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succinic acid and Biotinidase Deficiency

succinic acid has been researched along with Biotinidase Deficiency in 2 studies

Succinic Acid: A water-soluble, colorless crystal with an acid taste that is used as a chemical intermediate, in medicine, the manufacture of lacquers, and to make perfume esters. It is also used in foods as a sequestrant, buffer, and a neutralizing agent. (Hawley's Condensed Chemical Dictionary, 12th ed, p1099; McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed, p1851)
succinic acid : An alpha,omega-dicarboxylic acid resulting from the formal oxidation of each of the terminal methyl groups of butane to the corresponding carboxy group. It is an intermediate metabolite in the citric acid cycle.

Biotinidase Deficiency: The late onset form of MULTIPLE CARBOXYLASE DEFICIENCY (deficiency of the activities of biotin-dependent enzymes propionyl-CoA carboxylase, methylcrotonyl-CoA carboxylase, and PYRUVATE CARBOXYLASE) due to a defect or deficiency in biotinidase which is essential for recycling BIOTIN.

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19902 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
OLSON, RE1
MILLER, ON1
MISTRY, SP1
DAKSHINAMURTI, K1

Other Studies

2 other studies available for succinic acid and Biotinidase Deficiency

ArticleYear
The effect of vitamin deficiencies upon the metabolism of cardiac muscle in vitro; the effect of biotin deficiency in ducks with observations on the metabolism of radioactive carbon-labeled succinate.
    The Journal of biological chemistry, 1948, Volume: 175, Issue:2

    Topics: Animals; Avitaminosis; Biotinidase Deficiency; Carbon; Ducks; In Vitro Techniques; Myocardium; Succi

1948
Effect of succinate on amino acid incorporation in biotin deficiency.
    Biochimica et biophysica acta, 1961, May-27, Volume: 49

    Topics: Amino Acids; Biotin; Biotinidase Deficiency; Succinates; Succinic Acid

1961