thioctic acid has been researched along with Amino Acid Metabolism Disorders, Inborn in 5 studies
Thioctic Acid: An octanoic acid bridged with two sulfurs so that it is sometimes also called a pentanoic acid in some naming schemes. It is biosynthesized by cleavage of LINOLEIC ACID and is a coenzyme of oxoglutarate dehydrogenase (KETOGLUTARATE DEHYDROGENASE COMPLEX). It is used in DIETARY SUPPLEMENTS.
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 4 (80.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 1 (20.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Tort, F | 1 |
Ferrer-Cortès, X | 1 |
Thió, M | 1 |
Navarro-Sastre, A | 1 |
Matalonga, L | 1 |
Quintana, E | 1 |
Bujan, N | 1 |
Arias, A | 1 |
García-Villoria, J | 1 |
Acquaviva, C | 1 |
Vianey-Saban, C | 1 |
Artuch, R | 1 |
García-Cazorla, À | 1 |
Briones, P | 1 |
Ribes, A | 1 |
da COSTA, S | 1 |
da SILVA, J | 1 |
CORREIA, JA | 1 |
MALDONADO, FE | 1 |
ROSSIER, A | 1 |
CALDERA, R | 1 |
ODIEVRE, M | 1 |
Hiraga, K | 1 |
Kochi, H | 1 |
Hayasaka, K | 1 |
Kikuchi, G | 1 |
Nyhan, WL | 1 |
Galamon, T | 1 |
Szulc-Kuberska, J | 1 |
Tronczyńska, J | 1 |
5 other studies available for thioctic acid and Amino Acid Metabolism Disorders, Inborn
Article | Year |
---|---|
Mutations in the lipoyltransferase LIPT1 gene cause a fatal disease associated with a specific lipoylation defect of the 2-ketoacid dehydrogenase complexes.
Topics: Acidosis, Lactic; Acyltransferases; Amino Acid Metabolism, Inborn Errors; Animals; Cells, Cultured; | 2014 |
[Metabolic significance of alpha-lipoic acid. V. Comparative action of alpha-lipoic acid, vitamin B 12 and cocarboxylase on metabolism of copper and iron and on aminoacidurias. (Further observations)].
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Copper; Corrinoids; Hematinics; Humans; Iron; Pro | 1963 |
[RECENT IDEAS ON CYSTINOSIS].
Topics: Amino Acid Metabolism, Inborn Errors; Blood Chemical Analysis; Citric Acid Cycle; Cystinosis; Dimerc | 1963 |
Defective glycine cleavage system in nonketotic hyperglycinemia. Occurrence of a less active glycine decarboxylase and an abnormal aminomethyl carrier protein.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acid Oxidoreductases; Aminomethyltransferase; Brain; Car | 1981 |
Studies on the effect of alpha-lipoic acid on disturbances in histidine metabolism.
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Child; Decarboxylation; Histidine; Humans; Ketoglu | 1971 |