tyrosine has been researched along with Cerebral Pseudosclerosis in 17 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 11 (64.71) | 18.7374 |
1990's | 5 (29.41) | 18.2507 |
2000's | 1 (5.88) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Kurup, PA; Kurup, RK | 1 |
Groth, CG; Ringdén, O | 1 |
Katz, AJ | 1 |
Thiel, HJ; Weidle, E | 1 |
Rabinowitz, JG | 1 |
Perlmutter, DH; Teckman, J | 1 |
Honnda, K; Inamoto, T; Tanaka, K; Tokunaga, Y; Uemoto, S; Yamaoka, Y | 1 |
Kumada, S; Okaniwa, M | 1 |
Kohgo, Y; Ono, M | 1 |
Möhler, M; Stremmel, W; Wagner, V | 1 |
Dimmick, JE; Hardwick, DF | 1 |
Deze, J; Völler, GW | 1 |
Mowat, AP | 1 |
Mowat, A | 1 |
Berggård, I; Evrin, PE; Peterson, PA | 1 |
Davidson, M; Silverberg, M | 1 |
7 review(s) available for tyrosine and Cerebral Pseudosclerosis
Article | Year |
---|---|
Transplantation in relation to the treatment of inherited disease.
Topics: alpha 1-Antitrypsin Deficiency; Amyloidosis; Bone Marrow Transplantation; Fabry Disease; Gaucher Disease; Genetic Diseases, Inborn; Gout; Granulomatous Disease, Chronic; Hemoglobinopathies; Hemophilia A; Hepatolenticular Degeneration; Humans; Immunologic Deficiency Syndromes; Kidney Transplantation; Leukodystrophy, Metachromatic; Liver Transplantation; Lymphocytes; Metabolism, Inborn Errors; Mucopolysaccharidoses; Nephritis, Hereditary; Niemann-Pick Diseases; Osteopetrosis; Oxalates; Oxalic Acid; Transplantation; Tyrosine; Uremia | 1984 |
Conceptual advances in the pathogenesis and treatment of childhood metabolic liver disease.
Topics: alpha 1-Antitrypsin Deficiency; Child; Gaucher Disease; Hepatolenticular Degeneration; Humans; Liver Diseases; Metabolism, Inborn Errors; Tyrosine | 1995 |
[Progressive neuronal degeneration and childhood cirrhosis].
Topics: Galactosemias; Glycogen Storage Disease Type IV; Hepatolenticular Degeneration; Humans; Infant; Liver Cirrhosis; Metabolism, Inborn Errors; Peripheral Nervous System Diseases; Tyrosine | 1995 |
[Liver cirrhosis associated with metabolic disorders].
Topics: alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Galactosemias; Glycogen Storage Disease; Hemochromatosis; Hepatolenticular Degeneration; Humans; Liver Cirrhosis; Metabolism, Inborn Errors; Tyrosine | 1995 |
[Hereditary liver diseases. Recent molecular genetic aspects].
Topics: alpha 1-Antitrypsin; Animals; Bilirubin; Cholestasis, Intrahepatic; Cystic Fibrosis; Disease Models, Animal; Genetic Therapy; Hepatolenticular Degeneration; Humans; Jaundice, Chronic Idiopathic; Liver Diseases; Metabolism, Inborn Errors; Molecular Biology; Tyrosine | 1998 |
Metabolic cirrhoses of infancy and early childhood.
Topics: Amino Acid Metabolism, Inborn Errors; Cystic Fibrosis; Cystinosis; Fructose Intolerance; Galactosemias; Genetics, Medical; Glycogen Storage Disease Type IV; Hepatolenticular Degeneration; Humans; Iatrogenic Disease; Infant; Infant, Newborn; Lipid Metabolism, Inborn Errors; Liver; Liver Cirrhosis; Metabolism, Inborn Errors; Mucopolysaccharidoses; Niemann-Pick Diseases; Polycystic Kidney Diseases; Tyrosine | 1976 |
[Basis, clinical picture and therapy of diseases of the extrapyramidal-motoric system (EPMS)].
Topics: Acetylcholine; Athetosis; Basal Ganglia Diseases; Catecholamines; Chorea; Dopamine; Dystonia Musculorum Deformans; Hepatolenticular Degeneration; Humans; Hyperkinesis; Myoclonus; Parkinson Disease; Tremor; Tyrosine | 1975 |
1 trial(s) available for tyrosine and Cerebral Pseudosclerosis
Article | Year |
---|---|
Hypothalamic digoxin and isoprenoid pathway dysfunction relation to alcoholic addiction, alcoholic cirrhosis, and acquired hepatocerebral degeneration--relation to hemispheric chemical dominance.
Topics: Adult; Alcoholism; Analysis of Variance; Cholesterol; Digoxin; Disease Susceptibility; Dolichols; Dominance, Cerebral; Enzyme Inhibitors; Erythrocytes; Female; Glycoconjugates; Glycosaminoglycans; Hepatolenticular Degeneration; Humans; Hydroxymethylglutaryl CoA Reductases; Hypothalamus; Liver Cirrhosis, Alcoholic; Male; Membrane Proteins; Neurotransmitter Agents; Polyisoprenyl Phosphates; Sodium-Potassium-Exchanging ATPase; Tryptophan; Tyrosine; Ubiquinone | 2003 |
9 other study(ies) available for tyrosine and Cerebral Pseudosclerosis
Article | Year |
---|---|
Diagnostic procedures in the evaluation of hepatic diseases. Metabolic errors.
Topics: Adolescent; Adult; alpha 1-Antitrypsin Deficiency; Child; Fructose Intolerance; Galactosemias; Hepatolenticular Degeneration; Humans; Infant, Newborn; Liver Diseases; Metabolism, Inborn Errors; Phenotype; Tyrosine | 1983 |
[Tyrosinosis with hepatolenticular degeneration (Wilson's disease)].
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Corneal Diseases; Hepatolenticular Degeneration; Humans; Male; Tyrosine | 1983 |
Abnormalities of the liver and other organs.
Topics: Abnormalities, Multiple; alpha 1-Antitrypsin Deficiency; Amino Acid Metabolism, Inborn Errors; Colitis; Colon; Cystinosis; Heart Failure; Hemochromatosis; Hepatolenticular Degeneration; Humans; Liver; Liver Diseases; Necrosis; Radiography; Sclerosis; Tyrosine | 1980 |
Living-related liver transplantation for inborn errors of metabolism.
Topics: Adolescent; Adult; Child; Child, Preschool; Fathers; Female; Glycogen Storage Disease Type IV; Hepatolenticular Degeneration; Humans; Infant; Liver Transplantation; Male; Metabolism, Inborn Errors; Mothers; Porphyria, Hepatoerythropoietic; Survival Rate; Tissue Donors; Tyrosine | 1994 |
Liver disorders in children: the indications for liver replacement in parenchymal and metabolic diseases.
Topics: Amino Acid Metabolism, Inborn Errors; Budd-Chiari Syndrome; Child; Cholangitis; Crigler-Najjar Syndrome; Hepatitis, Chronic; Hepatolenticular Degeneration; Humans; Infant; Liver Cirrhosis; Liver Diseases; Liver Transplantation; Porphyrias; Tyrosine | 1987 |
The management of metabolic disorders of the liver.
Topics: alpha 1-Antitrypsin Deficiency; Child, Preschool; Fructose Intolerance; Galactosemias; Genetic Counseling; Glycogen Storage Disease; Hepatolenticular Degeneration; Humans; Hydrolases; Infant; Infant, Newborn; Liver Diseases; Metabolic Diseases; Phenotype; Prognosis; Tyrosine | 1985 |
Screening for inborn errors of metabolism. Report of a WHO Scientific Group.
Topics: Adrenal Hyperplasia, Congenital; Amino Acid Metabolism, Inborn Errors; Carrier State; Ceruloplasmin; Cholinesterases; Cystic Fibrosis; Diagnostic Services; Female; Galactosemias; Genetic Diseases, Inborn; Hepatolenticular Degeneration; Humans; Infant; Infant, Newborn; Male; Maple Syrup Urine Disease; Metabolism, Inborn Errors; Phenylketonurias; Porphyrias; Tyrosine; World Health Organization | 1968 |
Differentiation of glomerular, tubular, and normal proteinuria: determinations of urinary excretion of beta-2-macroglobulin, albumin, and total protein.
Topics: Acidosis, Renal Tubular; Albuminuria; Amino Acid Metabolism, Inborn Errors; Cadmium Poisoning; Creatinine; Cystinosis; Diagnosis, Differential; Female; Glomerulonephritis; Hepatolenticular Degeneration; Humans; Immune Sera; Immunodiffusion; Kidney Glomerulus; Kidney Tubules; Laurence-Moon Syndrome; Male; Molecular Weight; Nephritis, Hereditary; Nephrotic Syndrome; Proteinuria; Serum Globulins; Tyrosine | 1969 |
Nutritional requirements of infants and children with liver disease.
Topics: Adolescent; Bile; Body Weight; Carbohydrate Metabolism, Inborn Errors; Child; Child, Preschool; Cystic Fibrosis; Female; Galactosemias; Glycogen; Hepatitis A; Hepatolenticular Degeneration; Humans; India; Infant; Infant Nutritional Physiological Phenomena; Liver Diseases; Male; Tyrosine | 1970 |