Page last updated: 2024-08-23

ursodeoxycholic acid and Syndrome

ursodeoxycholic acid has been researched along with Syndrome in 66 studies

Research

Studies (66)

TimeframeStudies, this research(%)All Research%
pre-19902 (3.03)18.7374
1990's7 (10.61)18.2507
2000's25 (37.88)29.6817
2010's25 (37.88)24.3611
2020's7 (10.61)2.80

Authors

AuthorsStudies
Fujiwara, K; Katano, T; Kataoka, H; Matsuura, K; Nagura, Y; Naitoh, I; Nojiri, S; Suzuki, T1
Hussain, N; Trivedi, PJ1
Chen, H; Gao, X; Hong, X; Hu, S; Jin, X; Qiao, Z; Xia, C; Xiang, X; Xu, Y; Zhang, P1
Hirai, K; Honda, K; Murahashi, M; Takaki, Y1
Ben Azouz, S; Boukriba, S; Cherif, D; Debbabi, H; Ghayeb, F; Hassine, H; Kchir, H; Maamouri, N; Yacoub, H1
Guan, L; Li, X; Li, Y; Lin, X; Wang, N; Zhang, X1
Figueiredo, LM; Horta, D; Lourenço, L; Martins, A1
Díaz Ramírez, GS; Donado Gómez, JH; Marín Zuluaga, JI; Martínez Casas, OY; Muñoz Maya, O; Restrepo Gutiérrez, JC; Santos, Ó1
Ben Mansour, W; Bouhlel, W; Guediche, A; Jemmali, D; Loghmari, MH; Safer, L1
Barbu, V; Corpechot, C; Delaunay, JL; Huynh, MT; Muller, L; Tran, CT1
García-Pajares, F; Madrigal Rubiales, B; Tejedor-Tejada, J1
Bancel, B; Brunel, T; Goubault, P; Mabrut, JY; Mohkam, K; Rode, A1
Ando, Y; Ikeda, C; Ishizawa, T; Kakizaki, Y; Kobayashi, T; Makino, N; Matsuda, A; Murakami, R; Sato, H; Sugahara, S; Tsunoda, M; Ueno, Y1
Hagymási, K; Tulassay, Z1
Czaja, AJ1
Bresson-Hadni, S; Efe, C; Heurgué-Berlot, A; Kav, T; Masi, C; Muratori, L; Muratori, P; Ozaslan, E; Purnak, T; Schiano, TD; Thiéfin, G; Torgutalp, M; Wahlin, S1
Lohse, AW; Zenouzi, R1
Adeyi, O; Fung, S; Mason, M; Millar, BA1
Anantharajah, A; Grigg, A; Lokan, J; Yeh, P1
Bunchorntavakul, C; Reddy, KR1
Abudumijiti, H; Chen, K; Dai, W; Guo, C; Li, J; Li, S; Liu, T; Lu, J; Lu, W; Wang, C; Wang, F; Wang, J; Xia, Y; Yang, J; Zhang, H; Zheng, Y; Zhou, Y; Zhou, Z; Zhu, R1
Cazzagon, N; Colloredo, G; Del Ross, T; Floreani, A; Franceschet, I; Invernizzi, P; Lleo, A; Mescoli, C; Motta, R; Roncalli, M; Rosina, F1
Anastaze Stelle, K; Cachat, F; Chehade, H; Perez, MH1
Endo, T; Fukuda, S; Igarashi, G; Kijima, H; Kurose, A; Mikami, K; Ohta, R; Sakamoto, J; Satake, R; Sawada, N; Yoshimura, T1
Beuers, U; Rust, C2
Dienes, HP; Frenzel, C; Galle, PR; Herkel, J; Kanzler, S; Kasper, HU; Lohse, AW; Lüth, S; Schramm, C1
Betterle, C; Bisconte, MG; Gentile, C; Gentile, M; Leo, P; Lucia, E; Mazzone, C; Morabito, F; Perugini, D; Romeo, F; Verta, M; Vigna, E1
Erlinger, S2
Arulprakash, S; Bala, MR; Kumar, SJ; Pugazhendhi, T; Sasi, AD1
Altiparmak, E; Efe, C; Karaaslan, Y; Muratori, P; Ozaslan, E; Ozbalkan, Z; Purnak, T; Wahlin, S1
Chapman, RW; Culver, EL1
McKiernan, P1
Davenport, M1
Kaganov, BS; Kamenets, EA; Machulan, IV; Strokova, TV; Zakharova, EIu1
Fuchs, J; Lieber, J; Piersma, FE; Schäfer, JF; Sturm, E; Szavay, PO1
Löhr, HF1
Baragiotta, A; Floreani, A; Guido, M1
Ben Ammar, A; Chaabouni, H; Cheikh, I; Ouerghi, H; Said, Y1
Manns, MP; Strassburg, CP1
Bueverov, AO1
Ditelberg, J; Kaplan, MM; Vallone, TM1
Hayashida, K; Kadokawa, Y; Kohno, S; Kusakari, C; Mizuta, Y; Murata, I; Nakanuma, Y; Ohba, K; Omagari, K; Takeshima, F1
Baldo, V; Blasone, L; Carderi, I; Caroli, D; Ferrara, F; Floreani, A; Rizzotto, ER1
Chazouillères, O; Poupon, R; Rosmorduc, O; Serfaty, L; Wendum, D1
Benderitter, T; Bourlière, M; Calvet, B; Halfon, P; Harafa, A; Igual, JP; Larroque, O; Martini, F; Ouzan, D; Penaranda, G; Renou, C; Sokolowsky, S1
Beuers, U; Pusl, T1
Trauner, M; Zollner, G1
Bernard-Chabert, B; Cadiot, G; Diebold, MD; Frémond, L; Geoffroy, P; Heurgué, A; Louvet, H; Pennaforte, JL; Picot, R; Schmit, JL; Thiéfin, G; Vitry, F; Yaziji, N1
Angulo, P; Lindor, KD; Silveira, MG; Talwalkar, JA1
O'Leary, JG; Pratt, DS1
Il'chenko, LIu; Mikheeva, OM1
Stiefelhagen, P1
Gossard, AA; Lindor, KD1
Bianchi, L; Menges, M; Mueller, T1
Iida, S; Makino, I; Ohkubo, H; Okuda, K1
Degott, C; Duclos-Vallée, JC; Erlinger, S; Ganne-Carrié, N; Hadengue, A; Robin, E1
Ampola, M; Buie, TM; Elias, ER; Frieden, R; Irons, M; Salen, G; Tint, GS1
O'Brien, CB; Reddy, KR; Saul, SH; Shields, DS1
Feeney, SJ; Hara, K; Ikuno, N; Mackay, IR; Matsuo, I; Omagari, K; Shirono, K; Whittingham, S1
Csáti, S; Kiss, Z; Lonovics, J; Nagy, F; Schneider, G; Wölfling, J1
Chazouillères, O; Montembault, S; Poupon, R; Rosmorduc, O; Serfaty, L; Wendum, D1
da Silva, JA; de Medeiros, BC; de Medeiros, CR; Lacerda, MA; Telles, JE1
Abdullah, MA; Abomelha, AM; Al-Hasnan, Z; Okamoto, E1
Anzani, A; Erenbourg, L; Fontana, U; Portaleone, B; Reggiani, P; Vercesi, M1

Reviews

19 review(s) available for ursodeoxycholic acid and Syndrome

ArticleYear
The Inconvenient Truth of Primary Biliary Cholangitis/Autoimmune Hepatitis Overlap Syndrome.
    Clinics in liver disease, 2022, Volume: 26, Issue:4

    Topics: Disease Progression; Hepatitis, Autoimmune; Humans; Liver Cirrhosis, Biliary; Syndrome; Ursodeoxycholic Acid

2022
Ulcerative colitis complicated by primary sclerosing cholangitis and autoimmune hepatitis overlap syndrome: a case report and literature review.
    Frontiers in immunology, 2023, Volume: 14

    Topics: Adult; Cholangitis, Sclerosing; Colitis, Ulcerative; Connective Tissue Diseases; Hepatitis, Autoimmune; Humans; Liver Diseases; Male; Syndrome; Ursodeoxycholic Acid

2023
Low-Phospholipid Associated Cholelithiasis (LPAC) syndrome: A synthetic review.
    Journal of visceral surgery, 2019, Volume: 156, Issue:4

    Topics: Adult; Age Factors; ATP Binding Cassette Transporter, Subfamily B; Bile; Bile Duct Neoplasms; Cholagogues and Choleretics; Cholangiocarcinoma; Cholangitis; Cholangitis, Sclerosing; Cholecystectomy; Cholelithiasis; Codon, Nonsense; Diagnosis, Differential; Female; Gallstones; Humans; Lithiasis; Liver Abscess; Liver Cirrhosis, Biliary; Liver Diseases; Mutation; Phosphatidylcholines; Pregnancy; Pregnancy Complications; Recurrence; Syndrome; Ultrasonography; Ursodeoxycholic Acid

2019
[Review of overlap syndromes in autoimmune liver diseases. Diagnostic and therapeutic difficulties].
    Orvosi hetilap, 2013, Jun-16, Volume: 154, Issue:24

    Topics: Adrenal Cortex Hormones; Autoantibodies; Autoimmunity; Cholangitis, Sclerosing; Diagnosis, Differential; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Liver Diseases; Syndrome; Ursodeoxycholic Acid

2013
Diagnosis and management of the overlap syndromes of autoimmune hepatitis.
    Canadian journal of gastroenterology = Journal canadien de gastroenterologie, 2013, Volume: 27, Issue:7

    Topics: Adult; Alkaline Phosphatase; Cholangitis, Sclerosing; Cholestasis; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2013
Diagnosis and management of overlap syndromes.
    Clinics in liver disease, 2015, Volume: 19, Issue:1

    Topics: Autoantibodies; Cholagogues and Choleretics; Cholangitis, Sclerosing; Diagnosis, Differential; Disease Progression; Hepatitis, Autoimmune; Humans; Immunoglobulins; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Liver Transplantation; Syndrome; Ursodeoxycholic Acid

2015
Combination therapy of ursodeoxycholic acid and budesonide for PBC-AIH overlap syndrome: a meta-analysis.
    Drug design, development and therapy, 2015, Volume: 9

    Topics: Budesonide; Chi-Square Distribution; Cholagogues and Choleretics; Drug Therapy, Combination; Glucocorticoids; Hepatitis, Autoimmune; Humans; Liver Cirrhosis, Biliary; Odds Ratio; Randomized Controlled Trials as Topic; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2015
Streptococcus pneumoniae-Associated Hemolytic and Uremic Syndrome With Cholestasis: A Case Report and Brief Literature Review.
    Clinical pediatrics, 2016, Volume: 55, Issue:2

    Topics: Anti-Bacterial Agents; Cephalosporins; Child, Preschool; Cholagogues and Choleretics; Cholestasis; Diagnosis, Differential; Female; Humans; Peritoneal Dialysis; Pneumonia, Pneumococcal; Syndrome; Uremia; Ursodeoxycholic Acid

2016
Overlap syndromes among autoimmune liver diseases.
    World journal of gastroenterology, 2008, Jun-07, Volume: 14, Issue:21

    Topics: Adolescent; Adult; Child; Cholagogues and Choleretics; Cholangitis, Sclerosing; Female; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Liver Transplantation; Male; Middle Aged; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2008
Systematic review: management options for primary sclerosing cholangitis and its variant forms - IgG4-associated cholangitis and overlap with autoimmune hepatitis.
    Alimentary pharmacology & therapeutics, 2011, Volume: 33, Issue:12

    Topics: Animals; Cholangitis, Sclerosing; Disease Progression; Female; Hepatitis, Autoimmune; Humans; Immunoglobulin G; Immunosuppressive Agents; Male; Mice; Syndrome; Ursodeoxycholic Acid

2011
Biliary atresia: clinical aspects.
    Seminars in pediatric surgery, 2012, Volume: 21, Issue:3

    Topics: Adrenal Cortex Hormones; Anti-Inflammatory Agents; Biliary Atresia; Chemotherapy, Adjuvant; Cholagogues and Choleretics; Humans; Liver Transplantation; Portoenterostomy, Hepatic; Postoperative Complications; Prognosis; Spleen; Syndrome; Ursodeoxycholic Acid

2012
[Autoimmune hepatitis and overlap syndrome: therapy].
    Praxis, 2002, Aug-21, Volume: 91, Issue:34

    Topics: Azathioprine; Cholangitis, Sclerosing; Drug Therapy, Combination; Haplotypes; Hepatitis, Autoimmune; HLA Antigens; Humans; Liver Cirrhosis, Biliary; Prednisolone; Syndrome; Ursodeoxycholic Acid

2002
[Primary biliary liver cirrhosis and overlap syndrome. Diagnosis and therapy].
    Der Internist, 2004, Volume: 45, Issue:1

    Topics: Antibodies, Antinuclear; Autoantibodies; Autoimmune Diseases; Hepatitis, Autoimmune; HLA-DR Antigens; HLA-DR Serological Subtypes; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Liver Function Tests; Mitochondria, Liver; Prognosis; Syndrome; Ursodeoxycholic Acid

2004
Flare-up of autoimmune hepatitis after delivery in a patient with primary biliary cirrhosis: postpartum overlap syndrome of primary biliary cirrhosis and autoimmune hepatitis.
    Digestive diseases and sciences, 2005, Volume: 50, Issue:1

    Topics: Adult; Alanine Transaminase; Alkaline Phosphatase; Cholagogues and Choleretics; Female; gamma-Glutamyltransferase; Hepatitis, Autoimmune; Humans; Liver Cirrhosis, Biliary; Puerperal Disorders; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2005
Overlap syndromes.
    Seminars in liver disease, 2005, Volume: 25, Issue:3

    Topics: Adult; Age of Onset; Aged; Cholagogues and Choleretics; Cholangitis, Sclerosing; Comorbidity; Diagnosis, Differential; Disease Progression; Female; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Liver Failure; Male; Prognosis; Syndrome; Ursodeoxycholic Acid

2005
Ursodeoxycholic acid treatment of vanishing bile duct syndromes.
    World journal of gastroenterology, 2006, Jun-14, Volume: 12, Issue:22

    Topics: Apoptosis; Bile Acids and Salts; Bile Duct Diseases; Bile Ducts, Intrahepatic; Cholagogues and Choleretics; Cholestasis; Humans; Liver Cirrhosis; Liver Failure; Syndrome; Ursodeoxycholic Acid

2006
Molecular mechanisms of cholestasis.
    Wiener medizinische Wochenschrift (1946), 2006, Volume: 156, Issue:13-14

    Topics: ATP-Binding Cassette Transporters; Bile Acids and Salts; Bilirubin; Cholestasis, Intrahepatic; DNA Mutational Analysis; Hepatocytes; Humans; Inactivation, Metabolic; Liver; Membrane Transport Proteins; Receptors, Cytoplasmic and Nuclear; Rifampin; Risk Factors; Syndrome; Ursodeoxycholic Acid

2006
Cholestasis and cholestatic syndromes.
    Current opinion in gastroenterology, 2007, Volume: 23, Issue:3

    Topics: Animals; Bile Acids and Salts; Biological Transport; Cholangiopancreatography, Endoscopic Retrograde; Cholestasis; Humans; Prognosis; Syndrome; Ursodeoxycholic Acid

2007
Drug-induced vanishing bile duct syndrome: response to ursodiol.
    The American journal of gastroenterology, 1996, Volume: 91, Issue:7

    Topics: Antipsychotic Agents; Bile Duct Diseases; Cholagogues and Choleretics; Cholestasis; Chronic Disease; Female; Humans; Liver Function Tests; Middle Aged; Prochlorperazine; Syndrome; Ursodeoxycholic Acid

1996

Trials

1 trial(s) available for ursodeoxycholic acid and Syndrome

ArticleYear
[Does post-cholecystectomy syndrome exist? Epidemiologic features and therapeutic effects of ursodeoxycholic acid].
    Minerva medica, 1986, Oct-06, Volume: 77, Issue:38

    Topics: Cholecystectomy; Deoxycholic Acid; Double-Blind Method; Dyspepsia; Female; Follow-Up Studies; Humans; Male; Syndrome; Ursodeoxycholic Acid

1986

Other Studies

46 other study(ies) available for ursodeoxycholic acid and Syndrome

ArticleYear
Primary Sclerosing Cholangitis and Autoimmune Hepatitis Overlapping Syndrome Complicated by Ulcerative Colitis.
    Internal medicine (Tokyo, Japan), 2022, Aug-15, Volume: 61, Issue:16

    Topics: Adult; Biopsy; Cholangitis, Sclerosing; Colitis, Ulcerative; Connective Tissue Diseases; Hepatitis, Autoimmune; Humans; Male; Syndrome; Ursodeoxycholic Acid

2022
Coexistence of primary biliary cirrhosis-autoimmune hepatitis overlap syndrome and membranous nephropathy: A case report.
    Clinical nephrology, 2023, Volume: 99, Issue:1

    Topics: Azathioprine; Glomerulonephritis, Membranous; Hepatitis, Autoimmune; Humans; Liver Cirrhosis, Biliary; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2023
L-carbocisteine can cause cholestasis with vanishing bile duct syndrome in children: A case report.
    Medicine, 2022, Nov-11, Volume: 101, Issue:45

    Topics: Bile Ducts, Intrahepatic; Bilirubin; Carbocysteine; Child; Cholestasis; Female; Humans; Jaundice; Syndrome; Ursodeoxycholic Acid

2022
Overlap syndrome of primary biliary cholangitis and primary sclerosing cholangitis: two case reports.
    Journal of medical case reports, 2023, Apr-28, Volume: 17, Issue:1

    Topics: Cholangitis, Sclerosing; Connective Tissue Diseases; Constriction, Pathologic; Female; Hepatitis, Autoimmune; Humans; Liver Cirrhosis, Biliary; Middle Aged; Syndrome; Ursodeoxycholic Acid

2023
A complex case of low-phospholipid-associated cholelithiasis syndrome.
    Revista espanola de enfermedades digestivas, 2020, Volume: 112, Issue:7

    Topics: Adult; Cholangiopancreatography, Endoscopic Retrograde; Cholecystectomy; Choledocholithiasis; Female; Humans; Phospholipids; Syndrome; Ursodeoxycholic Acid

2020
Autoimmune hepatitis - primary biliary cholangitis overlap syndrome. Long-term outcomes of a retrospective cohort in a university hospital.
    Gastroenterologia y hepatologia, 2018, Volume: 41, Issue:9

    Topics: Adrenal Cortex Hormones; Adult; Colombia; Disease Progression; Female; Follow-Up Studies; Hepatitis, Autoimmune; Hospitals, University; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Liver Transplantation; Male; Middle Aged; Retrospective Studies; Syndrome; Ursodeoxycholic Acid

2018
Primary biliary cholangitis : therapeutic and evolving aspects about 46 cases.
    La Tunisie medicale, 2018, Volume: 96, Issue:1

    Topics: Adrenal Cortex Hormones; Adult; Aged; Aged, 80 and over; Diagnosis, Differential; Disease Progression; Drug Therapy, Combination; Female; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis; Liver Cirrhosis, Biliary; Liver Transplantation; Male; Middle Aged; Prevalence; Retrospective Studies; Syndrome; Treatment Outcome; Ursodeoxycholic Acid; Young Adult

2018
Expanding the mutational spectrum of the ABCB4 gene in inherited adult cholestatic liver disorders with four novel pathogenic variants.
    Revista espanola de enfermedades digestivas, 2019, Volume: 111, Issue:1

    Topics: Adult; ATP Binding Cassette Transporter, Subfamily B; Cholagogues and Choleretics; Cholelithiasis; Cholestasis, Intrahepatic; Female; Gene-Environment Interaction; High-Throughput Nucleotide Sequencing; Humans; Mutation, Missense; Pedigree; Phenotype; Phospholipids; Pregnancy; Pregnancy Complications; Pruritus; Syndrome; Ursodeoxycholic Acid; Young Adult

2019
Hepatobiliary and Pancreatic: Sertraline-induced vanishing bile duct syndrome treated with plasmapheresis.
    Journal of gastroenterology and hepatology, 2019, Volume: 34, Issue:3

    Topics: Adult; Bile Duct Diseases; Bile Ducts, Intrahepatic; Chemical and Drug Induced Liver Injury; Female; Humans; Plasmapheresis; Selective Serotonin Reuptake Inhibitors; Sertraline; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2019
A novel pathogenic variant of ATP-binding cassette subfamily B member 4 causing gallstones in a young adult.
    Clinical journal of gastroenterology, 2019, Volume: 12, Issue:6

    Topics: Adult; ATP-Binding Cassette Transporters; Biliary Tract Diseases; Cholagogues and Choleretics; Colic; Gallstones; Heterozygote; Humans; Male; Mutation; Phospholipids; Recurrence; Syndrome; Ursodeoxycholic Acid

2019
Sequential presentation of primary biliary cirrhosis and autoimmune hepatitis.
    European journal of gastroenterology & hepatology, 2014, Volume: 26, Issue:5

    Topics: Adolescent; Adult; Aged; Biomarkers; Disease Progression; Drug Therapy, Combination; Europe; Female; Gastrointestinal Agents; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver; Liver Cirrhosis, Biliary; Liver Transplantation; Male; Middle Aged; Remission Induction; Retrospective Studies; Risk Factors; Syndrome; Time Factors; Treatment Outcome; United States; Ursodeoxycholic Acid; Young Adult

2014
Long-term outcome in PSC/AIH "overlap syndrome": does immunosuppression also treat the PSC component?
    Journal of hepatology, 2014, Volume: 61, Issue:5

    Topics: Adult; Cholangitis, Sclerosing; Disease Progression; Follow-Up Studies; Hepatitis, Autoimmune; Humans; Immunosuppression Therapy; Liver Transplantation; Male; Middle Aged; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2014
Vanishing bile duct syndrome in the context of concurrent temozolomide for glioblastoma.
    BMJ case reports, 2014, Nov-28, Volume: 2014

    Topics: Antineoplastic Agents, Alkylating; Biopsy, Needle; Brain Neoplasms; Chemical and Drug Induced Liver Injury; Cholestyramine Resin; Common Bile Duct Diseases; Dacarbazine; Female; Follow-Up Studies; Glioblastoma; Humans; Immunohistochemistry; Jaundice; Liver Function Tests; Middle Aged; Syndrome; Temozolomide; Treatment Outcome; Ursodeoxycholic Acid

2014
Vanishing bile duct syndrome and immunodeficiency preceding the diagnosis of Hodgkin lymphoma.
    Internal medicine journal, 2014, Volume: 44, Issue:12a

    Topics: Aged; Antineoplastic Combined Chemotherapy Protocols; Bile Ducts, Intrahepatic; Bleomycin; Cholagogues and Choleretics; Cholestasis; Doxorubicin; Hodgkin Disease; Humans; Immunocompromised Host; Male; Neutropenia; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2014
The overlap syndrome between primary biliary cirrhosis and primary sclerosing cholangitis.
    Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver, 2015, Volume: 47, Issue:5

    Topics: Arthritis, Psoriatic; Autoantibodies; Cholangitis, Sclerosing; Comorbidity; Female; Humans; Liver; Liver Cirrhosis, Biliary; Middle Aged; Mitochondria; Syndrome; Tumor Necrosis Factor-alpha; Ursodeoxycholic Acid

2015
Two Cases of Primary Sclerosing Cholangitis Overlapping with Autoimmune Hepatitis in Adults.
    Internal medicine (Tokyo, Japan), 2017, Volume: 56, Issue:5

    Topics: Biopsy; Cholangiography; Cholangitis, Sclerosing; Drug Therapy, Combination; Glucocorticoids; Hepatitis, Autoimmune; Humans; Liver; Male; Middle Aged; Syndrome; Tomography, X-Ray Computed; Ursodeoxycholic Acid; Young Adult

2017
Characteristics and long-term prognosis of the autoimmune hepatitis/primary sclerosing cholangitis overlap syndrome.
    Journal of clinical gastroenterology, 2009, Volume: 43, Issue:1

    Topics: Adolescent; Adult; Aged; Cholangiography; Cholangitis, Sclerosing; Disease Progression; Drug Therapy, Combination; Female; Fibrosis; Follow-Up Studies; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis; Male; Middle Aged; Prognosis; Retrospective Studies; Syndrome; Ursodeoxycholic Acid; Young Adult

2009
Autoimmune hemolityc anemia concomitant with sequential autoimmune hepatitis-primary biliary cirrhosis overlap syndrome and Hashimoto's thyroiditis: a new entity of autoimmune polyendocrine syndrome.
    Journal of endocrinological investigation, 2009, Volume: 32, Issue:3

    Topics: Anemia, Hemolytic, Autoimmune; Anti-Inflammatory Agents; Budesonide; Female; Hashimoto Disease; Hepatitis, Autoimmune; Humans; Liver Cirrhosis, Biliary; Middle Aged; Polyendocrinopathies, Autoimmune; Syndrome; Ursodeoxycholic Acid

2009
[Right upper quadrant abdominal pain and fever. Genetic phospholipid deficiency].
    Gastroenterologie clinique et biologique, 2009, Volume: 33, Issue:10-11 Supp

    Topics: Abdominal Pain; ATP Binding Cassette Transporter, Subfamily B; Cholagogues and Choleretics; Cholecystectomy; Cholelithiasis; Female; Fever; Gallstones; Genetic Markers; Humans; Middle Aged; Pedigree; Phospholipids; Point Mutation; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2009
Overlap syndrome: autoimmune hepatitis with primary biliary cirrhosis.
    The Journal of the Association of Physicians of India, 2010, Volume: 58

    Topics: Adult; Autoantibodies; Biopsy; Cholagogues and Choleretics; Female; Hepatitis, Autoimmune; Humans; Liver Cirrhosis, Biliary; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2010
Autoimmune liver disease in patients with systemic lupus erythematosus: a retrospective analysis of 147 cases.
    Scandinavian journal of gastroenterology, 2011, Volume: 46, Issue:6

    Topics: Adult; Antibodies, Antinuclear; Azathioprine; Biopsy; Enzyme-Linked Immunosorbent Assay; Female; Hepatitis, Autoimmune; Humans; Hydroxychloroquine; Immunoblotting; Immunoglobulin G; Liver Cirrhosis, Biliary; Lupus Erythematosus, Systemic; Middle Aged; Prednisolone; Prevalence; Retrospective Studies; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2011
Neonatal jaundice.
    Clinics and research in hepatology and gastroenterology, 2012, Volume: 36, Issue:3

    Topics: Biliary Atresia; Bilirubin; Cholagogues and Choleretics; Cholestasis; Diagnosis, Differential; Diagnostic Techniques, Digestive System; Diet; Energy Intake; Hepatitis; Hepatomegaly; Humans; Incidence; Infant, Newborn; Jaundice, Neonatal; Prognosis; Splenomegaly; Syndrome; Ursodeoxycholic Acid; Vitamins

2012
[A case report of Byler's syndrome].
    Eksperimental'naia i klinicheskaia gastroenterologiia = Experimental & clinical gastroenterology, 2012, Issue:1

    Topics: Child, Preschool; Cholestasis, Intrahepatic; Diagnosis, Differential; Female; Humans; Liver Function Tests; Rifampin; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2012
Low phospholipid-associated cholestasis and cholelithiasis.
    Clinics and research in hepatology and gastroenterology, 2012, Volume: 36 Suppl 1

    Topics: Age Distribution; ATP Binding Cassette Transporter, Subfamily B; Cholagogues and Choleretics; Cholelithiasis; Cholestasis; Diagnosis, Differential; Female; Genotype; Humans; Mutation; Phenotype; Phospholipids; Pregnancy; Pregnancy Complications; Risk Factors; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2012
Surgical treatment of inspissated bile syndrome using a 2-stage pure laparoscopic approach: a case report.
    Journal of pediatric surgery, 2012, Volume: 47, Issue:12

    Topics: Cholangiography; Cholecystectomy, Laparoscopic; Cholecystostomy; Cholestasis, Extrahepatic; Combined Modality Therapy; Female; Follow-Up Studies; Humans; Infant; Risk Assessment; Syndrome; Therapeutic Irrigation; Treatment Outcome; Ursodeoxycholic Acid

2012
Primary biliary cirrhosis-autoimmune hepatitis overlap syndrome: a cause of resistance to ursodeoxycholic treatment.
    Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver, 2003, Volume: 35, Issue:2

    Topics: Adult; Cholagogues and Choleretics; Drug Resistance; Female; Hepatitis, Autoimmune; Humans; Liver Cirrhosis, Biliary; Male; Syndrome; Ursodeoxycholic Acid

2003
[The overlap syndrome of autoimmune hepatitis and primary biliary cirrhosis. Clinical and therapeutic analysis of 5 cases].
    La Tunisie medicale, 2003, Volume: 81, Issue:7

    Topics: Adult; Antibodies, Antinuclear; Autoantibodies; Azathioprine; Cholagogues and Choleretics; Clinical Enzyme Tests; Enzyme-Linked Immunosorbent Assay; Female; Fluorescent Antibody Technique; Follow-Up Studies; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Middle Aged; Prednisone; Retrospective Studies; Syndrome; Time Factors; Ursodeoxycholic Acid

2003
[Treatment of autoimmune hepatic diseases].
    Klinicheskaia meditsina, 2004, Volume: 82, Issue:10

    Topics: Adult; Autoimmune Diseases; Child; Cholagogues and Choleretics; Cholangitis, Sclerosing; Cholestasis, Intrahepatic; Drug Therapy, Combination; Glucocorticoids; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Liver Diseases; Prognosis; Risk Factors; Syndrome; Time Factors; Ursodeoxycholic Acid

2004
Reversal of cirrhosis in a patient with primary biliary cirrhosis-autoimmune hepatitis overlap syndrome.
    Digestive diseases and sciences, 2005, Volume: 50, Issue:1

    Topics: Cholagogues and Choleretics; Colchicine; Dose-Response Relationship, Drug; Drug Administration Schedule; Drug Therapy, Combination; Female; Glucocorticoids; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Methotrexate; Middle Aged; Prednisone; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2005
Clinical course and outcome of autoimmune hepatitis/primary sclerosing cholangitis overlap syndrome.
    The American journal of gastroenterology, 2005, Volume: 100, Issue:7

    Topics: Adolescent; Adult; Cholagogues and Choleretics; Cholangitis, Sclerosing; Female; Follow-Up Studies; Hepatitis, Autoimmune; Humans; Immunosuppression Therapy; Male; Prospective Studies; Survival Analysis; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2005
Long term outcome and response to therapy of primary biliary cirrhosis-autoimmune hepatitis overlap syndrome.
    Journal of hepatology, 2006, Volume: 44, Issue:2

    Topics: Adult; Aged; Biopsy; Cholagogues and Choleretics; Disease Progression; Drug Therapy, Combination; Female; Follow-Up Studies; Glucocorticoids; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Male; Middle Aged; Retrospective Studies; Syndrome; Time Factors; Treatment Outcome; Ursodeoxycholic Acid

2006
Primary biliary cirrhosis-autoimmune hepatitis overlap syndrome: complete biochemical and histological response to therapy with ursodesoxycholic acid.
    Journal of gastroenterology and hepatology, 2006, Volume: 21, Issue:4

    Topics: Hepatitis, Autoimmune; Humans; Liver Cirrhosis, Biliary; Male; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2006
Overlap syndrome of primary biliary cirrhosis and autoimmune hepatitis: a retrospective study of 115 cases of autoimmune liver disease.
    Gastroenterologie clinique et biologique, 2007, Volume: 31, Issue:1

    Topics: Adolescent; Adult; Aged; Aged, 80 and over; Biopsy; Cholagogues and Choleretics; Cholangitis, Sclerosing; Drug Therapy, Combination; Female; France; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver; Liver Cirrhosis, Biliary; Liver Function Tests; Male; Medical Records; Middle Aged; Retrospective Studies; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

2007
Overlap of autoimmune hepatitis and primary biliary cirrhosis: long-term outcomes.
    The American journal of gastroenterology, 2007, Volume: 102, Issue:6

    Topics: Ascites; Esophageal and Gastric Varices; Female; Gastrointestinal Hemorrhage; Hepatitis, Autoimmune; Humans; Hypertension, Portal; Liver Cirrhosis, Biliary; Liver Transplantation; Male; Middle Aged; Syndrome; Ursodeoxycholic Acid

2007
[Non-hepatic manifestations of the overlap syndrome (a case report)].
    Eksperimental'naia i klinicheskaia gastroenterologiia = Experimental & clinical gastroenterology, 2006, Issue:6

    Topics: Anti-Inflammatory Agents; Budesonide; Cholagogues and Choleretics; Diagnosis, Differential; Drug Therapy, Combination; Dry Eye Syndromes; Female; Humans; Liver Diseases; Middle Aged; Syndrome; Ursodeoxycholic Acid; Xerostomia

2006
[Autoimmune cholestasis syndrome. Ursodeoxycholic acid is the drug standard].
    MMW Fortschritte der Medizin, 2007, May-24, Volume: 149, Issue:21

    Topics: Anti-Inflammatory Agents; Autoimmune Diseases; Budesonide; Cholagogues and Choleretics; Cholangitis, Sclerosing; Cholestasis, Intrahepatic; Disease-Free Survival; Drug Therapy, Combination; Humans; Liver Cirrhosis, Biliary; Liver Function Tests; Liver Transplantation; Syndrome; Ursodeoxycholic Acid

2007
Development of autoimmune hepatitis in primary biliary cirrhosis.
    Liver international : official journal of the International Association for the Study of the Liver, 2007, Volume: 27, Issue:8

    Topics: Adult; Alanine Transaminase; Anti-Inflammatory Agents; Aspartate Aminotransferases; Azathioprine; Cholagogues and Choleretics; Disease Progression; Drug Therapy, Combination; Female; Follow-Up Studies; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Middle Aged; Prednisone; Retrospective Studies; Syndrome; Time Factors; Treatment Outcome; Ursodeoxycholic Acid

2007
Autoimmune hepatitis 2 years after the diagnosis of primary sclerosing cholangitis: an unusual overlap syndrome in a 17-year-old adolescent.
    European journal of gastroenterology & hepatology, 2008, Volume: 20, Issue:3

    Topics: Adolescent; Cholagogues and Choleretics; Cholangiopancreatography, Endoscopic Retrograde; Cholangitis, Sclerosing; Female; Follow-Up Studies; Hepatitis, Autoimmune; Humans; Syndrome; Ursodeoxycholic Acid

2008
Ursodeoxycholic acid oral tolerance test in patients with constitutional hyperbilirubinemias and effect of phenobarbital.
    Gastroenterology, 1981, Volume: 81, Issue:1

    Topics: Administration, Oral; Adult; Deoxycholic Acid; Female; Gilbert Disease; Humans; Hyperbilirubinemia, Hereditary; Jaundice, Chronic Idiopathic; Male; Phenobarbital; Syndrome; Ursodeoxycholic Acid

1981
Primary biliary cirrhosis-autoimmune hepatitis overlap syndrome. Corticoresistance and effective treatment by cyclosporine A.
    Digestive diseases and sciences, 1995, Volume: 40, Issue:5

    Topics: Adult; Autoimmune Diseases; Cyclosporine; Female; Hepatitis; Humans; Liver Cirrhosis, Biliary; Prednisolone; Syndrome; Ursodeoxycholic Acid

1995
Abnormal cholesterol metabolism in the Smith-Lemli-Opitz syndrome: report of clinical and biochemical findings in four patients and treatment in one patient.
    American journal of medical genetics, 1994, May-01, Volume: 50, Issue:4

    Topics: Abnormalities, Multiple; Adolescent; Bile Acids and Salts; Child; Child, Preschool; Cholesterol; Cholesterol, Dietary; Dehydrocholesterols; Face; Female; Genes, Recessive; Humans; Infant; Intellectual Disability; Lipid Metabolism, Inborn Errors; Male; Microcephaly; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Sterols; Syndrome; Ursodeoxycholic Acid

1994
Autoimmune cholangitis syndrome with a bias towards primary biliary cirrhosis.
    Pathology, 1996, Volume: 28, Issue:3

    Topics: Antibodies, Antinuclear; Autoimmune Diseases; Cholangitis; Enzyme-Linked Immunosorbent Assay; Female; Fluorescent Antibody Technique; Gastrointestinal Agents; Humans; Immunoblotting; Liver Cirrhosis, Biliary; Middle Aged; Pyruvate Dehydrogenase Complex; Syndrome; Ursodeoxycholic Acid

1996
[The ursodeoxycholic acid-p-aminobenzoic acid test in the diagnosis of small bowel bacterial overgrowth syndrome].
    Orvosi hetilap, 1997, May-18, Volume: 138, Issue:20

    Topics: 4-Aminobenzoic Acid; Adult; Breath Tests; Female; Humans; Intestinal Diseases; Intestinal Mucosa; Intestine, Small; Male; Syndrome; Ursodeoxycholic Acid

1997
Primary biliary cirrhosis-autoimmune hepatitis overlap syndrome: clinical features and response to therapy.
    Hepatology (Baltimore, Md.), 1998, Volume: 28, Issue:2

    Topics: Adrenal Cortex Hormones; Adult; Aged; Cholagogues and Choleretics; Drug Therapy, Combination; Female; Hepatitis, Autoimmune; Humans; Immunosuppressive Agents; Liver Cirrhosis, Biliary; Male; Middle Aged; Syndrome; Treatment Outcome; Ursodeoxycholic Acid

1998
Cholestasis secondary to Hodgkin's disease: report of 2 cases of vanishing bile duct syndrome.
    Haematologica, 1998, Volume: 83, Issue:11

    Topics: Adult; Bile Ducts; Biopsy; Cholestasis, Intrahepatic; Fatal Outcome; Female; Hodgkin Disease; Humans; Liver Cirrhosis, Biliary; Liver Function Tests; Middle Aged; Syndrome; Ursodeoxycholic Acid

1998
Arthrogryposis, renal dysfunction and cholestasis syndrome.
    Saudi medical journal, 2000, Volume: 21, Issue:3

    Topics: Abnormalities, Multiple; Acidosis, Renal Tubular; Arthrogryposis; Atrophy; Cholestasis; Consanguinity; Corpus Callosum; Female; Genes, Recessive; Hearing Loss, Sensorineural; Heart Defects, Congenital; Humans; Infant, Newborn; Pedigree; Retrospective Studies; Saudi Arabia; Syndrome; Ursodeoxycholic Acid

2000