stearic acid has been researched along with Zellweger Syndrome in 3 studies
octadecanoic acid : A C18 straight-chain saturated fatty acid component of many animal and vegetable lipids. As well as in the diet, it is used in hardening soaps, softening plastics and in making cosmetics, candles and plastics.
Zellweger Syndrome: An autosomal recessive disorder due to defects in PEROXISOME biogenesis which involves more than 13 genes encoding peroxin proteins of the peroxisomal membrane and matrix. Zellweger syndrome is typically seen in the neonatal period with features such as dysmorphic skull; MUSCLE HYPOTONIA; SENSORINEURAL HEARING LOSS; visual compromise; SEIZURES; progressive degeneration of the KIDNEYS and the LIVER. Zellweger-like syndrome refers to phenotypes resembling the neonatal Zellweger syndrome but seen in children or adults with apparently intact peroxisome biogenesis.
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 3 (100.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Poulos, A | 2 |
| Usher, S | 2 |
| Paton, BC | 1 |
| Singh, H | 1 |
| Johnson, D | 1 |
| Koike, R | 1 |
| Tsuji, S | 1 |
| Ohno, T | 1 |
| Suzuki, Y | 1 |
| Orii, T | 1 |
| Miyatake, T | 1 |
3 other studies available for stearic acid and Zellweger Syndrome
| Article | Year |
|---|---|
Fatty acid synthesis from [2-14C]acetate in normal and peroxisome-deficient (Zellweger) fibroblasts.
Topics: Acetates; Carbon Radioisotopes; Cholesterol Esters; Fatty Acids; Fatty Acids, Monounsaturated; Fibro | 1993 |
Metabolism of branched chain fatty acids in peroxisomal disorders.
Topics: Adrenoleukodystrophy; Cells, Cultured; Chondrodysplasia Punctata; Fatty Acids; Fibroblasts; Heptanoi | 1990 |
Physiological significance of fatty acid elongation system in adrenoleukodystrophy.
Topics: Adrenoleukodystrophy; Fatty Acids; Fatty Acids, Unsaturated; Fibroblasts; Humans; Oxidation-Reductio | 1991 |