Page last updated: 2024-08-25

triheptanoin and Mitochondrial Diseases

triheptanoin has been researched along with Mitochondrial Diseases in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's3 (75.00)24.3611
2020's1 (25.00)2.80

Authors

AuthorsStudies
Barshop, BA; Chan, B; Gangoiti, JA; Gaston, G; Gillingham, MB; Harding, CO; Winn, S1
Borges, K; Carrasco-Pozo, C; Simmons, D; Tan, KN1
Behringer, S; Spiekerkoetter, U; Tucci, S1
Brunengraber, H; Roe, CR1

Other Studies

4 other study(ies) available for triheptanoin and Mitochondrial Diseases

ArticleYear
Cardiac tissue citric acid cycle intermediates in exercised very long-chain acyl-CoA dehydrogenase-deficient mice fed triheptanoin or medium-chain triglyceride.
    Journal of inherited metabolic disease, 2020, Volume: 43, Issue:6

    Topics: Acyl-CoA Dehydrogenase, Long-Chain; Animals; Citric Acid Cycle; Congenital Bone Marrow Failure Syndromes; Dietary Fats; Fatty Acids; Female; Lipid Metabolism, Inborn Errors; Liver; Male; Mice; Mitochondrial Diseases; Muscular Diseases; Myocardium; Oxidation-Reduction; Triglycerides

2020
Triheptanoin protects against status epilepticus-induced hippocampal mitochondrial dysfunctions, oxidative stress and neuronal degeneration.
    Journal of neurochemistry, 2018, Volume: 144, Issue:4

    Topics: Animals; Anticonvulsants; CA1 Region, Hippocampal; CA3 Region, Hippocampal; Citric Acid Cycle; Convulsants; Hippocampus; Male; Mice; Mitochondrial Diseases; Nerve Degeneration; Oxidative Stress; Pilocarpine; Status Epilepticus; Triglycerides

2018
De novo fatty acid biosynthesis and elongation in very long-chain acyl-CoA dehydrogenase-deficient mice supplemented with odd or even medium-chain fatty acids.
    The FEBS journal, 2015, Volume: 282, Issue:21

    Topics: Acyl-CoA Dehydrogenase, Long-Chain; Animals; Congenital Bone Marrow Failure Syndromes; Dietary Fats; Disease Models, Animal; Fatty Acids; Female; Lipid Metabolism, Inborn Errors; Liver; Male; Mice; Mice, 129 Strain; Mice, Inbred C57BL; Mice, Knockout; Mitochondrial Diseases; Muscular Diseases; Myocardium; Oxidation-Reduction; Peroxisomes; Triglycerides

2015
Anaplerotic treatment of long-chain fat oxidation disorders with triheptanoin: Review of 15 years Experience.
    Molecular genetics and metabolism, 2015, Volume: 116, Issue:4

    Topics: Administration, Oral; Adolescent; Adult; Carnitine; Child; Child, Preschool; Citric Acid; Fatty Acids; Female; Humans; Infant; Infant, Newborn; Lactic Acid; Lipid Metabolism, Inborn Errors; Malates; Male; Middle Aged; Mitochondrial Diseases; Oxidation-Reduction; Succinic Acid; Survival Analysis; Treatment Outcome; Triglycerides

2015