Page last updated: 2024-10-21

urea and Pachyonychia Congenita

urea has been researched along with Pachyonychia Congenita in 1 studies

pseudourea: clinical use; structure
isourea : A carboximidic acid that is the imidic acid tautomer of urea, H2NC(=NH)OH, and its hydrocarbyl derivatives.

Pachyonychia Congenita: A group of inherited ectodermal dysplasias whose most prominent clinical feature is hypertrophic nail dystrophy resulting in PACHYONYCHIA. Several specific subtypes of pachyonychia congenita have been associated with mutations in genes that encode KERATINS.

Research Excerpts

ExcerptRelevanceReference
"Pachyonychia congenita is a rare genetic disorder characterized mainly by hypertrophy of the nails and hyperkeratosis of the skin and mucosae."1.36Oral manifestations of pachyonychia congenita. ( da Silva Santos, PS; Lellis, RF; Mannarino, F; Osório, LH, 2010)

Research

Studies (1)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's1 (100.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
da Silva Santos, PS1
Mannarino, F1
Lellis, RF1
Osório, LH1

Other Studies

1 other study available for urea and Pachyonychia Congenita

ArticleYear
Oral manifestations of pachyonychia congenita.
    Dermatology online journal, 2010, Oct-15, Volume: 16, Issue:10

    Topics: Adult; Anti-Inflammatory Agents; Dexamethasone; Female; Humans; Leukoplakia, Oral; Malocclusion; Mou

2010