Page last updated: 2024-08-23

sulfur and Amino Acid Metabolism Disorders, Inborn

sulfur has been researched along with Amino Acid Metabolism Disorders, Inborn in 13 studies

Research

Studies (13)

TimeframeStudies, this research(%)All Research%
pre-199011 (84.62)18.7374
1990's0 (0.00)18.2507
2000's1 (7.69)29.6817
2010's0 (0.00)24.3611
2020's1 (7.69)2.80

Authors

AuthorsStudies
Stipanuk, MH1
ALBANESE, AA; HOLT, LE1
Mann, GV; Perry, N1
Finkelstein, JD1
Hansen, S; MacDougall, L; Perry, TL; Warrington, PD1
Cooper, AJ1
Cotton, RC; Danks, DM; Goldsmith, D; Patrick, MG1
Frimpter, GW; Horwith, M; Kozlowski, KK1
Frimpter, GW1
Crawhall, JC; Purkiss, P; Stanbury, JB1
Coignet, J; Laurent, B1
Brown, DA; Turner, B; Wilcken, B1
Berlow, S1

Reviews

5 review(s) available for sulfur and Amino Acid Metabolism Disorders, Inborn

ArticleYear
Metabolism of Sulfur-Containing Amino Acids: How the Body Copes with Excess Methionine, Cysteine, and Sulfide.
    The Journal of nutrition, 2020, 10-01, Volume: 150, Issue:Suppl 1

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Animals; Cystathionine beta-Synthase; Cysteine; Glycine N-Methyltransferase; Homocysteine; Humans; Hydrogen Sulfide; Liver; Methionine; S-Adenosylmethionine; Serine; Sulfides; Sulfur; Thiosulfates

2020
Inborn errors of sulfur-containing amino acid metabolism.
    The Journal of nutrition, 2006, Volume: 136, Issue:6 Suppl

    Topics: Adenosylhomocysteinase; Amino Acid Metabolism, Inborn Errors; Amino Acids, Sulfur; Betaine-Homocysteine S-Methyltransferase; Cystathionine gamma-Lyase; Glycine N-Methyltransferase; Humans; Kidney; Liver; Methionine; Methionine Adenosyltransferase; Sulfur

2006
Biochemistry of sulfur-containing amino acids.
    Annual review of biochemistry, 1983, Volume: 52

    Topics: Adenosine; Amino Acid Metabolism, Inborn Errors; Animals; Cysteine; Deoxyadenosines; Homocysteine; Humans; Methionine; Oxidoreductases; Oxidoreductases Acting on Sulfur Group Donors; S-Adenosylmethionine; Structure-Activity Relationship; Sulfur; Sulfurtransferases; Thionucleosides; Thiosulfate Sulfurtransferase

1983
Aminoacidurias due to inherited disorders of metabolism (first of two parts).
    The New England journal of medicine, 1973, Oct-18, Volume: 289, Issue:16

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Child; Cystathionine; Cysteine; Cystine; Disulfides; Female; Homocystinuria; Humans; Infant, Newborn; Lactates; Male; Methionine; Oxidoreductases; Phenylalanine; Phenylketonurias; Pregnancy; Pyruvates; Sulfhydryl Compounds; Sulfites; Sulfur; Tyrosine

1973
Abnormalities in the metabolism of sulfur-containing amino acids.
    Advances in clinical chemistry, 1967, Volume: 9

    Topics: Amino Acid Metabolism, Inborn Errors; Humans; Sulfur

1967

Other Studies

8 other study(ies) available for sulfur and Amino Acid Metabolism Disorders, Inborn

ArticleYear
Observations on sulfur amino acid deficiencies in rats; chemical and morphological changes in the blood.
    The Journal of biological chemistry, 1946, Volume: 165, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Amino Acids, Sulfur; Animals; Blood; Blood Chemical Analysis; Rats; Sulfur

1946
AMINOACIDURIA AFTER DIETARY LOADING IN HUMAN SUBJECTS.
    The American journal of clinical nutrition, 1964, Volume: 14

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Cystine; Diet; Dietary Proteins; Humans; Kidney; Lysine; Nitrogen; Ornithine; Proteins; Renal Aminoacidurias; Sulfur; Urine

1964
Sulfur-containing amino acids in the plasma and urine of homocystinurics.
    Clinica chimica acta; international journal of clinical chemistry, 1967, Volume: 15, Issue:3

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acids; Child; Child, Preschool; Chromatography, Paper; Homocysteine; Homocystine; Homocystinuria; Humans; Infant; Infant, Newborn; Intellectual Disability; Iodoacetates; Methionine; Sulfoxides; Sulfur; Ultraviolet Rays

1967
A screening test for sulphur-containing metabolites in urine using auxotrophic mutants of Escherichia coli K12.
    Biochemical medicine, 1975, Volume: 12, Issue:3

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Biological Assay; Cystathionine; Cystinuria; Escherichia coli; Homocystinuria; Humans; Infant, Newborn; Methods; Mutation; S-Adenosylhomocysteine; S-Adenosylmethionine; Sulfur

1975
Distribution of sulfur in urine of patients with cystathioninuria before and during administration of pyridoxine.
    Metabolism: clinical and experimental, 1976, Volume: 25, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Cystathionine; Humans; Male; Pyridoxine; Sulfates; Sulfur

1976
Metabolism of sulfur-containing amino acids in a patient excreting -mercaptolactate-cysteine disulfide.
    Biochemical medicine, 1973, Volume: 7, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Autoanalysis; Carbon Isotopes; Cysteine; Cystine; Disulfides; Humans; Intellectual Disability; Lactates; Male; Methionine; Sulfur; Sulfur Isotopes; Taurine; Time Factors

1973
[Cystathionuria and defective enzyme regulation].
    Clinica chimica acta; international journal of clinical chemistry, 1973, Jan-24, Volume: 43, Issue:2

    Topics: Administration, Oral; Amino Acid Metabolism, Inborn Errors; Child; Chromatography, Ion Exchange; Chromatography, Paper; Cystathionine; Cysteine; Electrophoresis, Paper; Female; Homocysteine; Homocystine; Homoserine; Humans; Hydro-Lyases; Hydrocortisone; Liver; Lyases; Methionine; Pyridoxine; Sulfur

1973
Detection of abnormal sulphur-containing amino acid excretion in a mass urine-screening programme.
    The Medical journal of Australia, 1972, Jun-03, Volume: 1, Issue:23

    Topics: Amino Acid Metabolism, Inborn Errors; Cystathionine; Female; Homocystinuria; Humans; Infant; Male; Mass Screening; Methionine; Renal Aminoacidurias; Sulfur

1972