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thioctic acid and Inborn Errors of Metabolism

thioctic acid has been researched along with Inborn Errors of Metabolism in 2 studies

Thioctic Acid: An octanoic acid bridged with two sulfurs so that it is sometimes also called a pentanoic acid in some naming schemes. It is biosynthesized by cleavage of LINOLEIC ACID and is a coenzyme of oxoglutarate dehydrogenase (KETOGLUTARATE DEHYDROGENASE COMPLEX). It is used in DIETARY SUPPLEMENTS.

Research Excerpts

ExcerptRelevanceReference
" This infant was found to have lactic acidosis, low cerebrospinal fluid glucose, hyperalaninemia, and increased levels of urine lactate, pyruvate and alanine."7.65Hyperalaninemia hyperpyruvicemia and lactic acidosis due to pyruvate carboxylase deficiency of the liver; treatment with thiamine and lipoic acid. ( Komiya, K; Maesaka, H; Misugi, K; Tada, K, 1976)
" This infant was found to have lactic acidosis, low cerebrospinal fluid glucose, hyperalaninemia, and increased levels of urine lactate, pyruvate and alanine."3.65Hyperalaninemia hyperpyruvicemia and lactic acidosis due to pyruvate carboxylase deficiency of the liver; treatment with thiamine and lipoic acid. ( Komiya, K; Maesaka, H; Misugi, K; Tada, K, 1976)

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19902 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Maesaka, H1
Komiya, K1
Misugi, K1
Tada, K1
Clayton, BE1
Dobbs, RH1
Patrick, AD1

Other Studies

2 other studies available for thioctic acid and Inborn Errors of Metabolism

ArticleYear
Hyperalaninemia hyperpyruvicemia and lactic acidosis due to pyruvate carboxylase deficiency of the liver; treatment with thiamine and lipoic acid.
    European journal of pediatrics, 1976, May-04, Volume: 122, Issue:2

    Topics: Acidosis; Alanine; Female; Glucose; Humans; Infant; Intellectual Disability; Lactates; Liver; Metabo

1976
Leigh's subacute necrotizing encephalopathy: clinical and biochemical study, with special reference to therapy with lipoate.
    Archives of disease in childhood, 1967, Volume: 42, Issue:225

    Topics: Blood Chemical Analysis; Brain Diseases; Brain Stem; Child; Child, Preschool; Clinical Enzyme Tests;

1967