stiripentol has been researched along with Epilepsies, Myoclonic in 57 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 1 (1.75) | 18.2507 |
| 2000's | 8 (14.04) | 29.6817 |
| 2010's | 33 (57.89) | 24.3611 |
| 2020's | 15 (26.32) | 2.80 |
| Authors | Studies |
|---|---|
| García-Peñas, JJ; Gil Nagel-Rein, A; Sánchez-Carpintero, R; Villanueva-Haba, V | 1 |
| Heulard, I; Reversat, L; Riban, V; Si Hocine, H; Verleye, M | 1 |
| Vasquez, A; Wirrell, EC; Youssef, PE | 1 |
| Chancharme, L; Chemaly, N; Chiron, C; Nabbout, R | 1 |
| Frampton, JE | 1 |
| Agarwal, A; Auvin, S; Chiron, C; Farfel, G; Galer, BS; Gil-Nagel, A; Knupp, K; Laux, L; Lock, M; Mistry, A; Morrison, G; Nabbout, R; Sanchez-Carpintero, R; Stephani, U; Villeneuve, N; Wirrell, E; Zuberi, S | 1 |
| Caraballo, RH; Cross, JH; Guerrini, R; Lagae, L; Nabbout, R; Vigevano, F | 1 |
| Samanta, D | 1 |
| Fulton, SP; Mudigoudar, BD; Wheless, JW | 1 |
| House, PM; Stodieck, S; Trabs, M; Trabs, N | 1 |
| Bjørnvold, M; Burns, ML; Heger, K; Johannessen Landmark, C; Johannessen, SI; Lund, C; Sætre, E | 1 |
| Critchley, D; Gidal, B; Morrison, G; Patsalos, PN; Szaflarski, JP; VanLandingham, K | 1 |
| Andrade, DM; Marques, P; Sadoway, T; Selvarajah, A; Tabarestani, S; Zulfiqar Ali, Q | 1 |
| Inoue, Y; Matsui, D; Ohtsuka, Y; Suzuki, K; Yamada, M | 1 |
| Buxton, L; Dahle, EJ; Handy, L; Johnson, KJ; Mensah, JA; Metcalf, CS; Pernici, CD; Smith, MD; West, PJ; Wilcox, KS | 1 |
| Bragazzi, NL; Brigo, F; Igwe, SC | 1 |
| Hashimoto, T; Kitaoka, T; Kyotani, S; Morimoto, M; Shimakawa, S | 1 |
| Cross, JH; Lightfoot, P; Myers, KA; Patil, SG; Scheffer, IE | 1 |
| Chiron, C | 3 |
| Clifford, T; Coyle, D; Elliott, J; McCoy, B; Wells, GA | 1 |
| Aydınlı, N; Bektaş, G; Çalışkan, M; Ozkan, MU; Özmen, M; Tatlı, B; Uzunhan, TA; Yıldız, EP | 1 |
| Baud, L; Bouderlique, E; Chemaly, N; Daudon, M; Deschênes, G; Frochot, V; Haymann, JP; Huguet, L; Le Dudal, M; Letavernier, E; Martori, C; Nabbout, R; Perez, J; Tang, E; Vandermeersch, S | 1 |
| Eschbach, K; Knupp, KG | 1 |
| Kang, JQ; Smith, NK; Warner, TA | 1 |
| Ikeda, H; Imai, K; Inoue, Y; Kagawa, Y; Takahashi, Y; Yamamoto, Y | 1 |
| Chancharme, L; Chugani, H; de Menezes, MS; Devinsky, O; Franz, DN; Hamiwka, L; Hernandez, A; Laux, L; Le Guern, ME; Mikati, MA; Morse, RP; Saneto, RP; Sullivan, J; Valencia, I; Wirrell, EC | 1 |
| Baraban, SC; Dinday, MT; Hortopan, GA | 1 |
| Brigo, F; Storti, M | 1 |
| Inoue, Y; Ohtsuka, Y | 2 |
| Boor, R; Reese, JP; Rosenow, F; Schubert-Bast, S; Stephani, U; Strzelczyk, A | 1 |
| Hirose, S; Iai, M; Ihara, Y; Ishii, A; Kouga, T; Osaka, H; Shimbo, H; Yamakawa, K; Yamashita, S | 1 |
| Hansen, MB; Johannesen, KM | 1 |
| Chhun, S; Chiron, C; Dulac, O; Jullien, V; Pons, G; Rey, E; Tod, M | 1 |
| Specchio, N; Trivisano, M; Vigevano, F | 1 |
| Benninger, F; Dressler, A; Feucht, M; Grassl, R; Gröppel, G; Mühlebner, A; Reiter-Fink, E; Reithofer, E; Trimmel-Schwahofer, P | 1 |
| Aras, LM; Isla, J; Mingorance-Le Meur, A | 1 |
| Brigo, F; Igwe, SC | 1 |
| Balestrini, S; Sisodiya, SM | 1 |
| Barnerias, C; Chemaly, N; Chiron, C; De Liso, P; Desguerre, I; Dulac, O; Hully, M; Laschet, J; Leunen, D; Nabbout, R | 1 |
| Fukuda, M; Imai, K; Inoue, Y; Jogamoto, T; Ohtsuka, Y; Suzuki, Y; Takahashi, Y; Yamamoto, Y | 1 |
| Barsi, P; Claes, L; De Jonghe, P; Fogarasi, A; Hegyi, M; Herczegfalvi, A; Karcagi, V; Neuwirth, M; Pálmafy, B; Paraicz, E; Siegler, Z; Tegzes, A | 1 |
| Baba, H; Fukushima, K; Ikeda, S; Inoue, Y; Oguni, H; Ohtani, H; Ohtsuka, Y; Takahashi, Y; Tohyama, J | 1 |
| Fisher, JL | 1 |
| Chemaly, N; Chipaux, M; Chiron, C; Copioli, C; Desguerre, I; Dulac, O; Nabbout, R | 1 |
| Cao, D; Inoue, Y; Ogiwara, I; Ohtani, H; Ohtani, S; Takahashi, Y; Yamakawa, K | 1 |
| Plosker, GL | 1 |
| Chiron, C; Dellatolas, G; Dulac, O; Pons, G; Rey, E; Thanh, TN; Vincent, J | 1 |
| Chiron, C; Dulac, O; Kröll-Seger, J; Portilla, P | 1 |
| Augier, S; Chiron, C; Cucherat, M; Dulac, O; Guerrini, R; Gueyffier, F; Kassaï, B; Pons, G; Rey, E; Vincent, J | 1 |
| Blehaut, H; Chiron, C; d'Athis, P; Dulac, O; Musial, C; Perez, J; Rey, E; Vincent, J | 1 |
| Trevathan, E | 1 |
| Chiron, C; d'Athis, P; Dulac, O; Marchand, MC; Pons, G; Rey, E; Tran, A; Vincent, J | 1 |
| Dulac, O | 1 |
18 review(s) available for stiripentol and Epilepsies, Myoclonic
| Article | Year |
|---|---|
Cannabidiol for the treatment of Lennox-Gastaut syndrome and Dravet syndrome: experts' recommendations for its use in clinical practice in Spain.
Topics: Anticonvulsants; Cannabidiol; Clobazam; Clonazepam; Diazepam; Dioxolanes; Drug Administration Schedule; Drug Synergism; Drug Therapy, Combination; Epilepsies, Myoclonic; Humans; Lennox Gastaut Syndrome; Phenobarbital; Practice Guidelines as Topic; Pyrrolidinones; Spain; Triazoles; Valproic Acid | 2021 |
Stiripentol for the treatment of seizures associated with Dravet syndrome in patients 6 months and older and taking clobazam.
Topics: Anticonvulsants; Child; Child, Preschool; Clobazam; Epilepsies, Myoclonic; Humans; Observational Studies as Topic; Randomized Controlled Trials as Topic; Seizures | 2023 |
Stiripentol: A Review in Dravet Syndrome.
Topics: Anticonvulsants; Dioxolanes; Epilepsies, Myoclonic; Humans; Seizures | 2019 |
Dravet syndrome: Treatment options and management of prolonged seizures.
Topics: Anticonvulsants; Diet, Ketogenic; Dioxolanes; Epilepsies, Myoclonic; Humans; Seizures; Valproic Acid | 2019 |
Changing Landscape of Dravet Syndrome Management: An Overview.
Topics: Anticonvulsants; Cannabidiol; Dioxolanes; Epilepsies, Myoclonic; Fenfluramine; Genetic Therapy; Humans; Oligonucleotides, Antisense | 2020 |
Dravet Syndrome: A Review of Current Management.
Topics: Anticonvulsants; Cannabidiol; Child; Dioxolanes; Epilepsies, Myoclonic; Fenfluramine; Genetic Testing; Humans | 2020 |
Clinical implications of trials investigating drug-drug interactions between cannabidiol and enzyme inducers or inhibitors or common antiseizure drugs.
Topics: Anticonvulsants; Cannabidiol; Clinical Trials as Topic; Clobazam; Cytochrome P-450 CYP2C19; Cytochrome P-450 CYP2C19 Inducers; Cytochrome P-450 CYP2C19 Inhibitors; Cytochrome P-450 CYP3A; Cytochrome P-450 CYP3A Inducers; Cytochrome P-450 CYP3A Inhibitors; Dioxolanes; Dose-Response Relationship, Drug; Drug Interactions; Drug Therapy, Combination; Epilepsies, Myoclonic; Fatty Acids, Monounsaturated; Humans; Lennox Gastaut Syndrome; Valproic Acid | 2020 |
Stiripentol (Diacomit) for Dravet syndrome.
Topics: Adolescent; Anticonvulsants; Cannabidiol; Child; Child, Preschool; Clinical Trials as Topic; Cytochrome P-450 Enzyme Inducers; Dioxolanes; Drug Therapy, Combination; Epilepsies, Myoclonic; Humans | 2021 |
Antiepileptic drugs for the treatment of infants with severe myoclonic epilepsy.
Topics: Adolescent; Anticonvulsants; Child; Child, Preschool; Dioxolanes; Epilepsies, Myoclonic; Female; Humans; Male; Patient Dropouts; Randomized Controlled Trials as Topic; Seizures | 2017 |
Stiripentol for the treatment of seizures associated with Dravet syndrome.
Topics: Anticonvulsants; Dioxolanes; Epilepsies, Myoclonic; Humans; Seizures | 2019 |
Stiripentol for the treatment of seizures in Dravet syndrome.
Topics: Animals; Anticonvulsants; Child; Dioxolanes; Drug Approval; Epilepsies, Myoclonic; Humans; Seizures; Status Epilepticus | 2019 |
Antiepileptic drugs for the treatment of severe myoclonic epilepsy in infancy.
Topics: Adolescent; Anticonvulsants; Child; Child, Preschool; Dioxolanes; Epilepsies, Myoclonic; Female; Humans; Male; Randomized Controlled Trials as Topic; Seizures | 2013 |
Antiepileptic drugs for the treatment of infants with severe myoclonic epilepsy.
Topics: Adolescent; Anticonvulsants; Child; Child, Preschool; Dioxolanes; Epilepsies, Myoclonic; Female; Humans; Male; Randomized Controlled Trials as Topic; Seizures | 2015 |
The effects of stiripentol on GABA(A) receptors.
Topics: Anticonvulsants; Dioxolanes; Epilepsies, Myoclonic; GABA-A Receptor Agonists; Humans; Receptors, GABA-A; Syndrome | 2011 |
Current therapeutic procedures in Dravet syndrome.
Topics: Anticonvulsants; Child, Preschool; Dioxolanes; Epilepsies, Myoclonic; Humans; Infant; Syndrome | 2011 |
Stiripentol : in severe myoclonic epilepsy of infancy (dravet syndrome).
Topics: Anticonvulsants; Child, Preschool; Dioxolanes; Dose-Response Relationship, Drug; Drug Interactions; Epilepsies, Myoclonic; Humans; Infant; Infant, Newborn; Meta-Analysis as Topic; Molecular Structure; Randomized Controlled Trials as Topic; Severity of Illness Index; Treatment Outcome | 2012 |
Severe myoclonic epilepsy in infancy: a systematic review and a meta-analysis of individual patient data.
Topics: Adolescent; Adult; Anticonvulsants; Child; Child, Preschool; Databases as Topic; Dioxolanes; Epilepsies, Myoclonic; Female; Follow-Up Studies; Humans; Male; Odds Ratio; Placebos; Publication Bias; Randomized Controlled Trials as Topic; Treatment Outcome | 2008 |
Epileptic encephalopathy.
Topics: Adolescent; Age Factors; Anti-Anxiety Agents; Anticonvulsants; Benzodiazepines; Brain Diseases; Child; Child, Preschool; Clobazam; Dioxolanes; Electroencephalography; Epilepsies, Myoclonic; Epilepsy; Humans; Infant; Infant, Newborn; Landau-Kleffner Syndrome; Spasms, Infantile; Treatment Outcome | 2001 |
8 trial(s) available for stiripentol and Epilepsies, Myoclonic
| Article | Year |
|---|---|
Fenfluramine for Treatment-Resistant Seizures in Patients With Dravet Syndrome Receiving Stiripentol-Inclusive Regimens: A Randomized Clinical Trial.
Topics: Adolescent; Anticonvulsants; Child; Child, Preschool; Dioxolanes; Double-Blind Method; Drug Resistant Epilepsy; Drug Therapy, Combination; Epilepsies, Myoclonic; Female; Fenfluramine; Humans; Male; Selective Serotonin Reuptake Inhibitors | 2020 |
Effectiveness of add-on stiripentol to clobazam and valproate in Japanese patients with Dravet syndrome: additional supportive evidence.
Topics: Adolescent; Adult; Anticonvulsants; Asian People; Benzodiazepines; Child; Child, Preschool; Clobazam; Dioxolanes; Dose-Response Relationship, Drug; Drug Administration Schedule; Drug Therapy, Combination; Epilepsies, Myoclonic; Female; Humans; Infant; Japan; Male; Treatment Outcome; Valproic Acid; Young Adult | 2014 |
Long-term safety and efficacy of stiripentol for the treatment of Dravet syndrome: A multicenter, open-label study in Japan.
Topics: Adolescent; Adult; Anticonvulsants; Benzodiazepines; Child; Child, Preschool; Clobazam; Dioxolanes; Dose-Response Relationship, Drug; Drug Therapy, Combination; Epilepsies, Myoclonic; Female; Humans; Infant; Japan; Male; Treatment Outcome; Valproic Acid; Young Adult | 2015 |
Ketogenic diet also benefits Dravet syndrome patients receiving stiripentol: a prospective pilot study.
Topics: Anticonvulsants; Child; Child, Preschool; Diet, Ketogenic; Dioxolanes; Epilepsies, Myoclonic; Female; Humans; Male; Pilot Projects; Prospective Studies; Seizures; Syndrome | 2011 |
[Long-term efficacy and tolerance of stiripentaol in severe myoclonic epilepsy of infancy (Dravet's syndrome)].
Topics: Anti-Anxiety Agents; Anticonvulsants; Benzodiazepines; Child, Preschool; Clobazam; Dioxolanes; Epilepsies, Myoclonic; Female; Humans; Infant; Male; Severity of Illness Index; Treatment Outcome; Valproic Acid | 2002 |
Stiripentol: efficacy and tolerability in children with epilepsy.
Topics: Adolescent; Adult; Age Factors; Anticonvulsants; Child; Child, Preschool; Dioxolanes; Drug Therapy, Combination; Epilepsies, Myoclonic; Epilepsies, Partial; Epilepsy; Female; Follow-Up Studies; Humans; Infant; Infant, Newborn; Male; Placebos; Single-Blind Method; Treatment Outcome | 1999 |
Epilepsy syndrome-specific anti-epileptic drug therapy for children.
Topics: Adult; Anticonvulsants; Child; Dioxolanes; Epilepsies, Myoclonic; Epilepsy; Humans; Infant; Syndrome | 2000 |
Stiripentol in severe myoclonic epilepsy in infancy: a randomised placebo-controlled syndrome-dedicated trial. STICLO study group.
Topics: Anti-Anxiety Agents; Anticonvulsants; Benzodiazepines; Child, Preschool; Clobazam; Dioxolanes; Double-Blind Method; Drug Therapy, Combination; Epilepsies, Myoclonic; Female; Humans; Infant; Male; Syndrome; Valproic Acid | 2000 |
31 other study(ies) available for stiripentol and Epilepsies, Myoclonic
| Article | Year |
|---|---|
Stiripentol inhibits spike-and-wave discharges in animal models of absence seizures: A new mechanism of action involving T-type calcium channels.
Topics: Animals; Anticonvulsants; Calcium Channels, T-Type; Dioxolanes; Disease Models, Animal; Electroencephalography; Epilepsies, Myoclonic; Epilepsy, Absence; Humans; Pentylenetetrazole; Rats; Rats, Wistar; Seizures | 2022 |
Initiating stiripentol before 2 years of age in patients with Dravet syndrome is safe and beneficial against status epilepticus.
Topics: Anticonvulsants; Child, Preschool; Epilepsies, Myoclonic; Female; Humans; Infant; Male; Retrospective Studies; Seizures; Status Epilepticus; Treatment Outcome | 2023 |
Influence of stiripentol on perampanel serum levels.
Topics: Adult; Anticonvulsants; Dioxolanes; Drug Therapy, Combination; Drug-Related Side Effects and Adverse Reactions; Epilepsies, Myoclonic; Female; Humans; Male; Nitriles; Pyridones | 2020 |
Pharmacokinetic Variability During Long-Term Therapeutic Drug Monitoring of Valproate, Clobazam, and Levetiracetam in Patients With Dravet Syndrome.
Topics: Adolescent; Adult; Anticonvulsants; Benzodiazepines; Child; Child, Preschool; Clobazam; Dioxolanes; Drug Monitoring; Epilepsies, Myoclonic; Epilepsy; Female; Humans; Levetiracetam; Male; Middle Aged; Norway; Retrospective Studies; Valproic Acid; Young Adult | 2020 |
Starting stiripentol in adults with Dravet syndrome? Watch for ammonia and carnitine.
Topics: Adult; Ammonia; Anticonvulsants; Carnitine; Cohort Studies; Dioxolanes; Epilepsies, Myoclonic; Female; Humans; Hyperammonemia; Male; Middle Aged; Retrospective Studies | 2020 |
Long-term safety and effectiveness of stiripentol in patients with Dravet syndrome: Interim report of a post-marketing surveillance study in Japan.
Topics: Adolescent; Adult; Anticonvulsants; Child; Child, Preschool; Dioxolanes; Epilepsies, Myoclonic; Epileptic Syndromes; Humans; Infant; Japan; Middle Aged; Pharmaceutical Preparations; Product Surveillance, Postmarketing; Seizures; Spasms, Infantile; Young Adult | 2021 |
Development of an antiseizure drug screening platform for Dravet syndrome at the NINDS contract site for the Epilepsy Therapy Screening Program.
Topics: Animals; Anticonvulsants; Body Temperature; Dioxolanes; Drug Resistant Epilepsy; Drug Therapy, Combination; Epilepsies, Myoclonic; Female; Gene Knock-In Techniques; High-Throughput Screening Assays; Hyperthermia; Injections, Intraperitoneal; Male; Mice; National Institute of Neurological Disorders and Stroke (U.S.); NAV1.1 Voltage-Gated Sodium Channel; Seizures; United States | 2021 |
Marked efficacy of combined three-drug therapy (Sodium Valproate, Topiramate and Stiripentol) in a patient with Dravet syndrome.
Topics: Anticonvulsants; Child, Preschool; Dioxolanes; Drug Therapy, Combination; Epilepsies, Myoclonic; Epilepsy; Female; Fructose; Humans; Topiramate; Valproic Acid | 2018 |
Stiripentol efficacy and safety in Dravet syndrome: a 12-year observational study.
Topics: Adolescent; Adult; Anticonvulsants; Child; Child, Preschool; Dioxolanes; Epilepsies, Myoclonic; Female; Humans; Infant; Longitudinal Studies; Male; Mutation; NAV1.1 Voltage-Gated Sodium Channel; Retrospective Studies; Treatment Outcome; Young Adult | 2018 |
Long-term pragmatic use of stiripentol for Dravet syndrome.
Topics: Anticonvulsants; Dioxolanes; Epilepsies, Myoclonic; Humans; NAV1.1 Voltage-Gated Sodium Channel | 2018 |
Economic Evaluation of Stiripentol for Dravet Syndrome: A Cost-Utility Analysis.
Topics: Anticonvulsants; Canada; Child; Clobazam; Cost-Benefit Analysis; Dioxolanes; Drug Therapy, Combination; Epilepsies, Myoclonic; Humans; Quality-Adjusted Life Years; Valproic Acid | 2018 |
Efficacy of Stiripentol and the Clinical Outcome in Dravet Syndrome.
Topics: Adolescent; Anticonvulsants; Child; Child, Preschool; Cognitive Dysfunction; Dioxolanes; Drug Resistant Epilepsy; Epilepsies, Myoclonic; Female; Humans; Male; Retrospective Studies; Seizures; Treatment Outcome | 2019 |
Stiripentol protects against calcium oxalate nephrolithiasis and ethylene glycol poisoning.
Topics: Animals; Calcium Oxalate; Dioxolanes; Epilepsies, Myoclonic; Ethylene Glycol; Female; Hepatocytes; Humans; Hyperoxaluria, Primary; Kidney; Male; Nephrolithiasis; Rats; Rats, Sprague-Dawley | 2019 |
The therapeutic effect of stiripentol in Gabrg2
Topics: Animals; Anticonvulsants; Diazepam; Dioxolanes; Epilepsies, Myoclonic; Gene Knock-In Techniques; Mice; Mice, Inbred C57BL; Mice, Transgenic; Receptors, GABA-A; Treatment Outcome | 2019 |
Impact of CYP2C19 Phenotypes on Clinical Efficacy of Stiripentol in Japanese Patients With Dravet Syndrome.
Topics: Adolescent; Adult; Anticonvulsants; Asian People; Child; Child, Preschool; Clobazam; Cytochrome P-450 CYP2C19; Dioxolanes; Drug Interactions; Drug Therapy, Combination; Epilepsies, Myoclonic; Female; Humans; Infant; Japan; Male; Retrospective Studies; Valproic Acid; Young Adult | 2020 |
Stiripentol in Dravet syndrome: results of a retrospective U.S. study.
Topics: Anticonvulsants; Benzodiazepines; Child; Child, Preschool; Clobazam; Dioxolanes; Drug Therapy, Combination; Epilepsies, Myoclonic; Female; Humans; Infant; Male; Retrospective Studies; Seizures; Treatment Outcome; United States; Valproic Acid | 2013 |
Drug screening in Scn1a zebrafish mutant identifies clemizole as a potential Dravet syndrome treatment.
Topics: Animals; Anticonvulsants; Benzimidazoles; Bromides; Diazepam; Dioxolanes; Drug Evaluation, Preclinical; Epilepsies, Myoclonic; Gene Expression Profiling; Mutation; NAV1.1 Voltage-Gated Sodium Channel; Potassium Compounds; Seizures; Valproic Acid; Voltage-Gated Sodium Channel beta-1 Subunit; Zebrafish; Zebrafish Proteins | 2013 |
Evaluation of health-care utilization in patients with Dravet syndrome and on adjunctive treatment with stiripentol and clobazam.
Topics: Adolescent; Adult; Anticonvulsants; Benzodiazepines; Child; Child, Preschool; Clobazam; Dioxolanes; Epilepsies, Myoclonic; Female; Health Care Costs; Health Services; Hospitalization; Humans; Male; Patient Acceptance of Health Care; Treatment Outcome; Young Adult | 2014 |
Effect of CYP2C19 polymorphisms on stiripentol administration in Japanese cases of Dravet syndrome.
Topics: Adolescent; Anticonvulsants; Asian People; Child; Child, Preschool; Cytochrome P-450 CYP2C19; Dioxolanes; Epilepsies, Myoclonic; Female; Humans; Infant; Male; Pharmacogenetics; Polymorphism, Single Nucleotide; Retrospective Studies | 2015 |
[Dravet syndrome is a rare genetic epileptic disorder that can be mistaken for fever cramps].
Topics: Anticonvulsants; Diagnosis, Differential; Dioxolanes; Epilepsies, Myoclonic; Fever; Humans; Infant, Newborn; Male; Mutation; NAV1.1 Voltage-Gated Sodium Channel; Twins, Monozygotic | 2014 |
Pharmacokinetics of clobazam and N-desmethylclobazam in children with dravet syndrome receiving concomitant stiripentol and valproic Acid.
Topics: Anticonvulsants; Benzodiazepines; Body Weight; Child; Child, Preschool; Clobazam; Dioxolanes; Drug Interactions; Drug Therapy, Combination; Epilepsies, Myoclonic; Female; Humans; Male; Prospective Studies; Randomized Controlled Trials as Topic; Valproic Acid | 2015 |
Extending the use of stiripentol to other epileptic syndromes: a case of PCDH19-related epilepsy.
Topics: Age of Onset; Anticonvulsants; Autistic Disorder; Benzodiazepines; Cadherins; Child; Clobazam; Cognition Disorders; Dioxolanes; Drug Resistant Epilepsy; Drug Therapy, Combination; Epilepsies, Myoclonic; Epilepsy; Female; Fever; Humans; Intellectual Disability; Protocadherins; Syndrome; Treatment Outcome; Valproic Acid | 2015 |
Efficacy and tolerability of the ketogenic diet in Dravet syndrome - Comparison with various standard antiepileptic drug regimen.
Topics: Adolescent; Anticonvulsants; Benzodiazepines; Bromides; Child; Child, Preschool; Clobazam; Diet, Ketogenic; Dioxolanes; Epilepsies, Myoclonic; Female; Fructose; Humans; Infant; Levetiracetam; Male; Piracetam; Retrospective Studies; Seizures; Topiramate; Treatment Outcome; Vagus Nerve Stimulation; Valproic Acid; Young Adult | 2015 |
The European patient with Dravet syndrome: results from a parent-reported survey on antiepileptic drug use in the European population with Dravet syndrome.
Topics: Adolescent; Anticonvulsants; Benzodiazepines; Child; Child, Preschool; Clobazam; Dioxolanes; Epilepsies, Myoclonic; Europe; Female; Humans; Male; NAV1.1 Voltage-Gated Sodium Channel; Sodium Channel Blockers; Valproic Acid | 2015 |
Audit of use of stiripentol in adults with Dravet syndrome.
Topics: Adolescent; Adult; Anticonvulsants; Child; Child, Preschool; Dioxolanes; Epilepsies, Myoclonic; Female; Humans; Male; Mutation; NAV1.1 Voltage-Gated Sodium Channel | 2017 |
Patients with dravet syndrome in the era of stiripentol: A French cohort cross-sectional study.
Topics: Adolescent; Age Factors; Anticonvulsants; Benzodiazepines; Child; Child, Preschool; Clobazam; Cross-Sectional Studies; Dioxolanes; Drug Therapy, Combination; Epilepsies, Myoclonic; Female; Follow-Up Studies; France; Humans; Male; NAV1.1 Voltage-Gated Sodium Channel; Severity of Illness Index; Treatment Failure; Valproic Acid; Young Adult | 2016 |
Add-on stiripentol elevates serum valproate levels in patients with or without concomitant topiramate therapy.
Topics: Adolescent; Adult; Anticonvulsants; Benzodiazepines; Child; Child, Preschool; Clobazam; Cytochrome P-450 CYP2C19; Cytochrome P-450 CYP2C9; Dioxolanes; Dose-Response Relationship, Drug; Drug Therapy, Combination; Epilepsies, Myoclonic; Female; Fructose; Humans; Infant; Male; Polymorphism, Genetic; Retrospective Studies; Topiramate; Valproic Acid | 2017 |
[Clinical and genetic diagnosis of Dravet syndrome: report of 20 cases].
Topics: Adolescent; Anticonvulsants; Child; Child, Preschool; Dioxolanes; DNA Mutational Analysis; Electroencephalography; Epilepsies, Myoclonic; Epilepsy, Absence; Epilepsy, Complex Partial; Female; Humans; Hungary; Infant; Intellectual Disability; Magnetic Resonance Imaging; Male; Mutation; Myoclonic Epilepsy, Juvenile; NAV1.1 Voltage-Gated Sodium Channel; Nerve Tissue Proteins; Psychomotor Disorders; Seizures, Febrile; Sodium Channels | 2008 |
Stiripentol open study in Japanese patients with Dravet syndrome.
Topics: Adolescent; Adult; Anticonvulsants; Aryl Hydrocarbon Hydroxylases; Benzodiazepines; Child; Child, Preschool; Clobazam; Cytochrome P-450 CYP2C19; Dioxolanes; Drug Administration Schedule; Drug Therapy, Combination; Epilepsies, Myoclonic; Epilepsy, Tonic-Clonic; Female; Humans; Infant; Male; Medical Records; Middle Aged; Retrospective Studies; Syndrome; Treatment Outcome | 2009 |
Efficacy of stiripentol in hyperthermia-induced seizures in a mouse model of Dravet syndrome.
Topics: Age Factors; Animals; Anticonvulsants; Benzodiazepines; Clobazam; Dioxolanes; Disease Models, Animal; Drug Therapy, Combination; Electroencephalography; Epilepsies, Myoclonic; Genetic Predisposition to Disease; Hyperthermia, Induced; Mice; Mice, Transgenic; NAV1.1 Voltage-Gated Sodium Channel; Nerve Tissue Proteins; Seizures; Sodium Channels | 2012 |
Topiramate in the treatment of highly refractory patients with Dravet syndrome.
Topics: Anticonvulsants; Dioxolanes; Drug Therapy, Combination; Electroencephalography; Epilepsies, Myoclonic; Epilepsy, Tonic-Clonic; Female; Follow-Up Studies; Fructose; Humans; Infant; Male; Retrospective Studies; Seizures, Febrile; Status Epilepticus; Topiramate; Treatment Outcome | 2006 |