Page last updated: 2024-08-23

transferrin and Anemia, Cooley's

transferrin has been researched along with Anemia, Cooley's in 64 studies

Research

Studies (64)

TimeframeStudies, this research(%)All Research%
pre-19903 (4.69)18.7374
1990's13 (20.31)18.2507
2000's13 (20.31)29.6817
2010's31 (48.44)24.3611
2020's4 (6.25)2.80

Authors

AuthorsStudies
Altermatt, P; Doucerain, C; Dürrenberger, F; Flace, A; Ingoglia, G; Kalleda, N; Manolova, V; Nyffenegger, N1
Adly, A; Ebeid, FSE; Elalfy, MS; Fradette, C; Hamdy, M; Lee, D; Rozova, A; Temin, NT; Tricta, F1
Azarkeivan, A; Hosseini, S; Janani, L; Sajadi Hezaveh, Z; Shidfar, F1
Hojjati, MT; Hosseini, T; Naseri, P; Rahmani, R; Safaroghli-Azar, A; Tarighi, S1
Forni, GL; Pinto, VM1
Doucerain, C; Dürrenberger, F; Flace, A; Manolova, V; Nyffenegger, N1
Biemond, BJ; Boshuizen, M; Juffermans, NP; van Bruggen, R; van der Ploeg, K; von Bonsdorff, L; Zeerleder, SS1
Huang, A; Huang, C; Qin, X; Zhang, M; Zhu, X1
Knutson, MD1
Mendes, P; Parmar, JH1
Acquila, M; Bicocchi, MP; Calvillo, M; Cangemi, G; Dufour, C; Fioredda, F; Gastaldi, R; Gatti, C; Gattorno, M; Martini, A; Melioli, G; Miano, M; Pistorio, A; Riccardi, F1
Aghajan, M; Booten, S; Casu, C; Freier, S; Gardenghi, S; Guo, S; Monia, BP; Peralta, R; Rivella, S; Watt, A1
de Swart, L; Maas, RP; Swinkels, DW; Voets, PJ1
Fleming, MD; Schmidt, PJ1
Lane, DJ; Richardson, DR1
Baek, JH; Buehler, PW; Gelderman-Fuhrmann, MP; Opitz, L; Puglia, M; Schaer, CA; Schaer, DJ; Vallelian, F; Vostal, J1
Biemond, BJ; Brittenham, GM; Cabantchik, ZI; de Swart, L; Evans, PJ; Furman, Y; Galanello, R; Hendriks, JC; Hider, RC; Hod, EA; Janssen, MC; MacKenzie, MA; Mattijssen, VE; Origa, R; Porter, JB; Swinkels, DW; van der Vorm, LN; Wojczyk, B1
Bao, W; Blanc, L; Chen, H; Choesang, T; Feola, M; Fleming, RE; Follenzi, A; Ginzburg, YZ; Li, G; Li, H; Pham, P; Rivella, S; Sun, S; Westerman, M1
Arosio, C; Mariani, R; Pelloni, I; Pelucchi, S; Piperno, A1
Ellervik, C; Hasselbalch, HC; Henriksen, LF; Kanters, JK; Petri, AS1
An, X; Bao, W; Chen, H; Choesang, T; Feola, M; Fleming, RE; Follenzi, A; Garcia-Santos, D; Ginzburg, YZ; Li, G; Li, H; Li, J; Liu, J; Mohandas, N; Pham, P; Ponka, P; Rivella, S; Sun, S; Zhang, J1
Ozment, CP; Turi, JL1
Gohil, NK; Saxena, R; Sharma, M1
Admoni, O; Fink, D; Koren, A; Levin, C; Tennenbaum-Rakover, Y1
Bouhassira, EE; Breuer, W; Cabantchik, ZI; Fabry, ME; Ginzburg, YZ; Hall, CB; Li, H; Rybicki, AC; Suzuka, SM; von Bonsdorff, L1
Chantharaksri, U; Fucharoen, S; Jirasomprasert, T; Jittangprasert, P; Limenta, LM; Morales, NP; Wilairat, P; Yamanont, P1
Chattipakorn, N; Fucharoen, S; Lailerd, N; Phisalaphong, C; Porter, JB; Srichairatanakool, S; Thephinlap, C; Vadolas, J; Winichagoon, P1
Bonini-Domingos, CR; Estevão, IF; Peitl Junior, P1
Abete, C; Carta, MP; Cocco, P; Dessì, S; Lai, ME; Mandas, A; Spiga, A; Vacquer, S1
Castro, JA; Ferragut, JF; Guix, P; López-Escribano, H; Parera, MM; Picornell, A; Ramon, MM1
Dorrington, KL; Lakhal, S; León-Velarde, F; Mole, DR; Nickol, AH; Privat, C; Rivera-Ch, M; Robbins, PA; Smith, TG; Talbot, NP1
Attar, S; Breuer, W; Cabantchik, ZI; Ghoti, H; Rachmilewitz, E; Sohn, YS; Weiss, G1
Anderson, GJ; Badrick, AC; Darshan, D; Frazer, DM; McLaren, GD; Wilkins, SJ1
Barisani, D; Ganz, T; Hayashi, H; Mariani, R; Modignani, GL; Nemeth, E; Pelucchi, S; Piperno, A; Pozzi, M; Ravasi, G; Tomosugi, N; Trombini, P1
Charoensakdi, R; Chokchaichamnankit, D; Fucharoen, S; Hatairaktham, S; Kalpravidh, RW; Panichkul, N; Siritanaratkul, N; Srisomsap, C; Subhasitanont, P; Svasti, J; Weeraphan, C1
Lane, DJ; Lawen, A1
An, X; Chasis, JA; De Franceschi, L; Ginzburg, Y; Li, H; Liu, J; Mohandas, N; Xue, F; Zhang, J1
Altay, C; Aslan, D1
BURGIO, GR; LO JACONO, F1
GIUFFRE, L; PRIOLISI, A2
Breuer, W; Cabantchik, ZI; Hershko, C; Pootrakul, P; Sametband, M; Sirankapracha, P1
Coelho, M; Costa, L; Faustino, P; Ferreira, L; Fonseca, A; Martins, R; Miranda, A; Nunes, B; Picanço, I; Rodrigues, O; Romão, L; Seixas, T1
De Gobbi, M; Miniero, R; Roetto, A; Tardivo, I1
Caruso, V; Dürken, M; Engelhardt, R; Fischer, R; Grosse, R; Janka, GE; Lund, U; Magnano, C; Nielsen, P1
Faa, G; Galanello, R; Ganz, T; Giagu, N; Maccioni, L; Nemeth, E; Origa, R1
Arosio, P; Biasiotto, G; Cremonesi, L; Dongiovanni, P; Fargion, S; Fracanzani, AL; Maggioni, M; Pulixi, EA; Valenti, L1
Fibach, E; Prus, E1
Iancu, TC; Shiloh, H1
Peters, TJ; Raja, KB; Simpson, RJ1
Angelucci, E; Argiolu, F; Baronciani, D; Becchelli, G; Borgna Pignatti, C; Campisi, S; Careddu, F; Conter, V; De Nunzio, A; Giardini, C1
Williamson, B1
Cheung, MC; Goldberg, JD; Kan, YW1
Cooper, CE; Porter, JB1
AL-Refaie, F; Cochrane, J; Davis, B; Hoffbrand, AV; Jackson, BF; Prescott, E; Siritanakatkul, N; Wonke, B1
Angelucci, E; Annibali, M; Baronciani, D; Erer, B; Galimberti, M; Gaziev, D; Giardini, C; Lucarelli, G; Muretto, P; Polchi, P; Rapa, S; Ripalti, M1
Collell, M; Dresow, B; Dürken, M; Engelhardt, R; Fischer, R; Nielsen, P; Piga, A; Politis, C; Reller, K1
Luo, LY; Rees, DC; Singh, BM; Thein, SL; Wickramasinghe, S1
Bartfay, WJ; Lehotay, DC; Liu, PP; Sher, GD1
Boelaert, JR; Cantinieaux, B; Cornu, G; Fondu, P; Janssens, A; Kerrels, V; Lejeune, M; Vermylen, C; Winand, J1
Abramov, A; Breuer, W; Cabantchik, ZI; Hershko, C; Ronson, A; Slotki, IN1
Kazimierska, E; Swiatkowska-Stodulska, R; Weyer-Hepka, J1
Bortone, L; Cappellini, MD; Cighetti, G; Duca, L; Fiorelli, G; Nava, I; Sala, S1
al-Refaie, FN; Hoffbrand, AV; Kontoghiorghes, GJ; Wickens, DG; Wonke, B1

Reviews

11 review(s) available for transferrin and Anemia, Cooley's

ArticleYear
Management of Iron Overload in Beta-Thalassemia Patients: Clinical Practice Update Based on Case Series.
    International journal of molecular sciences, 2020, Nov-20, Volume: 21, Issue:22

    Topics: Adult; beta-Thalassemia; Blood Transfusion; Cardiomyopathies; Chelation Therapy; Deferoxamine; Drug Monitoring; Female; Heart; Humans; Iron; Iron Chelating Agents; Iron Overload; Liver; Male; Middle Aged; Pancreas; Transferrin; Transfusion Reaction

2020
Therapeutic use of transferrin to modulate anemia and conditions of iron toxicity.
    Blood reviews, 2017, Volume: 31, Issue:6

    Topics: Anemia; Animals; beta-Thalassemia; Demyelinating Diseases; Humans; Hyperoxia; Iron Overload; Lung Injury; Macular Degeneration; Oxidative Stress; Reperfusion Injury; Stem Cell Transplantation; Transferrin

2017
Non-transferrin-bound iron transporters.
    Free radical biology & medicine, 2019, Volume: 133

    Topics: beta-Thalassemia; Calcium Channels, L-Type; Calcium Channels, N-Type; Cation Transport Proteins; Hemochromatosis; Humans; Ion Transport; Iron; Iron Overload; Liver; Transcription Factors; Transferrin; TRPC6 Cation Channel

2019
[Non-transferrin-bound iron: a promising biomarker in iron overload disorders].
    Nederlands tijdschrift voor geneeskunde, 2013, Volume: 157, Issue:49

    Topics: Anemia, Sickle Cell; beta-Thalassemia; Biomarkers; Hemochromatosis; Humans; Iron; Iron Overload; Myelodysplastic Syndromes; Oxidation-Reduction; Reactive Oxygen Species; Transferrin

2013
Modulation of hepcidin as therapy for primary and secondary iron overload disorders: preclinical models and approaches.
    Hematology/oncology clinics of North America, 2014, Volume: 28, Issue:2

    Topics: Animals; beta-Thalassemia; Disease Models, Animal; Gene Expression; Genistein; Hepcidins; Humans; Iron; Iron Overload; Transferrin

2014
The active role of vitamin C in mammalian iron metabolism: much more than just enhanced iron absorption!
    Free radical biology & medicine, 2014, Volume: 75

    Topics: Anemia; Animals; Ascorbic Acid; Astrocytes; Basic Helix-Loop-Helix Transcription Factors; beta-Thalassemia; Biological Transport; Erythropoiesis; Ferritins; Hemochromatosis; Humans; Hypoxia-Inducible Factor 1, alpha Subunit; Iron; Transferrin

2014
Increased iron stores prolong the QT interval - a general population study including 20 261 individuals and meta-analysis of thalassaemia major.
    British journal of haematology, 2016, Volume: 174, Issue:5

    Topics: Adult; Aged; Aged, 80 and over; beta-Thalassemia; Case-Control Studies; Female; Ferritins; Hemochromatosis; Humans; Inflammation; Iron; Iron Overload; Long QT Syndrome; Male; Middle Aged; Netherlands; Sex Factors; Transferrin; Young Adult

2016
Iron overload following red blood cell transfusion and its impact on disease severity.
    Biochimica et biophysica acta, 2009, Volume: 1790, Issue:7

    Topics: Anemia, Hemolytic, Congenital; beta-Thalassemia; Cardiomyopathies; Erythrocyte Transfusion; Humans; Infant, Newborn; Infant, Premature, Diseases; Iron; Iron Chelating Agents; Iron Overload; Liver Diseases; Transferrin

2009
Mammalian iron homeostasis in health and disease: uptake, storage, transport, and molecular mechanisms of action.
    Antioxidants & redox signaling, 2013, Jun-20, Volume: 18, Issue:18

    Topics: Anemia; Animals; beta-Thalassemia; Biological Transport; Cation Transport Proteins; Gene Expression Regulation; Hemochromatosis; Hepcidins; Homeostasis; Humans; Iron; Proteolysis; Transferrin

2013
Morphologic observations in iron overload: an update.
    Advances in experimental medicine and biology, 1994, Volume: 356

    Topics: Animals; beta-Thalassemia; Birds; Diet; Ferritins; Heart; Hemochromatosis; Hemosiderin; Humans; Infant; Infant, Newborn; Iron; Lemur; Mice; Mice, Mutant Strains; Myocardium; Neuroblastoma; Reindeer; Transferrin

1994
Ribonucleotide reductase, lipoxygenase and the intracellular low-molecular-weight iron pool.
    Biochemical Society transactions, 1997, Volume: 25, Issue:1

    Topics: beta-Thalassemia; Blood Transfusion; Deferoxamine; Electron Spin Resonance Spectroscopy; Humans; Iron; Iron Chelating Agents; Kinetics; Lipoxygenase; Models, Chemical; Neutrophils; Oxidation-Reduction; Ribonucleotide Reductases; Transferrin

1997

Trials

4 trial(s) available for transferrin and Anemia, Cooley's

ArticleYear
Efficacy and safety of early-start deferiprone in infants and young children with transfusion-dependent beta thalassemia: Evidence for iron shuttling to transferrin in a randomized, double-blind, placebo-controlled, clinical trial (START).
    American journal of hematology, 2023, Volume: 98, Issue:9

    Topics: beta-Thalassemia; Child; Child, Preschool; Ferritins; Humans; Infant; Iron; Iron Chelating Agents; Iron Overload; Pyridones; Transferrin

2023
The effect of quercetin on iron overload and inflammation in β-thalassemia major patients: A double-blind randomized clinical trial.
    Complementary therapies in medicine, 2019, Volume: 46

    Topics: Adult; beta-Thalassemia; C-Reactive Protein; Double-Blind Method; Female; Ferritins; Humans; Inflammation; Iron; Iron Overload; Male; Quercetin; Transferrin

2019
Labile plasma iron (LPI) as an indicator of chelatable plasma redox activity in iron-overloaded beta-thalassemia/HbE patients treated with an oral chelator.
    Blood, 2004, Sep-01, Volume: 104, Issue:5

    Topics: beta-Thalassemia; Biomarkers; Deferiprone; Erythrocyte Membrane; Follow-Up Studies; Hemoglobin E; Humans; Iron; Iron Chelating Agents; Iron Overload; Oxidation-Reduction; Predictive Value of Tests; Pyridones; Transferrin

2004
Long-term trial of deferiprone in 51 transfusion-dependent iron overloaded patients.
    Blood, 1998, Jan-01, Volume: 91, Issue:1

    Topics: Adult; Aged; Aged, 80 and over; Anemia, Sickle Cell; beta-Thalassemia; Blood Transfusion; Chelating Agents; Chelation Therapy; Combined Modality Therapy; Deferiprone; Female; Hemoglobins; Humans; Iron; Iron Overload; Liver; Male; Middle Aged; Pyridones; Splenectomy; Transferrin; Transfusion Reaction

1998

Other Studies

49 other study(ies) available for transferrin and Anemia, Cooley's

ArticleYear
Ferroportin inhibitor vamifeport ameliorates ineffective erythropoiesis in a mouse model of β-thalassemia with blood transfusions.
    Haematologica, 2023, 10-01, Volume: 108, Issue:10

    Topics: Animals; beta-Thalassemia; Blood Transfusion; Erythropoiesis; Humans; Iron; Iron Overload; Mice; Thalassemia; Transferrin

2023
Investigation of correlation between H63D and C282Y mutations in HFE gene and serum Ferritin level in beta-thalassemia major patients.
    Transfusion clinique et biologique : journal de la Societe francaise de transfusion sanguine, 2019, Volume: 26, Issue:4

    Topics: Alleles; beta 2-Microglobulin; beta-Thalassemia; Blood Transfusion; Cross-Sectional Studies; Female; Ferritins; Gene Frequency; Hemochromatosis; Hemochromatosis Protein; Humans; Iran; Iron Overload; Male; Point Mutation; Prognosis; Receptors, Transferrin; Transferrin; Transfusion Reaction

2019
The Oral Ferroportin Inhibitor VIT-2763 Improves Erythropoiesis without Interfering with Iron Chelation Therapy in a Mouse Model of β-Thalassemia.
    International journal of molecular sciences, 2021, Jan-16, Volume: 22, Issue:2

    Topics: Administration, Oral; Animals; Benzimidazoles; beta-Thalassemia; Cation Transport Proteins; Cells, Cultured; Deferasirox; Drug Combinations; Drug Interactions; Erythropoiesis; Female; Iron; Iron Chelating Agents; Male; Mice; Mice, Inbred C57BL; Oxazoles; Pyridines; Transferrin

2021
Analysis of Glycosylation Profiles of Serum Glycoprotein from Iron Overload Thalassemia.
    Clinical laboratory, 2018, Jul-01, Volume: 64, Issue:7

    Topics: Adolescent; Adult; alpha-Thalassemia; beta-Thalassemia; Databases, Protein; Female; Ferritins; Glycoproteins; Glycosylation; Hepcidins; Humans; Iron Overload; Lectins; Male; Middle Aged; Protein Array Analysis; Reproducibility of Results; Transferrin; Young Adult

2018
A computational model to understand mouse iron physiology and disease.
    PLoS computational biology, 2019, Volume: 15, Issue:1

    Topics: Animals; beta-Thalassemia; Computational Biology; Iron; Iron Metabolism Disorders; Liver; Mice; Models, Biological; Transferrin

2019
Diagnostic potential of hepcidin testing in pediatrics.
    European journal of haematology, 2013, Volume: 90, Issue:4

    Topics: Adolescent; Adult; Anemia; Anemia, Iron-Deficiency; Antimicrobial Cationic Peptides; Arthritis, Juvenile; beta-Thalassemia; Biomarkers; Case-Control Studies; Child; Child, Preschool; Female; Hepcidins; Humans; Interleukin 1 Receptor Antagonist Protein; Iron; Iron, Dietary; Male; Puberty; Reference Values; Transferrin; Young Adult

2013
Reducing TMPRSS6 ameliorates hemochromatosis and β-thalassemia in mice.
    The Journal of clinical investigation, 2013, Volume: 123, Issue:4

    Topics: Animals; Antimicrobial Cationic Peptides; beta-Thalassemia; Cells, Cultured; Female; Gene Knockdown Techniques; Hemochromatosis; Hemochromatosis Protein; Hepatocytes; Hepcidins; Histocompatibility Antigens Class I; Iron; Liver; Male; Membrane Proteins; Mice; Mice, Inbred C57BL; Mice, Knockout; Oligonucleotides, Antisense; RNA, Messenger; Serine Endopeptidases; Spleen; Transferrin

2013
Integrative proteome and transcriptome analysis of extramedullary erythropoiesis and its reversal by transferrin treatment in a mouse model of beta-thalassemia.
    Journal of proteome research, 2015, Feb-06, Volume: 14, Issue:2

    Topics: Animals; beta-Thalassemia; Disease Models, Animal; Erythropoiesis; Mice; Mice, Inbred C57BL; Proteome; Transcriptome; Transferrin

2015
Second international round robin for the quantification of serum non-transferrin-bound iron and labile plasma iron in patients with iron-overload disorders.
    Haematologica, 2016, Volume: 101, Issue:1

    Topics: Adult; Aged; beta-Thalassemia; Blood Transfusion; Female; Hemochromatosis; Humans; Iron; Male; Middle Aged; Myelodysplastic Syndromes; Transferrin

2016
Increased hepcidin in transferrin-treated thalassemic mice correlates with increased liver BMP2 expression and decreased hepatocyte ERK activation.
    Haematologica, 2016, Volume: 101, Issue:3

    Topics: Animals; Antibodies, Neutralizing; Apoproteins; beta-Thalassemia; Bone Morphogenetic Protein 2; Bone Morphogenetic Protein 6; Butadienes; Cytokines; Disease Models, Animal; Gene Expression Regulation; Hepatocytes; Hepcidins; Humans; Liver; Mice; Mice, Transgenic; Mitogen-Activated Protein Kinase 1; Mitogen-Activated Protein Kinase 3; Muscle Proteins; Nitriles; Phosphorylation; RNA, Messenger; Signal Transduction; Smad Proteins; Transferrin

2016
Does aceruloplasminemia modulate iron phenotype in thalassemia intermedia?
    Blood cells, molecules & diseases, 2016, Volume: 57

    Topics: alpha-Globins; Base Sequence; beta-Globins; beta-Thalassemia; Ceruloplasmin; Deferoxamine; Exons; Gene Expression; Humans; Introns; Iron; Iron Chelating Agents; Iron Metabolism Disorders; Iron Overload; Male; Middle Aged; Molecular Sequence Data; Mutation; Neurodegenerative Diseases; Phenotype; Transferrin

2016
Decreasing TfR1 expression reverses anemia and hepcidin suppression in β-thalassemic mice.
    Blood, 2017, 03-16, Volume: 129, Issue:11

    Topics: Anemia; Animals; Apoproteins; beta-Thalassemia; Erythropoiesis; Hepcidins; Iron Overload; Mice; Receptors, Transferrin; Transferrin

2017
Fluorescence assay of non-transferrin-bound iron in thalassemic sera using bacterial siderophore.
    Analytical biochemistry, 2009, Nov-15, Volume: 394, Issue:2

    Topics: Adolescent; Adult; Apoproteins; Azotobacter vinelandii; beta-Thalassemia; Calibration; Child; Child, Preschool; Feasibility Studies; Female; Fluorescence; Humans; India; Iron; Male; Siderophores; Spectrometry, Fluorescence; Transferrin; Young Adult

2009
Non-transferrin-bound labile plasma iron and iron overload in sickle-cell disease: a comparative study between sickle-cell disease and beta-thalassemic patients.
    European journal of haematology, 2010, Jan-01, Volume: 84, Issue:1

    Topics: Adolescent; Adult; Anemia, Sickle Cell; beta-Thalassemia; Chelation Therapy; Child; Cohort Studies; Comorbidity; Endocrine System Diseases; Ferritins; Greece; Hepatitis C, Chronic; Humans; Hypersplenism; Inflammation; Iron; Iron Chelating Agents; Iron Overload; Myocardium; Splenectomy; Transferrin; Transfusion Reaction; Young Adult

2010
Transferrin therapy ameliorates disease in beta-thalassemic mice.
    Nature medicine, 2010, Volume: 16, Issue:2

    Topics: Animals; Apoptosis; beta-Thalassemia; Cell Survival; Disease Models, Animal; Erythropoietin; Hematopoiesis, Extramedullary; Mice; Splenomegaly; Transferrin

2010
Pharmacokinetics of deferiprone in patients with β-thalassaemia: impact of splenectomy and iron status.
    Clinical pharmacokinetics, 2011, Volume: 50, Issue:1

    Topics: Administration, Oral; Adult; Area Under Curve; beta-Thalassemia; Deferiprone; Female; Ferritins; Hemoglobin E; Humans; Iron; Iron Chelating Agents; Iron Overload; Male; Pyridones; Splenectomy; Transferrin; Transfusion Reaction

2011
Reversal of cardiac iron loading and dysfunction in thalassemic mice by curcuminoids.
    Medicinal chemistry (Shariqah (United Arab Emirates)), 2011, Volume: 7, Issue:1

    Topics: Animals; beta-Thalassemia; Curcumin; Heart; Heart Rate; Humans; Iron; Iron Chelating Agents; Iron Overload; Iron, Dietary; Lipid Peroxidation; Male; Malondialdehyde; Mice; Mice, Inbred C57BL; Mice, Knockout; Transferrin

2011
Serum ferritin and transferrin saturation levels in β⁰ and β(+) thalassemia patients.
    Genetics and molecular research : GMR, 2011, Apr-12, Volume: 10, Issue:2

    Topics: Adult; Age Factors; Aged; Aged, 80 and over; beta-Thalassemia; Female; Ferritins; Hemochromatosis; Heterozygote; Humans; Iron; Male; Middle Aged; Mutation; Polymerase Chain Reaction; Sex Factors; Transferrin

2011
Evidence for a proatherogenic biochemical phenotype in beta thalassemia minor and intermedia.
    Acta haematologica, 2011, Volume: 126, Issue:2

    Topics: Acetyl-CoA C-Acetyltransferase; Adult; Antimicrobial Cationic Peptides; Atherosclerosis; beta-Thalassemia; Cholesterol, HDL; Erythropoietin; Female; Hepcidins; Humans; Interleukin-1alpha; Iron; Italy; Leukocytes, Mononuclear; Male; Middle Aged; Oxidative Stress; Phenotype; Risk Factors; RNA, Messenger; Severity of Illness Index; Sterol Esterase; Transferrin; Tumor Necrosis Factor-alpha

2011
Effect of co-inheritance of β-thalassemia and hemochromatosis mutations on iron overload.
    Hemoglobin, 2012, Volume: 36, Issue:1

    Topics: beta-Thalassemia; DNA Mutational Analysis; Female; Ferritins; Genotype; Hemochromatosis; Hemochromatosis Protein; Histocompatibility Antigens Class I; Humans; Iron Overload; Male; Membrane Proteins; Mutation; Retrospective Studies; Spain; Transferrin

2012
Regulation of hepcidin expression at high altitude.
    Blood, 2012, Jan-19, Volume: 119, Issue:3

    Topics: Adult; Altitude; Antimicrobial Cationic Peptides; beta-Thalassemia; Case-Control Studies; Erythropoiesis; Erythropoietin; Ferritins; Gene Expression Regulation; Growth Differentiation Factor 15; Hepcidins; Homeostasis; Humans; Hypoxia; Iron; Iron Metabolism Disorders; Iron, Dietary; Transferrin

2012
The role of endocytic pathways in cellular uptake of plasma non-transferrin iron.
    Haematologica, 2012, Volume: 97, Issue:5

    Topics: Adolescent; Adult; beta-Thalassemia; Biological Transport; Biomarkers; Cells, Cultured; Cytosol; Endocytosis; Endosomes; Humans; Insulinoma; Iron; Iron Chelating Agents; Macrophages; Microscopy, Fluorescence; Myocytes, Cardiac; Transferrin; Young Adult

2012
Stimulated erythropoiesis with secondary iron loading leads to a decrease in hepcidin despite an increase in bone morphogenetic protein 6 expression.
    British journal of haematology, 2012, Volume: 157, Issue:5

    Topics: Anemia, Hemolytic; Animals; Antimicrobial Cationic Peptides; beta-Thalassemia; Bone Morphogenetic Protein 6; Disease Models, Animal; Erythropoiesis; Extracellular Signal-Regulated MAP Kinases; Female; Growth Differentiation Factor 15; Hemolysis; Hepcidins; Iron Overload; Male; Mice; Mice, Inbred C57BL; Mice, Transgenic; Phenylhydrazines; Phosphorylation; Receptors, Transferrin; Signal Transduction; Smad Proteins; Spleen; Transferrin

2012
Hepcidin expression in iron overload diseases is variably modulated by circulating factors.
    PloS one, 2012, Volume: 7, Issue:5

    Topics: Adult; Aged; Antimicrobial Cationic Peptides; beta-Thalassemia; Biopsy; Cytokines; Gene Expression Regulation; Hemochromatosis; Hemochromatosis Protein; Hep G2 Cells; Hepcidins; Histocompatibility Antigens Class I; Humans; Iron; Iron Overload; Liver; Membrane Proteins; Middle Aged; RNA, Messenger; Transferrin

2012
Role of curcuminoids in ameliorating oxidative modification in β-thalassemia/Hb E plasma proteome.
    The Journal of nutritional biochemistry, 2013, Volume: 24, Issue:3

    Topics: Adult; Antioxidants; beta-Thalassemia; Curcuma; Dietary Supplements; Female; Hemoglobin E; Humans; Iron Chelating Agents; Iron Overload; Male; Middle Aged; Oxidative Stress; Plant Extracts; Protein Carbonylation; Proteome; Proteomics; Transferrin; Up-Regulation; Young Adult

2013
Quantitative analysis of murine terminal erythroid differentiation in vivo: novel method to study normal and disordered erythropoiesis.
    Blood, 2013, Feb-21, Volume: 121, Issue:8

    Topics: Anemia; Animals; beta-Thalassemia; Bone Marrow Cells; Cell Differentiation; Cell Separation; Disease Progression; Erythroblasts; Erythropoiesis; Female; Flow Cytometry; Hematopoietic Stem Cells; Male; Mice; Mice, Inbred C57BL; Mice, Knockout; Reproducibility of Results; Spleen; Transferrin

2013
Incidence of high erythrocyte count in infants and young children with iron deficiency anemia: re-evaluation of an old parameter.
    Journal of pediatric hematology/oncology, 2003, Volume: 25, Issue:4

    Topics: Age Factors; Anemia, Hypochromic; beta-Thalassemia; Child, Preschool; Diagnosis, Differential; Erythrocyte Count; Erythrocyte Indices; Female; Ferritins; Hematocrit; Hemoglobins; Humans; Incidence; Infant; Iron; Male; Polycythemia; Transferrin

2003
[Changes in transferrin following the administration of iron preparations in normal children and those with blood disorders].
    Bollettino della Societa italiana di biologia sperimentale, 1952, Volume: 28, Issue:12

    Topics: Anemia; Anemia, Pernicious; beta-Thalassemia; Blood; Blood Proteins; Erythroblasts; Humans; Iron; Iron Compounds; Transferrin

1952
[IMMUNOELECTROPHORETIC STUDY OF THE BLOOD IN THALASSEMIA MAJOR AND ITS RELATION TO SPLENECTOMY].
    Haematologica, 1963, Volume: 48

    Topics: beta-Thalassemia; Ceruloplasmin; Haptoglobins; Humans; Immunoelectrophoresis; Lipoproteins; Serum Globulins; Splenectomy; Thalassemia; Transferrin

1963
[ON SOME PARTICULAR ASPECTS OF IRON KINETICS IN SUBJECTS WITH THALASSEMIA MAJOR].
    La Pediatria, 1964, Jun-30, Volume: 72

    Topics: beta-Thalassemia; Hematologic Tests; Humans; Iron; Iron Isotopes; Kinetics; Thalassemia; Transferrin

1964
The role of HFE mutations on iron metabolism in beta-thalassemia carriers.
    Journal of human genetics, 2004, Volume: 49, Issue:12

    Topics: Alleles; Amino Acid Substitution; beta-Thalassemia; Female; Gene Frequency; Hemochromatosis; Hemochromatosis Protein; Heterozygote; Histocompatibility Antigens Class I; Humans; Iron; Male; Membrane Proteins; Point Mutation; Quantitative Trait Loci; Transferrin

2004
Heterozygous beta-thalassemia and homozygous H63D hemochromatosis in a child: an 18-year follow-up.
    Pediatric hematology and oncology, 2005, Volume: 22, Issue:2

    Topics: Age Factors; beta-Thalassemia; Child, Preschool; Ferritins; Hemochromatosis; Hemoglobins; Heterozygote; Homozygote; Humans; Iron; Longitudinal Studies; Male; Mutation, Missense; Transferrin

2005
Non-transferrin-bound iron during blood transfusion cycles in beta-thalassemia major.
    Annals of the New York Academy of Sciences, 2005, Volume: 1054

    Topics: Adolescent; Adult; beta-Thalassemia; Blood Specimen Collection; Blood Transfusion; Chelation Therapy; Combined Modality Therapy; Deferoxamine; Drug Administration Schedule; Humans; Iron; Iron Chelating Agents; Liver; Magnetic Resonance Imaging; Prospective Studies; Receptors, Transferrin; Reproducibility of Results; Time Factors; Transferrin

2005
Liver iron concentrations and urinary hepcidin in beta-thalassemia.
    Haematologica, 2007, Volume: 92, Issue:5

    Topics: Adolescent; Adult; Antimicrobial Cationic Peptides; beta-Thalassemia; Blood Transfusion; Chelation Therapy; Combined Modality Therapy; Deferoxamine; Erythropoiesis; Female; Ferritins; Gene Expression Regulation; Hepcidins; Humans; Intestinal Absorption; Iron; Iron Chelating Agents; Iron Overload; Iron, Dietary; Liver; Macrophages; Male; Severity of Illness Index; Transferrin

2007
Relative contribution of iron genes, dysmetabolism and hepatitis C virus (HCV) in the pathogenesis of altered iron regulation in HCV chronic hepatitis.
    Haematologica, 2007, Volume: 92, Issue:8

    Topics: Adult; Antimicrobial Cationic Peptides; beta-Thalassemia; Cation Transport Proteins; Cholesterol, LDL; Fatty Liver; Ferritins; Genotype; GPI-Linked Proteins; Hemochromatosis Protein; Hepacivirus; Hepatitis C, Chronic; Hepcidins; Histocompatibility Antigens Class I; Humans; Iron; Iron Overload; Liver; Liver Cirrhosis; Male; Membrane Proteins; Middle Aged; Mutation; Promoter Regions, Genetic; Receptors, Transferrin; Transferrin

2007
The labile iron pool in human erythroid cells.
    British journal of haematology, 2008, Volume: 142, Issue:2

    Topics: Antigens, CD; beta-Thalassemia; Bone Marrow Cells; Cells, Cultured; Deferiprone; Erythroblasts; Erythrocytes; Erythropoiesis; Flow Cytometry; Fluoresceins; Fluorescent Dyes; Humans; Iron; Iron Chelating Agents; Pyridones; Reticulocytes; Transferrin

2008
Intestinal iron absorption studies in mouse models of iron-overload.
    British journal of haematology, 1994, Volume: 86, Issue:1

    Topics: alpha-Thalassemia; Animals; beta-Thalassemia; Body Weight; Disease Models, Animal; Intestinal Absorption; Iron; Male; Mice; Mice, Inbred BALB C; Mice, Inbred C57BL; Thalassemia; Transferrin

1994
Iron removal in ex-thalassemics after BMT: preliminary results from the phlebotomy program. Italian Cooperative Group for Phlebotomy in Ex-thalassemic.
    Bone marrow transplantation, 1993, Volume: 12 Suppl 1

    Topics: Adolescent; Adult; Anemia; beta-Thalassemia; Bloodletting; Bone Marrow Transplantation; Child; Combined Modality Therapy; Ferritins; Hemochromatosis; Humans; Iron; Liver Diseases; Postoperative Period; Shock; Transferrin; Transfusion Reaction

1993
Towards non-invasive prenatal diagnosis.
    Nature genetics, 1996, Volume: 14, Issue:3

    Topics: Amniocentesis; beta-Thalassemia; Cell Nucleus; Chorionic Villi Sampling; Cytodiagnosis; Erythroblasts; Female; Fetus; Humans; Polymerase Chain Reaction; Pregnancy; Prenatal Diagnosis; Transferrin

1996
Prenatal diagnosis of sickle cell anaemia and thalassaemia by analysis of fetal cells in maternal blood.
    Nature genetics, 1996, Volume: 14, Issue:3

    Topics: Anemia, Sickle Cell; Antibodies; beta-Thalassemia; Erythrocytes; Female; Fetus; Hemoglobins; Humans; Immunomagnetic Separation; Microscopy; Polymerase Chain Reaction; Pregnancy; Prenatal Diagnosis; Transferrin

1996
Treatment of iron overload in the "ex-thalassemic". Report from the phlebotomy program.
    Annals of the New York Academy of Sciences, 1998, Jun-30, Volume: 850

    Topics: Adolescent; Alanine Transaminase; beta-Thalassemia; Bone Marrow Transplantation; Female; Ferritins; Follow-Up Studies; Humans; Iron; Liver; Male; Morbidity; Phlebotomy; Postoperative Complications; Time Factors; Transferrin

1998
Iron overload and antioxidant status in patients with beta-thalassemia major.
    Annals of the New York Academy of Sciences, 1998, Jun-30, Volume: 850

    Topics: Antioxidants; Ascorbic Acid; beta-Thalassemia; Deferoxamine; Humans; Iron; Iron Chelating Agents; Liver; Transferrin; Vitamin A; Vitamin E

1998
Nontransfusional iron overload in thalassemia. Association with hereditary hemochromatosis.
    Annals of the New York Academy of Sciences, 1998, Jun-30, Volume: 850

    Topics: Adolescent; Adult; Aged; beta-Thalassemia; Blood Transfusion; Child; DNA; Female; Ferritins; Globins; Hemochromatosis; Hemochromatosis Protein; Hemoglobins; Histocompatibility Antigens Class I; HLA Antigens; Humans; Iron; Male; Membrane Proteins; Middle Aged; Point Mutation; Transferrin

1998
Effect of transfusion on lipid peroxidation products in the plasma of thalassemic patients.
    Transfusion, 1999, Volume: 39, Issue:3

    Topics: Aldehydes; beta-Thalassemia; Biomarkers; Chelation Therapy; Deferiprone; Deferoxamine; Erythrocyte Transfusion; Free Radicals; Humans; Iron; Iron Chelating Agents; Iron Overload; Lipid Peroxidation; Pilot Projects; Pyridones; Transferrin

1999
Ferritin-associated iron induces neutrophil dysfunction in hemosiderosis.
    The Journal of laboratory and clinical medicine, 1999, Volume: 133, Issue:4

    Topics: Adolescent; beta-Thalassemia; Blood Transfusion; Catalase; Chelating Agents; Child; Child, Preschool; Deferoxamine; Female; Ferritins; Hemosiderosis; Humans; Iron; Luminescent Measurements; Male; Neutrophils; Phagocytosis; Tetradecanoylphorbol Acetate; Transferrin

1999
The assessment of serum nontransferrin-bound iron in chelation therapy and iron supplementation.
    Blood, 2000, May-01, Volume: 95, Issue:9

    Topics: beta-Thalassemia; Chelating Agents; Deferoxamine; Dietary Supplements; Drug Monitoring; Enzyme-Linked Immunosorbent Assay; Humans; Iron; Red-Cell Aplasia, Pure; Transferrin; Transfusion Reaction

2000
[Thalassemia minor: case report].
    Wiadomosci lekarskie (Warsaw, Poland : 1960), 2001, Volume: 54, Issue:7-8

    Topics: Adult; beta-Thalassemia; Humans; Male; Transferrin

2001
Oxidative status and malondialdehyde in beta-thalassaemia patients.
    European journal of clinical investigation, 2002, Volume: 32 Suppl 1

    Topics: Adult; Antioxidants; beta-Thalassemia; Female; Humans; Iron; Iron Chelating Agents; Iron Overload; Male; Malondialdehyde; Middle Aged; Oxidative Stress; Peroxides; Transferrin

2002
Serum non-transferrin-bound iron in beta-thalassaemia major patients treated with desferrioxamine and L1.
    British journal of haematology, 1992, Volume: 82, Issue:2

    Topics: Adolescent; Adult; beta-Thalassemia; Child; Child, Preschool; Deferiprone; Deferoxamine; Ferritins; Humans; Iron; Iron Chelating Agents; Patient Compliance; Pyridones; Transferrin

1992