Pathways > Adrenoleukodystrophy, X-Linked
Page last updated: 2024-10-06
Adrenoleukodystrophy, X-Linked
Proteins (10)
| Protein | Synonyms | Taxonomy |
|---|
| Peroxisomal carnitine O-octanoyltransferase | COT; EC 2.3.1.137 | Homo sapiens (human) |
| Long-chain-fatty-acid--CoA ligase 1 | EC 6.2.1.3; Acyl-CoA synthetase 1; ACS1; Arachidonate--CoA ligase; 6.2.1.15; Long-chain acyl-CoA synthetase 1; LACS 1; Long-chain acyl-CoA synthetase 2; LACS 2; Long-chain fatty acid-CoA ligase 2; Palmitoyl-CoA ligase 1; Palmitoyl-CoA ligase 2; Phytanate- | Homo sapiens (human) |
| Mitochondrial carnitine/acylcarnitine carrier protein | Carnitine/acylcarnitine translocase; CAC; Solute carrier family 25 member 20 | Homo sapiens (human) |
| Peroxisomal membrane protein PEX14 | PTS1 receptor-docking protein; Peroxin-14; Peroxisomal membrane anchor protein PEX14 | Homo sapiens (human) |
| Carnitine O-palmitoyltransferase 2, mitochondrial | EC 2.3.1.21; Carnitine palmitoyltransferase II; CPT II | Homo sapiens (human) |
| Carnitine O-acetyltransferase | Carnitine acetylase; EC 2.3.1.137; EC 2.3.1.7; Carnitine acetyltransferase; CAT; CrAT | Homo sapiens (human) |
| ATP-binding cassette sub-family D member 1 | EC 7.6.2.4; Adrenoleukodystrophy protein; ALDP | Homo sapiens (human) |
| Peroxisomal membrane protein PEX13 | Peroxin-13 | Homo sapiens (human) |
| Peroxisomal membrane protein 11C | Peroxin-11C; Peroxisomal biogenesis factor 11C; Protein PEX11 homolog gamma; PEX11-gamma | Homo sapiens (human) |
| ATP-binding cassette sub-family D member 2 | Adrenoleukodystrophy-like 1; Adrenoleukodystrophy-related protein; hALDR | Homo sapiens (human) |
Compounds (12)
| Compound | Description |
|---|
| acetylcarnitine | An acetic acid ester of CARNITINE that facilitates movement of ACETYL COA into the matrices of mammalian MITOCHONDRIA during the oxidation of FATTY ACIDS. |
| levocarnitine | |
| lauric acid | |
| Adenosine Triphosphate | An adenine nucleotide containing three phosphate groups esterified to the sugar moiety. In addition to its crucial roles in metabolism adenosine triphosphate is a neurotransmitter. |
| adenosine diphosphate | Adenosine 5'-(trihydrogen diphosphate). An adenine nucleotide containing two phosphate groups esterified to the sugar moiety at the 5'-position. |
| Coenzyme A | |
| S-tetradecanoyl-coenzyme A | |
| hexacosanoic acid | a C(26) saturated acid |
| lignoceric acid | RN given refers to parent cpd; structure |
| lauroyl-coenzyme a | |
| lignoceroyl-coenzyme a | |
| acetyl coenzyme a | Acetyl CoA participates in the biosynthesis of fatty acids and sterols, in the oxidation of fatty acids and in the metabolism of many amino acids. It also acts as a biological acetylating agent. |