triheptanoin has been researched along with Mitochondrial Diseases in 4 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 3 (75.00) | 24.3611 |
2020's | 1 (25.00) | 2.80 |
Authors | Studies |
---|---|
Barshop, BA; Chan, B; Gangoiti, JA; Gaston, G; Gillingham, MB; Harding, CO; Winn, S | 1 |
Borges, K; Carrasco-Pozo, C; Simmons, D; Tan, KN | 1 |
Behringer, S; Spiekerkoetter, U; Tucci, S | 1 |
Brunengraber, H; Roe, CR | 1 |
4 other study(ies) available for triheptanoin and Mitochondrial Diseases
Article | Year |
---|---|
Cardiac tissue citric acid cycle intermediates in exercised very long-chain acyl-CoA dehydrogenase-deficient mice fed triheptanoin or medium-chain triglyceride.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Animals; Citric Acid Cycle; Congenital Bone Marrow Failure Syndromes; Dietary Fats; Fatty Acids; Female; Lipid Metabolism, Inborn Errors; Liver; Male; Mice; Mitochondrial Diseases; Muscular Diseases; Myocardium; Oxidation-Reduction; Triglycerides | 2020 |
Triheptanoin protects against status epilepticus-induced hippocampal mitochondrial dysfunctions, oxidative stress and neuronal degeneration.
Topics: Animals; Anticonvulsants; CA1 Region, Hippocampal; CA3 Region, Hippocampal; Citric Acid Cycle; Convulsants; Hippocampus; Male; Mice; Mitochondrial Diseases; Nerve Degeneration; Oxidative Stress; Pilocarpine; Status Epilepticus; Triglycerides | 2018 |
De novo fatty acid biosynthesis and elongation in very long-chain acyl-CoA dehydrogenase-deficient mice supplemented with odd or even medium-chain fatty acids.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Animals; Congenital Bone Marrow Failure Syndromes; Dietary Fats; Disease Models, Animal; Fatty Acids; Female; Lipid Metabolism, Inborn Errors; Liver; Male; Mice; Mice, 129 Strain; Mice, Inbred C57BL; Mice, Knockout; Mitochondrial Diseases; Muscular Diseases; Myocardium; Oxidation-Reduction; Peroxisomes; Triglycerides | 2015 |
Anaplerotic treatment of long-chain fat oxidation disorders with triheptanoin: Review of 15 years Experience.
Topics: Administration, Oral; Adolescent; Adult; Carnitine; Child; Child, Preschool; Citric Acid; Fatty Acids; Female; Humans; Infant; Infant, Newborn; Lactic Acid; Lipid Metabolism, Inborn Errors; Malates; Male; Middle Aged; Mitochondrial Diseases; Oxidation-Reduction; Succinic Acid; Survival Analysis; Treatment Outcome; Triglycerides | 2015 |