Pathways > Adrenoleukodystrophy, X-Linked
Page last updated: 2024-10-06

Adrenoleukodystrophy, X-Linked

Proteins (10)

ProteinSynonymsTaxonomy
Peroxisomal carnitine O-octanoyltransferaseCOT; EC 2.3.1.137Homo sapiens (human)
Long-chain-fatty-acid--CoA ligase 1EC 6.2.1.3; Acyl-CoA synthetase 1; ACS1; Arachidonate--CoA ligase; 6.2.1.15; Long-chain acyl-CoA synthetase 1; LACS 1; Long-chain acyl-CoA synthetase 2; LACS 2; Long-chain fatty acid-CoA ligase 2; Palmitoyl-CoA ligase 1; Palmitoyl-CoA ligase 2; Phytanate-Homo sapiens (human)
Mitochondrial carnitine/acylcarnitine carrier proteinCarnitine/acylcarnitine translocase; CAC; Solute carrier family 25 member 20Homo sapiens (human)
Peroxisomal membrane protein PEX14PTS1 receptor-docking protein; Peroxin-14; Peroxisomal membrane anchor protein PEX14Homo sapiens (human)
Carnitine O-palmitoyltransferase 2, mitochondrialEC 2.3.1.21; Carnitine palmitoyltransferase II; CPT IIHomo sapiens (human)
Carnitine O-acetyltransferaseCarnitine acetylase; EC 2.3.1.137; EC 2.3.1.7; Carnitine acetyltransferase; CAT; CrATHomo sapiens (human)
ATP-binding cassette sub-family D member 1EC 7.6.2.4; Adrenoleukodystrophy protein; ALDPHomo sapiens (human)
Peroxisomal membrane protein PEX13Peroxin-13Homo sapiens (human)
Peroxisomal membrane protein 11CPeroxin-11C; Peroxisomal biogenesis factor 11C; Protein PEX11 homolog gamma; PEX11-gammaHomo sapiens (human)
ATP-binding cassette sub-family D member 2Adrenoleukodystrophy-like 1; Adrenoleukodystrophy-related protein; hALDRHomo sapiens (human)

Compounds (12)

CompoundDescription
acetylcarnitineAn acetic acid ester of CARNITINE that facilitates movement of ACETYL COA into the matrices of mammalian MITOCHONDRIA during the oxidation of FATTY ACIDS.
levocarnitine
lauric acid
Adenosine TriphosphateAn adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter.
adenosine diphosphateAdenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position.
Coenzyme A
S-tetradecanoyl-coenzyme A
hexacosanoic acida C(26) saturated acid
lignoceric acidRN given refers to parent cpd; structure
lauroyl-coenzyme a
lignoceroyl-coenzyme a
acetyl coenzyme aAcetyl CoA participates in the biosynthesis of fatty acids and sterols, in the oxidation of fatty acids and in the metabolism of many amino acids. It also acts as a biological acetylating agent.