thiosulfates has been researched along with Pseudoxanthoma Elasticum in 2 studies
Thiosulfates: Inorganic salts of thiosulfuric acid possessing the general formula R2S2O3.
thiosulfate(2-) : A divalent inorganic anion obtained by removal of both protons from thiosulfuric acid.
Pseudoxanthoma Elasticum: An inherited disorder of connective tissue with extensive degeneration and calcification of ELASTIC TISSUE primarily in the skin, eye, and vasculature. At least two forms exist, autosomal recessive and autosomal dominant. This disorder is caused by mutations of one of the ATP-BINDING CASSETTE TRANSPORTERS. Patients are predisposed to MYOCARDIAL INFARCTION and GASTROINTESTINAL HEMORRHAGE.
| Excerpt | Relevance | Reference |
|---|---|---|
| " Numerous side-effects prompted dosage adjustment to 10 g intravenously daily." | 5.56 | Severe early-onset manifestations of pseudoxanthoma elasticum resulting from the cumulative effects of several deleterious mutations in ENPP1, ABCC6 and HBB: transient improvement in ectopic calcification with sodium thiosulfate. ( Bourrat, E; Kauffenstein, G; Leftheriotis, G; Martin, L; Navasiolava, N; Nitschke, Y; Omarjee, L; Rutsch, F; Vanakker, OM; Verschuere, S; Vignon, MD, 2020) |
| " Numerous side-effects prompted dosage adjustment to 10 g intravenously daily." | 1.56 | Severe early-onset manifestations of pseudoxanthoma elasticum resulting from the cumulative effects of several deleterious mutations in ENPP1, ABCC6 and HBB: transient improvement in ectopic calcification with sodium thiosulfate. ( Bourrat, E; Kauffenstein, G; Leftheriotis, G; Martin, L; Navasiolava, N; Nitschke, Y; Omarjee, L; Rutsch, F; Vanakker, OM; Verschuere, S; Vignon, MD, 2020) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 2 (100.00) | 2.80 |
| Authors | Studies |
|---|---|
| Omarjee, L | 1 |
| Nitschke, Y | 1 |
| Verschuere, S | 1 |
| Bourrat, E | 1 |
| Vignon, MD | 1 |
| Navasiolava, N | 1 |
| Leftheriotis, G | 1 |
| Kauffenstein, G | 1 |
| Rutsch, F | 1 |
| Vanakker, OM | 1 |
| Martin, L | 1 |
| Boyce, AM | 1 |
| Gafni, RI | 1 |
| Ferreira, CR | 1 |
1 review available for thiosulfates and Pseudoxanthoma Elasticum
| Article | Year |
|---|---|
Generalized Arterial Calcification of Infancy: New Insights, Controversies, and Approach to Management.
Topics: Adenosine Monophosphate; Bone Density Conservation Agents; Calcinosis; Cardiovascular Agents; Chelat | 2020 |
1 other study available for thiosulfates and Pseudoxanthoma Elasticum
| Article | Year |
|---|---|
Severe early-onset manifestations of pseudoxanthoma elasticum resulting from the cumulative effects of several deleterious mutations in ENPP1, ABCC6 and HBB: transient improvement in ectopic calcification with sodium thiosulfate.
Topics: Calcinosis; Humans; Male; Multidrug Resistance-Associated Proteins; Mutation; Phenotype; Phosphoric | 2020 |