tyrosine and Cerebral Pseudosclerosis

tyrosine has been researched along with Cerebral Pseudosclerosis in 17 studies

Research

Studies (17)

TimeframeStudies, this research(%)All Research%
pre-199011 (64.71)18.7374
1990's5 (29.41)18.2507
2000's1 (5.88)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Kurup, PA; Kurup, RK1
Groth, CG; Ringdén, O1
Katz, AJ1
Thiel, HJ; Weidle, E1
Rabinowitz, JG1
Perlmutter, DH; Teckman, J1
Honnda, K; Inamoto, T; Tanaka, K; Tokunaga, Y; Uemoto, S; Yamaoka, Y1
Kumada, S; Okaniwa, M1
Kohgo, Y; Ono, M1
Möhler, M; Stremmel, W; Wagner, V1
Dimmick, JE; Hardwick, DF1
Deze, J; Völler, GW1
Mowat, AP1
Mowat, A1
Berggård, I; Evrin, PE; Peterson, PA1
Davidson, M; Silverberg, M1

Reviews

7 review(s) available for tyrosine and Cerebral Pseudosclerosis

ArticleYear
Transplantation in relation to the treatment of inherited disease.
    Transplantation, 1984, Volume: 38, Issue:4

    Topics: alpha 1-Antitrypsin Deficiency; Amyloidosis; Bone Marrow Transplantation; Fabry Disease; Gaucher Disease; Genetic Diseases, Inborn; Gout; Granulomatous Disease, Chronic; Hemoglobinopathies; Hemophilia A; Hepatolenticular Degeneration; Humans; Immunologic Deficiency Syndromes; Kidney Transplantation; Leukodystrophy, Metachromatic; Liver Transplantation; Lymphocytes; Metabolism, Inborn Errors; Mucopolysaccharidoses; Nephritis, Hereditary; Niemann-Pick Diseases; Osteopetrosis; Oxalates; Oxalic Acid; Transplantation; Tyrosine; Uremia

1984
Conceptual advances in the pathogenesis and treatment of childhood metabolic liver disease.
    Gastroenterology, 1995, Volume: 108, Issue:4

    Topics: alpha 1-Antitrypsin Deficiency; Child; Gaucher Disease; Hepatolenticular Degeneration; Humans; Liver Diseases; Metabolism, Inborn Errors; Tyrosine

1995
[Progressive neuronal degeneration and childhood cirrhosis].
    Ryoikibetsu shokogun shirizu, 1995, Issue:8

    Topics: Galactosemias; Glycogen Storage Disease Type IV; Hepatolenticular Degeneration; Humans; Infant; Liver Cirrhosis; Metabolism, Inborn Errors; Peripheral Nervous System Diseases; Tyrosine

1995
[Liver cirrhosis associated with metabolic disorders].
    Ryoikibetsu shokogun shirizu, 1995, Issue:7

    Topics: alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Galactosemias; Glycogen Storage Disease; Hemochromatosis; Hepatolenticular Degeneration; Humans; Liver Cirrhosis; Metabolism, Inborn Errors; Tyrosine

1995
[Hereditary liver diseases. Recent molecular genetic aspects].
    Deutsche medizinische Wochenschrift (1946), 1998, Apr-09, Volume: 123, Issue:15

    Topics: alpha 1-Antitrypsin; Animals; Bilirubin; Cholestasis, Intrahepatic; Cystic Fibrosis; Disease Models, Animal; Genetic Therapy; Hepatolenticular Degeneration; Humans; Jaundice, Chronic Idiopathic; Liver Diseases; Metabolism, Inborn Errors; Molecular Biology; Tyrosine

1998
Metabolic cirrhoses of infancy and early childhood.
    Perspectives in pediatric pathology, 1976, Volume: 3

    Topics: Amino Acid Metabolism, Inborn Errors; Cystic Fibrosis; Cystinosis; Fructose Intolerance; Galactosemias; Genetics, Medical; Glycogen Storage Disease Type IV; Hepatolenticular Degeneration; Humans; Iatrogenic Disease; Infant; Infant, Newborn; Lipid Metabolism, Inborn Errors; Liver; Liver Cirrhosis; Metabolism, Inborn Errors; Mucopolysaccharidoses; Niemann-Pick Diseases; Polycystic Kidney Diseases; Tyrosine

1976
[Basis, clinical picture and therapy of diseases of the extrapyramidal-motoric system (EPMS)].
    Zeitschrift fur Allgemeinmedizin, 1975, Mar-20, Volume: 51, Issue:8

    Topics: Acetylcholine; Athetosis; Basal Ganglia Diseases; Catecholamines; Chorea; Dopamine; Dystonia Musculorum Deformans; Hepatolenticular Degeneration; Humans; Hyperkinesis; Myoclonus; Parkinson Disease; Tremor; Tyrosine

1975

Trials

1 trial(s) available for tyrosine and Cerebral Pseudosclerosis

ArticleYear
Hypothalamic digoxin and isoprenoid pathway dysfunction relation to alcoholic addiction, alcoholic cirrhosis, and acquired hepatocerebral degeneration--relation to hemispheric chemical dominance.
    The International journal of neuroscience, 2003, Volume: 113, Issue:4

    Topics: Adult; Alcoholism; Analysis of Variance; Cholesterol; Digoxin; Disease Susceptibility; Dolichols; Dominance, Cerebral; Enzyme Inhibitors; Erythrocytes; Female; Glycoconjugates; Glycosaminoglycans; Hepatolenticular Degeneration; Humans; Hydroxymethylglutaryl CoA Reductases; Hypothalamus; Liver Cirrhosis, Alcoholic; Male; Membrane Proteins; Neurotransmitter Agents; Polyisoprenyl Phosphates; Sodium-Potassium-Exchanging ATPase; Tryptophan; Tyrosine; Ubiquinone

2003

Other Studies

9 other study(ies) available for tyrosine and Cerebral Pseudosclerosis

ArticleYear
Diagnostic procedures in the evaluation of hepatic diseases. Metabolic errors.
    Laboratory and research methods in biology and medicine, 1983, Volume: 7

    Topics: Adolescent; Adult; alpha 1-Antitrypsin Deficiency; Child; Fructose Intolerance; Galactosemias; Hepatolenticular Degeneration; Humans; Infant, Newborn; Liver Diseases; Metabolism, Inborn Errors; Phenotype; Tyrosine

1983
[Tyrosinosis with hepatolenticular degeneration (Wilson's disease)].
    Klinische Monatsblatter fur Augenheilkunde, 1983, Volume: 182, Issue:3

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Corneal Diseases; Hepatolenticular Degeneration; Humans; Male; Tyrosine

1983
Abnormalities of the liver and other organs.
    Radiologic clinics of North America, 1980, Volume: 18, Issue:2

    Topics: Abnormalities, Multiple; alpha 1-Antitrypsin Deficiency; Amino Acid Metabolism, Inborn Errors; Colitis; Colon; Cystinosis; Heart Failure; Hemochromatosis; Hepatolenticular Degeneration; Humans; Liver; Liver Diseases; Necrosis; Radiography; Sclerosis; Tyrosine

1980
Living-related liver transplantation for inborn errors of metabolism.
    Transplantation proceedings, 1994, Volume: 26, Issue:4

    Topics: Adolescent; Adult; Child; Child, Preschool; Fathers; Female; Glycogen Storage Disease Type IV; Hepatolenticular Degeneration; Humans; Infant; Liver Transplantation; Male; Metabolism, Inborn Errors; Mothers; Porphyria, Hepatoerythropoietic; Survival Rate; Tissue Donors; Tyrosine

1994
Liver disorders in children: the indications for liver replacement in parenchymal and metabolic diseases.
    Transplantation proceedings, 1987, Volume: 19, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Budd-Chiari Syndrome; Child; Cholangitis; Crigler-Najjar Syndrome; Hepatitis, Chronic; Hepatolenticular Degeneration; Humans; Infant; Liver Cirrhosis; Liver Diseases; Liver Transplantation; Porphyrias; Tyrosine

1987
The management of metabolic disorders of the liver.
    Pediatric annals, 1985, Volume: 14, Issue:7

    Topics: alpha 1-Antitrypsin Deficiency; Child, Preschool; Fructose Intolerance; Galactosemias; Genetic Counseling; Glycogen Storage Disease; Hepatolenticular Degeneration; Humans; Hydrolases; Infant; Infant, Newborn; Liver Diseases; Metabolic Diseases; Phenotype; Prognosis; Tyrosine

1985
Screening for inborn errors of metabolism. Report of a WHO Scientific Group.
    World Health Organization technical report series, 1968, Volume: 401

    Topics: Adrenal Hyperplasia, Congenital; Amino Acid Metabolism, Inborn Errors; Carrier State; Ceruloplasmin; Cholinesterases; Cystic Fibrosis; Diagnostic Services; Female; Galactosemias; Genetic Diseases, Inborn; Hepatolenticular Degeneration; Humans; Infant; Infant, Newborn; Male; Maple Syrup Urine Disease; Metabolism, Inborn Errors; Phenylketonurias; Porphyrias; Tyrosine; World Health Organization

1968
Differentiation of glomerular, tubular, and normal proteinuria: determinations of urinary excretion of beta-2-macroglobulin, albumin, and total protein.
    The Journal of clinical investigation, 1969, Volume: 48, Issue:7

    Topics: Acidosis, Renal Tubular; Albuminuria; Amino Acid Metabolism, Inborn Errors; Cadmium Poisoning; Creatinine; Cystinosis; Diagnosis, Differential; Female; Glomerulonephritis; Hepatolenticular Degeneration; Humans; Immune Sera; Immunodiffusion; Kidney Glomerulus; Kidney Tubules; Laurence-Moon Syndrome; Male; Molecular Weight; Nephritis, Hereditary; Nephrotic Syndrome; Proteinuria; Serum Globulins; Tyrosine

1969
Nutritional requirements of infants and children with liver disease.
    The American journal of clinical nutrition, 1970, Volume: 23, Issue:5

    Topics: Adolescent; Bile; Body Weight; Carbohydrate Metabolism, Inborn Errors; Child; Child, Preschool; Cystic Fibrosis; Female; Galactosemias; Glycogen; Hepatitis A; Hepatolenticular Degeneration; Humans; India; Infant; Infant Nutritional Physiological Phenomena; Liver Diseases; Male; Tyrosine

1970