valerates has been researched along with Acidosis in 27 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 27 (100.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Isselbacher, KJ; Tanaka, K | 1 |
| Kikawa, Y; Kikuchi, K; Ohta, S; Okamoto, M; Shigematsu, Y; Sudo, M | 1 |
| Bartlett, K; Leonard, JV; Ng, H | 1 |
| French, NP; Grauaug, A; Wysocki, SJ | 1 |
| Burton, BK; Challa, VR; Fischer, AQ; McLean, WT | 1 |
| Landaas, S | 2 |
| Porath, U; Schreier, K | 1 |
| Bruinvis, L; Drewes, JG; Duran, M; Ketting, D; van Sprang, FJ; Wadman, SK | 1 |
| Cohn, RM; Puschak, R; Rothman, R; Segal, S; Yudkoff, M | 1 |
| O'Brien, WE | 1 |
| Barness, LA | 2 |
| Jakobs, C; Landaas, S | 1 |
| Krieger, I; Tanaka, K | 1 |
| Dinesen, J; Gerdes, AM; Gregersen, N; Güttler, F; Holm, V; Lúdvigsson, P | 1 |
| Draffan, GH; Gompertz, D; Hull, D; Watts, JL | 1 |
| Callaghan, P; Newman, CG; Wilson, BD; Young, L | 1 |
| Senior, AE; Sherratt, HS | 1 |
| Daum, RS; Delvin, E; Goldman, H; Lamm, P; Mamer, OA; Scriver, CR | 1 |
| Eldjarn, L; Jellum, E; Schnitler, R; Stokke, O | 1 |
| Mandell, R; Shih, VE; Tanaka, K | 1 |
| Erickson, AM; Levy, HL; Lott, IT | 1 |
| Budd, MA; Efron, ML; Isselbacher, KJ; Tanaka, K | 1 |
| Isselbacher, KJ; Miller, EM; Tanaka, K | 1 |
| Isselbacher, KJ; Orr, JC; Tanaka, K | 1 |
1 review(s) available for valerates and Acidosis
| Article | Year |
|---|---|
[Congenital metabolic acidosis in the postnatal period].
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine | 1978 |
26 other study(ies) available for valerates and Acidosis
| Article | Year |
|---|---|
The isolation and identification of N-isovalerylglycine from urine of patients with isovaleric acidemia.
Topics: Acidosis; Amino Acids; Chemistry, Clinical; Child; Child, Preschool; Chromatography, Gas; Coenzyme A; Female; Humans; In Vitro Techniques; Leucine; Magnetic Resonance Spectroscopy; Male; Spectrum Analysis; Valerates | 1967 |
A simple method of determining 4-hydroxyisovaleric acid and its level in a patient with isovaleric acidemia.
Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Ketosis; Pentanoic Acids; Valerates | 1984 |
A combined defect of three mitochondrial carboxylases presenting as biotin-responsive 3-methylcrotonyl glycinuria and 3-hydroxyisovaleric aciduria.
Topics: Acidosis; Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Child, Preschool; Crotonates; Female; Fibroblasts; Glycine; Humans; Hydroxy Acids; Ligases; Mitochondria; Propionates; Pyruvate Carboxylase Deficiency Disease; Valerates | 1980 |
Organic aciduria associated with isovaleric acidemia.
Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Infant; Leucine; Pentanoic Acids; Valerates | 1983 |
Cerebellar hemorrhage complicating isovaleric acidemia: a case report.
Topics: Acidosis; Cerebellar Diseases; Cerebral Hemorrhage; Female; Hemiterpenes; Humans; Infant, Newborn; Pentanoic Acids; Valerates | 1981 |
Accumulation of 3-hydroxyisobutyric acid, 2-methyl-3-hydroxybutyric acid and 3-hydroxyisovaleric acid in ketoacidosis.
Topics: Acetates; Acidosis; Animals; Child; Child, Preschool; Chromatography, Gas; Diabetes Mellitus; Diabetic Ketoacidosis; Glutarates; Humans; Hydroxy Acids; Hydroxybutyrates; Infant; Isoleucine; Leucine; Male; Mass Spectrometry; Rats; Streptozocin; Valerates; Valine | 1975 |
Two sisters with isovaleric acidaemia, multiple attacks of ketoacidosis and normal development.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Coma; Female; Humans; Intelligence; Ketosis; Valerates; Vomiting | 1979 |
Glycine therapy in isovaleric acidemia.
Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Drug Administration Schedule; Female; Glycine; Humans; Keto Acids; Ketone Bodies; Lactates; Leucine; Pyruvates; Valerates | 1978 |
Inhibition of glycine synthase by branched-chain alpha-keto acids. A possible mechanism for abnormal glycine metabolism in ketotic hyperglycinemia.
Topics: Acidosis; Acyl Coenzyme A; Animals; Caproates; Glycine; Keto Acids; Ketosis; Liver; Male; Rats; Transferases; Valerates | 1978 |
Organic acidosis in infants.
Topics: Acidosis; Adult; Child; Humans; Infant; Infant, Newborn; Infant, Newborn, Diseases; Lactates; Methylmalonic Acid; Propionates; Pyruvates; Valerates | 1977 |
The occurrence of 2-hydroxyisovaleric acid in patients with lactic acidosis and ketoacidosis.
Topics: Acidosis; Adult; Child; Child, Preschool; Chromatography, Gas; Female; Humans; Hydroxy Acids; Hydroxybutyrates; Infant; Keto Acids; Lactates; Male; Mass Spectrometry; Valerates | 1977 |
Therapeutic effects of glycine in isovaleric acidemia.
Topics: Acidosis; Alkalies; Amino Acid Metabolism, Inborn Errors; Child; Female; Glycine; Humans; Inactivation, Metabolic; Ketosis; Oxidoreductases; Valerates | 1976 |
[Isovaleric acidemia].
Topics: Acidosis; Child, Preschool; Dietary Proteins; Female; Humans; Infant; Male; Metabolism, Inborn Errors; Oxidoreductases; Valerates | 1989 |
Biotin-responsive beta-methylcrotonylglycinuria.
Topics: Acidosis; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Chromatography, Gas; Fatty Acids; Glycine; Humans; Infant; Leucine; Male; Partial Pressure; Valerates; Valine; Vomiting | 1971 |
Neonatal death associated with isovalericacidaemia.
Topics: Acidosis; Bicarbonates; Chromatography; Chromatography, Gas; Coenzyme A; Electrolytes; Fatty Acids; Fatty Acids, Nonesterified; Glucose; Hemorrhage; Humans; Hypocalcemia; Infant Mortality; Infant, Newborn; Leucine; Male; Metabolism, Inborn Errors; Valerates | 1967 |
A comparison of the effects on blood glucose and ketone-body levels, and of the toxicities, of pent-4-enoic acid and four simple fatty acids.
Topics: Acetoacetates; Acidosis; Animals; Blood Glucose; Cycloparaffins; Fatty Acids; Fatty Acids, Nonesterified; Hydroxybutyrates; Hypoglycemia; Hypoglycemic Agents; Injections, Intraperitoneal; Ketone Bodies; Male; Mice; Rats; Valerates | 1969 |
An inherited disorder of isoleucine catabolism causing accumulation of alpha-methylacetoacetate and alpha-methyl-beta -hydroxybutyrate, and intermittent metabolic acidosis.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Butyrates; Cells, Cultured; Child; Child, Preschool; Chromatography, Gas; Chromatography, Paper; Chromatography, Thin Layer; Female; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Infant; Isoleucine; Keto Acids; Ketones; Male; Mass Spectrometry; Mutation; Pedigree; Phenotype; Skin; Valerates | 1973 |
Methylmalonic acid.
Topics: Acidosis; Awards and Prizes; Child; Coenzymes; Female; Fetal Diseases; Humans; Infant, Newborn; Infant, Newborn, Diseases; Isomerases; Lactates; Malonates; Metabolism, Inborn Errors; Methane; Pregnancy; Propionates; Pyruvates; Succinates; Valerates; Vitamin B 12; Vitamin B 12 Deficiency | 1973 |
The occurrence of beta-hydroxy-n-valeric acid in a patient with propionic and methylmalonic acidemia.
Topics: Acidosis; Amino Acids; Autoanalysis; Autopsy; Chromatography, Gas; Chromatography, Thin Layer; Fatty Acids, Nonesterified; Follow-Up Studies; Humans; Hydroxybutyrates; Infant; Infant, Newborn; Lactates; Liver; Male; Malonates; Propionates; Valerates; Vomiting | 1973 |
Diagnosis of isovaleric acidemia in cultured fibroblasts.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carbon Radioisotopes; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Heterozygote; Humans; Infant, Newborn; Leucine; Pregnancy; Prenatal Diagnosis; Skin; Valerates | 1973 |
Increased urinary excretion of 3-hydroxyisovaleric acid in patients with ketoacidosis.
Topics: Acetoacetates; Acidosis; Adult; Amino Acids; Child; Child, Preschool; Chromatography, Gas; Diabetes Mellitus; Encephalitis; Epilepsy; Female; Humans; Hydroxybutyrates; Infant; Lactates; Male; Mass Spectrometry; Valerates; Vomiting | 1974 |
Dietary treatment of an infant with isovaleric acidemia.
Topics: Acidosis; Diet Therapy; Fatty Acids; Humans; Infant; Leucine; Male; Valerates | 1972 |
Lipid biosynthesis and increase in isovaleric acid of plasma.
Topics: Acidosis; Coenzyme A; Humans; Lipids; Valerates | 1972 |
Isovaleric acidemia: a new genetic defect of leucine metabolism.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Butyrates; Caproates; Child, Preschool; Chromatography, Gas; Coenzyme A; Fatty Acids; Female; Humans; Leucine; Male; Propionates; Valerates | 1966 |
Hypoglycin A: a specific inhibitor of isovaleryl CoA dehydrogenase.
Topics: Acidosis; Alanine; Amino Acid Metabolism, Inborn Errors; Animals; Butyrates; Caproates; Carbon Dioxide; Carbon Isotopes; Carnitine; Chromatography, Gas; Coenzyme A; Cyclopropanes; In Vitro Techniques; Isoleucine; Leucine; Male; Oxidoreductases; Plant Poisoning; Rats; Valerates; Vomiting | 1971 |
Identification of beta-hydroxyisovaleric acid in the urine of a patient with isovaleric acidemia.
Topics: Acidosis; Chromatography, Gas; Metabolic Diseases; Oxidoreductases; Valerates | 1968 |