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succinic acid and Amino Acid Metabolism Disorders, Inborn

succinic acid has been researched along with Amino Acid Metabolism Disorders, Inborn in 5 studies

Succinic Acid: A water-soluble, colorless crystal with an acid taste that is used as a chemical intermediate, in medicine, the manufacture of lacquers, and to make perfume esters. It is also used in foods as a sequestrant, buffer, and a neutralizing agent. (Hawley's Condensed Chemical Dictionary, 12th ed, p1099; McGraw-Hill Dictionary of Scientific and Technical Terms, 4th ed, p1851)
succinic acid : An alpha,omega-dicarboxylic acid resulting from the formal oxidation of each of the terminal methyl groups of butane to the corresponding carboxy group. It is an intermediate metabolite in the citric acid cycle.

Research

Studies (5)

TimeframeStudies, this research(%)All Research%
pre-19902 (40.00)18.7374
1990's1 (20.00)18.2507
2000's0 (0.00)29.6817
2010's2 (40.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Gahr, M1
Connemann, BJ1
Schönfeldt-Lecuona, CJ1
Freudenmann, RW1
Lamp, J1
Keyser, B1
Koeller, DM1
Ullrich, K1
Braulke, T1
Mühlhausen, C1
Kodama, H1
Nose, O1
Okada, S1
Yabuuchi, H1
Oizumi, J1
Giudici, TA1
Ng, WG1
Shaw, KN1
Donnell, GN1
Burlina, AB1
Gibson, KM1
Ruitenbeek, W1
Bonafè, L1
Bennett, MJ1

Reviews

1 review available for succinic acid and Amino Acid Metabolism Disorders, Inborn

ArticleYear
[Succinic semialdehyde dehydrogenase deficiency: an inheritable neurometabolic disease].
    Fortschritte der Neurologie-Psychiatrie, 2013, Volume: 81, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Aminobutyrates; Animals; Brain Diseases, Metabolic, Inborn; Da

2013

Other Studies

4 other studies available for succinic acid and Amino Acid Metabolism Disorders, Inborn

ArticleYear
Glutaric aciduria type 1 metabolites impair the succinate transport from astrocytic to neuronal cells.
    The Journal of biological chemistry, 2011, May-20, Volume: 286, Issue:20

    Topics: Amino Acid Metabolism, Inborn Errors; Animals; Astrocytes; Biological Transport; Brain; Brain Diseas

2011
The study of organic acids metabolism in a patient with ornithine transcarbamylase (OTC) deficiency.
    Advances in experimental medicine and biology, 1982, Volume: 153

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Citrates; Citric Acid; Female; Humans; Ketoglu

1982
Propionate metabolism by cultured skin fibroblasts from normal individuals and patients with methylmalonicaciduria and propionicacidemia.
    Biochemical medicine, 1981, Volume: 26, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Fatty Acids, Nonesterified; Fibroblasts; Huma

1981
Profound neurological phenotype in a patient presenting with disordered isoleucine and energy metabolism.
    Journal of inherited metabolic disease, 1998, Volume: 21, Issue:8

    Topics: Acetyl-CoA C-Acyltransferase; Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Dicarboxylic Ac

1998