thiamine has been researched along with Amino Acid Metabolism Disorders, Inborn in 10 studies
thiamine(1+) : A primary alcohol that is 1,3-thiazol-3-ium substituted by (4-amino-2-methylpyrimidin-5-yl)methyl, methyl and 2-hydroxyethyl groups at positions 3, 4 and 5, respectively.
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 10 (100.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
PASCOLI, F | 1 |
DE CARLI, E | 1 |
Bartlett, K | 1 |
Cardi, E | 1 |
Casey, RE | 1 |
Zaleski, WA | 1 |
Philp, M | 1 |
Mendelson, IS | 1 |
MacKenzie, SL | 1 |
Rosenberg, LE | 1 |
Schreier, K | 1 |
Porath, U | 1 |
Pueschel, SM | 1 |
Bresnan, MJ | 1 |
Shih, VE | 1 |
Levy, HL | 1 |
Hillman, RE | 1 |
Knapp, A | 1 |
2 reviews available for thiamine and Amino Acid Metabolism Disorders, Inborn
Article | Year |
---|---|
Vitamin-responsive inborn errors of metabolism.
Topics: Acetyl-CoA Carboxylase; Acidosis; Amino Acid Metabolism, Inborn Errors; Animals; Biotin; Folic Acid; | 1983 |
[Congenital metabolic acidosis in the postnatal period].
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; G | 1978 |
8 other studies available for thiamine and Amino Acid Metabolism Disorders, Inborn
Article | Year |
---|---|
[Behavior of adrenal cortex in nutritional deficiency. 1. Vitamin B1 and amino acid deficiency].
Topics: Adrenal Cortex; Amino Acid Metabolism, Inborn Errors; Amino Acids; Thiamine; Thiamine Deficiency; Vi | 1957 |
[Inborn errors of amino acid metabolism treatable with B group vitamins: synoptic aspects].
Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Folic Acid; Humans; Nicotinic Acids; Pyridoxine; Thiam | 1980 |
Biochemical and clinical studies of a new case of alpha-aminoadipic aciduria.
Topics: 2-Aminoadipic Acid; Amino Acid Metabolism, Inborn Errors; Amino Acids, Dicarboxylic; Child; Female; | 1978 |
Use of cofactors in inborn errors of amino acid metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Female; Folic Acid; Humans; Infant, Newborn; Niacinami | 1979 |
Thiamine-responsive intermittent branched-chain ketoaciduria.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Child, Preschool; Dietary Protein | 1979 |
Megavitamin responsive aminoacidopathies.
Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Child; Drug Administration Schedule; Folic Acid; Human | 1976 |
Vitamin dependency syndromes.
Topics: Amino Acid Metabolism, Inborn Errors; Biotin; Coenzymes; Humans; Infant; Maple Syrup Urine Disease; | 1972 |
[Modern nutrition problems with special reference to genetic metabolic disorders].
Topics: Adolescent; Adult; Aged; Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Chromatograp | 1970 |