Page last updated: 2024-09-05

valienamine and Gangliosidosis, GM1

valienamine has been researched along with Gangliosidosis, GM1 in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's3 (75.00)29.6817
2010's1 (25.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Aguilar-Moncayo, M; Garcia Fernandez, JM; Higaki, K; Mena-Barragán, T; Nanba, E; Ohto, U; Ortiz Mellet, C; Shimizu, T; Suzuki, H; Suzuki, Y1
Brady, RO; Higaki, K; Itoh, M; Iwasaki, H; Matsuda, J; Matsuzaki, Y; Nanba, E; Noguchi, A; Ogawa, S; Ogawa, Y; Ohno, K; Oshima, A; Sakata, Y; Suzuki, O; Suzuki, Y; Takimoto, K; Tominaga, L; Watanabe, H; Yamamoto, Y; Yasuda, Y1
Higaki, K; Iida, M; Iwasaki, H; Nanba, E; Ogawa, S; Suzuki, Y; Tabe, M; Watanabe, H1
Kanto, M; Ogawa, S; Suzuki, Y1

Reviews

1 review(s) available for valienamine and Gangliosidosis, GM1

ArticleYear
Development and medical application of unsaturated carbaglycosylamine glycosidase inhibitors.
    Mini reviews in medicinal chemistry, 2007, Volume: 7, Issue:7

    Topics: Animals; Cyclohexenes; Drug Design; Enzyme Inhibitors; Gangliosidosis, GM1; Glycoside Hydrolases; Hexosamines; Humans; Mice; Molecular Chaperones; Structure-Activity Relationship

2007

Other Studies

3 other study(ies) available for valienamine and Gangliosidosis, GM1

ArticleYear
Structural basis of pharmacological chaperoning for human β-galactosidase.
    The Journal of biological chemistry, 2014, May-23, Volume: 289, Issue:21

    Topics: 1-Deoxynojirimycin; beta-Galactosidase; Catalytic Domain; Crystallography, X-Ray; Cyclohexenes; Enzyme Inhibitors; Enzyme Stability; Gangliosidosis, GM1; Hexosamines; Humans; Hydrogen Bonding; Hydrogen-Ion Concentration; Imino Sugars; Inositol; Kinetics; Models, Molecular; Molecular Structure; Mucopolysaccharidosis IV; Mutation; Protein Structure, Tertiary; Static Electricity; Structure-Activity Relationship

2014
Chemical chaperone therapy for brain pathology in G(M1)-gangliosidosis.
    Proceedings of the National Academy of Sciences of the United States of America, 2003, Dec-23, Volume: 100, Issue:26

    Topics: alpha-Glucosidases; Animals; beta-Galactosidase; Brain; Cells, Cultured; Cyclohexenes; DNA Primers; Enzyme Inhibitors; Fibroblasts; Gangliosidosis, GM1; Glycoside Hydrolase Inhibitors; Hexosamines; Humans; Mice; Mice, Inbred C57BL; Mice, Knockout; Mice, Transgenic; Polymerase Chain Reaction

2003
Fibroblast screening for chaperone therapy in beta-galactosidosis.
    Brain & development, 2006, Volume: 28, Issue:8

    Topics: Arginine; beta-Galactosidase; Cells, Cultured; Cyclohexenes; Dose-Response Relationship, Drug; Drug Evaluation, Preclinical; Fibroblasts; Gangliosidosis, GM1; Genotype; Glutamine; Hexosamines; Humans; Molecular Chaperones; Mucopolysaccharidosis IV; Mutation; Phenotype

2006