Page last updated: 2024-09-02

valerates and Acetonemia

valerates has been researched along with Acetonemia in 7 studies

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19907 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Kikawa, Y; Kikuchi, K; Ohta, S; Okamoto, M; Shigematsu, Y; Sudo, M1
Porath, U; Schreier, K1
Bruinvis, L; Drewes, JG; Duran, M; Ketting, D; van Sprang, FJ; Wadman, SK1
O'Brien, WE1
Kelly, S; Leikhim, E1
Krieger, I; Tanaka, K1
Bartlett, K; Cannon, RA; Conde, C; Gomez Vazquez, J; Lipson, M; Middleton, B; Nyhan, WL; Romanos, A; Sweetman, L1

Reviews

1 review(s) available for valerates and Acetonemia

ArticleYear
[Congenital metabolic acidosis in the postnatal period].
    Deutsche medizinische Wochenschrift (1946), 1978, Jun-02, Volume: 103, Issue:22

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine

1978

Other Studies

6 other study(ies) available for valerates and Acetonemia

ArticleYear
A simple method of determining 4-hydroxyisovaleric acid and its level in a patient with isovaleric acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 1984, Apr-27, Volume: 138, Issue:3

    Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Ketosis; Pentanoic Acids; Valerates

1984
Two sisters with isovaleric acidaemia, multiple attacks of ketoacidosis and normal development.
    European journal of pediatrics, 1979, Jun-28, Volume: 131, Issue:3

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Coma; Female; Humans; Intelligence; Ketosis; Valerates; Vomiting

1979
Inhibition of glycine synthase by branched-chain alpha-keto acids. A possible mechanism for abnormal glycine metabolism in ketotic hyperglycinemia.
    Archives of biochemistry and biophysics, 1978, Volume: 189, Issue:2

    Topics: Acidosis; Acyl Coenzyme A; Animals; Caproates; Glycine; Keto Acids; Ketosis; Liver; Male; Rats; Transferases; Valerates

1978
Isovalerylglycine detection by thin-layer chromatography: additional observations.
    Clinica chimica acta; international journal of clinical chemistry, 1975, Mar-10, Volume: 59, Issue:2

    Topics: Child; Chromatography, Gas; Chromatography, Thin Layer; Evaluation Studies as Topic; Glycine; Humans; Hydroxybutyrates; Ketosis; Male; Methods; Valerates

1975
Therapeutic effects of glycine in isovaleric acidemia.
    Pediatric research, 1976, Volume: 10, Issue:1

    Topics: Acidosis; Alkalies; Amino Acid Metabolism, Inborn Errors; Child; Female; Glycine; Humans; Inactivation, Metabolic; Ketosis; Oxidoreductases; Valerates

1976
3-Ketothiolase deficiency.
    European journal of pediatrics, 1986, Volume: 144, Issue:6

    Topics: 3-Hydroxybutyric Acid; Acetyl Coenzyme A; Acetyl-CoA C-Acyltransferase; Acyl Coenzyme A; Acyltransferases; Child; Female; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Infant; Isoleucine; Ketosis; Male; Valerates

1986