activator 28 subunit alpha; PA28a; PA28alpha	Homo sapiens (human)
Thiosulfate sulfurtransferase	EC 2.8.1.1; Rhodanese	Homo sapiens (human)
3-hydroxyisobutyryl-CoA hydrolase, mitochondrial	EC 3.1.2.4; 3-hydroxyisobutyryl-coenzyme A hydrolase; HIB-CoA hydrolase; HIBYL-CoA-H	Homo sapiens (human)
Proteasome activator complex subunit 2	11S regulator complex subunit beta; REG-beta; Activator of multicatalytic protease subunit 2; Proteasome activator 28 subunit beta; PA28b; PA28beta	Homo sapiens (human)
L-amino-acid oxidase	LAAO; LAO; EC 1.4.3.2; EC 1.4.3.25; Interleukin-4-induced protein 1; IL4-induced protein 1; hIL4I1; Protein Fig-1; hFIG1	Homo sapiens (human)
Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial	EC 2.3.1.168; 52 kDa mitochondrial autoantigen of primary biliary cirrhosis; Branched chain 2-oxo-acid dehydrogenase complex component E2; BCOADC-E2; Branched-chain alpha-keto acid dehydrogenase complex component E2; BCKAD-E2; BCKADE2; Dihydrolipoamide ac	Homo sapiens (human)
Antizyme inhibitor 1	AZI; AZI1; Ornithine decarboxylase antizyme inhibitor	Homo sapiens (human)
Persulfide dioxygenase ETHE1, mitochondrial	EC 1.13.11.18; Ethylmalonic encephalopathy protein 1; Hepatoma subtracted clone one protein; Sulfur dioxygenase ETHE1	Homo sapiens (human)
60 kDa lysophospholipase	LysoLP; EC 3.1.1.5; Lysophospholipase-transacylase	Homo sapiens (human)
1,2-dihydroxy-3-keto-5-methylthiopentene dioxygenase	EC 1.13.11.54; Acireductone dioxygenase (Fe(2+)-requiring); ARD; Fe-ARD; Membrane-type 1 matrix metalloproteinase cytoplasmic tail-binding protein 1; MTCBP-1; Submergence-induced protein-like factor; Sip-L	Homo sapiens (human)
Homogentisate 1,2-dioxygenase	EC 1.13.11.5; Homogentisate oxygenase; Homogentisic acid oxidase; Homogentisicase	Homo sapiens (human)
L-serine dehydratase/L-threonine deaminase	SDH; EC 4.3.1.17; L-serine deaminase; L-threonine dehydratase; TDH; 4.3.1.19	Homo sapiens (human)
Serine dehydratase-like	L-serine deaminase; L-serine dehydratase/L-threonine deaminase; L-threonine dehydratase; TDH; 4.3.1.19; Serine dehydratase 2; SDH 2; 4.3.1.17	Homo sapiens (human)
Argininosuccinate synthase	EC 6.3.4.5; Citrulline--aspartate ligase	Homo sapiens (human)
Dihydrolipoyl dehydrogenase, mitochondrial	EC 1.8.1.4; Dihydrolipoamide dehydrogenase; Glycine cleavage system L protein	Homo sapiens (human)
Isovaleryl-CoA dehydrogenase, mitochondrial	IVD; EC 1.3.8.4; Butyryl-CoA dehydrogenase; 1.3.8.1	Homo sapiens (human)
Sulfite oxidase, mitochondrial	EC 1.8.3.1	Homo sapiens (human)
Pyrroline-5-carboxylate reductase 3	P5C reductase 3; P5CR 3; EC 1.5.1.2; Pyrroline-5-carboxylate reductase-like protein	Homo sapiens (human)
Sodium/iodide cotransporter	Na(+)/I(-) cotransporter; Sodium-iodide symporter; Na(+)/I(-) symporter; Solute carrier family 5 member 5	Homo sapiens (human)
Antizyme inhibitor 2	AzI2; Arginine decarboxylase; ADC; ARGDC; Ornithine decarboxylase-like protein; ODC-like protein; ornithine decarboxylase paralog; ODC-p	Homo sapiens (human)
Phosphoserine aminotransferase	EC 2.6.1.52; Phosphohydroxythreonine aminotransferase; PSAT	Homo sapiens (human)
Trimethyllysine dioxygenase, mitochondrial	EC 1.14.11.8; Epsilon-trimethyllysine 2-oxoglutarate dioxygenase; Epsilon-trimethyllysine hydroxylase; TML hydroxylase; TML-alpha-ketoglutarate dioxygenase; TML dioxygenase; TMLD	Homo sapiens (human)
Creatine kinase U-type, mitochondrial	EC 2.7.3.2; Acidic-type mitochondrial creatine kinase; Mia-CK; Ubiquitous mitochondrial creatine kinase; U-MtCK	Homo sapiens (human)
Fumarylacetoacetase	FAA; EC 3.7.1.2; Beta-diketonase; Fumarylacetoacetate hydrolase	Homo sapiens (human)
Creatine kinase S-type, mitochondrial	EC 2.7.3.2; Basic-type mitochondrial creatine kinase; Mib-CK; Sarcomeric mitochondrial creatine kinase; S-MtCK	Homo sapiens (human)
Acetylserotonin O-methyltransferase	EC 2.1.1.4; Hydroxyindole O-methyltransferase; HIOMT	Homo sapiens (human)
Agmatinase, mitochondrial	EC 3.5.3.11; Agmatine ureohydrolase; AUH	Homo sapiens (human)
Methionine synthase reductase	MSR; EC 1.16.1.8; Aquacobalamin reductase; AqCbl reductase; 1.16.1.-	Homo sapiens (human)
2-aminoethanethiol dioxygenase	EC 1.13.11.19; Cysteamine dioxygenase	Homo sapiens (human)
Aspartoacylase	EC 3.5.1.15; Aminoacylase-2; ACY-2	Homo sapiens (human)
Lipoyl synthase, mitochondrial	EC 2.8.1.8; Lipoate synthase; LS; Lip-syn; Lipoic acid synthase	Homo sapiens (human)
Sarcosine dehydrogenase, mitochondrial	SarDH; EC 1.5.8.3; BPR-2	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 9	26S proteasome regulatory subunit p27	Homo sapiens (human)
Aspartate--tRNA ligase, cytoplasmic	EC 6.1.1.12; Aspartyl-tRNA synthetase; AspRS; Cell proliferation-inducing gene 40 protein	Homo sapiens (human)
Acidic amino acid decarboxylase GADL1	Aspartate 1-decarboxylase; ADC; HuADC; 4.1.1.11; Cysteine sulfinic acid decarboxylase; CSADC; HuCSADC; 4.1.1.29; Glutamate decarboxylase-like protein 1	Homo sapiens (human)
N-acetylglutamate synthase, mitochondrial	EC 2.3.1.1; Amino-acid acetyltransferase	Homo sapiens (human)
Type I iodothyronine deiodinase	EC 1.21.99.4; 5DI; DIOI; Type 1 DI; Type-I 5'-deiodinase	Homo sapiens (human)
Type II iodothyronine deiodinase	EC 1.21.99.4; 5DII; DIOII; Type 2 DI; Type-II 5'-deiodinase	Homo sapiens (human)
Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial	MCCase subunit alpha; EC 6.4.1.4; 3-methylcrotonyl-CoA carboxylase 1; 3-methylcrotonyl-CoA carboxylase biotin-containing subunit; 3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha	Homo sapiens (human)
Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial	MCCase subunit beta; EC 6.4.1.4; 3-methylcrotonyl-CoA carboxylase 2; 3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit; 3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta	Homo sapiens (human)
Dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial	EC 2.3.1.61; 2-oxoglutarate dehydrogenase complex component E2; OGDC-E2; Dihydrolipoamide succinyltransferase component of 2-oxoglutarate dehydrogenase complex; E2K	Homo sapiens (human)
Dimethylglycine dehydrogenase, mitochondrial	EC 1.5.8.4; ME2GLYDH	Homo sapiens (human)
Selenocysteine lyase	hSCL; EC 4.4.1.16	Homo sapiens (human)
2-amino-3-ketobutyrate coenzyme A ligase, mitochondrial	AKB ligase; EC 2.3.1.29; Aminoacetone synthase; Glycine acetyltransferase	Homo sapiens (human)
Lipoyltransferase 1, mitochondrial	EC 2.3.1.-; Lipoate biosynthesis protein; Lipoate-protein ligase; Lipoyl ligase	Homo sapiens (human)
Isoaspartyl peptidase/L-asparaginase	EC 3.4.19.5; EC 3.5.1.1; Asparaginase-like protein 1; Beta-aspartyl-peptidase; Isoaspartyl dipeptidase; L-asparagine amidohydrolase	Homo sapiens (human)
Urocanate hydratase	Urocanase; EC 4.2.1.49; Imidazolonepropionate hydrolase	Homo sapiens (human)
3-mercaptopyruvate sulfurtransferase	MST; EC 2.8.1.2	Homo sapiens (human)
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial	EC 1.2.4.4; Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain; BCKDE1A; BCKDH E1-alpha	Homo sapiens (human)
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial	EC 1.2.4.4; Branched-chain alpha-keto acid dehydrogenase E1 component beta chain; BCKDE1B; BCKDH E1-beta	Homo sapiens (human)
Enolase-phosphatase E1	EC 3.1.3.77; 2,3-diketo-5-methylthio-1-phosphopentane phosphatase; MASA homolog	Homo sapiens (human)
Selenide, water dikinase 2	EC 2.7.9.3; Selenium donor protein 2; Selenophosphate synthase 2	Homo sapiens (human)
Probable imidazolonepropionase	EC 3.5.2.7; Amidohydrolase domain-containing protein 1	Homo sapiens (human)
Methylthioribose-1-phosphate isomerase	M1Pi; MTR-1-P isomerase; EC 5.3.1.23; Mediator of RhoA-dependent invasion; S-methyl-5-thioribose-1-phosphate isomerase; Translation initiation factor eIF-2B subunit alpha/beta/delta-like protein	Homo sapiens (human)
Pterin-4-alpha-carbinolamine dehydratase	PHS; EC 4.2.1.96; 4-alpha-hydroxy-tetrahydropterin dehydratase; Dimerization cofactor of hepatocyte nuclear factor 1-alpha; DCoH; Dimerization cofactor of HNF1; Phenylalanine hydroxylase-stimulating protein; Pterin carbinolamine dehydratase; PCD	Homo sapiens (human)
Putative lipoyltransferase 2, mitochondrial	EC 2.3.1.181; Lipoate-protein ligase B; Lipoyl/octanoyl transferase; Octanoyl-[acyl-carrier-protein]-protein N-octanoyltransferase	Homo sapiens (human)
Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial	MMSDH; Malonate-semialdehyde dehydrogenase [acylating]; EC 1.2.1.18; EC 1.2.1.27; Aldehyde dehydrogenase family 6 member A1	Homo sapiens (human)
Hydroxylysine kinase	5-hydroxy-L-lysine kinase; EC 2.7.1.81; Aminoglycoside phosphotransferase domain-containing protein 1	Homo sapiens (human)
Proline dehydrogenase 1, mitochondrial	EC 1.5.5.2; Proline oxidase; Proline oxidase 2; p53-induced gene 6 protein	Homo sapiens (human)
Eukaryotic translation elongation factor 1 epsilon-1	Aminoacyl tRNA synthetase complex-interacting multifunctional protein 3; Elongation factor p18; Multisynthase complex auxiliary component p18	Homo sapiens (human)
Thyrotropin subunit beta	Thyroid-stimulating hormone subunit beta; TSH-B; TSH-beta; Thyrotropin beta chain	Homo sapiens (human)
Argininosuccinate lyase	ASAL; EC 4.3.2.1; Arginosuccinase	Homo sapiens (human)
4F2 cell-surface antigen heavy chain	4F2hc; 4F2 heavy chain antigen; Lymphocyte activation antigen 4F2 large subunit; Solute carrier family 3 member 2	Homo sapiens (human)
Glycine dehydrogenase (decarboxylating), mitochondrial	EC 1.4.4.2; Glycine cleavage system P protein; Glycine decarboxylase; Glycine dehydrogenase (aminomethyl-transferring)	Homo sapiens (human)
Glycine cleavage system H protein, mitochondrial	Lipoic acid-containing protein	Homo sapiens (human)
Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial	SBCAD; EC 1.3.8.5; 2-methyl branched chain acyl-CoA dehydrogenase; 2-MEBCAD; 2-methylbutyryl-coenzyme A dehydrogenase; 2-methylbutyryl-CoA dehydrogenase	Homo sapiens (human)
Aminomethyltransferase, mitochondrial	EC 2.1.2.10; Glycine cleavage system T protein; GCVT	Homo sapiens (human)
Alpha-aminoadipic semialdehyde dehydrogenase	Alpha-AASA dehydrogenase; EC 1.2.1.31; Aldehyde dehydrogenase family 7 member A1; 1.2.1.3; Antiquitin-1; Betaine aldehyde dehydrogenase; 1.2.1.8; Delta1-piperideine-6-carboxylate dehydrogenase; P6c dehydrogenase	Homo sapiens (human)
Glycine amidinotransferase, mitochondrial	EC 2.1.4.1; L-arginine:glycine amidinotransferase; Transamidinase	Homo sapiens (human)
2-iminobutanoate/2-iminopropanoate deaminase	EC 3.5.99.10; 14.5 kDa translational inhibitor protein; hp14.5; p14.5; Heat-responsive protein 12; Reactive intermediate imine deaminase A homolog; Translation inhibitor L-PSP ribonuclease; UK114 antigen homolog	Homo sapiens (human)
Selenocysteine-specific elongation factor	Elongation factor sec; Eukaryotic elongation factor, selenocysteine-tRNA-specific	Homo sapiens (human)
P protein	Melanocyte-specific transporter protein; Pink-eyed dilution protein homolog	Homo sapiens (human)
Methylglutaconyl-CoA hydratase, mitochondrial	EC 4.2.1.18; AU-specific RNA-binding enoyl-CoA hydratase; AU-binding protein/enoyl-CoA hydratase; Itaconyl-CoA hydratase; 4.2.1.56	Homo sapiens (human)
Ketimine reductase mu-crystallin	EC 1.5.1.25; NADP-regulated thyroid-hormone-binding protein	Homo sapiens (human)
Proteasome activator complex subunit 4	Proteasome activator PA200	Homo sapiens (human)
26S proteasome non-ATPase regulatory subunit 5	26S protease subunit S5 basic; 26S proteasome subunit S5B	Homo sapiens (human)
Proton-coupled amino acid transporter 4	Proton/amino acid transporter 4; Solute carrier family 36 member 4	Homo sapiens (human)
5-phosphohydroxy-L-lysine phospho-lyase	EC 4.2.3.134; Alanine--glyoxylate aminotransferase 2-like 2	Homo sapiens (human)
L-seryl-tRNA(Sec) kinase	EC 2.7.1.164; O-phosphoseryl-tRNA(Sec) kinase	Homo sapiens (human)
Inactive L-threonine 3-dehydrogenase, mitochondrial	Short chain dehydrogenase/reductase family 14E member 1 pseudogene	Homo sapiens (human)
Protein phosphatase 1K, mitochondrial	EC 3.1.3.16; PP2C domain-containing protein phosphatase 1K; PP2C-like mitochondrial protein; PP2C-type mitochondrial phosphoprotein phosphatase; PTMP; Protein phosphatase 2C isoform kappa; PP2C-kappa	Homo sapiens (human)
Carnosine N-methyltransferase	EC 2.1.1.22	Homo sapiens (human)
N-acetylaspartate synthetase	NAA synthetase; EC 2.3.1.17; Camello-like protein 3; N-acetyltransferase 8-like protein	Homo sapiens (human)
Choline transporter-like protein 1	CDw92; Solute carrier family 44 member 1	Homo sapiens (human)
Proteasome inhibitor PI31 subunit	hPI31	Homo sapiens (human)
Methylthioribulose-1-phosphate dehydratase	MTRu-1-P dehydratase; EC 4.2.1.109; APAF1-interacting protein; hAPIP	Homo sapiens (human)
Solute carrier family 25 member 44		Homo sapiens (human)
Selenocysteine insertion sequence-binding protein 2	SECIS-binding protein 2	Homo sapiens (human)
Alanine--glyoxylate aminotransferase 2, mitochondrial	AGT 2; EC 2.6.1.44; (R)-3-amino-2-methylpropionate--pyruvate transaminase; 2.6.1.40; Beta-ALAAT II; Beta-alanine-pyruvate aminotransferase; D-AIBAT	Homo sapiens (human)
Peroxisomal membrane protein 2	22 kDa peroxisomal membrane protein	Homo sapiens (human)
Mitochondrial dicarboxylate carrier	Solute carrier family 25 member 10	Homo sapiens (human)
Alpha-aminoadipic semialdehyde synthase, mitochondrial	LKR/SDH	Homo sapiens (human)
Isobutyryl-CoA dehydrogenase, mitochondrial	IBDH; EC 1.3.8.-; Activator-recruited cofactor 42 kDa component; ARC42; Acyl-CoA dehydrogenase family member 8; ACAD-8	Homo sapiens (human)
Membrane-associated transporter protein	Melanoma antigen AIM1; Protein AIM-1; Solute carrier family 45 member 2	Homo sapiens (human)

Compounds (160)

Compound	Description
hydronium ion
hydrogen sulfite
selenomethionine	Diagnostic aid in pancreas function determination.
selenic acid	A strong dibasic acid with the molecular formula H2SeO4. Included under this heading is the acid form, and inorganic salts of dihydrogen selenium tetraoxide.
urea	A compound formed in the liver from ammonia produced by the deamination of amino acids. It is the principal end product of protein catabolism and constitutes about one half of the total urinary solids.
Glutathione	A tripeptide with many roles in cells. It conjugates to drugs to make them more soluble for excretion, is a cofactor for some enzymes, is involved in protein disulfide bond rearrangement and reduces peroxides.
Arginine	An essential amino acid that is physiologically active in the L-form.
Thiamine Pyrophosphate	The coenzyme form of Vitamin B1 present in many animal tissues. It is a required intermediate in the PYRUVATE DEHYDROGENASE COMPLEX and the KETOGLUTARATE DEHYDROGENASE COMPLEX.
Succinate
acetic acid	Product of the oxidation of ethanol and of the destructive distillation of wood. It is used locally, occasionally internally, as a counterirritant and also as a reagent. (Stedman, 26th ed)
adenine	A purine base and a fundamental unit of ADENINE NUCLEOTIDES.
NADH
ammonium hydroxide	The hydroxy salt of ammonium ion. It is formed when AMMONIA reacts with water molecules in solution.
Ammonium
Copper	A heavy metal trace element with the atomic symbol Cu, atomic number 29, and atomic weight 63.55.
betaine	A naturally occurring compound that has been of interest for its role in osmoregulation. As a drug, betaine hydrochloride has been used as a source of hydrochloric acid in the treatment of hypochlorhydria. Betaine has also been used in the treatment of liver disorders, for hyperkalemia, for homocystinuria, and for gastrointestinal disturbances. (From Martindale, The Extra Pharmacopoeia, 30th ed, p1341)
hydroiodic acid
Copper	A heavy metal trace element with the atomic symbol Cu, atomic number 29, and atomic weight 63.55.
iron	A metallic element with atomic symbol Fe, atomic number 26, and atomic weight 55.85. It is an essential constituent of HEMOGLOBINS; CYTOCHROMES; and IRON-BINDING PROTEINS. It plays a role in cellular redox reactions and in the transport of OXYGEN.
Manganese	A trace element with atomic symbol Mn, atomic number 25, and atomic weight 54.94. It is concentrated in cell mitochondria, mostly in the pituitary gland, liver, pancreas, kidney, and bone, influences the synthesis of mucopolysaccharides, stimulates hepatic synthesis of cholesterol and fatty acids, and is a cofactor in many enzymes, including arginase and alkaline phosphatase in the liver. (From AMA Drug Evaluations Annual 1992, p2035)
Carbon Dioxide	A colorless, odorless gas that can be formed by the body and is necessary for the respiration cycle of plants and animals.
iodine	A nonmetallic element of the halogen group that is represented by the atomic symbol I, atomic number 53, and atomic weight of 126.90. It is a nutritionally essential element, especially important in thyroid hormone synthesis. In solution, it has anti-infective properties and is used topically.
choline	A basic constituent of lecithin that is found in many plants and animal organs. It is important as a precursor of acetylcholine, as a methyl donor in various metabolic processes, and in lipid metabolism.
Zinc	A metallic element of atomic number 30 and atomic weight 65.38. It is a necessary trace element in the diet, forming an essential part of many enzymes, and playing an important role in protein synthesis and in cell division. Zinc deficiency is associated with ANEMIA, short stature, HYPOGONADISM, impaired WOUND HEALING, and geophagia. It is known by the symbol Zn.
Orthophosphate
Dopamine Hydrochloride
hydrogen sulfide	A flammable, poisonous gas with a characteristic odor of rotten eggs. It is used in the manufacture of chemicals, in metallurgy, and as an analytical reagent. (From Merck Index, 11th ed)
Glutathione Disulfide	A GLUTATHIONE dimer formed by a disulfide bond between the cysteine sulfhydryl side chains during the course of being oxidized.
Flavin Mononucleotide	A coenzyme for a number of oxidative enzymes including NADH DEHYDROGENASE. It is the principal form in which RIBOFLAVIN is found in cells and tissues.
ubiquinol 1
coenzyme q10	Ubiquinone ring with a chain of 10 isoprene units; redox equilibrium with ubiqunol serving in mitochondrial inner membrane to transfer electrons; presence during reconstitution of acetylcholine receptor into phospholipid vesicles yields vesicles active in catalyzing carbamylcholine-sensitive Na+ flux; coenzyme Q10 depletion has been noted with use of statins
Cobalamins
Aspartate
fumarates	Compounds based on fumaric acid.
thyroxine	The major hormone derived from the thyroid gland. Thyroxine is synthesized via the iodination of tyrosines (MONOIODOTYROSINE) and the coupling of iodotyrosines (DIIODOTYROSINE) in the THYROGLOBULIN. Thyroxine is released from thyroglobulin by proteolysis and secreted into the blood. Thyroxine is peripherally deiodinated to form TRIIODOTHYRONINE which exerts a broad spectrum of stimulatory effects on cell metabolism.
adenosine	A nucleoside that is composed of ADENINE and D-RIBOSE. Adenosine or adenosine derivatives play many important biological roles in addition to being components of DNA and RNA. Adenosine itself is a neurotransmitter.
selenocysteine	A naturally occurring amino acid in both eukaryotic and prokaryotic organisms. It is found in tRNAs and in the catalytic site of some enzymes. The genes for glutathione peroxidase and formate dehydrogenase contain the TGA codon, which codes for this amino acid.
adenosine diphosphate	Adenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position.
formaldehyde	A highly reactive aldehyde gas formed by oxidation or incomplete combustion of hydrocarbons. In solution, it has a wide range of uses: in the manufacture of resins and textiles, as a disinfectant, and as a laboratory fixative or preservative. Formaldehyde solution (formalin) is considered a hazardous compound, and its vapor toxic. (From Reynolds, Martindale The Extra Pharmacopoeia, 30th ed, p717)
hydrogen carbonate
Hydrogen Peroxide	A strong oxidizing agent used in aqueous solution as a ripening agent, bleach, and topical anti-infective. It is relatively unstable and solutions deteriorate over time unless stabilized by the addition of acetanilide or similar organic materials.
iodine	A nonmetallic element of the halogen group that is represented by the atomic symbol I, atomic number 53, and atomic weight of 126.90. It is a nutritionally essential element, especially important in thyroid hormone synthesis. In solution, it has anti-infective properties and is used topically.
methanol	A colorless, flammable liquid used in the manufacture of FORMALDEHYDE and ACETIC ACID, in chemical synthesis, antifreeze, and as a solvent. Ingestion of methanol is toxic and may cause blindness.
Magnesium	A metallic element that has the atomic symbol Mg, atomic number 12, and atomic weight 24.31. It is important for the activity of many enzymes, especially those involved in OXIDATIVE PHOSPHORYLATION.
melatonin	A biogenic amine that is found in animals and plants. In mammals, melatonin is produced by the PINEAL GLAND. Its secretion increases in darkness and decreases during exposure to light. Melatonin is implicated in the regulation of SLEEP, mood, and REPRODUCTION. Melatonin is also an effective antioxidant.
Sodium	A member of the alkali group of metals. It has the atomic symbol Na, atomic number 11, and atomic weight 23.
Water	A clear, odorless, tasteless liquid that is essential for most animal and plant life and is an excellent solvent for many substances. The chemical formula is hydrogen oxide (H2O). (McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed)
Oxygen	An element with atomic symbol O, atomic number 8, and atomic weight [15.99903; 15.99977]. It is the most abundant element on earth and essential for respiration.
Guanosine Monophosphate	A guanine nucleotide containing one phosphate group esterified to the sugar moiety and found widely in nature.
5,6,7,8-tetrahydrofolic acid	RN given refers to (DL)-isomer
5,10-methylenetetrahydrofolate
5'-methylthioribose 1-phosphate
1,5-dihydro-FAD	chromophore component of E coli DNA photolyase
selenodiglutathione
Guanosine Diphosphate	A guanine nucleotide containing two phosphate groups esterified to the sugar moiety.
sapropterin	RN given refers to parent cpd; co-factor required for catalytic activity of nitric oxide synthases
4a-hydroxytetrahydrobiopterin	structure given in first source
pqq cofactor	A pyrrolo-quinoline having two adjacent keto-groups at the 4 and 5 positions and three acidic carboxyl groups. It is a coenzyme of some DEHYDROGENASES.
2-amino-4-(2-aminoethoxy)butanoic acid, (DL)-isomer
phosphohydroxypyruvic acid
Pyruvic Acid	An intermediate compound in the metabolism of carbohydrates, proteins, and fats. In thiamine deficiency, its oxidation is retarded and it accumulates in the tissues, especially in nervous structures. (From Stedman, 26th ed)
Selenite
sulfites	Inorganic salts of sulfurous acid.
dimethylselenide	RN given refers to unlabeled cpd
3-hydroxykynurenine, (L)-isomer
dopachrome	cyclization product of L-DOPA
delta-1-pyrroline-5-carboxylate	(L)-isomer is the biologically active form; RN given refers to cpd without isomeric designation; structure
imidazol-4-one-5-propionic acid	structure
gamma-trimethylaminobutyraldehyde	intermediate in biosynthesis of carnitine from lysine; structure in first source
Methylmethionine Sulfonium Chloride
adenosine monophosphate	Adenine nucleotide containing one phosphate group esterified to the sugar moiety in the 2'-, 3'-, or 5'-position.
nad	A coenzyme composed of ribosylnicotinamide 5'-diphosphate coupled to adenosine 5'-phosphate by pyrophosphate linkage. It is found widely in nature and is involved in numerous enzymatic reactions in which it serves as an electron carrier by being alternately oxidized (NAD+) and reduced (NADH). (Dorland, 27th ed)
NADP	Nicotinamide adenine dinucleotide phosphate. A coenzyme composed of ribosylnicotinamide 5'-phosphate (NMN) coupled by pyrophosphate linkage to the 5'-phosphate adenosine 2',5'-bisphosphate. It serves as an electron carrier in a number of reactions, being alternately oxidized (NADP+) and reduced (NADPH). (Dorland, 27th ed)
NADP	Nicotinamide adenine dinucleotide phosphate. A coenzyme composed of ribosylnicotinamide 5'-phosphate (NMN) coupled by pyrophosphate linkage to the 5'-phosphate adenosine 2',5'-bisphosphate. It serves as an electron carrier in a number of reactions, being alternately oxidized (NADP+) and reduced (NADPH). (Dorland, 27th ed)
saccharopine	lysine precursor in the aminoadipic acid-lysine pathway in yeast; minor descriptor (75-85); on-line & Index Medicus search LYSINE/analogs & derivatives (75-85); RN given refers to (L)-isomer
kynurenine	A metabolite of the essential amino acid tryptophan metabolized via the tryptophan-kynurenine pathway.
leukodopachrome	proposed metabolite in pathway from tyrosine to dopachrome; RN given refers to (S)-isomer; structure given in first source
methylselenic acid
alpha-Ketoglutarate
Oxaloacetate	An anionic form of oxaloacetic acid.
N-acetylaspartate
betaine aldehyde
formate
carnitine	A constituent of STRIATED MUSCLE and LIVER. It is an amino acid derivative and an essential cofactor for fatty acid metabolism.
isobutyryl-coenzyme a
Carbamyl Phosphate	The monoanhydride of carbamic acid with PHOSPHORIC ACID. It is an important intermediate metabolite and is synthesized enzymatically by CARBAMYL-PHOSPHATE SYNTHASE (AMMONIA) and CARBAMOYL-PHOSPHATE SYNTHASE (GLUTAMINE-HYDROLYZING).
tele-methylhistamine	histamine methyltransferase antagonist
kynurenic acid	A broad-spectrum excitatory amino acid antagonist used as a research tool.
Serotonin	A biochemical messenger and regulator, synthesized from the essential amino acid L-TRYPTOPHAN. In humans it is found primarily in the central nervous system, gastrointestinal tract, and blood platelets. Serotonin mediates several important physiological functions including neurotransmission, gastrointestinal motility, hemostasis, and cardiovascular integrity. Multiple receptor families (RECEPTORS, SEROTONIN) explain the broad physiological actions and distribution of this biochemical mediator.
5'-methylthioadenosine	structure
5'-deoxyadenosine	main heading DEOXYADENOSINE refers to the 3' cpd
Cystathionine	Sulfur-containing amino acid formed as an intermediate in the conversion of METHIONINE to CYSTEINE.
dopaquinone	proposed metabolite in pathway from tyrosine to dopachrome; RN given refers to cpd without isomeric designation; structure given in first source
monoiodotyrosine	A product from the iodination of tyrosine. In the biosynthesis of thyroid hormones (THYROXINE and TRIIODOTHYRONINE), tyrosine is first iodized to monoiodotyrosine.
2-keto-4-thiomethylbutyrate
3-phenylpyruvate
alpha-ketoglutaramate	deaminated metabolite of glutamine in csf of patients with hepatic coma; intermediate in the detoxification of ammonia in brain; structure
n(1)-acetylspermidine
hydrogen selenide	RN given refers to parent cpd
2-keto-4-hydroxyglutarate	RN given refers to parent cpd
glutamate
glycolate
adenosine triphosphate	An adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter.
alpha-ketobutyric acid	RN given refers to parent cpd; structure
Creatinine
methaneselenol	RN given refers to (75)Se-labeled cpd
Cysteine	A thiol-containing non-essential amino acid that is oxidized to form CYSTINE.
tiglyl-coenzyme a
acetoacetate
trimethyllysine	stimulates growth of tumor cells; RN given refers to (S)-isomer
polyglutamine	RN given for (D)-isomer
Spermidine	A polyamine formed from putrescine. It is found in almost all tissues in association with nucleic acids. It is found as a cation at all pH values, and is thought to help stabilize some membranes and nucleic acid structures. It is a precursor of spermine.
alpha-ketoadipic acid
gamma-butyrobetaine	RN given refers to hydroxide inner salt
cocobetaine	N-alkyl-betaine; cause of shampoo dermatitis
urocanic acid	4-Imidazoleacrylic acid.
3-aminopropionaldehyde	structure given in first source
glyoxylic acid	RN given refers to parent cpd
glycocyamine	RN given refers to parent cpd; structure
hydrogen cyanide	Hydrogen cyanide (HCN); A toxic liquid or colorless gas. It is found in the smoke of various tobacco products and released by combustion of nitrogen-containing organic materials.
indol-3-yl pyruvic acid
3-hydroxyanthranilic acid	An oxidation product of tryptophan metabolism. It may be a free radical scavenger and a carcinogen.
lipoamide	RN given refers to cpd without isomeric designation
N'-formylkynurenine	a photochemical breakdown product of tryptophan in proteins; RN given refers to parent cpd without isomeric designation
3-mercaptopyruvic acid	RN given refers to parent cpd; structure
5,6-dihydroxyindole
aspartame	Flavoring agent sweeter than sugar, metabolized as PHENYLALANINE and ASPARTIC ACID.
selenomethylselenocysteine	RN given refers to parent cpd
cysteine sulfinate
hydroxyl radical	The univalent radical OH. Hydroxyl radical is a potent oxidizing agent.
methacrylyl-coenzyme A
2-methylacetoacetyl-coenzyme A
2-acetamidoglucal	found in urine of patient with sialuria
adenosine 3'-phosphate-5'-phosphate
1-phospho-5-s-methylthioribulose
s-adenosylmethionine	Physiologic methyl radical donor involved in enzymatic transmethylation reactions and present in all living organisms. It possesses anti-inflammatory activity and has been used in treatment of chronic liver disease. (From Merck, 11th ed)
2,5-dihydroxy-1,4-dithiane-2,5-dicarboxylic acid	prodrug of 3-mercaptopyruvate; antidote to cyanide poisoning; structure in first source
Coenzyme A
Peremin
acetylgalactosamine	The N-acetyl derivative of galactosamine.
Dehydroascorbic Acid	The reversibly oxidized form of ascorbic acid. It is the lactone of 2,3-DIKETOGULONIC ACID and has antiscorbutic activity in man on oral ingestion.
selenocystathionine	structure in first source
Spermine	A biogenic polyamine formed from spermidine. It is found in a wide variety of organisms and tissues and is an essential growth factor in some bacteria. It is found as a polycation at all pH values. Spermine is associated with nucleic acids, particularly in viruses, and is thought to stabilize the helical structure.
Acetyl Coenzyme A	Acetyl CoA participates in the biosynthesis of fatty acids and sterols, in the oxidation of fatty acids and in the metabolism of many amino acids. It also acts as a biological acetylating agent.
isovaleryl-coenzyme A
glutaryl-coenzyme A
Flavin-Adenine Dinucleotide	A condensation product of riboflavin and adenosine diphosphate. The coenzyme of various aerobic dehydrogenases, e.g., D-amino acid oxidase and L-amino acid oxidase. (Lehninger, Principles of Biochemistry, 1982, p972)
heme	The color-furnishing portion of hemoglobin. It is found free in tissues and as the prosthetic group in many hemeproteins.
creolin	from refined coal tar oils
n-acetylaspartic acid
plasmenylserine	RN given refers to (L)-isomer
n-acetylglutamic acid	RN given refers to (L)-isomer
d-aspartic acid	The D-isomer of ASPARTIC ACID.
n-acetylserotonin
trimethylselenonium	product of selenite metabolism in rats; RN given refers to parent cpd
propionyl-coenzyme a	RN given refers to parent cpd
thiocyanate	RN given refers to parent cpd
oxalic acid	A strong dicarboxylic acid occurring in many plants and vegetables. It is produced in the body by metabolism of glyoxylic acid or ascorbic acid. It is not metabolized but excreted in the urine. It is used as an analytical reagent and general reducing agent.
4-hydroxyphenylpyruvic acid	RN given refers to parent cpd
lanthionine	a thioether analogue of cystine; RN given refers to (DL)-isomer; structure; a component of lantibiotics (BACTERIOCINS)

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Amino acid and derivative metabolism

Proteins (245)

Compounds (160)