valine has been researched along with Metabolic Acidosis in 23 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 15 (65.22) | 18.7374 |
1990's | 4 (17.39) | 18.2507 |
2000's | 3 (13.04) | 29.6817 |
2010's | 1 (4.35) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Cao, H; Chu, XP; Duan, B; Hansen, J; Huang, Y; Simon, RP; Wang, YZ; Xiong, ZG; Xu, TL; Yang, T; Yu, Y; Zhu, MX | 1 |
CHILDS, B; NYHAN, WL | 1 |
Cronberg, T; Jensen, K; Rytter, A; Wieloch, T | 1 |
Astruc, J; Bellet, H; Brunel, D; Froye, E; Luciani, JM; Magnan de Bornier, P | 1 |
Efron, ML | 1 |
Edelmann, CM; Finberg, L; Soriano, JR; Taitz, LS | 1 |
Thompson, JR; Zhou, X | 1 |
Anderstam, B; Bergström, J; Löfberg, E; Wernerman, J | 1 |
Bailey, JL; Caban, R; England, BK; Marinovic, AC; Maroni, BJ; Mitch, WE; Price, SR; Reaich, D | 1 |
Holecek, M; Sprongl, L; Tichý, M; Tilser, I | 1 |
Crevels, J; De Abreu, RA; Engelke, UF; Jongsma, HW; Moolenaar, SH; Nijhuis, JG; Nijland, R; Oeseburg, B; Van Cappellen Van Walsum, AM; Wevers, RA | 1 |
Landaas, S | 1 |
Porath, U; Schreier, K | 1 |
Grüttner, R; Held, KR; Plettner, C; Singh, S; Sternowsky, HJ | 1 |
Glassberg, R; Indo, Y; Tanaka, K; Yokota, I | 1 |
Hara, Y; Kelly, RA; May, RC; Mitch, WE | 1 |
Draffan, GH; Gompertz, D; Hull, D; Watts, JL | 1 |
Chaussain, JL; Georges, P; Job, JC; Olive, G | 1 |
Ando, T; Hull, D; Nyhan, WL; Rasmussen, K | 1 |
Frimpter, GW | 1 |
Ando, T; Fawcett, N; Julius, RL; Nyhan, WL; Rennert, OM | 1 |
Lindblad, B; Lindstrand, K; Svanberg, B; Zetterström, R | 1 |
Hsia, YE; Lilljeqvist, AC; Rosenberg, LE | 1 |
2 review(s) available for valine and Metabolic Acidosis
Article | Year |
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[Congenital metabolic acidosis in the postnatal period].
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine | 1978 |
Aminoacidurias due to inherited disorders of metabolism. 2.
Topics: Acidosis; Alanine; Amino Acid Metabolism, Inborn Errors; Arginase; Arginine; Carbamates; Citrulline; Dipeptides; Glutarates; Glycine; Histidine; Humans; Hydroxyproline; Hyperglycemia; Infant, Newborn; Keto Acids; Lysine; Malonates; Maple Syrup Urine Disease; Ornithine Carbamoyltransferase; Phosphotransferases; Proline; Sarcosine; Succinates; Urea; Valine | 1973 |
21 other study(ies) available for valine and Metabolic Acidosis
Article | Year |
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Extracellular spermine exacerbates ischemic neuronal injury through sensitization of ASIC1a channels to extracellular acidosis.
Topics: Acid Sensing Ion Channels; Acidosis; Amino Acid Transport System y+; Animals; Biophysics; Brain Injuries; Calcium; Cells, Cultured; CHO Cells; Cricetinae; Cricetulus; Disease Models, Animal; Dose-Response Relationship, Drug; Drug Combinations; Drug Interactions; Electric Stimulation; Embryo, Mammalian; Excitatory Amino Acid Antagonists; Extracellular Fluid; GABA Antagonists; Glucose; Hippocampus; Hydrogen-Ion Concentration; Hypoxia; Infarction, Middle Cerebral Artery; L-Lactate Dehydrogenase; Membrane Potentials; Mice; Mice, Knockout; Mutation; Nerve Tissue Proteins; Neurons; Oligonucleotides; Patch-Clamp Techniques; Picrotoxin; Putrescine; Sodium Channels; Spermine; Tetrazolium Salts; Time Factors; Transfection; Valine | 2011 |
FURTHER OBSERVATIONS OF A PATIENT WITH HYPERGLYCINEMIA.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Blood; Child; Diet; Diet Therapy; Glycine; Humans; Infections; Isoleucine; Leucine; Leukocyte Count; Methionine; Renal Aminoacidurias; Threonine; Toxicology; Valine | 1964 |
Selective sparing of hippocampal CA3 cells following in vitro ischemia is due to selective inhibition by acidosis.
Topics: Acidosis; Animals; Animals, Newborn; Calcium; Cell Death; Excitatory Amino Acid Antagonists; Excitatory Postsynaptic Potentials; Hippocampus; Hydrogen-Ion Concentration; Ischemia; Mice; Neural Inhibition; Neurons; Organ Culture Techniques; Patch-Clamp Techniques; Quinoxalines; Time Factors; Valine | 2005 |
[Neonatal leucinosis with favourable course. Therapeutic problems].
Topics: Acidosis; Child, Preschool; Diagnosis, Differential; Follow-Up Studies; Humans; Infant; Infant, Newborn; Isoleucine; Leucine; Male; Maple Syrup Urine Disease; Neurologic Examination; Peritoneal Dialysis; Seizures; Valine | 1977 |
Isovaleric acidemia.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Chromatography, Gas; Fatty Acids; Female; Humans; Infant; Intellectual Disability; Isoleucine; Leucine; Male; Valine | 1967 |
Hyperglycinemia with ketoacidosis and leukopenia. Metabolic studies on the nature of the defect.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Diet Therapy; Dietary Proteins; Glycine; Humans; Infant; Isoleucine; Leucine; Leukopenia; Lysine; Male; Valine | 1967 |
Regulation of glutamate dehydrogenase by branched-chain amino acids in skeletal muscle from rats and chicks.
Topics: Acidosis; Amino Acids, Branched-Chain; Ammonium Chloride; Animals; Chickens; Glutamate Dehydrogenase; Glutamine; Isoleucine; Keto Acids; Kinetics; Leucine; Male; Mitochondria, Muscle; Muscle, Skeletal; Rats; Rats, Sprague-Dawley; Valine | 1996 |
Correction of acidosis in dialysis patients increases branched-chain and total essential amino acid levels in muscle.
Topics: Acidosis; Adult; Aged; Aged, 80 and over; Amino Acids, Branched-Chain; Amino Acids, Essential; Bicarbonates; Dialysis; Female; Humans; Isoleucine; Leucine; Male; Middle Aged; Muscle, Skeletal; Valine | 1997 |
Mechanisms contributing to muscle-wasting in acute uremia: activation of amino acid catabolism.
Topics: 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide); Acidosis; Acute Disease; Administration, Oral; Amino Acids; Animals; Carbonates; Enzyme Activation; Isoenzymes; Isoleucine; Ketone Oxidoreductases; Male; Mitochondria; Multienzyme Complexes; Muscle, Skeletal; Rats; Rats, Sprague-Dawley; RNA, Messenger; Transfer RNA Aminoacylation; Uremia; Valine; Wasting Syndrome | 1998 |
Leucine and protein metabolism in rats with chronic renal insufficiency.
Topics: Acidosis; Animals; Body Weight; Cholesterol; Creatinine; Disease Models, Animal; Eating; Isoleucine; Kidney Failure, Chronic; Leucine; Male; Muscle, Skeletal; Nephrectomy; Proteins; Rats; Rats, Wistar; Urea; Uremia; Valine | 2001 |
1H-NMR spectroscopy of cerebrospinal fluid of fetal sheep during hypoxia-induced acidemia and recovery.
Topics: 3-Hydroxybutyric Acid; Acidosis; Animals; Choline; Citric Acid; Creatinine; Energy Metabolism; Female; Glucose; Hypoxanthine; Hypoxia; Inositol; Lactic Acid; Magnetic Resonance Spectroscopy; Pregnancy; Protons; Pyruvic Acid; Sheep; Succinic Acid; Valine | 2002 |
Accumulation of 3-hydroxyisobutyric acid, 2-methyl-3-hydroxybutyric acid and 3-hydroxyisovaleric acid in ketoacidosis.
Topics: Acetates; Acidosis; Animals; Child; Child, Preschool; Chromatography, Gas; Diabetes Mellitus; Diabetic Ketoacidosis; Glutarates; Humans; Hydroxy Acids; Hydroxybutyrates; Infant; Isoleucine; Leucine; Male; Mass Spectrometry; Rats; Streptozocin; Valerates; Valine | 1975 |
[Intermittent branched--chain ketoacidurie in ketotic hypoglycemia: investigations to localize the biochemical defect (author's transl)].
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Female; Fibroblasts; Humans; Hypoglycemia; Intellectual Disability; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine | 1976 |
Molecular characterization of variant alpha-subunit of electron transfer flavoprotein in three patients with glutaric acidemia type II--and identification of glycine substitution for valine-157 in the sequence of the precursor, producing an unstable matur
Topics: Acidosis; Base Sequence; Blotting, Northern; Cell Line; Electron-Transferring Flavoproteins; Flavoproteins; Genes, Recessive; Glutarates; Glycine; Humans; Metabolism, Inborn Errors; Molecular Sequence Data; Mutation; Polymerase Chain Reaction; Protein Conformation; Protein Precursors; Valine | 1991 |
Acidosis, not azotemia, stimulates branched-chain, amino acid catabolism in uremic rats.
Topics: Acidosis; Amino Acids, Branched-Chain; Animals; Dietary Proteins; Kidney Failure, Chronic; Leucine; Male; Muscles; Nephrectomy; Rats; Rats, Inbred Strains; Uremia; Valine | 1987 |
Biotin-responsive beta-methylcrotonylglycinuria.
Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Chromatography, Gas; Fatty Acids; Glycine; Humans; Infant; Leucine; Male; Partial Pressure; Valerates; Valine; Vomiting | 1971 |
Glycemic response to 24-hour fast in normal children and children with ketotic hypoglycemia: II. Hormonal and metabolic changes.
Topics: Acidosis; Alanine; Amino Acids; Autoanalysis; Blood Glucose; Child; Child, Preschool; Fasting; Fatty Acids, Nonesterified; Female; Glucagon; Growth Hormone; Hormones; Humans; Hydrocortisone; Hypoglycemia; Insulin; Isoleucine; Ketones; Ketosis; Leucine; Male; Valine | 1974 |
3-hydroxypropionate: significance of -oxidation of propionate in patients with propionic acidemia and methylmalonic acidemia.
Topics: Acidosis; Carbon Isotopes; Chromatography; Chromatography, Paper; Citrates; Humans; Hydroxylation; Injections, Intravenous; Isoleucine; Malonates; Mass Spectrometry; Metabolism, Inborn Errors; Oxidation-Reduction; Propionates; Valine | 1972 |
Response to dietary therapy in B 12 unresponsive methylmalonic acidemia.
Topics: Acidosis; Agranulocytosis; Blood Glucose; Cephalometry; Child Development; Diet Therapy; Electroencephalography; Female; Growth Disorders; Humans; Infant; Intelligence; Isoleucine; Lymphocytosis; Malonates; Metabolism, Inborn Errors; Methionine; Otitis Media; Threonine; Valine; Vitamin B 12 | 1973 |
The effect of cobamide coenzyme in methylmalonic acidemia.
Topics: Acidosis; Acute Disease; Child, Preschool; Coenzymes; Dietary Proteins; Female; Humans; Male; Malonates; Metabolism, Inborn Errors; Valine | 1969 |
Vitamin B12-dependent methylmalonicaciduria: amino acid toxicity, long chain ketonuria, and protective effect of vitamin B12.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Coenzyme A; Diet Therapy; Dietary Proteins; Humans; Isoleucine; Ketones; Leucine; Leukocytes; Male; Malonates; Methionine; Nutritional Requirements; Propionates; Threonine; Valine; Vitamin B 12 | 1970 |