trimethyloxamine has been researched along with BCKD Deficiency in 2 studies
trimethyloxamine: used in manufacture of quaternary ammonium cpds; insect attractant; warming agent for gas; oxidant; structure
trimethylamine N-oxide : A tertiary amine oxide resulting from the oxidation of the amino group of trimethylamine.
Excerpt | Relevance | Reference |
---|---|---|
"Maple syrup urine disease is caused by deficiency in the mitochondrial branched-chain alpha-ketoacid dehydrogenase (BCKD) complex." | 1.31 | Natural osmolyte trimethylamine N-oxide corrects assembly defects of mutant branched-chain alpha-ketoacid decarboxylase in maple syrup urine disease. ( Chuang, DT; Song, JL, 2001) |
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 2 (100.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Chuang, JL | 1 |
Wynn, RM | 1 |
Moss, CC | 1 |
Song, JL | 2 |
Li, J | 1 |
Awad, N | 1 |
Mandel, H | 1 |
Chuang, DT | 2 |
2 other studies available for trimethyloxamine and BCKD Deficiency
Article | Year |
---|---|
Structural and biochemical basis for novel mutations in homozygous Israeli maple syrup urine disease patients: a proposed mechanism for the thiamin-responsive phenotype.
Topics: Alleles; Blotting, Western; Centrifugation, Density Gradient; DNA, Complementary; Dose-Response Rela | 2004 |
Natural osmolyte trimethylamine N-oxide corrects assembly defects of mutant branched-chain alpha-ketoacid decarboxylase in maple syrup urine disease.
Topics: 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide); Dimerization; Enzyme Stability; Humans; Ketone Ox | 2001 |