Page last updated: 2024-10-20

trimethyloxamine and BCKD Deficiency

trimethyloxamine has been researched along with BCKD Deficiency in 2 studies

trimethyloxamine: used in manufacture of quaternary ammonium cpds; insect attractant; warming agent for gas; oxidant; structure
trimethylamine N-oxide : A tertiary amine oxide resulting from the oxidation of the amino group of trimethylamine.

Research Excerpts

ExcerptRelevanceReference
"Maple syrup urine disease is caused by deficiency in the mitochondrial branched-chain alpha-ketoacid dehydrogenase (BCKD) complex."1.31Natural osmolyte trimethylamine N-oxide corrects assembly defects of mutant branched-chain alpha-ketoacid decarboxylase in maple syrup urine disease. ( Chuang, DT; Song, JL, 2001)

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's2 (100.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Chuang, JL1
Wynn, RM1
Moss, CC1
Song, JL2
Li, J1
Awad, N1
Mandel, H1
Chuang, DT2

Other Studies

2 other studies available for trimethyloxamine and BCKD Deficiency

ArticleYear
Structural and biochemical basis for novel mutations in homozygous Israeli maple syrup urine disease patients: a proposed mechanism for the thiamin-responsive phenotype.
    The Journal of biological chemistry, 2004, Apr-23, Volume: 279, Issue:17

    Topics: Alleles; Blotting, Western; Centrifugation, Density Gradient; DNA, Complementary; Dose-Response Rela

2004
Natural osmolyte trimethylamine N-oxide corrects assembly defects of mutant branched-chain alpha-ketoacid decarboxylase in maple syrup urine disease.
    The Journal of biological chemistry, 2001, Oct-26, Volume: 276, Issue:43

    Topics: 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide); Dimerization; Enzyme Stability; Humans; Ketone Ox

2001