transferrin has been researched along with Anemia, Cooley's in 64 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 3 (4.69) | 18.7374 |
1990's | 13 (20.31) | 18.2507 |
2000's | 13 (20.31) | 29.6817 |
2010's | 31 (48.44) | 24.3611 |
2020's | 4 (6.25) | 2.80 |
Authors | Studies |
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Altermatt, P; Doucerain, C; Dürrenberger, F; Flace, A; Ingoglia, G; Kalleda, N; Manolova, V; Nyffenegger, N | 1 |
Adly, A; Ebeid, FSE; Elalfy, MS; Fradette, C; Hamdy, M; Lee, D; Rozova, A; Temin, NT; Tricta, F | 1 |
Azarkeivan, A; Hosseini, S; Janani, L; Sajadi Hezaveh, Z; Shidfar, F | 1 |
Hojjati, MT; Hosseini, T; Naseri, P; Rahmani, R; Safaroghli-Azar, A; Tarighi, S | 1 |
Forni, GL; Pinto, VM | 1 |
Doucerain, C; Dürrenberger, F; Flace, A; Manolova, V; Nyffenegger, N | 1 |
Biemond, BJ; Boshuizen, M; Juffermans, NP; van Bruggen, R; van der Ploeg, K; von Bonsdorff, L; Zeerleder, SS | 1 |
Huang, A; Huang, C; Qin, X; Zhang, M; Zhu, X | 1 |
Knutson, MD | 1 |
Mendes, P; Parmar, JH | 1 |
Acquila, M; Bicocchi, MP; Calvillo, M; Cangemi, G; Dufour, C; Fioredda, F; Gastaldi, R; Gatti, C; Gattorno, M; Martini, A; Melioli, G; Miano, M; Pistorio, A; Riccardi, F | 1 |
Aghajan, M; Booten, S; Casu, C; Freier, S; Gardenghi, S; Guo, S; Monia, BP; Peralta, R; Rivella, S; Watt, A | 1 |
de Swart, L; Maas, RP; Swinkels, DW; Voets, PJ | 1 |
Fleming, MD; Schmidt, PJ | 1 |
Lane, DJ; Richardson, DR | 1 |
Baek, JH; Buehler, PW; Gelderman-Fuhrmann, MP; Opitz, L; Puglia, M; Schaer, CA; Schaer, DJ; Vallelian, F; Vostal, J | 1 |
Biemond, BJ; Brittenham, GM; Cabantchik, ZI; de Swart, L; Evans, PJ; Furman, Y; Galanello, R; Hendriks, JC; Hider, RC; Hod, EA; Janssen, MC; MacKenzie, MA; Mattijssen, VE; Origa, R; Porter, JB; Swinkels, DW; van der Vorm, LN; Wojczyk, B | 1 |
Bao, W; Blanc, L; Chen, H; Choesang, T; Feola, M; Fleming, RE; Follenzi, A; Ginzburg, YZ; Li, G; Li, H; Pham, P; Rivella, S; Sun, S; Westerman, M | 1 |
Arosio, C; Mariani, R; Pelloni, I; Pelucchi, S; Piperno, A | 1 |
Ellervik, C; Hasselbalch, HC; Henriksen, LF; Kanters, JK; Petri, AS | 1 |
An, X; Bao, W; Chen, H; Choesang, T; Feola, M; Fleming, RE; Follenzi, A; Garcia-Santos, D; Ginzburg, YZ; Li, G; Li, H; Li, J; Liu, J; Mohandas, N; Pham, P; Ponka, P; Rivella, S; Sun, S; Zhang, J | 1 |
Ozment, CP; Turi, JL | 1 |
Gohil, NK; Saxena, R; Sharma, M | 1 |
Admoni, O; Fink, D; Koren, A; Levin, C; Tennenbaum-Rakover, Y | 1 |
Bouhassira, EE; Breuer, W; Cabantchik, ZI; Fabry, ME; Ginzburg, YZ; Hall, CB; Li, H; Rybicki, AC; Suzuka, SM; von Bonsdorff, L | 1 |
Chantharaksri, U; Fucharoen, S; Jirasomprasert, T; Jittangprasert, P; Limenta, LM; Morales, NP; Wilairat, P; Yamanont, P | 1 |
Chattipakorn, N; Fucharoen, S; Lailerd, N; Phisalaphong, C; Porter, JB; Srichairatanakool, S; Thephinlap, C; Vadolas, J; Winichagoon, P | 1 |
Bonini-Domingos, CR; Estevão, IF; Peitl Junior, P | 1 |
Abete, C; Carta, MP; Cocco, P; Dessì, S; Lai, ME; Mandas, A; Spiga, A; Vacquer, S | 1 |
Castro, JA; Ferragut, JF; Guix, P; López-Escribano, H; Parera, MM; Picornell, A; Ramon, MM | 1 |
Dorrington, KL; Lakhal, S; León-Velarde, F; Mole, DR; Nickol, AH; Privat, C; Rivera-Ch, M; Robbins, PA; Smith, TG; Talbot, NP | 1 |
Attar, S; Breuer, W; Cabantchik, ZI; Ghoti, H; Rachmilewitz, E; Sohn, YS; Weiss, G | 1 |
Anderson, GJ; Badrick, AC; Darshan, D; Frazer, DM; McLaren, GD; Wilkins, SJ | 1 |
Barisani, D; Ganz, T; Hayashi, H; Mariani, R; Modignani, GL; Nemeth, E; Pelucchi, S; Piperno, A; Pozzi, M; Ravasi, G; Tomosugi, N; Trombini, P | 1 |
Charoensakdi, R; Chokchaichamnankit, D; Fucharoen, S; Hatairaktham, S; Kalpravidh, RW; Panichkul, N; Siritanaratkul, N; Srisomsap, C; Subhasitanont, P; Svasti, J; Weeraphan, C | 1 |
Lane, DJ; Lawen, A | 1 |
An, X; Chasis, JA; De Franceschi, L; Ginzburg, Y; Li, H; Liu, J; Mohandas, N; Xue, F; Zhang, J | 1 |
Altay, C; Aslan, D | 1 |
BURGIO, GR; LO JACONO, F | 1 |
GIUFFRE, L; PRIOLISI, A | 2 |
Breuer, W; Cabantchik, ZI; Hershko, C; Pootrakul, P; Sametband, M; Sirankapracha, P | 1 |
Coelho, M; Costa, L; Faustino, P; Ferreira, L; Fonseca, A; Martins, R; Miranda, A; Nunes, B; Picanço, I; Rodrigues, O; Romão, L; Seixas, T | 1 |
De Gobbi, M; Miniero, R; Roetto, A; Tardivo, I | 1 |
Caruso, V; Dürken, M; Engelhardt, R; Fischer, R; Grosse, R; Janka, GE; Lund, U; Magnano, C; Nielsen, P | 1 |
Faa, G; Galanello, R; Ganz, T; Giagu, N; Maccioni, L; Nemeth, E; Origa, R | 1 |
Arosio, P; Biasiotto, G; Cremonesi, L; Dongiovanni, P; Fargion, S; Fracanzani, AL; Maggioni, M; Pulixi, EA; Valenti, L | 1 |
Fibach, E; Prus, E | 1 |
Iancu, TC; Shiloh, H | 1 |
Peters, TJ; Raja, KB; Simpson, RJ | 1 |
Angelucci, E; Argiolu, F; Baronciani, D; Becchelli, G; Borgna Pignatti, C; Campisi, S; Careddu, F; Conter, V; De Nunzio, A; Giardini, C | 1 |
Williamson, B | 1 |
Cheung, MC; Goldberg, JD; Kan, YW | 1 |
Cooper, CE; Porter, JB | 1 |
AL-Refaie, F; Cochrane, J; Davis, B; Hoffbrand, AV; Jackson, BF; Prescott, E; Siritanakatkul, N; Wonke, B | 1 |
Angelucci, E; Annibali, M; Baronciani, D; Erer, B; Galimberti, M; Gaziev, D; Giardini, C; Lucarelli, G; Muretto, P; Polchi, P; Rapa, S; Ripalti, M | 1 |
Collell, M; Dresow, B; Dürken, M; Engelhardt, R; Fischer, R; Nielsen, P; Piga, A; Politis, C; Reller, K | 1 |
Luo, LY; Rees, DC; Singh, BM; Thein, SL; Wickramasinghe, S | 1 |
Bartfay, WJ; Lehotay, DC; Liu, PP; Sher, GD | 1 |
Boelaert, JR; Cantinieaux, B; Cornu, G; Fondu, P; Janssens, A; Kerrels, V; Lejeune, M; Vermylen, C; Winand, J | 1 |
Abramov, A; Breuer, W; Cabantchik, ZI; Hershko, C; Ronson, A; Slotki, IN | 1 |
Kazimierska, E; Swiatkowska-Stodulska, R; Weyer-Hepka, J | 1 |
Bortone, L; Cappellini, MD; Cighetti, G; Duca, L; Fiorelli, G; Nava, I; Sala, S | 1 |
al-Refaie, FN; Hoffbrand, AV; Kontoghiorghes, GJ; Wickens, DG; Wonke, B | 1 |
11 review(s) available for transferrin and Anemia, Cooley's
Article | Year |
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Management of Iron Overload in Beta-Thalassemia Patients: Clinical Practice Update Based on Case Series.
Topics: Adult; beta-Thalassemia; Blood Transfusion; Cardiomyopathies; Chelation Therapy; Deferoxamine; Drug Monitoring; Female; Heart; Humans; Iron; Iron Chelating Agents; Iron Overload; Liver; Male; Middle Aged; Pancreas; Transferrin; Transfusion Reaction | 2020 |
Therapeutic use of transferrin to modulate anemia and conditions of iron toxicity.
Topics: Anemia; Animals; beta-Thalassemia; Demyelinating Diseases; Humans; Hyperoxia; Iron Overload; Lung Injury; Macular Degeneration; Oxidative Stress; Reperfusion Injury; Stem Cell Transplantation; Transferrin | 2017 |
Non-transferrin-bound iron transporters.
Topics: beta-Thalassemia; Calcium Channels, L-Type; Calcium Channels, N-Type; Cation Transport Proteins; Hemochromatosis; Humans; Ion Transport; Iron; Iron Overload; Liver; Transcription Factors; Transferrin; TRPC6 Cation Channel | 2019 |
[Non-transferrin-bound iron: a promising biomarker in iron overload disorders].
Topics: Anemia, Sickle Cell; beta-Thalassemia; Biomarkers; Hemochromatosis; Humans; Iron; Iron Overload; Myelodysplastic Syndromes; Oxidation-Reduction; Reactive Oxygen Species; Transferrin | 2013 |
Modulation of hepcidin as therapy for primary and secondary iron overload disorders: preclinical models and approaches.
Topics: Animals; beta-Thalassemia; Disease Models, Animal; Gene Expression; Genistein; Hepcidins; Humans; Iron; Iron Overload; Transferrin | 2014 |
The active role of vitamin C in mammalian iron metabolism: much more than just enhanced iron absorption!
Topics: Anemia; Animals; Ascorbic Acid; Astrocytes; Basic Helix-Loop-Helix Transcription Factors; beta-Thalassemia; Biological Transport; Erythropoiesis; Ferritins; Hemochromatosis; Humans; Hypoxia-Inducible Factor 1, alpha Subunit; Iron; Transferrin | 2014 |
Increased iron stores prolong the QT interval - a general population study including 20 261 individuals and meta-analysis of thalassaemia major.
Topics: Adult; Aged; Aged, 80 and over; beta-Thalassemia; Case-Control Studies; Female; Ferritins; Hemochromatosis; Humans; Inflammation; Iron; Iron Overload; Long QT Syndrome; Male; Middle Aged; Netherlands; Sex Factors; Transferrin; Young Adult | 2016 |
Iron overload following red blood cell transfusion and its impact on disease severity.
Topics: Anemia, Hemolytic, Congenital; beta-Thalassemia; Cardiomyopathies; Erythrocyte Transfusion; Humans; Infant, Newborn; Infant, Premature, Diseases; Iron; Iron Chelating Agents; Iron Overload; Liver Diseases; Transferrin | 2009 |
Mammalian iron homeostasis in health and disease: uptake, storage, transport, and molecular mechanisms of action.
Topics: Anemia; Animals; beta-Thalassemia; Biological Transport; Cation Transport Proteins; Gene Expression Regulation; Hemochromatosis; Hepcidins; Homeostasis; Humans; Iron; Proteolysis; Transferrin | 2013 |
Morphologic observations in iron overload: an update.
Topics: Animals; beta-Thalassemia; Birds; Diet; Ferritins; Heart; Hemochromatosis; Hemosiderin; Humans; Infant; Infant, Newborn; Iron; Lemur; Mice; Mice, Mutant Strains; Myocardium; Neuroblastoma; Reindeer; Transferrin | 1994 |
Ribonucleotide reductase, lipoxygenase and the intracellular low-molecular-weight iron pool.
Topics: beta-Thalassemia; Blood Transfusion; Deferoxamine; Electron Spin Resonance Spectroscopy; Humans; Iron; Iron Chelating Agents; Kinetics; Lipoxygenase; Models, Chemical; Neutrophils; Oxidation-Reduction; Ribonucleotide Reductases; Transferrin | 1997 |
4 trial(s) available for transferrin and Anemia, Cooley's
Article | Year |
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Efficacy and safety of early-start deferiprone in infants and young children with transfusion-dependent beta thalassemia: Evidence for iron shuttling to transferrin in a randomized, double-blind, placebo-controlled, clinical trial (START).
Topics: beta-Thalassemia; Child; Child, Preschool; Ferritins; Humans; Infant; Iron; Iron Chelating Agents; Iron Overload; Pyridones; Transferrin | 2023 |
The effect of quercetin on iron overload and inflammation in β-thalassemia major patients: A double-blind randomized clinical trial.
Topics: Adult; beta-Thalassemia; C-Reactive Protein; Double-Blind Method; Female; Ferritins; Humans; Inflammation; Iron; Iron Overload; Male; Quercetin; Transferrin | 2019 |
Labile plasma iron (LPI) as an indicator of chelatable plasma redox activity in iron-overloaded beta-thalassemia/HbE patients treated with an oral chelator.
Topics: beta-Thalassemia; Biomarkers; Deferiprone; Erythrocyte Membrane; Follow-Up Studies; Hemoglobin E; Humans; Iron; Iron Chelating Agents; Iron Overload; Oxidation-Reduction; Predictive Value of Tests; Pyridones; Transferrin | 2004 |
Long-term trial of deferiprone in 51 transfusion-dependent iron overloaded patients.
Topics: Adult; Aged; Aged, 80 and over; Anemia, Sickle Cell; beta-Thalassemia; Blood Transfusion; Chelating Agents; Chelation Therapy; Combined Modality Therapy; Deferiprone; Female; Hemoglobins; Humans; Iron; Iron Overload; Liver; Male; Middle Aged; Pyridones; Splenectomy; Transferrin; Transfusion Reaction | 1998 |
49 other study(ies) available for transferrin and Anemia, Cooley's
Article | Year |
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Ferroportin inhibitor vamifeport ameliorates ineffective erythropoiesis in a mouse model of β-thalassemia with blood transfusions.
Topics: Animals; beta-Thalassemia; Blood Transfusion; Erythropoiesis; Humans; Iron; Iron Overload; Mice; Thalassemia; Transferrin | 2023 |
Investigation of correlation between H63D and C282Y mutations in HFE gene and serum Ferritin level in beta-thalassemia major patients.
Topics: Alleles; beta 2-Microglobulin; beta-Thalassemia; Blood Transfusion; Cross-Sectional Studies; Female; Ferritins; Gene Frequency; Hemochromatosis; Hemochromatosis Protein; Humans; Iran; Iron Overload; Male; Point Mutation; Prognosis; Receptors, Transferrin; Transferrin; Transfusion Reaction | 2019 |
The Oral Ferroportin Inhibitor VIT-2763 Improves Erythropoiesis without Interfering with Iron Chelation Therapy in a Mouse Model of β-Thalassemia.
Topics: Administration, Oral; Animals; Benzimidazoles; beta-Thalassemia; Cation Transport Proteins; Cells, Cultured; Deferasirox; Drug Combinations; Drug Interactions; Erythropoiesis; Female; Iron; Iron Chelating Agents; Male; Mice; Mice, Inbred C57BL; Oxazoles; Pyridines; Transferrin | 2021 |
Analysis of Glycosylation Profiles of Serum Glycoprotein from Iron Overload Thalassemia.
Topics: Adolescent; Adult; alpha-Thalassemia; beta-Thalassemia; Databases, Protein; Female; Ferritins; Glycoproteins; Glycosylation; Hepcidins; Humans; Iron Overload; Lectins; Male; Middle Aged; Protein Array Analysis; Reproducibility of Results; Transferrin; Young Adult | 2018 |
A computational model to understand mouse iron physiology and disease.
Topics: Animals; beta-Thalassemia; Computational Biology; Iron; Iron Metabolism Disorders; Liver; Mice; Models, Biological; Transferrin | 2019 |
Diagnostic potential of hepcidin testing in pediatrics.
Topics: Adolescent; Adult; Anemia; Anemia, Iron-Deficiency; Antimicrobial Cationic Peptides; Arthritis, Juvenile; beta-Thalassemia; Biomarkers; Case-Control Studies; Child; Child, Preschool; Female; Hepcidins; Humans; Interleukin 1 Receptor Antagonist Protein; Iron; Iron, Dietary; Male; Puberty; Reference Values; Transferrin; Young Adult | 2013 |
Reducing TMPRSS6 ameliorates hemochromatosis and β-thalassemia in mice.
Topics: Animals; Antimicrobial Cationic Peptides; beta-Thalassemia; Cells, Cultured; Female; Gene Knockdown Techniques; Hemochromatosis; Hemochromatosis Protein; Hepatocytes; Hepcidins; Histocompatibility Antigens Class I; Iron; Liver; Male; Membrane Proteins; Mice; Mice, Inbred C57BL; Mice, Knockout; Oligonucleotides, Antisense; RNA, Messenger; Serine Endopeptidases; Spleen; Transferrin | 2013 |
Integrative proteome and transcriptome analysis of extramedullary erythropoiesis and its reversal by transferrin treatment in a mouse model of beta-thalassemia.
Topics: Animals; beta-Thalassemia; Disease Models, Animal; Erythropoiesis; Mice; Mice, Inbred C57BL; Proteome; Transcriptome; Transferrin | 2015 |
Second international round robin for the quantification of serum non-transferrin-bound iron and labile plasma iron in patients with iron-overload disorders.
Topics: Adult; Aged; beta-Thalassemia; Blood Transfusion; Female; Hemochromatosis; Humans; Iron; Male; Middle Aged; Myelodysplastic Syndromes; Transferrin | 2016 |
Increased hepcidin in transferrin-treated thalassemic mice correlates with increased liver BMP2 expression and decreased hepatocyte ERK activation.
Topics: Animals; Antibodies, Neutralizing; Apoproteins; beta-Thalassemia; Bone Morphogenetic Protein 2; Bone Morphogenetic Protein 6; Butadienes; Cytokines; Disease Models, Animal; Gene Expression Regulation; Hepatocytes; Hepcidins; Humans; Liver; Mice; Mice, Transgenic; Mitogen-Activated Protein Kinase 1; Mitogen-Activated Protein Kinase 3; Muscle Proteins; Nitriles; Phosphorylation; RNA, Messenger; Signal Transduction; Smad Proteins; Transferrin | 2016 |
Does aceruloplasminemia modulate iron phenotype in thalassemia intermedia?
Topics: alpha-Globins; Base Sequence; beta-Globins; beta-Thalassemia; Ceruloplasmin; Deferoxamine; Exons; Gene Expression; Humans; Introns; Iron; Iron Chelating Agents; Iron Metabolism Disorders; Iron Overload; Male; Middle Aged; Molecular Sequence Data; Mutation; Neurodegenerative Diseases; Phenotype; Transferrin | 2016 |
Decreasing TfR1 expression reverses anemia and hepcidin suppression in β-thalassemic mice.
Topics: Anemia; Animals; Apoproteins; beta-Thalassemia; Erythropoiesis; Hepcidins; Iron Overload; Mice; Receptors, Transferrin; Transferrin | 2017 |
Fluorescence assay of non-transferrin-bound iron in thalassemic sera using bacterial siderophore.
Topics: Adolescent; Adult; Apoproteins; Azotobacter vinelandii; beta-Thalassemia; Calibration; Child; Child, Preschool; Feasibility Studies; Female; Fluorescence; Humans; India; Iron; Male; Siderophores; Spectrometry, Fluorescence; Transferrin; Young Adult | 2009 |
Non-transferrin-bound labile plasma iron and iron overload in sickle-cell disease: a comparative study between sickle-cell disease and beta-thalassemic patients.
Topics: Adolescent; Adult; Anemia, Sickle Cell; beta-Thalassemia; Chelation Therapy; Child; Cohort Studies; Comorbidity; Endocrine System Diseases; Ferritins; Greece; Hepatitis C, Chronic; Humans; Hypersplenism; Inflammation; Iron; Iron Chelating Agents; Iron Overload; Myocardium; Splenectomy; Transferrin; Transfusion Reaction; Young Adult | 2010 |
Transferrin therapy ameliorates disease in beta-thalassemic mice.
Topics: Animals; Apoptosis; beta-Thalassemia; Cell Survival; Disease Models, Animal; Erythropoietin; Hematopoiesis, Extramedullary; Mice; Splenomegaly; Transferrin | 2010 |
Pharmacokinetics of deferiprone in patients with β-thalassaemia: impact of splenectomy and iron status.
Topics: Administration, Oral; Adult; Area Under Curve; beta-Thalassemia; Deferiprone; Female; Ferritins; Hemoglobin E; Humans; Iron; Iron Chelating Agents; Iron Overload; Male; Pyridones; Splenectomy; Transferrin; Transfusion Reaction | 2011 |
Reversal of cardiac iron loading and dysfunction in thalassemic mice by curcuminoids.
Topics: Animals; beta-Thalassemia; Curcumin; Heart; Heart Rate; Humans; Iron; Iron Chelating Agents; Iron Overload; Iron, Dietary; Lipid Peroxidation; Male; Malondialdehyde; Mice; Mice, Inbred C57BL; Mice, Knockout; Transferrin | 2011 |
Serum ferritin and transferrin saturation levels in β⁰ and β(+) thalassemia patients.
Topics: Adult; Age Factors; Aged; Aged, 80 and over; beta-Thalassemia; Female; Ferritins; Hemochromatosis; Heterozygote; Humans; Iron; Male; Middle Aged; Mutation; Polymerase Chain Reaction; Sex Factors; Transferrin | 2011 |
Evidence for a proatherogenic biochemical phenotype in beta thalassemia minor and intermedia.
Topics: Acetyl-CoA C-Acetyltransferase; Adult; Antimicrobial Cationic Peptides; Atherosclerosis; beta-Thalassemia; Cholesterol, HDL; Erythropoietin; Female; Hepcidins; Humans; Interleukin-1alpha; Iron; Italy; Leukocytes, Mononuclear; Male; Middle Aged; Oxidative Stress; Phenotype; Risk Factors; RNA, Messenger; Severity of Illness Index; Sterol Esterase; Transferrin; Tumor Necrosis Factor-alpha | 2011 |
Effect of co-inheritance of β-thalassemia and hemochromatosis mutations on iron overload.
Topics: beta-Thalassemia; DNA Mutational Analysis; Female; Ferritins; Genotype; Hemochromatosis; Hemochromatosis Protein; Histocompatibility Antigens Class I; Humans; Iron Overload; Male; Membrane Proteins; Mutation; Retrospective Studies; Spain; Transferrin | 2012 |
Regulation of hepcidin expression at high altitude.
Topics: Adult; Altitude; Antimicrobial Cationic Peptides; beta-Thalassemia; Case-Control Studies; Erythropoiesis; Erythropoietin; Ferritins; Gene Expression Regulation; Growth Differentiation Factor 15; Hepcidins; Homeostasis; Humans; Hypoxia; Iron; Iron Metabolism Disorders; Iron, Dietary; Transferrin | 2012 |
The role of endocytic pathways in cellular uptake of plasma non-transferrin iron.
Topics: Adolescent; Adult; beta-Thalassemia; Biological Transport; Biomarkers; Cells, Cultured; Cytosol; Endocytosis; Endosomes; Humans; Insulinoma; Iron; Iron Chelating Agents; Macrophages; Microscopy, Fluorescence; Myocytes, Cardiac; Transferrin; Young Adult | 2012 |
Stimulated erythropoiesis with secondary iron loading leads to a decrease in hepcidin despite an increase in bone morphogenetic protein 6 expression.
Topics: Anemia, Hemolytic; Animals; Antimicrobial Cationic Peptides; beta-Thalassemia; Bone Morphogenetic Protein 6; Disease Models, Animal; Erythropoiesis; Extracellular Signal-Regulated MAP Kinases; Female; Growth Differentiation Factor 15; Hemolysis; Hepcidins; Iron Overload; Male; Mice; Mice, Inbred C57BL; Mice, Transgenic; Phenylhydrazines; Phosphorylation; Receptors, Transferrin; Signal Transduction; Smad Proteins; Spleen; Transferrin | 2012 |
Hepcidin expression in iron overload diseases is variably modulated by circulating factors.
Topics: Adult; Aged; Antimicrobial Cationic Peptides; beta-Thalassemia; Biopsy; Cytokines; Gene Expression Regulation; Hemochromatosis; Hemochromatosis Protein; Hep G2 Cells; Hepcidins; Histocompatibility Antigens Class I; Humans; Iron; Iron Overload; Liver; Membrane Proteins; Middle Aged; RNA, Messenger; Transferrin | 2012 |
Role of curcuminoids in ameliorating oxidative modification in β-thalassemia/Hb E plasma proteome.
Topics: Adult; Antioxidants; beta-Thalassemia; Curcuma; Dietary Supplements; Female; Hemoglobin E; Humans; Iron Chelating Agents; Iron Overload; Male; Middle Aged; Oxidative Stress; Plant Extracts; Protein Carbonylation; Proteome; Proteomics; Transferrin; Up-Regulation; Young Adult | 2013 |
Quantitative analysis of murine terminal erythroid differentiation in vivo: novel method to study normal and disordered erythropoiesis.
Topics: Anemia; Animals; beta-Thalassemia; Bone Marrow Cells; Cell Differentiation; Cell Separation; Disease Progression; Erythroblasts; Erythropoiesis; Female; Flow Cytometry; Hematopoietic Stem Cells; Male; Mice; Mice, Inbred C57BL; Mice, Knockout; Reproducibility of Results; Spleen; Transferrin | 2013 |
Incidence of high erythrocyte count in infants and young children with iron deficiency anemia: re-evaluation of an old parameter.
Topics: Age Factors; Anemia, Hypochromic; beta-Thalassemia; Child, Preschool; Diagnosis, Differential; Erythrocyte Count; Erythrocyte Indices; Female; Ferritins; Hematocrit; Hemoglobins; Humans; Incidence; Infant; Iron; Male; Polycythemia; Transferrin | 2003 |
[Changes in transferrin following the administration of iron preparations in normal children and those with blood disorders].
Topics: Anemia; Anemia, Pernicious; beta-Thalassemia; Blood; Blood Proteins; Erythroblasts; Humans; Iron; Iron Compounds; Transferrin | 1952 |
[IMMUNOELECTROPHORETIC STUDY OF THE BLOOD IN THALASSEMIA MAJOR AND ITS RELATION TO SPLENECTOMY].
Topics: beta-Thalassemia; Ceruloplasmin; Haptoglobins; Humans; Immunoelectrophoresis; Lipoproteins; Serum Globulins; Splenectomy; Thalassemia; Transferrin | 1963 |
[ON SOME PARTICULAR ASPECTS OF IRON KINETICS IN SUBJECTS WITH THALASSEMIA MAJOR].
Topics: beta-Thalassemia; Hematologic Tests; Humans; Iron; Iron Isotopes; Kinetics; Thalassemia; Transferrin | 1964 |
The role of HFE mutations on iron metabolism in beta-thalassemia carriers.
Topics: Alleles; Amino Acid Substitution; beta-Thalassemia; Female; Gene Frequency; Hemochromatosis; Hemochromatosis Protein; Heterozygote; Histocompatibility Antigens Class I; Humans; Iron; Male; Membrane Proteins; Point Mutation; Quantitative Trait Loci; Transferrin | 2004 |
Heterozygous beta-thalassemia and homozygous H63D hemochromatosis in a child: an 18-year follow-up.
Topics: Age Factors; beta-Thalassemia; Child, Preschool; Ferritins; Hemochromatosis; Hemoglobins; Heterozygote; Homozygote; Humans; Iron; Longitudinal Studies; Male; Mutation, Missense; Transferrin | 2005 |
Non-transferrin-bound iron during blood transfusion cycles in beta-thalassemia major.
Topics: Adolescent; Adult; beta-Thalassemia; Blood Specimen Collection; Blood Transfusion; Chelation Therapy; Combined Modality Therapy; Deferoxamine; Drug Administration Schedule; Humans; Iron; Iron Chelating Agents; Liver; Magnetic Resonance Imaging; Prospective Studies; Receptors, Transferrin; Reproducibility of Results; Time Factors; Transferrin | 2005 |
Liver iron concentrations and urinary hepcidin in beta-thalassemia.
Topics: Adolescent; Adult; Antimicrobial Cationic Peptides; beta-Thalassemia; Blood Transfusion; Chelation Therapy; Combined Modality Therapy; Deferoxamine; Erythropoiesis; Female; Ferritins; Gene Expression Regulation; Hepcidins; Humans; Intestinal Absorption; Iron; Iron Chelating Agents; Iron Overload; Iron, Dietary; Liver; Macrophages; Male; Severity of Illness Index; Transferrin | 2007 |
Relative contribution of iron genes, dysmetabolism and hepatitis C virus (HCV) in the pathogenesis of altered iron regulation in HCV chronic hepatitis.
Topics: Adult; Antimicrobial Cationic Peptides; beta-Thalassemia; Cation Transport Proteins; Cholesterol, LDL; Fatty Liver; Ferritins; Genotype; GPI-Linked Proteins; Hemochromatosis Protein; Hepacivirus; Hepatitis C, Chronic; Hepcidins; Histocompatibility Antigens Class I; Humans; Iron; Iron Overload; Liver; Liver Cirrhosis; Male; Membrane Proteins; Middle Aged; Mutation; Promoter Regions, Genetic; Receptors, Transferrin; Transferrin | 2007 |
The labile iron pool in human erythroid cells.
Topics: Antigens, CD; beta-Thalassemia; Bone Marrow Cells; Cells, Cultured; Deferiprone; Erythroblasts; Erythrocytes; Erythropoiesis; Flow Cytometry; Fluoresceins; Fluorescent Dyes; Humans; Iron; Iron Chelating Agents; Pyridones; Reticulocytes; Transferrin | 2008 |
Intestinal iron absorption studies in mouse models of iron-overload.
Topics: alpha-Thalassemia; Animals; beta-Thalassemia; Body Weight; Disease Models, Animal; Intestinal Absorption; Iron; Male; Mice; Mice, Inbred BALB C; Mice, Inbred C57BL; Thalassemia; Transferrin | 1994 |
Iron removal in ex-thalassemics after BMT: preliminary results from the phlebotomy program. Italian Cooperative Group for Phlebotomy in Ex-thalassemic.
Topics: Adolescent; Adult; Anemia; beta-Thalassemia; Bloodletting; Bone Marrow Transplantation; Child; Combined Modality Therapy; Ferritins; Hemochromatosis; Humans; Iron; Liver Diseases; Postoperative Period; Shock; Transferrin; Transfusion Reaction | 1993 |
Towards non-invasive prenatal diagnosis.
Topics: Amniocentesis; beta-Thalassemia; Cell Nucleus; Chorionic Villi Sampling; Cytodiagnosis; Erythroblasts; Female; Fetus; Humans; Polymerase Chain Reaction; Pregnancy; Prenatal Diagnosis; Transferrin | 1996 |
Prenatal diagnosis of sickle cell anaemia and thalassaemia by analysis of fetal cells in maternal blood.
Topics: Anemia, Sickle Cell; Antibodies; beta-Thalassemia; Erythrocytes; Female; Fetus; Hemoglobins; Humans; Immunomagnetic Separation; Microscopy; Polymerase Chain Reaction; Pregnancy; Prenatal Diagnosis; Transferrin | 1996 |
Treatment of iron overload in the "ex-thalassemic". Report from the phlebotomy program.
Topics: Adolescent; Alanine Transaminase; beta-Thalassemia; Bone Marrow Transplantation; Female; Ferritins; Follow-Up Studies; Humans; Iron; Liver; Male; Morbidity; Phlebotomy; Postoperative Complications; Time Factors; Transferrin | 1998 |
Iron overload and antioxidant status in patients with beta-thalassemia major.
Topics: Antioxidants; Ascorbic Acid; beta-Thalassemia; Deferoxamine; Humans; Iron; Iron Chelating Agents; Liver; Transferrin; Vitamin A; Vitamin E | 1998 |
Nontransfusional iron overload in thalassemia. Association with hereditary hemochromatosis.
Topics: Adolescent; Adult; Aged; beta-Thalassemia; Blood Transfusion; Child; DNA; Female; Ferritins; Globins; Hemochromatosis; Hemochromatosis Protein; Hemoglobins; Histocompatibility Antigens Class I; HLA Antigens; Humans; Iron; Male; Membrane Proteins; Middle Aged; Point Mutation; Transferrin | 1998 |
Effect of transfusion on lipid peroxidation products in the plasma of thalassemic patients.
Topics: Aldehydes; beta-Thalassemia; Biomarkers; Chelation Therapy; Deferiprone; Deferoxamine; Erythrocyte Transfusion; Free Radicals; Humans; Iron; Iron Chelating Agents; Iron Overload; Lipid Peroxidation; Pilot Projects; Pyridones; Transferrin | 1999 |
Ferritin-associated iron induces neutrophil dysfunction in hemosiderosis.
Topics: Adolescent; beta-Thalassemia; Blood Transfusion; Catalase; Chelating Agents; Child; Child, Preschool; Deferoxamine; Female; Ferritins; Hemosiderosis; Humans; Iron; Luminescent Measurements; Male; Neutrophils; Phagocytosis; Tetradecanoylphorbol Acetate; Transferrin | 1999 |
The assessment of serum nontransferrin-bound iron in chelation therapy and iron supplementation.
Topics: beta-Thalassemia; Chelating Agents; Deferoxamine; Dietary Supplements; Drug Monitoring; Enzyme-Linked Immunosorbent Assay; Humans; Iron; Red-Cell Aplasia, Pure; Transferrin; Transfusion Reaction | 2000 |
[Thalassemia minor: case report].
Topics: Adult; beta-Thalassemia; Humans; Male; Transferrin | 2001 |
Oxidative status and malondialdehyde in beta-thalassaemia patients.
Topics: Adult; Antioxidants; beta-Thalassemia; Female; Humans; Iron; Iron Chelating Agents; Iron Overload; Male; Malondialdehyde; Middle Aged; Oxidative Stress; Peroxides; Transferrin | 2002 |
Serum non-transferrin-bound iron in beta-thalassaemia major patients treated with desferrioxamine and L1.
Topics: Adolescent; Adult; beta-Thalassemia; Child; Child, Preschool; Deferiprone; Deferoxamine; Ferritins; Humans; Iron; Iron Chelating Agents; Patient Compliance; Pyridones; Transferrin | 1992 |