Page last updated: 2024-09-02

valerates and Acidosis

valerates has been researched along with Acidosis in 27 studies

Research

Studies (27)

TimeframeStudies, this research(%)All Research%
pre-199027 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Isselbacher, KJ; Tanaka, K1
Kikawa, Y; Kikuchi, K; Ohta, S; Okamoto, M; Shigematsu, Y; Sudo, M1
Bartlett, K; Leonard, JV; Ng, H1
French, NP; Grauaug, A; Wysocki, SJ1
Burton, BK; Challa, VR; Fischer, AQ; McLean, WT1
Landaas, S2
Porath, U; Schreier, K1
Bruinvis, L; Drewes, JG; Duran, M; Ketting, D; van Sprang, FJ; Wadman, SK1
Cohn, RM; Puschak, R; Rothman, R; Segal, S; Yudkoff, M1
O'Brien, WE1
Barness, LA2
Jakobs, C; Landaas, S1
Krieger, I; Tanaka, K1
Dinesen, J; Gerdes, AM; Gregersen, N; Güttler, F; Holm, V; Lúdvigsson, P1
Draffan, GH; Gompertz, D; Hull, D; Watts, JL1
Callaghan, P; Newman, CG; Wilson, BD; Young, L1
Senior, AE; Sherratt, HS1
Daum, RS; Delvin, E; Goldman, H; Lamm, P; Mamer, OA; Scriver, CR1
Eldjarn, L; Jellum, E; Schnitler, R; Stokke, O1
Mandell, R; Shih, VE; Tanaka, K1
Erickson, AM; Levy, HL; Lott, IT1
Budd, MA; Efron, ML; Isselbacher, KJ; Tanaka, K1
Isselbacher, KJ; Miller, EM; Tanaka, K1
Isselbacher, KJ; Orr, JC; Tanaka, K1

Reviews

1 review(s) available for valerates and Acidosis

ArticleYear
[Congenital metabolic acidosis in the postnatal period].
    Deutsche medizinische Wochenschrift (1946), 1978, Jun-02, Volume: 103, Issue:22

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine

1978

Other Studies

26 other study(ies) available for valerates and Acidosis

ArticleYear
The isolation and identification of N-isovalerylglycine from urine of patients with isovaleric acidemia.
    The Journal of biological chemistry, 1967, Jun-25, Volume: 242, Issue:12

    Topics: Acidosis; Amino Acids; Chemistry, Clinical; Child; Child, Preschool; Chromatography, Gas; Coenzyme A; Female; Humans; In Vitro Techniques; Leucine; Magnetic Resonance Spectroscopy; Male; Spectrum Analysis; Valerates

1967
A simple method of determining 4-hydroxyisovaleric acid and its level in a patient with isovaleric acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 1984, Apr-27, Volume: 138, Issue:3

    Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Ketosis; Pentanoic Acids; Valerates

1984
A combined defect of three mitochondrial carboxylases presenting as biotin-responsive 3-methylcrotonyl glycinuria and 3-hydroxyisovaleric aciduria.
    Clinica chimica acta; international journal of clinical chemistry, 1980, Jan-15, Volume: 100, Issue:2

    Topics: Acidosis; Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Child, Preschool; Crotonates; Female; Fibroblasts; Glycine; Humans; Hydroxy Acids; Ligases; Mitochondria; Propionates; Pyruvate Carboxylase Deficiency Disease; Valerates

1980
Organic aciduria associated with isovaleric acidemia.
    Clinical chemistry, 1983, Volume: 29, Issue:5

    Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Infant; Leucine; Pentanoic Acids; Valerates

1983
Cerebellar hemorrhage complicating isovaleric acidemia: a case report.
    Neurology, 1981, Volume: 31, Issue:6

    Topics: Acidosis; Cerebellar Diseases; Cerebral Hemorrhage; Female; Hemiterpenes; Humans; Infant, Newborn; Pentanoic Acids; Valerates

1981
Accumulation of 3-hydroxyisobutyric acid, 2-methyl-3-hydroxybutyric acid and 3-hydroxyisovaleric acid in ketoacidosis.
    Clinica chimica acta; international journal of clinical chemistry, 1975, Oct-15, Volume: 64, Issue:2

    Topics: Acetates; Acidosis; Animals; Child; Child, Preschool; Chromatography, Gas; Diabetes Mellitus; Diabetic Ketoacidosis; Glutarates; Humans; Hydroxy Acids; Hydroxybutyrates; Infant; Isoleucine; Leucine; Male; Mass Spectrometry; Rats; Streptozocin; Valerates; Valine

1975
Two sisters with isovaleric acidaemia, multiple attacks of ketoacidosis and normal development.
    European journal of pediatrics, 1979, Jun-28, Volume: 131, Issue:3

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Coma; Female; Humans; Intelligence; Ketosis; Valerates; Vomiting

1979
Glycine therapy in isovaleric acidemia.
    The Journal of pediatrics, 1978, Volume: 92, Issue:5

    Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Drug Administration Schedule; Female; Glycine; Humans; Keto Acids; Ketone Bodies; Lactates; Leucine; Pyruvates; Valerates

1978
Inhibition of glycine synthase by branched-chain alpha-keto acids. A possible mechanism for abnormal glycine metabolism in ketotic hyperglycinemia.
    Archives of biochemistry and biophysics, 1978, Volume: 189, Issue:2

    Topics: Acidosis; Acyl Coenzyme A; Animals; Caproates; Glycine; Keto Acids; Ketosis; Liver; Male; Rats; Transferases; Valerates

1978
Organic acidosis in infants.
    South African medical journal = Suid-Afrikaanse tydskrif vir geneeskunde, 1977, May-14, Volume: 51, Issue:20

    Topics: Acidosis; Adult; Child; Humans; Infant; Infant, Newborn; Infant, Newborn, Diseases; Lactates; Methylmalonic Acid; Propionates; Pyruvates; Valerates

1977
The occurrence of 2-hydroxyisovaleric acid in patients with lactic acidosis and ketoacidosis.
    Clinica chimica acta; international journal of clinical chemistry, 1977, Aug-01, Volume: 78, Issue:3

    Topics: Acidosis; Adult; Child; Child, Preschool; Chromatography, Gas; Female; Humans; Hydroxy Acids; Hydroxybutyrates; Infant; Keto Acids; Lactates; Male; Mass Spectrometry; Valerates

1977
Therapeutic effects of glycine in isovaleric acidemia.
    Pediatric research, 1976, Volume: 10, Issue:1

    Topics: Acidosis; Alkalies; Amino Acid Metabolism, Inborn Errors; Child; Female; Glycine; Humans; Inactivation, Metabolic; Ketosis; Oxidoreductases; Valerates

1976
[Isovaleric acidemia].
    Ugeskrift for laeger, 1989, Oct-23, Volume: 151, Issue:43

    Topics: Acidosis; Child, Preschool; Dietary Proteins; Female; Humans; Infant; Male; Metabolism, Inborn Errors; Oxidoreductases; Valerates

1989
Biotin-responsive beta-methylcrotonylglycinuria.
    Lancet (London, England), 1971, Jul-03, Volume: 2, Issue:7714

    Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Chromatography, Gas; Fatty Acids; Glycine; Humans; Infant; Leucine; Male; Partial Pressure; Valerates; Valine; Vomiting

1971
Neonatal death associated with isovalericacidaemia.
    Lancet (London, England), 1967, Aug-26, Volume: 2, Issue:7513

    Topics: Acidosis; Bicarbonates; Chromatography; Chromatography, Gas; Coenzyme A; Electrolytes; Fatty Acids; Fatty Acids, Nonesterified; Glucose; Hemorrhage; Humans; Hypocalcemia; Infant Mortality; Infant, Newborn; Leucine; Male; Metabolism, Inborn Errors; Valerates

1967
A comparison of the effects on blood glucose and ketone-body levels, and of the toxicities, of pent-4-enoic acid and four simple fatty acids.
    The Journal of pharmacy and pharmacology, 1969, Volume: 21, Issue:2

    Topics: Acetoacetates; Acidosis; Animals; Blood Glucose; Cycloparaffins; Fatty Acids; Fatty Acids, Nonesterified; Hydroxybutyrates; Hypoglycemia; Hypoglycemic Agents; Injections, Intraperitoneal; Ketone Bodies; Male; Mice; Rats; Valerates

1969
An inherited disorder of isoleucine catabolism causing accumulation of alpha-methylacetoacetate and alpha-methyl-beta -hydroxybutyrate, and intermittent metabolic acidosis.
    Pediatric research, 1973, Volume: 7, Issue:3

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Butyrates; Cells, Cultured; Child; Child, Preschool; Chromatography, Gas; Chromatography, Paper; Chromatography, Thin Layer; Female; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Infant; Isoleucine; Keto Acids; Ketones; Male; Mass Spectrometry; Mutation; Pedigree; Phenotype; Skin; Valerates

1973
Methylmalonic acid.
    Pediatrics, 1973, Volume: 51, Issue:6

    Topics: Acidosis; Awards and Prizes; Child; Coenzymes; Female; Fetal Diseases; Humans; Infant, Newborn; Infant, Newborn, Diseases; Isomerases; Lactates; Malonates; Metabolism, Inborn Errors; Methane; Pregnancy; Propionates; Pyruvates; Succinates; Valerates; Vitamin B 12; Vitamin B 12 Deficiency

1973
The occurrence of beta-hydroxy-n-valeric acid in a patient with propionic and methylmalonic acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 1973, May-30, Volume: 45, Issue:4

    Topics: Acidosis; Amino Acids; Autoanalysis; Autopsy; Chromatography, Gas; Chromatography, Thin Layer; Fatty Acids, Nonesterified; Follow-Up Studies; Humans; Hydroxybutyrates; Infant; Infant, Newborn; Lactates; Liver; Male; Malonates; Propionates; Valerates; Vomiting

1973
Diagnosis of isovaleric acidemia in cultured fibroblasts.
    Clinica chimica acta; international journal of clinical chemistry, 1973, Nov-15, Volume: 48, Issue:4

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carbon Radioisotopes; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Heterozygote; Humans; Infant, Newborn; Leucine; Pregnancy; Prenatal Diagnosis; Skin; Valerates

1973
Increased urinary excretion of 3-hydroxyisovaleric acid in patients with ketoacidosis.
    Clinica chimica acta; international journal of clinical chemistry, 1974, Jul-15, Volume: 54, Issue:1

    Topics: Acetoacetates; Acidosis; Adult; Amino Acids; Child; Child, Preschool; Chromatography, Gas; Diabetes Mellitus; Encephalitis; Epilepsy; Female; Humans; Hydroxybutyrates; Infant; Lactates; Male; Mass Spectrometry; Valerates; Vomiting

1974
Dietary treatment of an infant with isovaleric acidemia.
    Pediatrics, 1972, Volume: 49, Issue:4

    Topics: Acidosis; Diet Therapy; Fatty Acids; Humans; Infant; Leucine; Male; Valerates

1972
Lipid biosynthesis and increase in isovaleric acid of plasma.
    Science (New York, N.Y.), 1972, Jun-23, Volume: 176, Issue:4041

    Topics: Acidosis; Coenzyme A; Humans; Lipids; Valerates

1972
Isovaleric acidemia: a new genetic defect of leucine metabolism.
    Proceedings of the National Academy of Sciences of the United States of America, 1966, Volume: 56, Issue:1

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Butyrates; Caproates; Child, Preschool; Chromatography, Gas; Coenzyme A; Fatty Acids; Female; Humans; Leucine; Male; Propionates; Valerates

1966
Hypoglycin A: a specific inhibitor of isovaleryl CoA dehydrogenase.
    Proceedings of the National Academy of Sciences of the United States of America, 1971, Volume: 68, Issue:1

    Topics: Acidosis; Alanine; Amino Acid Metabolism, Inborn Errors; Animals; Butyrates; Caproates; Carbon Dioxide; Carbon Isotopes; Carnitine; Chromatography, Gas; Coenzyme A; Cyclopropanes; In Vitro Techniques; Isoleucine; Leucine; Male; Oxidoreductases; Plant Poisoning; Rats; Valerates; Vomiting

1971
Identification of beta-hydroxyisovaleric acid in the urine of a patient with isovaleric acidemia.
    Biochimica et biophysica acta, 1968, May-01, Volume: 152, Issue:3

    Topics: Acidosis; Chromatography, Gas; Metabolic Diseases; Oxidoreductases; Valerates

1968