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trimethylamine and Amino Acid Metabolism Disorders, Inborn

trimethylamine has been researched along with Amino Acid Metabolism Disorders, Inborn in 5 studies

Research Excerpts

ExcerptRelevanceReference
" The aliphatic tertiary amine, trimethylamine, is such a volatile compound that is generated to excess in patients with a metabolic disorder known as trimethylaminuria (fish-odour syndrome)."4.82Trimethylaminuria (fish-odour syndrome) and oral malodour. ( Mitchell, SC, 2005)
"The profiles of urinary volatiles from patients with phenylketonuria, maple syrup urine disease, isovaleric acidemia, or trimethylaminuria (fish-odor syndrome) were in each case vastly different from the normal urinary volatiles profile."3.66Profiles of urinary volatiles from metabolic disorders characterized by unusual odors. ( Burke, DG; Danks, D; Halpern, B; Malegan, D; McCairns, E; Schlesinger, P; Wilken, B, 1983)

Research

Studies (5)

TimeframeStudies, this research(%)All Research%
pre-19902 (40.00)18.7374
1990's0 (0.00)18.2507
2000's3 (60.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Shimizu, M1
Kozono, M1
Murayama, N1
Yamazaki, H1
Mitchell, SC2
Smith, RL1
Burke, DG1
Halpern, B1
Malegan, D1
McCairns, E1
Danks, D1
Schlesinger, P1
Wilken, B1
Pike, MG1
King, GS1
Pettit, BR1
Leonard, JV1
Atherton, DJ1

Reviews

1 review available for trimethylamine and Amino Acid Metabolism Disorders, Inborn

ArticleYear
Trimethylaminuria (fish-odour syndrome) and oral malodour.
    Oral diseases, 2005, Volume: 11 Suppl 1

    Topics: Amino Acid Metabolism, Inborn Errors; Fish Products; Halitosis; Humans; Liver Diseases; Methylamines

2005

Other Studies

4 other studies available for trimethylamine and Amino Acid Metabolism Disorders, Inborn

ArticleYear
Bonitos with low content of malodorous trimethylamine as palliative care for self-reported Japanese trimethylaminuria subjects.
    Drug metabolism and pharmacokinetics, 2009, Volume: 24, Issue:6

    Topics: Amino Acid Metabolism, Inborn Errors; Asian People; Calcium Phosphates; Genetics, Population; Humans

2009
Trimethylamine and odorous sweat.
    Journal of inherited metabolic disease, 2003, Volume: 26, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Gas Chromatography-Mass Spectrometry; Humans; Methylamines; Od

2003
Profiles of urinary volatiles from metabolic disorders characterized by unusual odors.
    Clinical chemistry, 1983, Volume: 29, Issue:10

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Flame Ionization; Hemi

1983
Lactulose in trimethylaminuria, the fish-odour syndrome.
    Helvetica paediatrica acta, 1989, Volume: 43, Issue:4

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Child; Combined Modality Therapy; Disaccharides; F

1989