valine and Acetonemia

valine has been researched along with Acetonemia in 7 studies

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19907 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
TASHIAN, RE1
DANCIS, J; HUTZLER, J; LEVITZ, M1
SILBERMANSCHWARTZMAN, J1
Porath, U; Schreier, K1
Grüttner, R; Held, KR; Plettner, C; Singh, S; Sternowsky, HJ2
Chaussain, JL; Georges, P; Job, JC; Olive, G1

Reviews

1 review(s) available for valine and Acetonemia

ArticleYear
[Congenital metabolic acidosis in the postnatal period].
    Deutsche medizinische Wochenschrift (1946), 1978, Jun-02, Volume: 103, Issue:22

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine

1978

Other Studies

6 other study(ies) available for valine and Acetonemia

ArticleYear
Inhibition of brain glutamic acid decarboxylase by phenylalanine, valine, and leucine derivatives: a suggestion concerning the etiology of the neurological defect in phenylketonuria and branched-chain ketonuria.
    Metabolism: clinical and experimental, 1961, Volume: 10

    Topics: Amino Acids; Brain; Glutamate Decarboxylase; Humans; Intellectual Disability; Ketosis; Leucine; Lyases; Maple Syrup Urine Disease; Metabolic Diseases; Phenylalanine; Phenylketonurias; Valine

1961
THE DIAGNOSIS OF MAPLE SYRUP URINE DISEASE (BRANCHED- CHAIN KETOACIDURIA) BY THE IN VITRO STUDY OF THE PERIPHERAL LEUKOCYTE.
    Pediatrics, 1963, Volume: 32

    Topics: Chromatography; Humans; In Vitro Techniques; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Maple Syrup Urine Disease; Metabolism; Research; Valine

1963
[CLINICAL, BIOCHEMICAL, AND NEUROPATHOLOGIC ASPECTS OF MAPLE SYRUP URINE DISEASE. A KETOACIDURIA OF THE OPEN CHAIN AMINOACIDS LEUCINE, ISOLEUCINE AND VALINE].
    Anales. Universidad Nacional Mayor de San Marcos. Facultad de Medicina, 1963, Volume: 46

    Topics: Amino Acids; Genetics, Medical; Humans; Infant; Isoleucine; Keto Acids; Ketosis; Leucine; Maple Syrup Urine Disease; Nervous System Diseases; Neurosciences; Pathology; Valine

1963
[Ketotic hypoglycemia in intermittent branch-chain ketoaciduria. Enzymatic and gas chromatographic studies].
    Monatsschrift fur Kinderheilkunde, 1976, Volume: 124, Issue:5

    Topics: Child; Chromatography, Gas; Female; Fibroblasts; Humans; Hypoglycemia; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine

1976
[Intermittent branched--chain ketoacidurie in ketotic hypoglycemia: investigations to localize the biochemical defect (author's transl)].
    Monatsschrift fur Kinderheilkunde, 1976, Volume: 124, Issue:2

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Female; Fibroblasts; Humans; Hypoglycemia; Intellectual Disability; Isoleucine; Keto Acids; Ketosis; Leucine; Leukocytes; Valine

1976
Glycemic response to 24-hour fast in normal children and children with ketotic hypoglycemia: II. Hormonal and metabolic changes.
    The Journal of pediatrics, 1974, Volume: 85, Issue:6

    Topics: Acidosis; Alanine; Amino Acids; Autoanalysis; Blood Glucose; Child; Child, Preschool; Fasting; Fatty Acids, Nonesterified; Female; Glucagon; Growth Hormone; Hormones; Humans; Hydrocortisone; Hypoglycemia; Insulin; Isoleucine; Ketones; Ketosis; Leucine; Male; Valine

1974