Page last updated: 2024-11-05

thiotepa and Anhidrotic Ectodermal Dysplasia

thiotepa has been researched along with Anhidrotic Ectodermal Dysplasia in 1 studies

Thiotepa: A very toxic alkylating antineoplastic agent also used as an insect sterilant. It causes skin, gastrointestinal, CNS, and bone marrow damage. According to the Fourth Annual Report on Carcinogens (NTP 85-002, 1985), thiotepa may reasonably be anticipated to be a carcinogen (Merck Index, 11th ed).

Research Excerpts

ExcerptRelevanceReference
"X-linked EDA-ID1 (ectodermal dysplasia, anhidrotic, with immunodeficiency 1, Online Mendelian Inheritance in Man [OMIM] 300291), or NEMO (nuclear factor kappa B essential modulator) deficiency syndrome, is caused by mutations in the IKBKG/NEMO gene."1.56Successful Allogeneic Stem Cell Transplantation in Nuclear Factor-Kappa B Essential Modulator Deficiency Syndrome After Treosulfan-Based Conditioning: A Case Report. ( Bąbol-Pokora, K; Dąbrowska-Leonik, N; Frączkiewicz, J; Gul, K; Janeczko-Czarnecka, M; Kałwak, K; Martuszewski, A; Mielcarek-Siedziuk, M; Młynarski, W; Nowak, M; Paluszkiewicz, P; Salamonowicz-Bodzioch, M; Sierżęga-Staykov, K; Ussowicz, M; Wawrzyniak-Dzierżek, E; Wolska-Kuśnierz, B, 2020)

Research

Studies (1)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's1 (100.00)2.80

Authors

AuthorsStudies
Martuszewski, A1
Paluszkiewicz, P1
Sierżęga-Staykov, K1
Wawrzyniak-Dzierżek, E1
Salamonowicz-Bodzioch, M1
Frączkiewicz, J1
Janeczko-Czarnecka, M1
Mielcarek-Siedziuk, M1
Nowak, M1
Dąbrowska-Leonik, N1
Wolska-Kuśnierz, B1
Gul, K1
Bąbol-Pokora, K1
Młynarski, W1
Kałwak, K1
Ussowicz, M1

Other Studies

1 other study available for thiotepa and Anhidrotic Ectodermal Dysplasia

ArticleYear
Successful Allogeneic Stem Cell Transplantation in Nuclear Factor-Kappa B Essential Modulator Deficiency Syndrome After Treosulfan-Based Conditioning: A Case Report.
    Transplantation proceedings, 2020, Volume: 52, Issue:2

    Topics: Antilymphocyte Serum; Busulfan; Ectodermal Dysplasia; Hematopoietic Stem Cell Transplantation; Human

2020