valienamine has been researched along with Mucopolysaccharidosis IV in 2 studies
*Mucopolysaccharidosis IV: Genetic disorder of mucopolysaccharide metabolism characterized by skeletal abnormalities, joint instability, development of cervical myelopathy, and excessive urinary keratan sulfate. There are two biochemically distinct forms, each due to a deficiency of a different enzyme. [MeSH]
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 1 (50.00) | 29.6817 |
| 2010's | 1 (50.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Aguilar-Moncayo, M; Garcia Fernandez, JM; Higaki, K; Mena-Barragán, T; Nanba, E; Ohto, U; Ortiz Mellet, C; Shimizu, T; Suzuki, H; Suzuki, Y | 1 |
| Higaki, K; Iida, M; Iwasaki, H; Nanba, E; Ogawa, S; Suzuki, Y; Tabe, M; Watanabe, H | 1 |
2 other study(ies) available for valienamine and Mucopolysaccharidosis IV
| Article | Year |
|---|---|
Structural basis of pharmacological chaperoning for human β-galactosidase.
Topics: 1-Deoxynojirimycin; beta-Galactosidase; Catalytic Domain; Crystallography, X-Ray; Cyclohexenes; Enzyme Inhibitors; Enzyme Stability; Gangliosidosis, GM1; Hexosamines; Humans; Hydrogen Bonding; Hydrogen-Ion Concentration; Imino Sugars; Inositol; Kinetics; Models, Molecular; Molecular Structure; Mucopolysaccharidosis IV; Mutation; Protein Structure, Tertiary; Static Electricity; Structure-Activity Relationship | 2014 |
Fibroblast screening for chaperone therapy in beta-galactosidosis.
Topics: Arginine; beta-Galactosidase; Cells, Cultured; Cyclohexenes; Dose-Response Relationship, Drug; Drug Evaluation, Preclinical; Fibroblasts; Gangliosidosis, GM1; Genotype; Glutamine; Hexosamines; Humans; Molecular Chaperones; Mucopolysaccharidosis IV; Mutation; Phenotype | 2006 |