valine and Metabolic Acidosis

valine has been researched along with Metabolic Acidosis in 23 studies

Research

Studies (23)

TimeframeStudies, this research(%)All Research%
pre-199015 (65.22)18.7374
1990's4 (17.39)18.2507
2000's3 (13.04)29.6817
2010's1 (4.35)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Cao, H; Chu, XP; Duan, B; Hansen, J; Huang, Y; Simon, RP; Wang, YZ; Xiong, ZG; Xu, TL; Yang, T; Yu, Y; Zhu, MX1
CHILDS, B; NYHAN, WL1
Cronberg, T; Jensen, K; Rytter, A; Wieloch, T1
Astruc, J; Bellet, H; Brunel, D; Froye, E; Luciani, JM; Magnan de Bornier, P1
Efron, ML1
Edelmann, CM; Finberg, L; Soriano, JR; Taitz, LS1
Thompson, JR; Zhou, X1
Anderstam, B; Bergström, J; Löfberg, E; Wernerman, J1
Bailey, JL; Caban, R; England, BK; Marinovic, AC; Maroni, BJ; Mitch, WE; Price, SR; Reaich, D1
Holecek, M; Sprongl, L; Tichý, M; Tilser, I1
Crevels, J; De Abreu, RA; Engelke, UF; Jongsma, HW; Moolenaar, SH; Nijhuis, JG; Nijland, R; Oeseburg, B; Van Cappellen Van Walsum, AM; Wevers, RA1
Landaas, S1
Porath, U; Schreier, K1
Grüttner, R; Held, KR; Plettner, C; Singh, S; Sternowsky, HJ1
Glassberg, R; Indo, Y; Tanaka, K; Yokota, I1
Hara, Y; Kelly, RA; May, RC; Mitch, WE1
Draffan, GH; Gompertz, D; Hull, D; Watts, JL1
Chaussain, JL; Georges, P; Job, JC; Olive, G1
Ando, T; Hull, D; Nyhan, WL; Rasmussen, K1
Frimpter, GW1
Ando, T; Fawcett, N; Julius, RL; Nyhan, WL; Rennert, OM1
Lindblad, B; Lindstrand, K; Svanberg, B; Zetterström, R1
Hsia, YE; Lilljeqvist, AC; Rosenberg, LE1

Reviews

2 review(s) available for valine and Metabolic Acidosis

ArticleYear
[Congenital metabolic acidosis in the postnatal period].
    Deutsche medizinische Wochenschrift (1946), 1978, Jun-02, Volume: 103, Issue:22

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine

1978
Aminoacidurias due to inherited disorders of metabolism. 2.
    The New England journal of medicine, 1973, Oct-25, Volume: 289, Issue:17

    Topics: Acidosis; Alanine; Amino Acid Metabolism, Inborn Errors; Arginase; Arginine; Carbamates; Citrulline; Dipeptides; Glutarates; Glycine; Histidine; Humans; Hydroxyproline; Hyperglycemia; Infant, Newborn; Keto Acids; Lysine; Malonates; Maple Syrup Urine Disease; Ornithine Carbamoyltransferase; Phosphotransferases; Proline; Sarcosine; Succinates; Urea; Valine

1973

Other Studies

21 other study(ies) available for valine and Metabolic Acidosis

ArticleYear
Extracellular spermine exacerbates ischemic neuronal injury through sensitization of ASIC1a channels to extracellular acidosis.
    The Journal of neuroscience : the official journal of the Society for Neuroscience, 2011, Feb-09, Volume: 31, Issue:6

    Topics: Acid Sensing Ion Channels; Acidosis; Amino Acid Transport System y+; Animals; Biophysics; Brain Injuries; Calcium; Cells, Cultured; CHO Cells; Cricetinae; Cricetulus; Disease Models, Animal; Dose-Response Relationship, Drug; Drug Combinations; Drug Interactions; Electric Stimulation; Embryo, Mammalian; Excitatory Amino Acid Antagonists; Extracellular Fluid; GABA Antagonists; Glucose; Hippocampus; Hydrogen-Ion Concentration; Hypoxia; Infarction, Middle Cerebral Artery; L-Lactate Dehydrogenase; Membrane Potentials; Mice; Mice, Knockout; Mutation; Nerve Tissue Proteins; Neurons; Oligonucleotides; Patch-Clamp Techniques; Picrotoxin; Putrescine; Sodium Channels; Spermine; Tetrazolium Salts; Time Factors; Transfection; Valine

2011
FURTHER OBSERVATIONS OF A PATIENT WITH HYPERGLYCINEMIA.
    Pediatrics, 1964, Volume: 33

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Blood; Child; Diet; Diet Therapy; Glycine; Humans; Infections; Isoleucine; Leucine; Leukocyte Count; Methionine; Renal Aminoacidurias; Threonine; Toxicology; Valine

1964
Selective sparing of hippocampal CA3 cells following in vitro ischemia is due to selective inhibition by acidosis.
    The European journal of neuroscience, 2005, Volume: 22, Issue:2

    Topics: Acidosis; Animals; Animals, Newborn; Calcium; Cell Death; Excitatory Amino Acid Antagonists; Excitatory Postsynaptic Potentials; Hippocampus; Hydrogen-Ion Concentration; Ischemia; Mice; Neural Inhibition; Neurons; Organ Culture Techniques; Patch-Clamp Techniques; Quinoxalines; Time Factors; Valine

2005
[Neonatal leucinosis with favourable course. Therapeutic problems].
    Annales de pediatrie, 1977, Volume: 24, Issue:8-9

    Topics: Acidosis; Child, Preschool; Diagnosis, Differential; Follow-Up Studies; Humans; Infant; Infant, Newborn; Isoleucine; Leucine; Male; Maple Syrup Urine Disease; Neurologic Examination; Peritoneal Dialysis; Seizures; Valine

1977
Isovaleric acidemia.
    American journal of diseases of children (1960), 1967, Volume: 113, Issue:1

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Chromatography, Gas; Fatty Acids; Female; Humans; Infant; Intellectual Disability; Isoleucine; Leucine; Male; Valine

1967
Hyperglycinemia with ketoacidosis and leukopenia. Metabolic studies on the nature of the defect.
    Pediatrics, 1967, Volume: 39, Issue:6

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Diet Therapy; Dietary Proteins; Glycine; Humans; Infant; Isoleucine; Leucine; Leukopenia; Lysine; Male; Valine

1967
Regulation of glutamate dehydrogenase by branched-chain amino acids in skeletal muscle from rats and chicks.
    The international journal of biochemistry & cell biology, 1996, Volume: 28, Issue:7

    Topics: Acidosis; Amino Acids, Branched-Chain; Ammonium Chloride; Animals; Chickens; Glutamate Dehydrogenase; Glutamine; Isoleucine; Keto Acids; Kinetics; Leucine; Male; Mitochondria, Muscle; Muscle, Skeletal; Rats; Rats, Sprague-Dawley; Valine

1996
Correction of acidosis in dialysis patients increases branched-chain and total essential amino acid levels in muscle.
    Clinical nephrology, 1997, Volume: 48, Issue:4

    Topics: Acidosis; Adult; Aged; Aged, 80 and over; Amino Acids, Branched-Chain; Amino Acids, Essential; Bicarbonates; Dialysis; Female; Humans; Isoleucine; Leucine; Male; Middle Aged; Muscle, Skeletal; Valine

1997
Mechanisms contributing to muscle-wasting in acute uremia: activation of amino acid catabolism.
    Journal of the American Society of Nephrology : JASN, 1998, Volume: 9, Issue:3

    Topics: 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide); Acidosis; Acute Disease; Administration, Oral; Amino Acids; Animals; Carbonates; Enzyme Activation; Isoenzymes; Isoleucine; Ketone Oxidoreductases; Male; Mitochondria; Multienzyme Complexes; Muscle, Skeletal; Rats; Rats, Sprague-Dawley; RNA, Messenger; Transfer RNA Aminoacylation; Uremia; Valine; Wasting Syndrome

1998
Leucine and protein metabolism in rats with chronic renal insufficiency.
    Experimental and toxicologic pathology : official journal of the Gesellschaft fur Toxikologische Pathologie, 2001, Volume: 53, Issue:1

    Topics: Acidosis; Animals; Body Weight; Cholesterol; Creatinine; Disease Models, Animal; Eating; Isoleucine; Kidney Failure, Chronic; Leucine; Male; Muscle, Skeletal; Nephrectomy; Proteins; Rats; Rats, Wistar; Urea; Uremia; Valine

2001
1H-NMR spectroscopy of cerebrospinal fluid of fetal sheep during hypoxia-induced acidemia and recovery.
    Pediatric research, 2002, Volume: 52, Issue:1

    Topics: 3-Hydroxybutyric Acid; Acidosis; Animals; Choline; Citric Acid; Creatinine; Energy Metabolism; Female; Glucose; Hypoxanthine; Hypoxia; Inositol; Lactic Acid; Magnetic Resonance Spectroscopy; Pregnancy; Protons; Pyruvic Acid; Sheep; Succinic Acid; Valine

2002
Accumulation of 3-hydroxyisobutyric acid, 2-methyl-3-hydroxybutyric acid and 3-hydroxyisovaleric acid in ketoacidosis.
    Clinica chimica acta; international journal of clinical chemistry, 1975, Oct-15, Volume: 64, Issue:2

    Topics: Acetates; Acidosis; Animals; Child; Child, Preschool; Chromatography, Gas; Diabetes Mellitus; Diabetic Ketoacidosis; Glutarates; Humans; Hydroxy Acids; Hydroxybutyrates; Infant; Isoleucine; Leucine; Male; Mass Spectrometry; Rats; Streptozocin; Valerates; Valine

1975
[Intermittent branched--chain ketoacidurie in ketotic hypoglycemia: investigations to localize the biochemical defect (author's transl)].
    Monatsschrift fur Kinderheilkunde, 1976, Volume: 124, Issue:2

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Female; Fibroblasts; Humans; Hypoglycemia; Intellectual Disability; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine

1976
Molecular characterization of variant alpha-subunit of electron transfer flavoprotein in three patients with glutaric acidemia type II--and identification of glycine substitution for valine-157 in the sequence of the precursor, producing an unstable matur
    American journal of human genetics, 1991, Volume: 49, Issue:3

    Topics: Acidosis; Base Sequence; Blotting, Northern; Cell Line; Electron-Transferring Flavoproteins; Flavoproteins; Genes, Recessive; Glutarates; Glycine; Humans; Metabolism, Inborn Errors; Molecular Sequence Data; Mutation; Polymerase Chain Reaction; Protein Conformation; Protein Precursors; Valine

1991
Acidosis, not azotemia, stimulates branched-chain, amino acid catabolism in uremic rats.
    Kidney international, 1987, Volume: 32, Issue:6

    Topics: Acidosis; Amino Acids, Branched-Chain; Animals; Dietary Proteins; Kidney Failure, Chronic; Leucine; Male; Muscles; Nephrectomy; Rats; Rats, Inbred Strains; Uremia; Valine

1987
Biotin-responsive beta-methylcrotonylglycinuria.
    Lancet (London, England), 1971, Jul-03, Volume: 2, Issue:7714

    Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Chromatography, Gas; Fatty Acids; Glycine; Humans; Infant; Leucine; Male; Partial Pressure; Valerates; Valine; Vomiting

1971
Glycemic response to 24-hour fast in normal children and children with ketotic hypoglycemia: II. Hormonal and metabolic changes.
    The Journal of pediatrics, 1974, Volume: 85, Issue:6

    Topics: Acidosis; Alanine; Amino Acids; Autoanalysis; Blood Glucose; Child; Child, Preschool; Fasting; Fatty Acids, Nonesterified; Female; Glucagon; Growth Hormone; Hormones; Humans; Hydrocortisone; Hypoglycemia; Insulin; Isoleucine; Ketones; Ketosis; Leucine; Male; Valine

1974
3-hydroxypropionate: significance of -oxidation of propionate in patients with propionic acidemia and methylmalonic acidemia.
    Proceedings of the National Academy of Sciences of the United States of America, 1972, Volume: 69, Issue:10

    Topics: Acidosis; Carbon Isotopes; Chromatography; Chromatography, Paper; Citrates; Humans; Hydroxylation; Injections, Intravenous; Isoleucine; Malonates; Mass Spectrometry; Metabolism, Inborn Errors; Oxidation-Reduction; Propionates; Valine

1972
Response to dietary therapy in B 12 unresponsive methylmalonic acidemia.
    Pediatrics, 1973, Volume: 51, Issue:3

    Topics: Acidosis; Agranulocytosis; Blood Glucose; Cephalometry; Child Development; Diet Therapy; Electroencephalography; Female; Growth Disorders; Humans; Infant; Intelligence; Isoleucine; Lymphocytosis; Malonates; Metabolism, Inborn Errors; Methionine; Otitis Media; Threonine; Valine; Vitamin B 12

1973
The effect of cobamide coenzyme in methylmalonic acidemia.
    Acta paediatrica Scandinavica, 1969, Volume: 58, Issue:2

    Topics: Acidosis; Acute Disease; Child, Preschool; Coenzymes; Dietary Proteins; Female; Humans; Male; Malonates; Metabolism, Inborn Errors; Valine

1969
Vitamin B12-dependent methylmalonicaciduria: amino acid toxicity, long chain ketonuria, and protective effect of vitamin B12.
    Pediatrics, 1970, Volume: 46, Issue:4

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Coenzyme A; Diet Therapy; Dietary Proteins; Humans; Isoleucine; Ketones; Leucine; Leukocytes; Male; Malonates; Methionine; Nutritional Requirements; Propionates; Threonine; Valine; Vitamin B 12

1970