Page last updated: 2024-08-23

ursodeoxycholic acid and Cystic Fibrosis

ursodeoxycholic acid has been researched along with Cystic Fibrosis in 74 studies

Research

Studies (74)

Timeframe	Studies, this research(%)	All Research%
pre-1990	2 (2.70)	18.7374
1990's	41 (55.41)	18.2507
2000's	9 (12.16)	29.6817
2010's	19 (25.68)	24.3611
2020's	3 (4.05)	2.80

Authors

Authors	Studies
Karnsakul, W; Wasuwanich, P	1
Staufer, K	1
Alghisi, F; Alicandro, G; Asherova, I; Colombo, C; Corti, F; de Monestrol, I; Evans, H; Kashirskaya, N; Kondratyeva, E; Lewindon, PJ; Lindblad, A; Oliver, M; Ooi, CY; Padoan, R; Ramm, GA; Strandvik, B	1
Bertolini, A; Bodewes, FAJA; Jonker, JW; van de Peppel, IP; Verkade, HJ	1
Ashby, D; Cheng, K; Smyth, RL	3
Bebawy, M; Chellappan, DK; de Jesus Andreoli Pinto, T; Dua, K; Gupta, G; Hansbro, PM	1
Al Qatarneh, S; Lindblad, D; Michel, HK; Ozolek, J; Venkat, V; Weiner, DJ	1
Boëlle, PY; Clement, A; Corvol, H; Debray, D; Guillot, L	1
Heller, T; Kleiner, DE; Koh, C; Sakiani, S	1
Bolan, C; Cortese, C; Harnois, D; Mallea, J	1
Fisher, SE; Rabinowitz, SS; Schwarz, SM; Vo, HD; Xu, J	1
Alonso, EM; Harned, R; Karmazyn, B; Krishnamurthy, R; Leung, DH; Ling, S; Magee, JC; Marshall, BC; Molleston, JP; Murray, KF; Narkewicz, MR; Palermo, J; Paranjape, SM; Romero, R; Schwarzenberg, SJ; Sherker, AH; Siegel, MJ; Weymann, A; Ye, W	1
Drzymała-Czyż, S; Jończyk-Potoczna, K; Lisowska, A; Stajgis, M; Walkowiak, J	1
Alicandro, G; Biffi, A; Colombo, C; Corti, F; Crosignani, A; Motta, V; Setchell, KDR; Zhang, W	1
Narkewicz, MR	1
Houwen, RH; van der Doef, HP; van der Ent, CK; van der Feen, C	1
Boggia, B; Buonpensiero, P; De Gregorio, F; Di Pasqua, A; Ferri, P; Raia, V; Sepe, A; Siano, M	1
Dockter, G; Herrmann, U; Lammert, F	1
Bijvelds, MJ; Bodewes, FA; de Jonge, HR; Havinga, R; Verkade, HJ; Wouthuyzen-Bakker, M	1
Espach, C; Glasmacher, C; Griese, M; Hartl, D; Hector, A; Kappler, M; Lang, T; Schweiger-Kabesch, A	1
Hoskins, AC; Lewindon, PJ; O'Connell, NC; Pereira, TN; Ramm, GA; Setchell, KD; Shepherd, RW; Smith, JL	1
Bailey, M; Clark, D; Desmond, CP; Roberts, SK; Wilson, J	1
Alexander, GJ; Allison, ME; Bilton, D; Haworth, CS; Lomas, DJ; McKeon, D; Nash, KL	1
Barbara, L; Colombo, C; Giunta, AM; Maspero, D; Piceni Sereni, L; Roda, A; Roda, E	1
Bellamy, M; Geddes, D; Thomas, PS	1
Stiehl, A	2
Tanner, MS; Taylor, CJ	1
Poupon, R; Poupon, RE	2
Ghory, MJ; Hunter, GC; Rappaport, W; Shen, GK; Tsen, AC	1
Angelico, M; Antonelli, M; Bertasi, S; De Santis, A; Diamanti, S; Goffredo, F; Martino, F; Merli, M; Quattrucci, S; Servi, R	1
Lindblad, A; Strandvik, B	1
van Berge-Henegouwen, GP; Van de Meeberg, PC; van Erpecum, KJ	1
Luketic, VA; Sanyal, AJ	1
Cirillo, NW; Zwas, FR	1
Apostolo, MG; Bettinardi, N; Colombo, C; Crosignani, A; Giunta, A; Marzano, MT	1
Anagnostopoulos, C; Feigelson, J; Munck, A; Navarro, J; Pecau, Y; Poquet, M	1
Lacaille, F	1
Bowler, IM; Irving, HC; Littlewood, JM; O'Connor, PJ; Robinson, PJ; Southern, KW	1
Battezzati, PM; Bettinardi, N; Colombo, C; Giunta, A; Podda, M	1
Burke, AF; Campbell, GR; FitzGerald, MX; Hegarty, JE; Maguire, OC; O'Brien, SM; Rowlands, BJ	1
Champagne, J; Lacaille, F; Lenaerts, C; Lepage, G; Paradis, K; Rasquin-Weber, A; Ronco, N; Roy, CC; Sénéchal, L	1
Bijleveld, CM; Heijerman, HG; Houwen, RH; Sinaasappel, M; van de Meeberg, PC; Vanberge-Henegouwen, GP	1
Ashby, D; Cheng, K; Smyth, R	2
Bishop, WP; McCray, PB; Scher, H	1
Glaumann, H; Lindblad, A; Strandvik, B	1
Battezzati, PM; Colombo, C; Podda, M; Strazzabosco, M	1
Berenguer Lapuerta, J; Pérez-Aguilar, F	1
Battezzati, PM; Castellani, MR; Colombo, C; Comi, S; Crosignani, A; Giunta, A; Melzi, ML	1
Kowdley, KV	1
Economou, H; Fotoulaki, M; Galli-Tsinopoulou, A; Nousia-Arvanitakis, S; Xefteri, M	1
Beno, DW; Jiyamapa-Serna, VA; Kimura, RE; Lloyd-Still, JD; Uhing, MR	1
Chapman, J; Hardcastle, J; Hardcastle, PT; Taylor, CJ	1
Gatzen, M; Pausch, J	1
Chazalette, JP; Figarella, C; Galabert, C; Lecuire, A; Lengrand, D; Montet, JC; Sotta, C	1
Assaisso, M; Battezzati, PM; Colombo, C; Crosignani, A; Giunta, A; Podda, M; Setchell, KD; Zimmer-Nechemias, L	1
Apostolo, MG; Assaisso, M; Bottani, P; Colombo, C; Roman, B	1
Lerner, A; Rivlin, J	1
Assaisso, ML; Balistreri, WF; Castellani, MR; Colombo, C; Giunta, A; Seregni, E	1
Tanner, MS	1
Chazalette, JP; Dimier, JL; Galabert, C; Lengrand, D; Montet, JC	1
Montet, JC	1
Borum, M; Fromm, H; Malet, PF	1
Riely, CA	1
Assaisso, M; Battezzati, PM; Colombo, C; Crosignani, A; Giunta, A; Ronchi, M	1
Cotting, J; Lentze, MJ; Reichen, J	1
Colombo, C; Nakagawa, M; Setchell, KD	1
Colombo, C; Crosignani, A; Curcio, L; Giunta, A; Podda, M; Roda, A; Ronchi, M; Setchell, KD	1
Bilton, D; Sahl, B; Webb, AK	1
Howat, J; Salh, B; Webb, K	1

Reviews

29 review(s) available for ursodeoxycholic acid and Cystic Fibrosis

Article	Year
Cystic fibrosis-associated liver disease in children. Minerva pediatrica, 2020, Volume: 72, Issue:5 Topics: Adolescent; Adult; Age Factors; Alleles; alpha 1-Antitrypsin; Cause of Death; Child; Child, Preschool; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Esophageal and Gastric Varices; Female; Hepatomegaly; Homozygote; Humans; Hypertension, Portal; Liver; Male; Mutation; Prevalence; Primary Prevention; Sex Factors; Splenomegaly; Ursodeoxycholic Acid; Young Adult	2020
Current Treatment Options for Cystic Fibrosis-Related Liver Disease. International journal of molecular sciences, 2020, Nov-14, Volume: 21, Issue:22 Topics: Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Humans; Liver Diseases; Ursodeoxycholic Acid	2020
Diagnosis, follow-up and treatment of cystic fibrosis-related liver disease. Current opinion in pulmonary medicine, 2017, Volume: 23, Issue:6 Topics: Aftercare; Aminophenols; Aminopyridines; Benzodioxoles; Chloride Channel Agonists; Cholagogues and Choleretics; Cystic Fibrosis; Drug Combinations; Elasticity Imaging Techniques; Humans; Liver Diseases; Liver Transplantation; Quinolones; Ursodeoxycholic Acid	2017
Ursodeoxycholic acid for cystic fibrosis-related liver disease. The Cochrane database of systematic reviews, 2017, 09-11, Volume: 9 Topics: Adolescent; Adult; Bile; Child; Child, Preschool; Cholagogues and Choleretics; Chronic Disease; Cystic Fibrosis; Humans; Liver; Liver Diseases; Nutritional Status; Randomized Controlled Trials as Topic; Ursodeoxycholic Acid	2017
Hepatic Manifestations of Cystic Fibrosis. Clinics in liver disease, 2019, Volume: 23, Issue:2 Topics: Cholagogues and Choleretics; Cystic Fibrosis; Diagnosis, Differential; Humans; Hypertension, Portal; Liver Diseases; Liver Transplantation; Ursodeoxycholic Acid	2019
Cystic Fibrosis-Associated Liver Disease in Lung Transplant Recipients. Liver transplantation : official publication of the American Association for the Study of Liver Diseases and the International Liver Transplantation Society, 2019, Volume: 25, Issue:8 Topics: Aminophenols; Aminopyridines; Benzodioxoles; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Drug Combinations; Humans; Incidence; Liver Cirrhosis; Liver Transplantation; Lung Transplantation; Mutation; Postoperative Care; Quinolones; Survival Rate; Transplant Recipients; Treatment Outcome; Ursodeoxycholic Acid	2019
The liver in pediatric gastrointestinal disease. Journal of pediatric gastroenterology and nutrition, 2014, Volume: 59, Issue:3 Topics: Adolescent; Antibodies, Monoclonal; Azathioprine; Celiac Disease; Chemical and Drug Induced Liver Injury; Child; Child, Preschool; Cholagogues and Choleretics; Cholangitis, Sclerosing; Cystic Fibrosis; Humans; Infant; Inflammatory Bowel Diseases; Infliximab; Liver Diseases; Liver Function Tests; Mercaptopurine; Methotrexate; Tumor Necrosis Factor-alpha; Ursodeoxycholic Acid	2014
Ursodeoxycholic acid for cystic fibrosis-related liver disease. The Cochrane database of systematic reviews, 2014, Dec-15, Issue:12 Topics: Adolescent; Adult; Bile; Child; Child, Preschool; Cholagogues and Choleretics; Chronic Disease; Cystic Fibrosis; Humans; Liver; Liver Diseases; Randomized Controlled Trials as Topic; Ursodeoxycholic Acid	2014
Cystic fibrosis-associated liver disease. Best practice & research. Clinical gastroenterology, 2010, Volume: 24, Issue:5 Topics: Animals; Cholagogues and Choleretics; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Humans; Liver Cirrhosis; Liver Diseases; Liver Transplantation; Portasystemic Shunt, Transjugular Intrahepatic; Ursodeoxycholic Acid	2010
Ursodeoxycholic acid for cystic fibrosis-related liver disease. The Cochrane database of systematic reviews, 2012, Oct-17, Volume: 10 Topics: Cholagogues and Choleretics; Chronic Disease; Cystic Fibrosis; Humans; Liver Diseases; Randomized Controlled Trials as Topic; Ursodeoxycholic Acid	2012
Liver disease in cystic fibrosis. Archives of disease in childhood, 1995, Volume: 72, Issue:4 Topics: Adolescent; Adult; Bile Duct Diseases; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Disease Susceptibility; Genetic Therapy; Humans; Liver Diseases; Membrane Proteins; Ursodeoxycholic Acid	1995
Ursodeoxycholic acid therapy of chronic cholestatic conditions in adults and children. Pharmacology & therapeutics, 1995, Volume: 66, Issue:1 Topics: Adult; Bile Acids and Salts; Child; Cholestasis; Clinical Trials as Topic; Cystic Fibrosis; Female; Humans; Intestinal Absorption; Liver; Pregnancy; Pregnancy Complications; Ursodeoxycholic Acid	1995
Cystic fibrosis. Is treatment with ursodeoxycholic acid of value? Scandinavian journal of gastroenterology. Supplement, 1994, Volume: 204 Topics: Animals; Clinical Trials as Topic; Cystic Fibrosis; Gallbladder Diseases; Humans; Liver Diseases; Liver Function Tests; Ursodeoxycholic Acid	1994
Therapy with ursodeoxycholic acid in cholestatic liver disease. Scandinavian journal of gastroenterology. Supplement, 1993, Volume: 200 Topics: Cholangitis, Sclerosing; Cholestasis; Cholestasis, Intrahepatic; Cystic Fibrosis; Female; Humans; Liver Cirrhosis, Biliary; Liver Diseases; Liver Transplantation; Postoperative Care; Pregnancy; Pregnancy Complications; Recurrence; Ursodeoxycholic Acid	1993
The current status of ursodeoxycholate in the treatment of chronic cholestatic liver disease. The Gastroenterologist, 1994, Volume: 2, Issue:1 Topics: Alagille Syndrome; Biliary Atresia; Cholangitis, Sclerosing; Cholestasis; Chronic Disease; Cystic Fibrosis; Graft vs Host Disease; Humans; Liver Cirrhosis, Biliary; Liver Diseases; Ursodeoxycholic Acid	1994
Ursodeoxycholic acid in the treatment of chronic liver disease. The American journal of gastroenterology, 1994, Volume: 89, Issue:9 Topics: Chronic Disease; Clinical Trials as Topic; Cystic Fibrosis; Hepatitis, Chronic; Humans; Liver Diseases; Randomized Controlled Trials as Topic; Ursodeoxycholic Acid	1994
Oral bile acids in cystic fibrosis-associated liver disease. Journal of the Royal Society of Medicine, 1994, Volume: 87 Suppl 21 Topics: Administration, Oral; Clinical Trials as Topic; Cystic Fibrosis; Dose-Response Relationship, Drug; Follow-Up Studies; Humans; Liver Diseases; Pilot Projects; Randomized Controlled Trials as Topic; Ursodeoxycholic Acid	1994
[Bile acids and their therapeutic use in children]. Archives de pediatrie : organe officiel de la Societe francaise de pediatrie, 1995, Volume: 2, Issue:12 Topics: Adult; Animals; Bile Acids and Salts; Cell Membrane; Child; Cholagogues and Choleretics; Cholestasis; Chronic Disease; Cystic Fibrosis; Humans; Immunosuppressive Agents; Ursodeoxycholic Acid	1995
Ursodeoxycholic acid in cystic fibrosis-related liver disease: a systematic review. Journal of the Royal Society of Medicine, 1997, Volume: 90 Suppl 31 Topics: Cholagogues and Choleretics; Cystic Fibrosis; Humans; Liver Diseases; Randomized Controlled Trials as Topic; Treatment Outcome; Ursodeoxycholic Acid	1997
Liver and biliary problems in cystic fibrosis. Seminars in liver disease, 1998, Volume: 18, Issue:3 Topics: Child; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Diagnosis, Differential; Humans; Liver; Liver Diseases; Prognosis; Ursodeoxycholic Acid	1998
[Hepatobiliary disease in cystic fibrosis]. Medicina clinica, 1998, Sep-19, Volume: 111, Issue:8 Topics: Bile Duct Diseases; Biomarkers; Cholagogues and Choleretics; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Humans; Liver Diseases; Ursodeoxycholic Acid	1998
Ursodeoxycholic acid therapy in hepatobiliary disease. The American journal of medicine, 2000, Apr-15, Volume: 108, Issue:6 Topics: Biliary Tract Diseases; Bone Marrow Transplantation; Cholagogues and Choleretics; Cholangitis, Sclerosing; Cholestasis; Chronic Disease; Cystic Fibrosis; Female; Graft Rejection; Graft vs Host Disease; Humans; Liver Cirrhosis, Biliary; Liver Diseases; Liver Transplantation; Parenteral Nutrition, Total; Pregnancy; Pregnancy Complications; Ursodeoxycholic Acid	2000
Ursodeoxycholic acid for cystic fibrosis-related liver disease. The Cochrane database of systematic reviews, 2000, Issue:2 Topics: Cholagogues and Choleretics; Cystic Fibrosis; Humans; Liver Diseases; Ursodeoxycholic Acid	2000
[Treatment of cholestatic liver diseases]. Medizinische Klinik (Munich, Germany : 1983), 2002, Mar-15, Volume: 97, Issue:3 Topics: Adult; Age Factors; Anti-Inflammatory Agents; Azathioprine; Bile; Child; Cholagogues and Choleretics; Cholangitis, Sclerosing; Cholestasis; Cholestasis, Intrahepatic; Chronic Disease; Controlled Clinical Trials as Topic; Cystic Fibrosis; Drug Therapy, Combination; Female; Hepatitis; Humans; Immunosuppressive Agents; Infant, Newborn; Liver Cirrhosis, Biliary; Male; Prednisolone; Pregnancy; Pregnancy Complications; Time Factors; Ursodeoxycholic Acid	2002
Ursodeoxycholic acid for the treatment of cholestatic diseases. Progress in liver diseases, 1992, Volume: 10 Topics: Adult; Child; Cholangitis, Sclerosing; Cholestasis; Cystic Fibrosis; Female; Humans; Liver Cirrhosis, Alcoholic; Liver Cirrhosis, Biliary; Liver Transplantation; Pregnancy; Pregnancy Complications; Ursodeoxycholic Acid	1992
Liver disease in cystic fibrosis. The Netherlands journal of medicine, 1992, Volume: 41, Issue:3-4 Topics: Cystic Fibrosis; Humans; Liver Diseases; Ursodeoxycholic Acid	1992
[New aspects of cystic fibrosis liver disease]. Harefuah, 1992, May-01, Volume: 122, Issue:9 Topics: Adolescent; Cystic Fibrosis; Humans; Liver Diseases; Male; Ursodeoxycholic Acid	1992
[Therapy of cholestatic liver diseases with ursodeoxycholic acid: a new treatment principle]. Zeitschrift fur Gastroenterologie. Verhandlungsband, 1991, Volume: 26 Topics: Adult; Child; Cholangitis, Sclerosing; Cystic Fibrosis; Humans; Liver Cirrhosis, Biliary; Liver Function Tests; Ursodeoxycholic Acid	1991
[Ursodeoxycholic acid. Physical properties and hepatoprotective activity]. Pathologie-biologie, 1991, Volume: 39, Issue:6 Topics: Animals; Bile Acids and Salts; Chemical Phenomena; Chemistry, Physical; Cholestasis; Cystic Fibrosis; Humans; Rats; Ursodeoxycholic Acid	1991

Trials

9 trial(s) available for ursodeoxycholic acid and Cystic Fibrosis

Article	Year
The benign course of liver disease in adults with cystic fibrosis and the effect of ursodeoxycholic acid. Liver international : official journal of the International Association for the Study of the Liver, 2007, Volume: 27, Issue:10 Topics: Adolescent; Adult; Child; Cholagogues and Choleretics; Cystic Fibrosis; Disease Progression; Female; Follow-Up Studies; Humans; Hypertension, Portal; Liver Diseases; Liver Function Tests; Male; Middle Aged; Severity of Illness Index; Treatment Outcome; Ursodeoxycholic Acid	2007
Malabsorption of vitamin E in cystic fibrosis improved after ursodeoxycholic acid. Lancet (London, England), 1995, Nov-04, Volume: 346, Issue:8984 Topics: Adult; Cystic Fibrosis; Gastrointestinal Agents; Humans; Intestinal Absorption; Malabsorption Syndromes; Male; Ursodeoxycholic Acid; Vitamin E	1995
Effect of a medium dose of ursodeoxycholic acid with or without taurine supplementation on the nutritional status of patients with cystic fibrosis: a randomized, placebo-controlled, crossover trial. Journal of pediatric gastroenterology and nutrition, 1994, Volume: 19, Issue:2 Topics: Absorption; Adolescent; Adult; Bile Acids and Salts; Child; Cross-Over Studies; Cystic Fibrosis; Dietary Fats; Female; Humans; Liver Diseases; Male; Nutritional Status; Placebos; Prospective Studies; Taurine; Ursodeoxycholic Acid	1994
Ursodeoxycholic acid for liver disease associated with cystic fibrosis: a double-blind multicenter trial. The Italian Group for the Study of Ursodeoxycholic Acid in Cystic Fibrosis. Hepatology (Baltimore, Md.), 1996, Volume: 23, Issue:6 Topics: 5'-Nucleotidase; Adolescent; Adult; Child; Child, Preschool; Cystic Fibrosis; Double-Blind Method; Drug Therapy, Combination; Female; gamma-Glutamyltransferase; Gastrointestinal Agents; Humans; Liver Diseases; Male; Nutritional Status; Prealbumin; Taurine; Ursodeoxycholic Acid	1996
Serum bile acids and ursodeoxycholic acid treatment in cystic fibrosis-related liver disease. European journal of gastroenterology & hepatology, 1996, Volume: 8, Issue:5 Topics: Adolescent; Adult; Bile Acids and Salts; Cholagogues and Choleretics; Cystic Fibrosis; Female; Humans; Liver Diseases; Male; Ursodeoxycholic Acid	1996
Ursodeoxycholic acid improves the hepatic metabolism of essential fatty acids and retinol in children with cystic fibrosis. The Journal of pediatrics, 1997, Volume: 130, Issue:1 Topics: Adolescent; Child; Cholagogues and Choleretics; Cross-Over Studies; Cystic Fibrosis; Double-Blind Method; Fatty Acids, Essential; Female; Humans; Lipid Metabolism; Liver; Liver Function Tests; Male; Ursodeoxycholic Acid; Vitamin A; Vitamins	1997
Low-dose versus high-dose ursodeoxycholic acid in cystic fibrosis-related cholestatic liver disease. Results of a randomized study with 1-year follow-up. Scandinavian journal of gastroenterology, 1997, Volume: 32, Issue:4 Topics: Adolescent; Adult; Child; Cholagogues and Choleretics; Cholestasis, Intrahepatic; Clinical Enzyme Tests; Cystic Fibrosis; Female; Follow-Up Studies; Humans; Male; Time Factors; Ursodeoxycholic Acid	1997
A two-year prospective study of the effect of ursodeoxycholic acid on urinary bile acid excretion and liver morphology in cystic fibrosis-associated liver disease. Hepatology (Baltimore, Md.), 1998, Volume: 27, Issue:1 Topics: Adolescent; Adult; Bile Acids and Salts; Child; Cystic Fibrosis; Female; Gas Chromatography-Mass Spectrometry; Humans; Liver; Liver Diseases; Liver Function Tests; Male; Prospective Studies; Spectrometry, Mass, Fast Atom Bombardment; Treatment Outcome; Ursodeoxycholic Acid	1998
Ursodeoxycholic acid therapy in cystic fibrosis-associated liver disease: a dose-response study. Hepatology (Baltimore, Md.), 1992, Volume: 16, Issue:4 Topics: Bile Acids and Salts; Cystic Fibrosis; Dose-Response Relationship, Drug; Duodenum; Enzymes; Humans; Liver; Liver Diseases; Ursodeoxycholic Acid	1992

Other Studies

36 other study(ies) available for ursodeoxycholic acid and Cystic Fibrosis

Article	Year
Ursodeoxycholic acid and liver disease associated with cystic fibrosis: A multicenter cohort study. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2022, Volume: 21, Issue:2 Topics: Cholagogues and Choleretics; Cohort Studies; Cystic Fibrosis; Humans; Hypertension, Portal; Retrospective Studies; Ursodeoxycholic Acid; Young Adult	2022
Advancements in nano drug delivery systems: a challenge for biofilms in respiratory diseases. Panminerva medica, 2018, Volume: 60, Issue:1 Topics: Anti-Infective Agents; Bacterial Adhesion; Biofilms; Cystic Fibrosis; Deoxycholic Acid; Drug Delivery Systems; Escherichia coli; Humans; Methicillin-Resistant Staphylococcus aureus; Nanomedicine; Pseudomonas aeruginosa; Pulmonary Disease, Chronic Obstructive; Staphylococcus aureus; Ursodeoxycholic Acid	2018
Pancreatic Cystosis and Intrahepatic Biliopathy in a Young Adult with Cystic Fibrosis. The Journal of pediatrics, 2018, Volume: 203 Topics: Abdominal Pain; Adolescent; Biopsy; Cholagogues and Choleretics; Cholangiopancreatography, Magnetic Resonance; Cholangitis, Sclerosing; Constipation; Contraceptives, Oral; Cystic Fibrosis; Female; Humans; Jaundice; Liver; Liver Diseases; Lung Diseases; Ovarian Cysts; Pancreas; Pancreatic Cyst; Pruritus; Radiography, Abdominal; Tomography, X-Ray Computed; Ursodeoxycholic Acid; Weight Loss	2018
Cystic Fibrosis Liver Disease: Outcomes and Risk Factors in a Large Cohort of French Patients. Hepatology (Baltimore, Md.), 2019, Volume: 69, Issue:4 Topics: Adolescent; Child; Cystic Fibrosis; Female; France; Humans; Incidence; Liver Diseases; Male; Retrospective Studies; Risk Factors; Ursodeoxycholic Acid; Young Adult	2019
Baseline Ultrasound and Clinical Correlates in Children with Cystic Fibrosis. The Journal of pediatrics, 2015, Volume: 167, Issue:4 Topics: Analysis of Variance; Body Mass Index; Child; Child, Preschool; Cystic Fibrosis; Female; Humans; Liver Cirrhosis; Male; Nutritional Status; Prospective Studies; Pseudomonas aeruginosa; Pseudomonas Infections; Risk Factors; Ultrasonography; Ursodeoxycholic Acid	2015
Supplementation of ursodeoxycholic acid improves fat digestion and absorption in cystic fibrosis patients with mild liver involvement. European journal of gastroenterology & hepatology, 2016, Volume: 28, Issue:6 Topics: Adolescent; Adult; Breath Tests; Carbon Isotopes; Child; Child, Preschool; Cholagogues and Choleretics; Cystic Fibrosis; Dietary Fats; Dietary Supplements; Female; Humans; Liver Diseases; Male; Triglycerides; Ursodeoxycholic Acid; Young Adult	2016
Long-Term Ursodeoxycholic Acid Therapy Does Not Alter Lithocholic Acid Levels in Patients with Cystic Fibrosis with Associated Liver Disease. The Journal of pediatrics, 2016, Volume: 177 Topics: Adolescent; Adult; Bile Acids and Salts; Biotransformation; Child; Child, Preschool; Cystic Fibrosis; Deoxycholic Acid; Female; Humans; Lithocholic Acid; Liver Diseases; Male; Tandem Mass Spectrometry; Ursodeoxycholic Acid; Young Adult	2016
Cystic Fibrosis Liver Disease and Ursodeoxycholic Acid: One Small Step Forward, Miles to Go. The Journal of pediatrics, 2016, Volume: 177 Topics: Bile Acids and Salts; Cystic Fibrosis; Humans; Liver; Liver Diseases; Ursodeoxycholic Acid	2016
Ursodeoxycholic acid treatment is associated with improvement of liver stiffness in cystic fibrosis patients. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2016, Volume: 15, Issue:6 Topics: Adolescent; Child; Cholagogues and Choleretics; Cystic Fibrosis; Drug Monitoring; Elasticity Imaging Techniques; Female; Humans; Liver; Liver Cirrhosis; Liver Function Tests; Male; Netherlands; Treatment Outcome; Ultrasonography; Ursodeoxycholic Acid	2016
Ursodeoxycholic acid treatment in patients with cystic fibrosis at risk for liver disease. Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver, 2010, Volume: 42, Issue:6 Topics: Child; Child, Preschool; Cholagogues and Choleretics; Chronic Disease; Cystic Fibrosis; Dose-Response Relationship, Drug; Female; Follow-Up Studies; Humans; Infant; Italy; Liver Diseases; Male; Morbidity; Retrospective Studies; Survival Rate; Treatment Outcome; Ursodeoxycholic Acid	2010
Ursodeoxycholate modulates bile flow and bile salt pool independently from the cystic fibrosis transmembrane regulator (Cftr) in mice. American journal of physiology. Gastrointestinal and liver physiology, 2012, May-01, Volume: 302, Issue:9 Topics: Animals; Bile; Bile Acids and Salts; Cholagogues and Choleretics; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Liver; Mice; Mice, Inbred C57BL; Mice, Knockout; Treatment Outcome; Ursodeoxycholic Acid	2012
Ursodeoxycholic acid therapy in cystic fibrosis liver disease--a retrospective long-term follow-up case-control study. Alimentary pharmacology & therapeutics, 2012, Volume: 36, Issue:3 Topics: Adolescent; Adult; Case-Control Studies; Chemical and Drug Induced Liver Injury; Child; Child, Preschool; Cholagogues and Choleretics; Cystic Fibrosis; Female; Humans; Infant; Liver Function Tests; Longitudinal Studies; Male; Retrospective Studies; Ursodeoxycholic Acid; Young Adult	2012
Endogenous ursodeoxycholic acid and cholic acid in liver disease due to cystic fibrosis. Hepatology (Baltimore, Md.), 2004, Volume: 39, Issue:6 Topics: Adolescent; Bile Acids and Salts; Child; Child, Preschool; Cholic Acid; Cystic Fibrosis; Female; Humans; Infant; Liver Diseases; Male; Predictive Value of Tests; Prognosis; Ursodeoxycholic Acid	2004
A single centre experience of liver disease in adults with cystic fibrosis 1995-2006. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2008, Volume: 7, Issue:3 Topics: Adult; Cholagogues and Choleretics; Comorbidity; Cystic Fibrosis; Female; Humans; Hypertension, Portal; Liver Cirrhosis; Liver Diseases; Liver Transplantation; Male; Platelet Count; Prospective Studies; Splenomegaly; Thrombocytopenia; Ursodeoxycholic Acid	2008
Evaluation of an oral ursodeoxycholic acid load in the assessment of bile acid malabsorption in cystic fibrosis. Digestive diseases and sciences, 1983, Volume: 28, Issue:4 Topics: Adolescent; Bile Acids and Salts; Chenodeoxycholic Acid; Child; Child, Preschool; Cholic Acids; Cystic Fibrosis; Deoxycholic Acid; Feces; Female; Humans; Intestinal Absorption; Intestinal Mucosa; Lipid Metabolism; Lipids; Male; Ursodeoxycholic Acid	1983
[Treatment of cholestatic liver diseases with phenobarbital and ursodeoxycholic acid]. Zeitschrift fur Gastroenterologie, 1993, Volume: 31 Suppl 2 Topics: Cholestasis, Intrahepatic; Cystic Fibrosis; Female; Humans; Liver Diseases; Liver Function Tests; Male; Phenobarbital; Pregnancy; Pregnancy Complications; Treatment Outcome; Ursodeoxycholic Acid	1993
Surgical treatment of symptomatic biliary stones in patients with cystic fibrosis. The American surgeon, 1995, Volume: 61, Issue:9 Topics: Adolescent; Adult; Cholangiopancreatography, Endoscopic Retrograde; Cholangitis; Cholecystectomy; Cholecystitis; Cholelithiasis; Cystic Fibrosis; Female; Gallstones; Humans; Male; Ursodeoxycholic Acid	1995
Liver cirrhosis in cystic fibrosis--therapeutic implications and long term follow up. Archives of disease in childhood, 1993, Volume: 68, Issue:5 Topics: Adolescent; Adult; Cause of Death; Child; Cystic Fibrosis; Female; Follow-Up Studies; Heart-Lung Transplantation; Humans; Hypertension, Portal; Liver Cirrhosis; Liver Transplantation; Male; Portacaval Shunt, Surgical; Splenectomy; Time Factors; Treatment Outcome; Ursodeoxycholic Acid	1993
The role of hepatobiliary scintigraphy in cystic fibrosis. Hepatology (Baltimore, Md.), 1996, Volume: 23, Issue:2 Topics: Adolescent; Adult; Biliary Tract; Child; Child, Preschool; Cystic Fibrosis; Female; Follow-Up Studies; Humans; Infant; Liver; Liver Diseases; Male; Prospective Studies; Radionuclide Imaging; Taurine; Ultrasonography; Ursodeoxycholic Acid	1996
Ursodeoxycholic acid improves cholestasis in infants with cystic fibrosis. The Annals of pharmacotherapy, 1997, Volume: 31, Issue:9 Topics: Cholagogues and Choleretics; Cholestasis; Cystic Fibrosis; Female; Humans; Infant, Newborn; Liver Function Tests; Male; Treatment Outcome; Ursodeoxycholic Acid	1997
Delayed intestinal visualization at hepatobiliary scintigraphy is associated with response to long-term treatment with ursodeoxycholic acid in patients with cystic fibrosis-associated liver disease. Journal of hepatology, 1999, Volume: 31, Issue:4 Topics: Adolescent; Adult; Bile Ducts; Child; Child, Preschool; Cholagogues and Choleretics; Cystic Fibrosis; Female; Humans; Intestines; Liver; Liver Diseases; Male; Radionuclide Imaging; Time Factors; Treatment Failure; Ultrasonography; Ursodeoxycholic Acid	1999
Long-term prospective study of the effect of ursodeoxycholic acid on cystic fibrosis-related liver disease. Journal of clinical gastroenterology, 2001, Volume: 32, Issue:4 Topics: Adolescent; Adult; Child; Child, Preschool; Cholagogues and Choleretics; Cystic Fibrosis; Female; Humans; Liver Diseases; Liver Function Tests; Longitudinal Studies; Male; Prospective Studies; Treatment Outcome; Ultrasonography; Ursodeoxycholic Acid	2001
Ursodeoxycholic acid ameliorates ibuprofen-induced enteropathy in the rat. Journal of pediatric gastroenterology and nutrition, 2001, Volume: 32, Issue:3 Topics: Animals; Anti-Inflammatory Agents, Non-Steroidal; Catheterization; Cholagogues and Choleretics; Cystic Fibrosis; Disease Models, Animal; Ibuprofen; Intestinal Diseases; Intestines; Lipase; Male; Random Allocation; Rats; Rats, Sprague-Dawley; Serositis; Ulcer; Ursodeoxycholic Acid	2001
Ursodeoxycholic acid action on the transport function of the small intestine in normal and cystic fibrosis mice. The Journal of pharmacy and pharmacology, 2001, Volume: 53, Issue:11 Topics: Animals; Bile Acids and Salts; Biological Transport; Calcium; Cholagogues and Choleretics; Cystic Fibrosis; Dose-Response Relationship, Drug; In Vitro Techniques; Intestinal Mucosa; Intestine, Small; Male; Mast Cells; Membrane Potentials; Mice; Mice, Inbred Strains; Mice, Transgenic; Ursodeoxycholic Acid	2001
Effects of ursodeoxycholic acid on liver function in patients with cystic fibrosis and chronic cholestasis. The Journal of pediatrics, 1992, Volume: 121, Issue:1 Topics: 5'-Nucleotidase; Adolescent; Adult; Alanine Transaminase; Alkaline Phosphatase; Aspartate Aminotransferases; Bile Acids and Salts; Bilirubin; Child; Cholestasis; Chronic Disease; Cystic Fibrosis; Female; gamma-Glutamyltransferase; Humans; Liver; Male; Ursodeoxycholic Acid	1992
Scintigraphic documentation of an improvement in hepatobiliary excretory function after treatment with ursodeoxycholic acid in patients with cystic fibrosis and associated liver disease. Hepatology (Baltimore, Md.), 1992, Volume: 15, Issue:4 Topics: Adolescent; Bile Ducts; Child; Cystic Fibrosis; Female; Humans; Liver; Liver Diseases; Male; Radionuclide Imaging; Ursodeoxycholic Acid	1992
Liver and biliary problems in cystic fibrosis. Journal of the Royal Society of Medicine, 1992, Volume: 85 Suppl 19 Topics: Adolescent; Adult; Age Factors; Animals; Biliary Tract Diseases; Child; Child, Preschool; Cystic Fibrosis; Female; Humans; Infant; Infant, Newborn; Liver Diseases; Liver Transplantation; Male; Rats; Ursodeoxycholic Acid	1992
[Use of ursodeoxycholic acid in the treatment of hepato-biliary complications in cystic fibrosis]. Pathologie-biologie, 1991, Volume: 39, Issue:6 Topics: Adolescent; Adult; Child; Cholestasis; Cystic Fibrosis; Female; Humans; Liver; Male; Ursodeoxycholic Acid	1991
Cystic fibrosis: another use for urso? Gastroenterology, 1991, Volume: 100, Issue:3 Topics: Adolescent; Adult; Child; Cholestasis; Cystic Fibrosis; Humans; Liver; Nutritional Status; Ursodeoxycholic Acid	1991
Liver dysfunction in cystic fibrosis--beneficial effect of bile acid treatment. Gastroenterology, 1991, Volume: 100, Issue:5 Pt 1 Topics: Bile Acids and Salts; Child; Cholestasis; Cystic Fibrosis; Humans; Liver Function Tests; Taurine; Ursodeoxycholic Acid	1991
Effects of taurine and ursodeoxycholic acid on liver function tests in patients with cystic fibrosis. Acta Universitatis Carolinae. Medica, 1990, Volume: 36, Issue:1-4 Topics: Bile Acids and Salts; Child; Cystic Fibrosis; Female; Humans; Liver Function Tests; Male; Taurine; Ursodeoxycholic Acid	1990
Effects of ursodeoxycholic acid treatment on nutrition and liver function in patients with cystic fibrosis and longstanding cholestasis. Gut, 1990, Volume: 31, Issue:8 Topics: Adolescent; Adult; Child; Cholestasis; Chronic Disease; Cystic Fibrosis; Deoxycholic Acid; Female; Humans; Liver; Liver Function Tests; Male; Nutritional Status; Prospective Studies; Ursodeoxycholic Acid	1990
Comprehensive study of the biliary bile acid composition of patients with cystic fibrosis and associated liver disease before and after UDCA administration. Hepatology (Baltimore, Md.), 1990, Volume: 12, Issue:2 Topics: Adolescent; Bile Acids and Salts; Child; Chromatography, High Pressure Liquid; Cystic Fibrosis; Deoxycholic Acid; Female; Gas Chromatography-Mass Spectrometry; Humans; Liver Diseases; Male; Mass Spectrometry; Ursodeoxycholic Acid	1990
Effects of ursodeoxycholic acid therapy for liver disease associated with cystic fibrosis. The Journal of pediatrics, 1990, Volume: 117, Issue:3 Topics: Adolescent; Bile Acids and Salts; Child; Cystic Fibrosis; Deoxycholic Acid; Female; Humans; Liver Diseases; Liver Function Tests; Male; Taurine; Ursodeoxycholic Acid	1990
Cholecystectomy as the treatment of choice in cystic fibrosis. American journal of surgery, 1990, Volume: 160, Issue:3 Topics: Cholecystitis; Cystic Fibrosis; Deoxycholic Acid; Humans; Ursodeoxycholic Acid	1990
Ursodeoxycholic acid dissolution of gallstones in cystic fibrosis. Thorax, 1988, Volume: 43, Issue:6 Topics: Adult; Cholecystography; Cholelithiasis; Cystic Fibrosis; Deoxycholic Acid; Female; Humans; Male; Ursodeoxycholic Acid	1988