valine and Chorea

valine has been researched along with Chorea in 8 studies

Research

Studies (8)

TimeframeStudies, this research(%)All Research%
pre-19901 (12.50)18.7374
1990's0 (0.00)18.2507
2000's4 (50.00)29.6817
2010's1 (12.50)24.3611
2020's2 (25.00)2.80

Authors

AuthorsStudies
Cances, C; Damaj, L; de Lonlay, P; Doummar, D; Espil, C; Fluss, J; François-Heude, MC; Kern, I; Lebigot, E; Leboucq, N; Lenaers, G; Meyer, P; Munnich, A; Roubertie, A; Roze, E; Spitz, MA; Torre, S; Touati, G; Warde, MTA1
Heim, B; Seppi, K1
Bashir, H; Jankovic, J1
Bird, TD; Chen, DH; Feleke, A; Fink, J; Lipe, H; Matsushita, M; Meaney, B; Rainier, S; Raskind, WH; Tisch, L; Wolff, J1
Djarmati, A; Dragasević, N; Klein, C; Kostić, VS; Momcilović, D; Stefanova, E; Svetel, M1
Asmus, F; Chinnery, PF; Devlin, A; Gasser, T; Munz, M; Zimprich, A1
Fialkow, RZ; Haria, DM; Maru, MC1
Bruck, J; Gerstenbrand, F; Gnad, H; Gründig, E; Prosenz, P; Simanyi, M1

Reviews

1 review(s) available for valine and Chorea

ArticleYear
Treatment options for chorea.
    Expert review of neurotherapeutics, 2018, Volume: 18, Issue:1

    Topics: Antipsychotic Agents; Chorea; Deep Brain Stimulation; Dopamine Antagonists; Humans; Piperidines; Tetrabenazine; Transcranial Magnetic Stimulation; Valine; Vesicular Monoamine Transport Proteins

2018

Other Studies

7 other study(ies) available for valine and Chorea

ArticleYear
Movement disorders in valine métabolism diseases caused by HIBCH and ECHS1 deficiencies.
    European journal of neurology, 2022, Volume: 29, Issue:11

    Topics: Abnormalities, Multiple; Amino Acid Metabolism, Inborn Errors; Chorea; Coenzyme A; Dystonia; Dystonic Disorders; Enoyl-CoA Hydratase; Humans; Leigh Disease; Movement Disorders; Thiolester Hydrolases; Valine

2022
Valbenazine as treatment for Huntington's disease chorea.
    The Lancet. Neurology, 2023, Volume: 22, Issue:6

    Topics: Chorea; Humans; Huntington Disease; Tetrabenazine; Valine

2023
Presence of alanine-to-valine substitutions in myofibrillogenesis regulator 1 in paroxysmal nonkinesigenic dyskinesia: confirmation in 2 kindreds.
    Archives of neurology, 2005, Volume: 62, Issue:4

    Topics: Alanine; Amino Acid Substitution; Chorea; Chromosome Mapping; Chromosomes, Human, Pair 2; DNA Mutational Analysis; Exons; Female; Genes, Dominant; Genetic Markers; Genetic Predisposition to Disease; Genetic Testing; Haplotypes; Humans; Male; Muscle Proteins; Mutation, Missense; Pedigree; Protein Structure, Secondary; Valine

2005
Clinical characteristics of paroxysmal nonkinesigenic dyskinesia in Serbian family with Myofibrillogenesis regulator 1 gene mutation.
    Movement disorders : official journal of the Movement Disorder Society, 2006, Volume: 21, Issue:11

    Topics: Adolescent; Adult; Alanine; Chorea; DNA Mutational Analysis; Family Health; Female; Humans; Male; Middle Aged; Muscle Proteins; Mutation; Valine; Yugoslavia

2006
Clinical differentiation of genetically proven benign hereditary chorea and myoclonus-dystonia.
    Movement disorders : official journal of the Movement Disorder Society, 2007, Oct-31, Volume: 22, Issue:14

    Topics: Adolescent; Arginine; Child; Chorea; DNA Mutational Analysis; Dystonic Disorders; Exons; Family Health; Female; Genotype; Glycine; Humans; Male; Mutation; Myoclonus; Nuclear Proteins; Sarcoglycans; Thyroid Nuclear Factor 1; Transcription Factors; Valine

2007
Choreiform movements in dialysis patient taking valacyclovir and famciclovir.
    Southern medical journal, 2001, Volume: 94, Issue:6

    Topics: 2-Aminopurine; Acyclovir; Aged; Aged, 80 and over; Chorea; Drug Interactions; Famciclovir; Herpes Zoster; Humans; Kidney Failure, Chronic; Male; Renal Dialysis; Valacyclovir; Valine

2001
[The effect of the administration of amino acids, especially of L-dopa and alpha-methyldopa, on the composition of cerebrospinal fluid in extrapyramidal syndromes. II. Alterations of cerebrospinal fluid in patients with Parkinson's disease and chorea fol
    Deutsche Zeitschrift fur Nervenheilkunde, 1969, Volume: 196, Issue:3

    Topics: Alanine Transaminase; Amino Acids; Aspartate Aminotransferases; Chorea; Humans; Methyldopa; Parkinson Disease; Valine

1969